| scholarly article | Q13442814 |
| P819 | ADS bibcode | 2012PLoSO...732419P |
| P356 | DOI | 10.1371/JOURNAL.PONE.0032419 |
| P932 | PMC publication ID | 3293807 |
| P698 | PubMed publication ID | 22403656 |
| P5875 | ResearchGate publication ID | 221689535 |
| P2093 | author name string | John H Wolfe | |
| Ramona Rozen | |||
| Michael K Parente | |||
| Cassia N Cearley | |||
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| P275 | copyright license | Creative Commons Attribution 4.0 International | Q20007257 |
| P6216 | copyright status | copyrighted | Q50423863 |
| P433 | issue | 3 | |
| P407 | language of work or name | English | Q1860 |
| P921 | main subject | lysosomal storage disease | Q675010 |
| P304 | page(s) | e32419 | |
| P577 | publication date | 2012-03-05 | |
| P1433 | published in | PLOS One | Q564954 |
| P1476 | title | Dysregulation of gene expression in a lysosomal storage disease varies between brain regions implicating unexpected mechanisms of neuropathology | |
| P478 | volume | 7 |
| Q26853349 | Animal models for lysosomal storage disorders |
| Q43671074 | Astrocytosis in infantile neuronal ceroid lipofuscinosis: friend or foe? |
| Q35664978 | Bilateral single-site intracerebral injection of a nonpathogenic herpes simplex virus-1 vector decreases anxiogenic behavior in MPS VII mice |
| Q33755372 | Brain RNA-Seq Profiling of the Mucopolysaccharidosis Type II Mouse Model |
| Q41838423 | Circadian profiling in two mouse models of lysosomal storage disorders; Niemann Pick type-C and Sandhoff disease |
| Q37705073 | Clinical neurogenetics: neuropathic lysosomal storage disorders |
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| Q27318087 | Evaluation of AAV-mediated Gene Therapy for Central Nervous System Disease in Canine Mucopolysaccharidosis VII. |
| Q35623843 | Ex vivo gene therapy using patient iPSC-derived NSCs reverses pathology in the brain of a homologous mouse model |
| Q89682420 | Genetic Base of Behavioral Disorders in Mucopolysaccharidoses: Transcriptomic Studies |
| Q42100984 | High-resolution magnetic resonance microscopy and diffusion tensor imaging to assess brain structural abnormalities in the murine mucopolysaccharidosis VII model. |
| Q35180647 | Identification of a biomarker in cerebrospinal fluid for neuronopathic forms of Gaucher disease |
| Q27318642 | Immune-Mediated Inflammation May Contribute to the Pathogenesis of Cardiovascular Disease in Mucopolysaccharidosis Type I |
| Q40217404 | Integrated analysis of proteome and transcriptome changes in the mucopolysaccharidosis type VII mouse hippocampus |
| Q58571217 | Lysosomal and network alterations in human mucopolysaccharidosis type VII iPSC-derived neurons |
| Q91591025 | Metabolomics profiling reveals profound metabolic impairments in mice and patients with Sandhoff disease |
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| Q51758684 | The Aging of Iron Man. |
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| Q91185200 | Variation among intact tissue samples reveals the core transcriptional features of human CNS cell classes |
| Q37076523 | β-glucuronidase mRNA levels are correlated with gait and working memory in premutation females: understanding the role of FMR1 premutation alleles |
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