scholarly article | Q13442814 |
P50 | author | Alexandra Durr | Q60820298 |
Brandon Durant | Q61827272 | ||
James P. O'Callaghan | Q64408371 | ||
Emmanuel Brouillet | Q42839922 | ||
P2093 | author name string | Hua Yu | |
Fanny Mochel | |||
Raphael Schiffmann | |||
Sandrine Humbert | |||
Vanessa C. Wheeler | |||
Xingli Meng | |||
P2860 | cites work | Detection of early behavioral markers of Huntington's disease in R6/2 mice employing an automated social home cage | Q45293617 |
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Mitochondrial respiration and ATP production are significantly impaired in striatal cells expressing mutant huntingtin | Q45297269 | ||
HD CAG repeat implicates a dominant property of huntingtin in mitochondrial energy metabolism | Q45298206 | ||
Brain white-matter volume loss and glucose hypometabolism precede the clinical symptoms of Huntington's disease. | Q45299986 | ||
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Transcriptional repression of PGC-1alpha by mutant huntingtin leads to mitochondrial dysfunction and neurodegeneration. | Q45302702 | ||
Thermoregulatory and metabolic defects in Huntington's disease transgenic mice implicate PGC-1alpha in Huntington's disease neurodegeneration | Q45302924 | ||
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Brain regional levels of adenosine and adenosine nucleotides in rats killed by high-energy focused microwave irradiation. | Q49141284 | ||
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Huntingtin interacting proteins are genetic modifiers of neurodegeneration | Q21145230 | ||
Focused microwave irradiation of the brain preserves in vivo protein phosphorylation: comparison with other methods of sacrifice and analysis of multiple phosphoproteins | Q23914346 | ||
AMP-activated protein kinase phosphorylation in brain is dependent on method of killing and tissue preparation | Q23918058 | ||
Creatine synthesis and transport during rat embryogenesis: spatiotemporal expression of AGAT, GAMT and CT1. | Q24811264 | ||
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A novel gene containing a trinucleotide repeat that is expanded and unstable on Huntington's disease chromosomes. | Q27860836 | ||
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Dysregulated brain creatine kinase is associated with hearing impairment in mouse models of Huntington disease | Q30499300 | ||
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Combination therapy with coenzyme Q10 and creatine produces additive neuroprotective effects in models of Parkinson's and Huntington's diseases | Q33837238 | ||
Reduced creatine kinase as a central and peripheral biomarker in Huntington's disease | Q33945688 | ||
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A polymorphic DNA marker genetically linked to Huntington's disease | Q34255139 | ||
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Energy deficit in Huntington disease: why it matters | Q37834195 | ||
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Neurochemistry and toxin models in Huntington's disease. | Q40599311 | ||
Cell loss in the motor and cingulate cortex correlates with symptomatology in Huntington's disease | Q42469950 | ||
Increases in cortical glutamate concentrations in transgenic amyotrophic lateral sclerosis mice are attenuated by creatine supplementation. | Q43572865 | ||
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Measurement of sarcoplasmic reticulum Ca2+ ATPase activity using high-performance liquid chromatography | Q44933316 | ||
Cerebral creatine kinase deficiency influences metabolite levels and morphology in the mouse brain: a quantitative in vivo 1H and 31P magnetic resonance study | Q45039952 | ||
Increased glucose metabolism and ATP level in brain tissue of Huntington's disease transgenic mice | Q45290567 | ||
Relationship between trinucleotide repeat expansion and phenotypic variation in Huntington's disease | Q45290871 | ||
Paradoxical delay in the onset of disease caused by super-long CAG repeat expansions in R6/2 mice. | Q45292233 | ||
P6195 | funding scheme | extramural research | Q124503498 |
P433 | issue | 2 | |
P407 | language of work or name | English | Q1860 |
P921 | main subject | cell biology | Q7141 |
Huntington's disease | Q190564 | ||
human behavior | Q3769299 | ||
muscular system | Q7060553 | ||
P5008 | on focus list of Wikimedia project | Wikimedia–NIOSH collaboration | Q104416361 |
P304 | page(s) | 1361-1370 | |
P577 | publication date | 2012-01-06 | |
P1433 | published in | Journal of Biological Chemistry | Q867727 |
P859 | sponsor | NIOSH Health Effects Laboratory Division | Q123344455 |
P1476 | title | Early alterations of brain cellular energy homeostasis in Huntington disease models | |
P478 | volume | 287 |
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