scholarly article | Q13442814 |
P356 | DOI | 10.3109/07853890.2013.783994 |
P698 | PubMed publication ID | 23651009 |
P2093 | author name string | Christopher L-H Huang | |
Claire A Martin | |||
Gareth D K Matthews | |||
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Loss-of-function mutations in the cardiac calcium channel underlie a new clinical entity characterized by ST-segment elevation, short QT intervals, and sudden cardiac death | Q24675134 | ||
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Paradoxic abbreviation of repolarization in epicardium of the right ventricular outflow tract during augmentation of Brugada-type ST segment elevation | Q43858714 | ||
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Cellular and ionic basis for the sex-related difference in the manifestation of the Brugada syndrome and progressive conduction disease phenotypes | Q44723715 | ||
Delay in right ventricular activation contributes to Brugada syndrome | Q44781964 | ||
Gender difference and drug challenge in Brugada syndrome | Q44803535 | ||
Are women with severely symptomatic brugada syndrome different from men? | Q46056314 | ||
Action potential alternans in the right ventricular outflow tract in a patient with asymptomatic Brugada syndrome | Q46201813 | ||
High-density substrate mapping in Brugada syndrome: combined role of conduction and repolarization heterogeneities in arrhythmogenesis. | Q46269742 | ||
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QTc behavior during exercise and genetic testing for the long-QT syndrome. | Q51498727 | ||
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A complex double deletion in LMNA underlies progressive cardiac conduction disease, atrial arrhythmias, and sudden death. | Q54383005 | ||
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The prevalence, incidence and prognostic value of the Brugada-type electrocardiogram: a population-based study of four decades | Q33146752 | ||
Natural history of Brugada syndrome: insights for risk stratification and management | Q33147491 | ||
Clinical and molecular characterization of patients with catecholaminergic polymorphic ventricular tachycardia. | Q33147854 | ||
Body surface area of ST elevation and the presence of late potentials correlate to the inducibility of ventricular tachyarrhythmias in Brugada syndrome | Q33148073 | ||
Proposed diagnostic criteria for the Brugada syndrome: consensus report | Q33148286 | ||
Risk stratification in the long-QT syndrome. | Q33148941 | ||
Implantable cardioverter defibrillator in high-risk long QT syndrome patients | Q33148945 | ||
Natural history of Brugada syndrome: the prognostic value of programmed electrical stimulation of the heart | Q33148999 | ||
Short QT Syndrome: a familial cause of sudden death | Q33149259 | ||
Efficacy of quinidine in high-risk patients with Brugada syndrome | Q33151791 | ||
Targeted mutational analysis of the RyR2-encoded cardiac ryanodine receptor in sudden unexplained death: a molecular autopsy of 49 medical examiner/coroner's cases | Q33152066 | ||
Long-term prognosis of individuals with right precordial ST-segment-elevation Brugada syndrome | Q33152228 | ||
Arrhythmogenic right ventricular dysplasia: a United States experience | Q33153393 | ||
Risk stratification of individuals with the Brugada electrocardiogram: a meta-analysis | Q33154041 | ||
Mouse models of long QT syndrome | Q33154363 | ||
Outcome after implantation of a cardioverter-defibrillator in patients with Brugada syndrome: a multicenter study | Q33154495 | ||
Calcium channel blockers and beta-blockers versus beta-blockers alone for preventing exercise-induced arrhythmias in catecholaminergic polymorphic ventricular tachycardia | Q33155477 | ||
Risk factors for aborted cardiac arrest and sudden cardiac death in children with the congenital long-QT syndrome | Q33156201 | ||
Repolarization heterogeneity in the right ventricular outflow tract: correlation with ventricular arrhythmias in Brugada patients and in an in vitro canine Brugada model | Q33156240 | ||
Sudden cardiac arrest associated with early repolarization | Q33156255 | ||
Long-term prognosis of probands with Brugada-pattern ST-elevation in leads V1-V3. | Q33157954 | ||
Long-term prognosis of patients diagnosed with Brugada syndrome: Results from the FINGER Brugada Syndrome Registry | Q33158291 | ||
Idiopathic ventricular fibrillation | Q33160592 | ||
Risk stratification in Brugada syndrome: results of the PRELUDE (PRogrammed ELectrical stimUlation preDictive valuE) registry. | Q33160801 | ||
Brugada syndrome 2012. | Q33161523 | ||
Catecholaminergic polymorphic ventricular tachycardia in children. A 7-year follow-up of 21 patients | Q33173888 | ||
Autonomic and antiarrhythmic drug modulation of ST segment elevation in patients with Brugada syndrome | Q33174622 | ||
Early repolarization | Q33539317 | ||
A mutation in the beta 3 subunit of the cardiac sodium channel associated with Brugada ECG phenotype | Q33572315 | ||
An international compendium of mutations in the SCN5A-encoded cardiac sodium channel in patients referred for Brugada syndrome genetic testing | Q33655317 | ||
Cellular basis for the Brugada syndrome and other mechanisms of arrhythmogenesis associated with ST-segment elevation | Q33876613 | ||
The syndrome of right bundle branch block ST segment elevation in V1 to V3 and sudden death--the Brugada syndrome | Q33935865 | ||
Ventricular fibrillation with prominent early repolarization associated with a rare variant of KCNJ8/KATP channel | Q34015485 | ||
Early repolarization: electrocardiographic phenotypes associated with favorable long-term outcome | Q34027142 | ||
Genetics of sudden cardiac death | Q34203505 | ||
Sudden death associated with short-QT syndrome linked to mutations in HERG. | Q34283788 | ||
Short QT syndrome: pharmacological treatment | Q34314532 | ||
Cellular basis for the electrocardiographic J wave | Q34370136 | ||
Brugada syndrome: report of the second consensus conference: endorsed by the Heart Rhythm Society and the European Heart Rhythm Association. | Q34385271 | ||
Mutations in the cardiac L-type calcium channel associated with inherited J-wave syndromes and sudden cardiac death. | Q34395488 | ||
Empiric quinidine therapy for asymptomatic Brugada syndrome: time for a prospective registry | Q34422572 | ||
Arrhythmogenic marker for the sudden unexplained death syndrome in Thai men. | Q34444862 | ||
Out-of-hospital cardiac arrest in the 1990's: a population-based study in the Maastricht area on incidence, characteristics and survival | Q34445532 | ||
Brugada syndrome: from cell to bedside | Q34667046 | ||
Long QT syndrome, Brugada syndrome, and conduction system disease are linked to a single sodium channel mutation | Q34785746 | ||
Mapping of reentrant spontaneous polymorphic ventricular tachycardia in a Scn5a+/- mouse model | Q34979810 | ||
Estradiol promotes sudden cardiac death in transgenic long QT type 2 rabbits while progesterone is protective | Q35427930 | ||
Dantrolene rescues arrhythmogenic RYR2 defect in a patient-specific stem cell model of catecholaminergic polymorphic ventricular tachycardia | Q36037969 | ||
Reduced Na(+) and higher K(+) channel expression and function contribute to right ventricular origin of arrhythmias in Scn5a+/- mice | Q36079245 | ||
Sodium channels as macromolecular complexes: implications for inherited arrhythmia syndromes | Q36140857 | ||
The congenital long QT syndromes from genotype to phenotype: clinical implications | Q36335249 | ||
Cardiac channel molecular autopsy: insights from 173 consecutive cases of autopsy-negative sudden unexplained death referred for postmortem genetic testing. | Q36399631 | ||
The role of molecular autopsy in unexplained sudden cardiac death | Q36443125 | ||
From pulsus to pulseless: the saga of cardiac alternans | Q36489923 | ||
In vitro modeling of ryanodine receptor 2 dysfunction using human induced pluripotent stem cells | Q37005193 | ||
Haplotype-sharing analysis implicates chromosome 7q36 harboring DPP6 in familial idiopathic ventricular fibrillation | Q37156064 | ||
Prevalence of the congenital long-QT syndrome. | Q37442080 | ||
Early repolarization syndrome – a new electrical disorder associated with sudden cardiac death –. | Q37788474 | ||
Cardiac ion channel mutations in the sudden infant death syndrome | Q37826837 | ||
Genetics of ion-channel disorders. | Q37997324 | ||
Brugada electrocardiographic pattern induced by fever | Q37997443 | ||
Ryanodine receptor physiology and its role in disease | Q37997675 | ||
Electrocardiographic characteristics and SCN5A mutations in idiopathic ventricular fibrillation associated with early repolarization | Q39452561 | ||
Trafficking defects and gating abnormalities of a novel SCN5A mutation question gene-specific therapy in long QT syndrome type 3. | Q39722604 | ||
Spatial and temporal heterogeneities are localized to the right ventricular outflow tract in a heterozygotic Scn5a mouse model | Q39814350 | ||
Right ventricular fibrosis and conduction delay in a patient with clinical signs of Brugada syndrome: a combined electrophysiological, genetic, histopathologic, and computational study. | Q40355175 | ||
Early afterdepolarizations: mechanism of induction and block. A role for L-type Ca2+ current | Q41256047 | ||
Structure of a complex between a voltage-gated calcium channel beta-subunit and an alpha-subunit domain. | Q41858723 | ||
Distribution, splicing and glucocorticoid-induced expression of cardiac alpha 1C and alpha 1D voltage-gated Ca2+ channel mRNAs | Q42448384 | ||
KCNH2-K897T is a genetic modifier of latent congenital long-QT syndrome | Q42665516 | ||
Regional variations in action potential alternans in isolated murine Scn5a (+/-) hearts during dynamic pacing | Q43102967 | ||
P433 | issue | 4 | |
P407 | language of work or name | English | Q1860 |
P304 | page(s) | 364-374 | |
P577 | publication date | 2013-05-08 | |
P1433 | published in | Annals of Medicine | Q4767853 |
P1476 | title | The role of ion channelopathies in sudden cardiac death: implications for clinical practice | |
P478 | volume | 45 |
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