| scholarly article | Q13442814 |
| P50 | author | Jorgen K. Kanters | Q50884207 |
| Lis Frydenreich Hasholt | Q107650480 | ||
| P2093 | author name string | Michael Christiansen | |
| Troels Tolstrup Nielsen | |||
| Anne Nørremølle | |||
| Christian Munch Hagen | |||
| Dominik Pesta | |||
| Frederik Heurlin Aidt | |||
| Signe Marie Borch Nielsen | |||
| P2860 | cites work | The Huntington's disease protein interacts with p53 and CREB-binding protein and represses transcription | Q22254119 |
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| Trinucleotide repeat elongation in the Huntingtin gene in Huntington disease patients from 71 Danish families | Q42609324 | ||
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| Evidence for impairment of energy metabolism in vivo in Huntington's disease using localized 1H NMR spectroscopy | Q45290303 | ||
| Weight loss in Huntington disease increases with higher CAG repeat number | Q45291411 | ||
| Mitochondrial defect in Huntington's disease caudate nucleus | Q45291734 | ||
| Detection of early behavioral markers of Huntington's disease in R6/2 mice employing an automated social home cage | Q45293617 | ||
| Neuropathological classification of Huntington's disease | Q45297167 | ||
| Mitochondrial respiration and ATP production are significantly impaired in striatal cells expressing mutant huntingtin | Q45297269 | ||
| p53 mediates cellular dysfunction and behavioral abnormalities in Huntington's disease | Q45297400 | ||
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| Mutant huntingtin aggregates impair mitochondrial movement and trafficking in cortical neurons | Q45300079 | ||
| Early degenerative changes in transgenic mice expressing mutant huntingtin involve dendritic abnormalities but no impairment of mitochondrial energy production | Q45302993 | ||
| Mitochondrial dysfunction in Huntington's disease: the bioenergetics of isolated and in situ mitochondria from transgenic mice | Q45304684 | ||
| Increased caspase-2, calpain activations and decreased mitochondrial complex II activity in cells expressing exogenous huntingtin exon 1 containing CAG repeat in the pathogenic range | Q45306567 | ||
| Development and implementation of standardized respiratory chain spectrophotometric assays for clinical diagnosis | Q45859940 | ||
| Differential regulation of respiratory chain subunits by a CREB-dependent signal transduction pathway. Role of cyclic AMP in cytochrome c and COXIV gene expression | Q72695013 | ||
| Compound heterozygous mutations in the flavoprotein gene of the respiratory chain complex II in a patient with Leigh syndrome | Q73621669 | ||
| High-resolution respirometry: OXPHOS protocols for human cells and permeabilized fibers from small biopsies of human muscle | Q82370039 | ||
| Mitochondrial respiratory control and early defects of oxidative phosphorylation in the failing human heart | Q84838077 | ||
| P407 | language of work or name | English | Q1860 |
| P921 | main subject | Huntington's disease | Q190564 |
| striatum | Q1319792 | ||
| P304 | page(s) | 72-74 | |
| P577 | publication date | 2013-04-02 | |
| P1433 | published in | PLOS Currents | Q7119653 |
| P1476 | title | Dysfunctional mitochondrial respiration in the striatum of the Huntington's disease transgenic R6/2 mouse model | |
| P478 | volume | 5 |
| Q27314860 | Amitriptyline improves motor function via enhanced neurotrophin signaling and mitochondrial functions in the murine N171-82Q Huntington disease model. |
| Q60302578 | Complex spatio-temporal distribution and genomic ancestry of mitochondrial DNA haplogroups in 24,216 Danes |
| Q37649092 | Expression of alternative oxidase in Drosophila ameliorates diverse phenotypes due to cytochrome oxidase deficiency |
| Q33562672 | High-resolution respirometry of fine-needle muscle biopsies in pre-manifest Huntington's disease expansion mutation carriers shows normal mitochondrial respiratory function. |
| Q41949133 | Metabolic Stress and Disorders Related to Alterations in Mitochondrial Fission or Fusion |
| Q35647382 | Mitochondrial bioenergetic alterations after focal traumatic brain injury in the immature brain. |
| Q38458943 | Mutant Huntingtin and Elusive Defects in Oxidative Metabolism and Mitochondrial Calcium Handling |
| Q39035184 | Oxidative metabolism and Ca2+ handling in striatal mitochondria from YAC128 mice, a model of Huntington's disease |
| Q28397230 | Oxygen consumption deficit in Huntington disease mouse brain under metabolic stress |
| Q36141861 | Persistently Altered Brain Mitochondrial Bioenergetics After Apparently Successful Resuscitation From Cardiac Arrest. |
| Q60304737 | Schizophrenia-associated mt-DNA SNPs exhibit highly variable haplogroup affiliation and nuclear ancestry: Bi-genomic dependence raises major concerns for link to disease |
| Q28072937 | The chicken or the egg: mitochondrial dysfunction as a cause or consequence of toxicity in Huntington's disease |
| Q47442924 | Towards an Understanding of Energy Impairment in Huntington's Disease Brain |
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