| P50 | author | Jerzy Duszyński | Q19635956 |
| | Joanna Szczepanowska | Q60662489 |
| | Dominika Malińska | Q63363678 |
| | Mariusz R Wieckowski | Q38327644 |
| P2860 | cites work | Basic mechanisms for recognition and transport of synaptic cargos | Q21198895 |
| | Premature ageing in mice expressing defective mitochondrial DNA polymerase | Q24294365 |
| | A forty-kilodalton protein of the inner membrane is the mitochondrial calcium uniporter | Q24306850 |
| | Mitochondrial fusion in human cells is efficient, requires the inner membrane potential, and is mediated by mitofusins. | Q24541558 |
| | Disruption of mitochondrial DNA replication in Drosophila increases mitochondrial fast axonal transport in vivo | Q27335303 |
| | The mtDNA T8993G (NARP) mutation results in an impairment of oxidative phosphorylation that can be improved by antioxidants | Q28248174 |
| | Patients with Leber hereditary optic neuropathy fail to compensate impaired oxidative phosphorylation | Q28261663 |
| | Mitochondrial fusion and fission in cell life and death | Q28299119 |
| | Mitochondrial DNA rearrangements in young onset parkinsonism: two case reports | Q28362183 |
| | Mitochondrial respiratory-chain diseases | Q29614474 |
| | Mitochondrial dynamics--fusion, fission, movement, and mitophagy--in neurodegenerative diseases | Q29615646 |
| | Mitochondria: more than just a powerhouse | Q29617386 |
| | Mitochondrial DNA-depleted neuroblastoma (Rho degrees) cells exhibit altered calcium signaling | Q30305575 |
| | Mitochondrial DNA mutations affect calcium handling in differentiated neurons | Q30493814 |
| | Altered mitochondrial structure and motion dynamics in living cells with energy metabolism defects revealed by real time microscope imaging | Q33205800 |
| | Mitochondrial mosaics in the liver of 3 infants with mtDNA defects | Q33461789 |
| | Mechanism of neurodegeneration of neurons with mitochondrial DNA mutations | Q33742421 |
| | Increased production of reactive oxygen species in hyperglycemic conditions requires dynamic change of mitochondrial morphology | Q34479807 |
| | Biochemical phenotypes associated with the mitochondrial ATP6 gene mutations at nt8993. | Q34637419 |
| | Abnormal calcium homeostasis and mitochondrial polarization in a human encephalomyopathy | Q34723156 |
| | Interactions between mitochondrial bioenergetics and cytoplasmic calcium in cultured cerebellar granule cells. | Q35196254 |
| | Human extraocular muscles in mitochondrial diseases: comparing chronic progressive external ophthalmoplegia with Leber's hereditary optic neuropathy. | Q35593390 |
| | New insights into the bioenergetics of mitochondrial disorders using intracellular ATP reporters | Q35973374 |
| | Kinase signaling cascades in the mitochondrion: a matter of life or death. | Q35979108 |
| | Mitochondria in homeostasis of reactive oxygen species in cell, tissues, and organism | Q36231438 |
| | Yeast Cells Lacking the Mitochondrial Gene Encoding the ATP Synthase Subunit 6 Exhibit a Selective Loss of Complex IV and Unusual Mitochondrial Morphology | Q57246529 |
| | Two cases of NADH-coenzyme Q reductase deficiency: relationship to MELAS syndrome | Q70323219 |
| | Increased activities of antioxidant enzymes and decreased ATP concentration in cultured myoblasts with the 3243A-->G mutation in mitochondrial DNA | Q73189920 |
| | An out-of-frame cytochrome b gene deletion from a patient with parkinsonism is associated with impaired complex III assembly and an increase in free radical production | Q73192853 |
| | Decreased ATP synthesis is phenotypically expressed during increased energy demand in fibroblasts containing mitochondrial tRNA mutations | Q77892921 |
| | Mitochondrial diseases | Q80391768 |
| | Short- and long-term alterations of mitochondrial morphology, dynamics and mtDNA after transient oxidative stress | Q81582355 |
| | Calcium uptake by rat kidney mitochondria | Q36441249 |
| | The regulatory role of mitochondria in capacitative calcium entry | Q36507700 |
| | Oxidative stress, mitochondria and mtDNA-mutator mice | Q36663410 |
| | Mitochondrial control of calcium-channel gating: a mechanism for sustained signaling and transcriptional activation in T lymphocytes | Q37253977 |
| | Regulation of mitochondrial dehydrogenases by calcium ions | Q37469373 |
| | Mitochondrial dynamics in human NADH:ubiquinone oxidoreductase deficiency. | Q37585724 |
| | Mitochondrial DNA mutations and human disease | Q37599004 |
| | Mitochondrial fusion proteins: dual regulators of morphology and metabolism | Q37676501 |
| | Multi-site control and regulation of mitochondrial energy production. | Q37708340 |
| | Mitochondrial DNA mutation-elicited oxidative stress, oxidative damage, and altered gene expression in cultured cells of patients with MERRF syndrome | Q37735748 |
| | Mitochondrial consumption of cytosolic ATP: not so fast. | Q37864389 |
| | Functional F1-ATPase essential in maintaining growth and membrane potential of human mitochondrial DNA-depleted rho degrees cells | Q38550417 |
| | The optimized allotopic expression of ND1 or ND4 genes restores respiratory chain complex I activity in fibroblasts harboring mutations in these genes | Q38914398 |
| | Effect of selenite on basic mitochondrial function in human osteosarcoma cells with chronic mitochondrial stress. | Q39509681 |
| | Antioxidant defence systems and generation of reactive oxygen species in osteosarcoma cells with defective mitochondria: effect of selenium | Q39742744 |
| | Mitochondrial ND5 gene variation associated with encephalomyopathy and mitochondrial ATP consumption | Q40067062 |
| | Impaired mitochondrial Ca2+ homeostasis in respiratory chain-deficient cells but efficient compensation of energetic disadvantage by enhanced anaerobic glycolysis due to low ATP steady state levels. | Q40131652 |
| | Mitochondrial bioenergetics and structural network organization | Q40171308 |
| | Proteolytic processing of OPA1 links mitochondrial dysfunction to alterations in mitochondrial morphology | Q40227379 |
| | Involvement of protein kinase C delta in the alteration of mitochondrial mass in human cells under oxidative stress. | Q40265671 |
| | Diabetes-associated mitochondrial DNA mutation A3243G impairs cellular metabolic pathways necessary for beta cell function. | Q40273572 |
| | Enhanced ROS production and antioxidant defenses in cybrids harbouring mutations in mtDNA. | Q40373090 |
| | Influence of a mitochondrial genetic defect on capacitative calcium entry and mitochondrial organization in the osteosarcoma cells. | Q40482450 |
| | Antioxidant defences and homeostasis of reactive oxygen species in different human mitochondrial DNA-depleted cell lines. | Q40517974 |
| | Leber hereditary optic neuropathy mtDNA mutations disrupt glutamate transport in cybrid cell lines. | Q40519925 |
| | Biochemical analysis of respiratory function in cybrid cell lines harbouring mitochondrial DNA mutations. | Q40523353 |
| | Differentiation-specific effects of LHON mutations introduced into neuronal NT2 cells | Q40749783 |
| | A calcium signaling defect in the pathogenesis of a mitochondrial DNA inherited oxidative phosphorylation deficiency | Q40938846 |
| | Mitochondrial DNA background modifies the bioenergetics of NARP/MILS ATP6 mutant cells | Q42010130 |
| | Altered mitochondrial function in fibroblasts containing MELAS or MERRF mitochondrial DNA mutations. | Q42077715 |
| | Inefficient coupling between proton transport and ATP synthesis may be the pathogenic mechanism for NARP and Leigh syndrome resulting from the T8993G mutation in mtDNA. | Q42533734 |
| | Oxidative stress-dependent p66Shc phosphorylation in skin fibroblasts of children with mitochondrial disorders | Q43131078 |
| | Biochemical-clinical correlation in patients with different loads of the mitochondrial DNA T8993G mutation | Q43885529 |
| | Extracellular pH modifies mitochondrial control of capacitative calcium entry in Jurkat cells. | Q45166513 |
| | Antioxidant defences in cybrids harboring mtDNA mutations associated with Leber's hereditary optic neuropathy | Q45273391 |
| | Deficiency of subunits of Complex I and mitochondrial encephalomyopathy | Q48107157 |
| | MELAS: clinical features, biochemistry, and molecular genetics | Q48496312 |
| | Adult-onset MELAS. Evidence for involvement of neurons as well as cerebral vasculature in strokelike episodes | Q48958839 |
| | Quantitation and origin of the mitochondrial membrane potential in human cells lacking mitochondrial DNA. | Q50519005 |
| | Mitochondrial network complexity and pathological decrease in complex I activity are tightly correlated in isolated human complex I deficiency. | Q53675259 |
| P433 | issue | 10 | |
| P407 | language of work or name | English | Q1860 |
| P304 | page(s) | 1740-1746 | |
| P577 | publication date | 2012-03-03 | |
| P1433 | published in | Biochimica et Biophysica Acta | Q864239 |
| P1476 | title | Effect of mtDNA point mutations on cellular bioenergetics | |
| P478 | volume | 1817 | |