scholarly article | Q13442814 |
P2093 | author name string | D Fischer | |
A Kaplan | |||
W Sly | |||
D Achord | |||
P2860 | cites work | Protein measurement with the Folin phenol reagent | Q20900776 |
Phosphohexosyl components of a lysosomal enzyme are recognized by pinocytosis receptors on human fibroblasts | Q35027280 | ||
Quantitative aspects of pinocytosis and the intracellular fate of N-acetyl-alpha-D-glucosaminidase in Sanfilippo B fibroblasts | Q40367761 | ||
Inherited disorders of lysosomal metabolism | Q40690248 | ||
A hypothesis for I-cell disease: defective hydrolases that do not enter lysosomes | Q41511911 | ||
Corrective factors for inborn errors of mucopolysaccharide metabolism | Q44106737 | ||
The role of glycosidically bound mannose in the assimilation of beta-galactosidase by generalized gangliosidosis fibroblasts | Q46158124 | ||
Purification of human liver acid beta-D-galactosidases using affinity chromatography | Q46506571 | ||
31 P nuclear magnetic resonance studies on the phosphoglycopeptides obtained from rat brain glycoprotein | Q48387206 | ||
Identification of phosphoglycoproteins obtained from rat brain | Q48387218 | ||
Beta-glucuronidase deficiency mucopolysaccharidosis: methods for enzymatic diagnosis. | Q64905667 | ||
Multiple isoelectric and recognition forms of human β-glucuronidase activity | Q66915910 | ||
Uptake of beta-glucuronidase by deficient human fibroblasts | Q68515835 | ||
A recognition marker required for uptake of a lysosomal enzyme by cultured fibroblasts | Q68684301 | ||
In vitro correction of deficient human fibroblasts by beta-glucuronidase from different human sources | Q69820185 | ||
Polymorphism of the somatic antigen of yeast | Q70010584 | ||
P433 | issue | 5 | |
P407 | language of work or name | English | Q1860 |
P921 | main subject | D-mannopyranose 6-phosphate | Q259546 |
P304 | page(s) | 1088-93 | |
P577 | publication date | 1977-11-01 | |
P1433 | published in | Journal of Clinical Investigation | Q3186904 |
P1476 | title | Phosphohexosyl recognition is a general characteristic of pinocytosis of lysosomal glycosidases by human fibroblasts | |
P478 | volume | 60 |
Q72808331 | 23 Determinants in the uptake of lysosomal enzymes by cultured fibroblasts |
Q34244952 | A novel mouse model of a patient mucolipidosis II mutation recapitulates disease pathology |
Q41919201 | Addition of a mannose-6-phosphatecontaining oligosaccharide alters cellular processing of low density lipoprotein by parental and ldl-receptor-defective chinese hamster ovary cells |
Q40084938 | Advances in the Treatment of Inherited Metabolic Diseases |
Q41046090 | An alternative hypothesis of cellular transport of lysosomal enzymes in fibroblasts. Effect of inhibitors of lysosomal enzyme endocytosis on intra- and extra-cellular lysosomal enzyme activities |
Q36342851 | Association of alkaline-phosphatase-positive reticulum cells in bone marrow with granulocytic precursors |
Q38355242 | Binding of phosphorylated oligosaccharides to immobilized phosphomannosyl receptors |
Q41642494 | Binding receptors for alpha-L-fucosidase in human B-lymphoid cell lines |
Q41543241 | Carbohydrate composition of human placental N-acetylhexosaminidase A and B |
Q40199990 | Carbohydrate composition of purified serum glycoproteins in mucolipidosis II and mucolipidosis III. |
Q37607826 | Carbohydrate recognition by the mannose-6-phosphate receptors |
Q33925076 | Cationic sites on granzyme B contribute to cytotoxicity by promoting its uptake into target cells |
Q39665119 | Cell surface-associated lysosomal enzymes in cultured human skin fibroblasts |
Q36529054 | Cell- and ligand-specific dephosphorylation of acid hydrolases: evidence that the mannose 6-phosphatase is controlled by compartmentalization |
Q60570643 | Characteristics of lysosomal phosphomannosyl-enzyme receptors in the rat heart |
Q35399911 | Characterization of a membrane-associated receptor from bovine liver that binds phosphomannosyl residues of bovine testicular beta-galactosidase |
Q36201432 | Chick embryo fibroblasts produce two forms of hyaluronidase |
Q41337499 | Chloroquine inhibits lysosomal enzyme pinocytosis and enhances lysosomal enzyme secretion by impairing receptor recycling |
Q41684104 | Chromatographic components of β-hexosaminidase in I-cell disease (Mucolipidosis II) |
Q39518901 | Coiling phagocytosis of Borrelia burgdorferi by primary human macrophages is controlled by CDC42Hs and Rac1 and involves recruitment of Wiskott-Aldrich syndrome protein and Arp2/3 complex. |
Q38355037 | Comparative kinetics of phosphomannosyl receptor-mediated pinocytosis of fibroblast secretion acid hydrolases and glycopeptides prepared from them |
Q42168358 | Compartmental distribution of beta-hexosaminidase isoenzymes in I-cell fibroblasts |
Q72135336 | Concanavalin A binding of soluble neutral maltase-glucoamylase in suckling rat intestine |
Q67441409 | Concanavalin A mediated uptake of enzymes by fibroblasts |
Q40848095 | Correlation of structural features of phosphomannans with their ability to inhibit pinocytosis of human beta-glucuronidase by human fibroblasts |
Q40103045 | Cytochemistry of cell glycoconjugates |
Q41974122 | Deficient phosphorylation of mannose residues of mannan in fibroblasts of patients with mucolipidoses II and III |
Q71142061 | Differential localisation of phosphorylated and non-phosphorylated forms of arylsulfatase A in lysosomes |
Q37330695 | Direct demonstration of binding of a lysosomal enzyme, alpha-L-iduronidase, to receptors on cultured fibroblasts |
Q72844718 | Effect of 2-deoxyglucose on lysosomal enzymes in cultured human skin fibroblasts |
Q41131364 | Effect of Tunicamycin on Transport of Lysosomal Enzymes in Cultured Skin Fibroblasts |
Q66929418 | Effect of temperature on extracellular accumulation of β-D-N-acetylglucosaminidase in I-cell disease fibroblast cultures |
Q40169902 | Effects of exogenous amines on mammalian cells, with particular reference to membrane flow |
Q35202302 | Endocytosis of lysosomal alpha-galactosidase A by cultured fibroblasts from patients with Fabry disease |
Q41957045 | Endocytosis of β-N-acetylglucosaminidase from sections of mucolipidosis-II and-III fibroblasts by non-parenchymal rat liver cells |
Q33972682 | Enzymatic identification of mannose 6-phosphate on the recognition marker for receptor-mediated pinocytosis of beta-glucuronidase by human fibroblasts |
Q71201241 | Enzyme replacement treatment for Tay-Sachs disease brain cells in culture utilizing concanavalin A-mediated hexosaminidase A uptake: biochemical and morphological evidence of GM2 mobilization |
Q38342838 | Enzymes approved for human therapy: indications, mechanisms and adverse effects |
Q45035921 | Epithelial Rat Liver Cells Have Cell Surface Receptors Recognizing a Phosphorylated Carbohydrate on Lysosomal Enzymes |
Q37037143 | Excretion-Reuptake Route of β-Hexosaminidase in Normal and I-Cell Disease Cultured Fibroblasts |
Q36201079 | Fibroblast receptor for lysosomal enzymes mediates pinocytosis of multivalent phosphomannan fragment |
Q35200101 | Five related Lebanese individuals with high plasma lysosomal hydrolases: a new defect in mannose-6-phosphate receptor recognition? |
Q70167416 | Glucose phosphotransferase and intracellular trafficking |
Q70140169 | Heterozygosity for phosphodiester glycosidase deficiency: a novel human mutation of lysosomal enzyme processing |
Q39633934 | Human Placenta α-N-Acetylglucosaminidase: Purification, Characterization and Demonstration of Multiple Recognition Forms |
Q67262700 | I-cell disease Desialylation of β-hexosaminidase and its effect on uptake by fibroblasts |
Q41040230 | I-cell disease. A hypothesis for the structure of the carbohydrate recognition site on beta-D-N-acetylhexosaminidase |
Q66984351 | I-cell disease: Deficiency of extracellular hydrolase phosphorylation |
Q33971527 | Identification of mannose 6-phosphate in glycoproteins that inhibit the assimilation of β-galactosidase by fibroblasts |
Q41492069 | Inhibition of receptor-mediated uptake of a lysosomal enzyme into fibroblasts by chloroquine, procaine and ammonia |
Q39890179 | Intracellular Localization of Exogenous beta-Glucuronidase in Cultured Skin Fibroblasts |
Q34333938 | Intracellular localization and trafficking of serine proteinase AhSub and cysteine proteinase AhCP of Acanthamoeba healyi |
Q41616394 | Isoelectric focusing of acid hydrolases in human fibroblasts and leucocytes |
Q38357734 | Isolation and Characterization of Phosphorylated Oligosaccharides from alpha-N-Acetylglucosaminidase that Are Recognized by Cell-Surface Receptors |
Q39659849 | Lectin-mediated uptake of lysosomal hydrolases by genetically deficient human fibroblasts |
Q70542304 | Ly-5 (T200) structural polymorphism: the identification of intramolecular sites of phosphorylation |
Q36218735 | Lysosomal dysfunction causes neurodegeneration in mucolipidosis II 'knock-in' mice |
Q36209357 | Lysosomal enzyme oligosaccharide phosphorylation in mouse lymphoma cells: specificity and kinetics of binding to the mannose 6-phosphate receptor in vivo |
Q42664604 | Lysosomal enzymes possess a common antigenic determinant in the cellular slime mold, Dictyostelium discoideum |
Q37896955 | Mannose 6-phosphate receptor homology (MRH) domain-containing lectins in the secretory pathway |
Q39488341 | Mannose 6-phosphate receptors and their role in targeting proteins to lysosomes |
Q40841876 | Mannose 6-phosphate/insulin-like growth factor II receptor is a death receptor for granzyme B during cytotoxic T cell-induced apoptosis. |
Q40510257 | Mannose 6-phosphorylated proteins are required for tumor necrosis factor-induced apoptosis: defective response in I-cell disease fibroblasts |
Q44133732 | Mannose reduces hyaluronan and leukocytes in wound granulation tissue and inhibits migration and hyaluronan-dependent monocyte binding |
Q43597217 | Membrane lectins on human monocytes. Maturation-dependent modulation of 6-phosphomannose and mannose receptors |
Q59325229 | Mod A: a post-translational mutation affecting phosphorylated and sulfated glycopeptides in Dictyostelium discoideum |
Q71065676 | Multiple molecular forms of lysosomal enzymes in mucolipidosis II |
Q38317442 | Mutational analysis of the binding site residues of the bovine cation-dependent mannose 6-phosphate receptor |
Q51769063 | N-glycosylation of the human melanocortin 1 receptor: occupancy of glycosylation sequons and functional role. |
Q66978399 | Neuraminidase in Cultured Fibroblasts and Leucocytes of Homozygotes and Heterozygotes for the Mucolipidosis II Gene (I-Cell Disease) |
Q39645378 | Neurochemical abnormality in I-cell disease: chemical analysis and a possible importance of beta-galactosidase deficiency |
Q44824438 | Oligosaccharide and Ganglioside Neuraminidase Activities of Mucolipidosis I (Sialidosis) and Mucolipidosis II (I-Cell Disease) Fibroblasts |
Q72868722 | Phosphomannosyl-enzyme receptors in rat liver. Subcellular distribution and role in intracellular transport of lysosomal enzymes |
Q36417995 | Phosphorylated oligosaccharides in lysosomal enzymes: identification of alpha-N-acetylglucosamine(1)phospho(6)mannose diester groups |
Q28264020 | Processing of the phosphorylated recognition marker in lysosomal enzymes. Characterization and partial purification of a microsomal alpha-N-acetylglucosaminyl phosphodiesterase |
Q36207136 | Recognition and receptor-mediated uptake of phosphorylated high mannose-type oligosaccharides by cultured human fibroblasts |
Q72935321 | Secretion by mononuclear phagocytes of lysosomal hydrolases bearing ligands for the mannose-6-phosphate receptor system of fibroblasts: Evidence for a second mechanism of spontaneous secretion? |
Q42935679 | Secretion of beta-N-acetylglucosaminidase isoenzymes by normal human fibroblasts |
Q39681854 | Segmental distribution of soluble neutral maltase activity in suckling rat intestine levels vary independently of membrane-bound maltase and lysosomal enzymes during development |
Q37333235 | Selective hepatic uptake of human β-hexosaminidase A by a specific glycoprotein recognition system on sinusoidal cells |
Q35131947 | Selective noncompetitive assimilation of bovine testicular beta-galactosidase and bovine liver beta-glucuronidase by generalized gangliosidosis fibroblasts |
Q45801798 | Separation and properties of molecular forms of α-galactosidase and α-N-acetylgalactosaminidase from blood lymphocytes and lymphoid cell lines transformed by Epstein-Barr virus |
Q40247015 | Structure, biosynthesis and functions of glycoprotein glycans |
Q40125258 | Sugar Residues on Protein |
Q40128818 | The Phosphomannosyl Recognition System for Intracellular and Intercellular Transport of Lysosomal Enzymes |
Q39675567 | The complementation of β-galactosidase in fused cells of mucolipidosis II with another variants of β-galactosidase deficiency using new single cell enzyme assay |
Q41807874 | The effect of chloroquine on the distribution of newly synthesized and old beta-hexosaminidase in fibroblasts |
Q42882149 | The effect of monensin on β-hexosaminidase transport in normal and I-cell fibroblasts |
Q72909086 | The mannose 6-phosphate receptor of Chinese hamster ovary cells. Compartmentalization of acid hydrolases in mutants with altered receptors |
Q70793074 | Transport and processing of lysosomal enzymes by smooth muscle cells and endothelial cells |
Q38354011 | Transport and processing of β-hexosaminidase in normal and mucolipidosis-II cultured fibroblasts. Effect of monensin and nigericin |
Q39246351 | Urinary lysosomal hydrolases in mucolipidosis II and mucolipidosis III |
Q41833706 | alpha-Glucosidase and N-acetylglucosamine-6-sulphatase are the major mannose-6-phosphate glycoproteins in human urine |
Search more.