| review article | Q7318358 |
| scholarly article | Q13442814 |
| P6179 | Dimensions Publication ID | 1031718995 |
| P356 | DOI | 10.1023/A:1006895209833 |
| P698 | PubMed publication ID | 9062899 |
| P2093 | author name string | J P Infante | |
| V A Huszagh | |||
| P2860 | cites work | Carnitine biosynthesis in hepatic peroxisomes. Demonstration of gamma-butyrobetaine hydroxylase activity | Q28292674 |
| Clofibrate-induced muscular syndrome. Report of a case with clinical, electromyographic and pathologic observations | Q28326913 | ||
| Severe deficiency of docosahexaenoic acid in peroxisomal disorders: a defect of delta 4 desaturation? | Q28330026 | ||
| Metabolic aspects of peroxisomal beta-oxidation | Q28333111 | ||
| Delta 5 desaturase activity in rat kidney microsomes | Q28582078 | ||
| Animal model of systemic carnitine deficiency: analysis in C3H-H-2 degrees strain of mouse associated with juvenile visceral steatosis | Q28590344 | ||
| The metabolism of 7,10,13,16,19-docosapentaenoic acid to 4,7,10,13,16,19-docosahexaenoic acid in rat liver is independent of a 4-desaturase | Q28646980 | ||
| Docosahexaenoic acid synthesis in human skin fibroblasts involves peroxisomal retroconversion of tetracosahexaenoic acid | Q28647093 | ||
| Respiratory chain enzyme defects in patients with idiopathic inflammatory myopathy. | Q33578093 | ||
| Increased mitochondrial DNA in blood vessels and ragged‐red fibers in mitochondrial myopathy, encephalopathy, lactic acidosis, and stroke‐like episodes (MELAS) | Q72081576 | ||
| Astrocytes play a major role in the control of neuronal proliferation in vitro | Q72250614 | ||
| Ethanol exposure causes a decrease in docosahexaenoic acid and an increase in docosapentaenoic acid in feline brains and retinas | Q72267800 | ||
| Adrenic acid delta 4 desaturation and fatty acid composition in liver microsomes of spontaneously diabetic Wistar BB rats | Q72335690 | ||
| Blood polyunsaturated fatty acids in patients with peroxisomal disorders. A multicenter study | Q72406532 | ||
| Retroconversion of docosahexaenoic acid in the rat | Q72534686 | ||
| n-3 fatty acids inhibit defects and fatty acid changes caused by phenytoin in early gestation in mice | Q72577371 | ||
| Synthesis of docosahexaenoic acid by retina and retinal pigment epithelium | Q72660172 | ||
| Alterations by clofibric acid of glycerolipid metabolism in rat-kidney | Q72862216 | ||
| SYNTHESIS OF FATTY ACIDS IN ANIMAL TISSUES. I. INCORPORATION OF C14-ACETYL COENZYME A INTO A VARIETY OF LONG CHAIN FATTY ACIDS BY SUBCELLULAR PARTICLES | Q76624565 | ||
| TRACER EXPERIMENTS TO ASSESS METABOLIC CONVERSIONS OF POLYUNSATURATED FATTY ACIDS | Q78492043 | ||
| The pathways of synthesis of fatty acids by mitochondria | Q79405487 | ||
| Levels of choline intermediates in the visual system structures and in peripheral nerve of the rat: Comparison with neural tissues of a lower vertebrate (Mustelus canis) and an invertebrate (Loligo pealei) | Q84306249 | ||
| Carnitine--metabolism and functions | Q34257158 | ||
| A FAMILIAL SYNDROME OF MULTIPLE CONGENITAL DEFECTS | Q34257272 | ||
| The relation between insulin sensitivity and the fatty-acid composition of skeletal-muscle phospholipids. | Q34359100 | ||
| Glycerolipid biosynthesis in peroxisomes (microbodies). | Q34387067 | ||
| A fatty acyl-CoA oxidizing system in rat liver peroxisomes; enhancement by clofibrate, a hypolipidemic drug | Q34585642 | ||
| Segregation patterns of a novel mutation in the mitochondrial tRNA glutamic acid gene associated with myopathy and diabetes mellitus. | Q35644235 | ||
| The biochemistry and molecular biology of plant lipid biosynthesis | Q36185495 | ||
| Ultrastructural localization of glycerolipid synthesis in rod cells of the isolated frog retina | Q36590492 | ||
| Preferential localization of active mitochondria in process tips of immature retinal oligodendrocytes | Q36686735 | ||
| Is Carnitine Essential in Children? | Q37223058 | ||
| Accumulation of glycerophosphocholine (GPC) by renal cells: osmotic regulation of GPC:choline phosphodiesterase | Q37588333 | ||
| Biochemical mechanisms of induction of hepatic peroxisome proliferation | Q38639915 | ||
| Carnitine: metabolism and clinical chemistry | Q38679131 | ||
| The fetal hydantoin syndrome | Q39338123 | ||
| Docosahexaenoate-containing phospholipids in sarcoplasmic reticulum and retinal photoreceptors. A proposal for a role in Ca2+-ATPase calcium transport | Q39482238 | ||
| Vitamin E and selenium participation in fatty acid desaturation. A proposal for an enzymatic function of these nutrients | Q39730622 | ||
| Carnitine metabolism and function in humans | Q39738534 | ||
| Synthesis of highly unsaturated phosphatidylcholines in the development of sperm motility: a role for epididymal glycerol-3-phosphorylcholine | Q39837705 | ||
| Role of phospholipids in transport and enzymic reactions | Q39902441 | ||
| Biosynthesis of acyl-specific glycerophospholipids in mammalian tissues. Postulation of new pathways | Q40177921 | ||
| Possible carnitine requirement of the newborn and the effect of genetic disease on the carnitine requirement. | Q40262774 | ||
| Teratogenic effects of alcohol in humans and laboratory animals | Q40284854 | ||
| Lethal neonatal deficiency of carnitine palmitoyltransferase II associated with dysgenesis of the brain and kidneys. | Q40473100 | ||
| Pathways for the uptake and conservation of docosahexaenoic acid in photoreceptors and synapses: biochemical and autoradiographic studies. | Q40816849 | ||
| Primary and secondary carnitine deficiency syndromes. | Q40954913 | ||
| beta-oxidation of fatty acids in mitochondria, peroxisomes, and bacteria: a century of continued progress | Q41018645 | ||
| The mechanism of arrest of neuronal migration in the Zellweger malformation: An hypothesis based upon cytoarchitectonic analysis | Q41038903 | ||
| Peroxisomal fatty acid oxidation and inhibitors of the mitochondrial carnitine palmitoyltransferase I in isolated rat hepatocytes | Q41142588 | ||
| Reevaluation of the pathways for the biosynthesis of polyunsaturated fatty acids | Q41144677 | ||
| Changes of mitochondrial mass in the hemopoietic stem cell line FDCP-mix after treatment with etoposide: a correlative study by multiparameter flow cytometry and confocal and electron microscopy. | Q41268620 | ||
| Cellular targets of 3′-azido-3′-deoxythymidine: an early (non-delayed) effect on oxidative phosphorylation | Q41322933 | ||
| Neuropathology of peroxisomal diseases | Q41366920 | ||
| Polyunsaturated fatty acids in the developing human brain, erythrocytes and plasma in peroxisomal disease: therapeutic implications | Q41366953 | ||
| Polyunsaturated fatty acids in peroxisomal disorders: a hypothesis and a proposal for treatment | Q41616952 | ||
| Retroconversion and delta 4 desaturation of docosatetraenoate (22:4(n-6)) and docosapentaenoate (22:5(n-3)) by human cells in culture | Q41687127 | ||
| Dietary omega-3 and polyunsaturated fatty acids modify fatty acyl composition and insulin binding in skeletal-muscle sarcolemma | Q41774579 | ||
| Multiple peroxisomal enzymatic deficiency disorders. A comparative biochemical and morphologic study of Zellweger cerebrohepatorenal syndrome and neonatal adrenoleukodystrophy | Q41806915 | ||
| Detection of a homologous series of C26-C38 polyenoic fatty acids in the brain of patients without peroxisomes (Zellweger's syndrome). | Q41855406 | ||
| Effects of alcohol on the generation and migration of cerebral cortical neurons | Q41933308 | ||
| Differential effects of fibrates on the acyl composition of microsomal phospholipids in rats | Q41947131 | ||
| Sex-related differences in the enhancing effects of perfluoro-octanoic acid on stearoyl-CoA desaturase and its influence on the acyl composition of phospholipid in rat liver. Comparison with clofibric acid and tiadenol | Q42108242 | ||
| Mitochondrial myopathy--a result of clofibrate/etofibrate treatment? Case report | Q42229767 | ||
| Levels of ethanolamine intermediates in the human and rat visual system structures: comparison with neural tissues of a lower vertebrate (Mustelus canis) and an invertebrate (Loligo pealei). | Q42289400 | ||
| Docosahexaenoic acid--a new therapeutic approach to peroxisomal-disorder patients: experience with two cases | Q42613246 | ||
| Chlorpromazine and carnitine-dependency of rat liver peroxisomal beta-oxidation of long-chain fatty acids | Q42855382 | ||
| Structure and lipid distribution of polyenoic very-long-chain fatty acids in the brain of peroxisome-deficient patients (Zellweger syndrome). | Q42857172 | ||
| Metabolism of fatty acids and their incorporation into phospholipids of the mitochondria and endoplasmic reticulum in isolated hepatocytes determined by isolation of fluorescence derivatives | Q43433043 | ||
| Role of peroxisomal fatty acyl-CoA beta-oxidation in phospholipid biosynthesis | Q43578547 | ||
| Activation of mitochondrial ATPase as evidence of loosely coupled oxidative phosphorylation in various skeletal muscle disorders. A histochemical fine-structural study | Q43717409 | ||
| Deficiency of long-chain 3-hydroxyacyl-CoA dehydrogenase: a cause of lethal myopathy and cardiomyopathy in early childhood | Q43792460 | ||
| De novo CDP-choline-dependent glycerophosphorylcholine synthesis and its involvement as an intermediate in phosphatidylcholine synthesis | Q43905729 | ||
| Acute Muscular Syndrome Associated with Administration of Clofibrate | Q44060847 | ||
| A new pathway for phosphatidylserine synthesis in rat liver microsomes | Q44282527 | ||
| Abnormal profiles of polyunsaturated fatty acids in the brain, liver, kidney and retina of patients with peroxisomal disorders | Q45156613 | ||
| The subcellular distribution of acyl CoA: dihydroxyacetone phosphate acyl transferase in guinea pig liver | Q45226059 | ||
| Effect of maternal ethanol consumption during pregnancy on the phospholipid molecular species composition of fetal guinea-pig brain, liver and plasma | Q46295625 | ||
| Evidence for peroxisomal retroconversion of adrenic acid (22:4(n-6)) and docosahexaenoic acids (22:6(n-3)) in isolated liver cells | Q46808524 | ||
| Peroxisomal and mitochondrial defects in the cerebro-hepato-renal syndrome | Q47974070 | ||
| Peripheral benzodiazepine stimulates secretion of growth hormone and mitochondrial proliferation in pituitary tumour GH3 cells. | Q48151791 | ||
| Pseudo-Zellweger syndrome: deficiencies in several peroxisomal oxidative activities | Q48422324 | ||
| Cytochemical and stereological analysis of rat cortical astrocytes during development in primary culture. Effect of prenatal exposure to ethanol | Q48477832 | ||
| Ethanol-induced disturbances of gliogenesis and neuronogenesis in the developing murine brain: an in vitro and in vivo immunohistochemical and ultrastructural study | Q48487807 | ||
| Alterations in the fatty acid composition of rat brain cells (neurons, astrocytes, and oligodendrocytes) and of subcellular fractions (myelin and synaptosomes) induced by a diet devoid of n-3 fatty acids | Q48636147 | ||
| The cerebrohepatorenal (Zellweger) syndrome. Increased levels and impaired degradation of very-long-chain fatty acids and their use in prenatal diagnosis | Q48670157 | ||
| Mitochondrial myopathy with loosely coupled oxidative phosphorylation in a case of Zellweger syndrome. A cytochemical-ultrastructural study. | Q48696869 | ||
| Severe plasmalogen deficiency in tissues of infants without peroxisomes (Zellweger syndrome). | Q48715988 | ||
| Postnatal development and isolation of peroxisomes from brain | Q48750294 | ||
| Mitochondrial myopathy of cerebro-hepato-renal (Zellweger) syndrome | Q48767114 | ||
| Biochemical studies in the liver and muscle of patients with Zellweger syndrome. | Q48797042 | ||
| Neuronal migration abnormality in peroxisomal bifunctional enzyme defect. | Q49124548 | ||
| Biosynthesis of long chain fatty acids by subcellular particles of mature brain. | Q49162055 | ||
| CPEO and carnitine deficiency overlapping in MELAS syndrome. | Q50518715 | ||
| Sequential appearance and ultrastructure of amphophilic cell foci, adenomas, and carcinomas in the liver of male and female rats treated with dehydroepiandrosterone. | Q51039847 | ||
| Acetate-1-14C incorporation into polyunsaturated fatty acids of phospholipids of developing chick brain. | Q51213571 | ||
| Incorporation of [1-14C]linoleate and linolenate into polyunsaturated fatty acids of phospholipids of the embryonic chick brain. | Q51219163 | ||
| Peroxisomal retroconversion of docosahexaenoic acid (22:6(n−3)) to eicosapentaenoic acid (20:5(n−3)) studied in isolated rat liver cells | Q51612193 | ||
| Docosahexaenoic acid therapy in docosahexaenoic acid-deficient patients with disorders of peroxisomal biogenesis. | Q52202523 | ||
| Zellweger syndrome: diagnostic assays, syndrome delineation, and potential therapy. | Q52261646 | ||
| Maternal ethanol consumption: effect on skeletal muscle development in guinea pig offspring. | Q53881500 | ||
| Peroxisomal assembly defects: clinical, pathologic, and biochemical findings in two patients in a newly identified complementation group. | Q54242010 | ||
| Phospholipid species containing long and very long polyenoic fatty acids remain with rhodopsin after hexane extraction of photoreceptor membranes | Q54388526 | ||
| Phospholipid specificity of bovine heart bc1 complex | Q58783113 | ||
| Rat liver peroxisomes catalyze the beta oxidation of fatty acids | Q67276534 | ||
| Heterogeneity of renal mitochondria of the rat | Q67382835 | ||
| Pathology of hepatic peroxisomes and mitochondria in patients with peroxisomal disorders | Q67653760 | ||
| Active transport of butyrobetaine and carnitine into isolated liver cells | Q67829995 | ||
| Astrocytes, not neurons, produce docosahexaenoic acid (22:6 omega-3) and arachidonic acid (20:4 omega-6) | Q67897384 | ||
| The extending astroglial process: development of glial cell shape, the growing tip, and interactions with neurons | Q67934520 | ||
| Do rat kidney cortex microsomes possess the enzymatic machinery to desaturate and chain elongate fatty acyl-CoA derivatives? | Q67978451 | ||
| Effect of high carbohydrate and high protein diets on microsomal fatty acid composition, "fluidity" and delta 6 desaturation activity in kidney and lung | Q67986803 | ||
| Alpha-tocopherol and fatty acid levels in red blood cells in patients treated with antiepileptic drugs | Q68063240 | ||
| Lethal neonatal multiorgan deficiency of carnitine palmitoyltransferase II | Q68073212 | ||
| Peroxisomal membrane ghosts in Zellweger syndrome--aberrant organelle assembly | Q68131442 | ||
| Schizophrenic patients treated with high dose phenothiazine or thioxanthene become deficient in polyunsaturated fatty acids in their thrombocytes | Q68232117 | ||
| The 22-kD peroxisomal integral membrane protein in Zellweger syndrome--presence, abundance, and association with a peroxisomal thiolase precursor protein | Q68296097 | ||
| The Zellweger syndrome: deficient conversion of docosahexaenoic acid (22:6(n-3)) to eicosapentaenoic acid (20:5(n-3)) and normal delta 4-desaturase activity in cultured skin fibroblasts | Q68418242 | ||
| Peroxisome proliferators enhance linoleic acid metabolism in rat liver. Increased biosynthesis of omega 6 polyunsaturated fatty acids | Q68461482 | ||
| Peroxisomal proliferation in heart and liver of mice receiving chlorpromazine, ethyl 2(5(4-chlorophenyl)pentyl) oxiran-2-carboxylic acid or high fat diet: a biochemical and morphometrical comparative study | Q68545013 | ||
| Biosynthesis and composition of phosphatides in outer and inner mitochondrial membranes | Q68583790 | ||
| Studies on the synthesis of fatty acids by a beef heart mitochondrial enzyme system | Q68584033 | ||
| Mitochondria and fetal alcohol syndrome | Q68671319 | ||
| Microsomal marker enzymes and their limitations in distinguishing the outer membrane of rat liver mitochondria from the microsomes | Q68736611 | ||
| Effect of chlorpromazine and trifluoperazine on cytoskeletal components and mitochondria in cultured mammalian cells | Q69044262 | ||
| Adrenomyeloneuropathic syndrome in a woman, associated with morphologic abnormalities of muscle mitochondria | Q69239972 | ||
| Evolution of mammalian endothermic metabolism: mitochondrial activity and cell composition | Q69325736 | ||
| Effect of fatty acid composition on insulin and IGF-I binding in retinoblastoma cells | Q69542399 | ||
| Changes of fatty acid composition of phospholipids and lipid structural order in rat liver mitochondrial membrane subsequent to galactosamine intoxication. Effect of clofibrate | Q69564828 | ||
| De novo sn-glycerol-3-phosphorylcholine synthetase activity in lung and muscle and its subcellular location | Q69647773 | ||
| Polyunsaturated fatty acid changes suggesting a new enzymatic defect in Zellweger syndrome | Q69669210 | ||
| Inhibition of carnitine palmitoyltransferase (CPT) by chlorpromazine in muscle of patients with CPT deficiency | Q69681111 | ||
| Effect of clofibric acid on the molecular species composition of diacyl glycerophosphocholine of rat liver microsomes | Q69891991 | ||
| Cardiac mitochondrial abnormalities in a mouse model of the fetal alcohol syndrome | Q69919049 | ||
| Vesicular transport of newly synthesized opsin from the Golgi apparatus toward the rod outer segment. Ultrastructural immunocytochemical and autoradiographic evidence in Xenopus retinas | Q69974905 | ||
| Active labeling of phosphatidylcholines by [1-14C]docosahexaenoate in isolated photoreceptor membranes | Q70006580 | ||
| Labeling of phosphatidylcholines of retina subcellular fractions by [1-14C]eicosatetraenoate (20:4(n-6)), docosapentaenoate (22:5(n-3)) and docosahexaenoate (22:6(n-3)) | Q70037543 | ||
| Peroxisomal defects in neonatal-onset and X-linked adrenoleukodystrophies | Q70043608 | ||
| Biosynthesis of peroxisomal beta-oxidation enzymes in infants with Zellweger syndrome | Q70316933 | ||
| Studies to determine if rat liver contains chain-length-specific acyl-CoA 6-desaturases | Q70480924 | ||
| Influence of omega-3 fatty acid treatment on cardiac phospholipid composition and coronary flow of streptozocin-diabetic rats | Q70699368 | ||
| The desaturation and elongation of linolenic acid and eicosapentaenoic acid by hepatocytes and liver microsomes from rainbow trout (Oncorhynchus mykiss) fed diets containing fish oil or olive oil | Q70883790 | ||
| Membrane fatty acid composition of tissues is related to body mass of mammals | Q70892264 | ||
| Interaction of rhodopsin with two unsaturated phosphatidylcholines: a deuterium nuclear magnetic resonance study | Q70997312 | ||
| Linolenic acid desaturation and chain elongation and rapid turnover of phospholipid n - 3 fatty acids in isolated rat liver cells | Q71027710 | ||
| Selective effects of isomeric cis and trans fatty acids on fatty acyl delta 9 and delta 6 desaturation by human skin fibroblasts | Q71027738 | ||
| Biosynthesis of docosahexaenoic acid in human cells: evidence that two different delta 6-desaturase activities may exist | Q71145718 | ||
| Generation of hydroxytrimethyllysine from trimethyllysine limits the carnitine biosynthesis in premature infants | Q71229296 | ||
| Peroxisomal fatty acid oxidation is selectively inhibited by phenothiazines in isolated hepatocytes | Q71384561 | ||
| Liver in the cerebro-hepato-renal syndrome: defective bile acid synthesis and abnormal mitochondria | Q71398272 | ||
| Arachidonic acid synthesis in isolated liver cells:" effects of (-)-carnitine and of (+)-decanoylcarnitine | Q71578094 | ||
| Studies on the regulation of arachidonic acid synthesis in isolated rat liver cells | Q71623065 | ||
| The effects of unsaturated fatty acids on the synthesis of arachidonic acid in rat kidney cells | Q71660410 | ||
| OXPHOS defects and mitochondrial DNA mutations in cardiomyopathy | Q71852995 | ||
| P433 | issue | 1-2 | |
| P921 | main subject | Zellweger syndrome | Q189167 |
| P304 | page(s) | 101-115 | |
| P577 | publication date | 1997-03-01 | |
| P1433 | published in | Molecular and Cellular Biochemistry | Q1573176 |
| P1476 | title | On the molecular etiology of decreased arachidonic (20:4n-6), docosapentaenoic (22:5n-6) and docosahexaenoic (22:6n-3) acids in Zellweger syndrome and other peroxisomal disorders | |
| P478 | volume | 168 |
| Q33547527 | A function for the vitamin E metabolite alpha-tocopherol quinone as an essential enzyme cofactor for the mitochondrial fatty acid desaturases |
| Q90449477 | A novel FADS2 isoform identified in human milk fat globule suppresses FADS2 mediated Δ6-desaturation of omega-3 fatty acids |
| Q37511756 | A role for peroxisome proliferator-activated receptor γ coactivator 1 (PGC-1) in the regulation of cardiac mitochondrial phospholipid biosynthesis |
| Q77363902 | Accumulation of glycolipids in mutant Chinese hamster ovary cells (Z65) with defective peroxisomal assembly and comparison of the metabolic rate of glycosphingolipids between Z65 cells and wild-type CHO-K1 cells |
| Q28647102 | Analysis of the putative role of 24-carbon polyunsaturated fatty acids in the biosynthesis of docosapentaenoic (22:5n-6) and docosahexaenoic (22:6n-3) acids |
| Q35197811 | Developmental genetic malformations of the cerebral cortex |
| Q38413096 | Diet, nutrients and metabolism: cogs in the wheel driving Alzheimer's disease pathology? |
| Q37221657 | Dietary management of long-chain 3-hydroxyacyl-CoA dehydrogenase deficiency (LCHADD). A case report and survey |
| Q37221642 | Docosahexaenoic acid and retinal function in children with long-chain 3-hydroxyacyl-CoA dehydrogenase deficiency. |
| Q33952072 | Effects of protein-energy malnutrition and human immunodeficiency virus-1 infection on essential fatty acid metabolism in children |
| Q43745212 | High levels of docosahexaenoic acid (22:6n-3)-containing phospholipids in high-frequency contraction muscles of hummingbirds and rattlesnakes |
| Q28802472 | Lipidomics for studying metabolism |
| Q37976699 | Long-chain polyunsaturated fatty acids in inborn errors of metabolism |
| Q33680413 | Mechanisms of resistance to pathogenesis in muscular dystrophies |
| Q43763486 | Polyunsaturated fatty acid deficiency during dietary treatment of very long-chain acyl-CoA dehydrogenase deficiency. Rescue with soybean oil. |
| Q34322451 | Polyunsaturated fatty acid synthesis and release by brain-derived cells in vitro. |
| Q35862864 | Polyunsaturated fatty acids: biochemical, nutritional and epigenetic properties |
| Q35049659 | Recent advances in the study of fatty acid desaturases from animals and lower eukaryotes |
| Q33843176 | Secondary carnitine deficiency and impaired docosahexaenoic (22:6n-3) acid synthesis: a common denominator in the pathophysiology of diseases of oxidative phosphorylation and beta-oxidation |
| Q50995439 | Serum n-3 Tetracosapentaenoic Acid and Tetracosahexaenoic Acid Increase Following Higher Dietary α-Linolenic Acid but not Docosahexaenoic Acid. |
| Q45238559 | Short-term carnitine supplementation does not augment LCPomega3 status of vegans and lacto-ovo-vegetarians |
| Q35997962 | The fatty acid desaturase 2 (FADS2) gene product catalyzes Δ4 desaturation to yield n-3 docosahexaenoic acid and n-6 docosapentaenoic acid in human cells |
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