| P2093 | author name string | Tracey A Rouault | |
| | Anamika Singh | |
| | Wing-Hang Tong | |
| | Nunziata Maio | |
| | Helge Uhrigshardt | |
| | Neetu Saxena | |
| P2860 | cites work | Characterization of the human HSC20, an unusual DnaJ type III protein, involved in iron–sulfur cluster biogenesis | Q24293446 |
| | Glutaredoxin 5 deficiency causes sideroblastic anemia by specifically impairing heme biosynthesis and depleting cytosolic iron in human erythroblasts | Q24305534 |
| | SDHAF1, encoding a LYR complex-II specific assembly factor, is mutated in SDH-defective infantile leukoencephalopathy | Q24313747 |
| | SDH5, a gene required for flavination of succinate dehydrogenase, is mutated in paraganglioma | Q24317137 |
| | MMS19 assembles iron-sulfur proteins required for DNA metabolism and genomic integrity | Q24337550 |
| | Iron/sulfur proteins biogenesis in prokaryotes: formation, regulation and diversity | Q27022996 |
| | Structure of Human J-type Co-chaperone HscB Reveals a Tetracysteine Metal-binding Domain | Q27651682 |
| | Interaction of J-Protein Co-Chaperone Jac1 with Fe–S Scaffold Isu Is Indispensable In Vivo and Conserved in Evolution | Q27677058 |
| | J-domain protein, Jac1p, of yeast mitochondria required for iron homeostasis and activity of Fe-S cluster proteins | Q27933878 |
| | Distinct clinical features of paraganglioma syndromes associated with SDHB and SDHD gene mutations | Q28278673 |
| | Succinate dehydrogenase kidney cancer: an aggressive example of the Warburg effect in cancer | Q28661212 |
| | The HSP70 chaperone machinery: J proteins as drivers of functional specificity | Q29616140 |
| | LYRM7/MZM1L is a UQCRFS1 chaperone involved in the last steps of mitochondrial Complex III assembly in human cells | Q32884553 |
| | Three hydrophobic amino acids in Escherichia coli HscB make the greatest contribution to the stability of the HscB-IscU complex | Q33804492 |
| | Co-evolution-driven switch of J-protein specificity towards an Hsp70 partner. | Q33845792 |
| | Succinate dehydrogenase - Assembly, regulation and role in human disease | Q33869389 |
| | Jac1, a mitochondrial J-type chaperone, is involved in the biogenesis of Fe/S clusters in Saccharomyces cerevisiae | Q34084359 |
| | Emerging concepts in the flavinylation of succinate dehydrogenase | Q34326128 |
| | Formation and properties of [4Fe-4S] clusters on the IscU scaffold protein | Q34654127 |
| | Biogenesis of iron-sulfur clusters in mammalian cells: new insights and relevance to human disease | Q35794543 |
| | HSC20 interacts with frataxin and is involved in iron-sulfur cluster biogenesis and iron homeostasis | Q35817466 |
| | A zinc finger-like domain of the molecular chaperone DnaJ is involved in binding to denatured protein substrates. | Q35843729 |
| | Missense mutations in the human SDHB gene increase protein degradation without altering intrinsic enzymatic function | Q36329838 |
| | Insertion mutants in Drosophila melanogaster Hsc20 halt larval growth and lead to reduced iron-sulfur cluster enzyme activities and impaired iron homeostasis | Q36728886 |
| | Molecular chaperones HscA/Ssq1 and HscB/Jac1 and their roles in iron-sulfur protein maturation | Q36799458 |
| | The iron-sulfur cluster assembly machineries in plants: current knowledge and open questions | Q37040353 |
| | Human mitochondrial chaperone (mtHSP70) and cysteine desulfurase (NFS1) bind preferentially to the disordered conformation, whereas co-chaperone (HSC20) binds to the structured conformation of the iron-sulfur cluster scaffold protein (ISCU). | Q37213806 |
| | Human ISD11 is essential for both iron-sulfur cluster assembly and maintenance of normal cellular iron homeostasis | Q37272356 |
| | Complex I deficiency: clinical features, biochemistry and molecular genetics | Q38042908 |
| | Functional assays in high-resolution clear native gels to quantify mitochondrial complexes in human biopsies and cell lines | Q40062365 |
| | Multiple molecules of Hsc70 and a dimer of DjA1 independently bind to an unfolded protein | Q40797490 |
| | Mutation of the iron-sulfur cluster assembly gene IBA57 causes severe myopathy and encephalopathy | Q41932516 |
| | Monothiol glutaredoxins function in storing and transporting [Fe2S2] clusters assembled on IscU scaffold proteins | Q42017629 |
| | Structure-based mutagenesis studies of the peptide substrate binding fragment of type I heat-shock protein 40 | Q42030110 |
| | The human mitochondrial ISCA1, ISCA2, and IBA57 proteins are required for [4Fe-4S] protein maturation | Q42072342 |
| | The mitochondrial Hsp70 chaperone Ssq1 facilitates Fe/S cluster transfer from Isu1 to Grx5 by complex formation | Q42153817 |
| | Role of DnaJ G/F-rich domain in conformational recognition and binding of protein substrates | Q42400784 |
| | Evaluation of the mitochondrial respiratory chain and oxidative phosphorylation system using blue native gel electrophoresis | Q42606879 |
| | Identification of essential residues in the type II Hsp40 Sis1 that function in polypeptide binding | Q43937089 |
| | Novel succinate dehydrogenase subunit B (SDHB) mutations in familial phaeochromocytomas and paragangliomas, but an absence of somatic SDHB mutations in sporadic phaeochromocytomas | Q44347017 |
| | Protein expression profiles in patients carrying NFU1 mutations. Contribution to the pathophysiology of the disease. | Q44364030 |
| | Chapter 12 Controlled expression of iron-sulfur cluster assembly components for respiratory chain complexes in mammalian cells | Q46059841 |
| | R46Q mutation in the succinate dehydrogenase B gene (SDHB) in a Japanese family with both abdominal and thoracic paraganglioma following metastasis | Q46685842 |
| | Genetic testing in pheochromocytoma or functional paraganglioma | Q46825172 |
| | Sequence-specific interaction between mitochondrial Fe-S scaffold protein Isu and Hsp70 Ssq1 is essential for their in vivo function | Q47657508 |
| | Bioinorganic chemistry: Electrons in Fe-S protein assembly | Q59598537 |
| | Organelle isolation: functional mitochondria from mouse liver, muscle and cultured filroblasts | Q60056610 |
| | A novel germline SDHB mutation in a gastrointestinal stromal tumor patient without bona fide features of the Carney–Stratakis dyad | Q60526951 |
| | Late-onset optic atrophy, ataxia, and myopathy associated with a mutation of a complex II gene | Q74284125 |
| | The C-terminal (331-376) sequence of Escherichia coli DnaJ is essential for dimerization and chaperone activity: a small angle X-ray scattering study in solution | Q81681117 |
| | Complex II deficiency--a case report and review of the literature | Q85902346 |
| P433 | issue | 3 | |
| P921 | main subject | identical protein binding | Q14762994 |
| | HscB mitochondrial iron-sulfur cluster cochaperone | Q21105347 |
| P304 | page(s) | 445-457 | |
| P577 | publication date | 2014-03-01 | |
| P1433 | published in | Cell Metabolism | Q1254684 |
| P1476 | title | Cochaperone binding to LYR motifs confers specificity of iron sulfur cluster delivery | |
| P478 | volume | 19 | |