| scholarly article | Q13442814 |
| P819 | ADS bibcode | 2014PLoSO...997222B |
| P356 | DOI | 10.1371/JOURNAL.PONE.0097222 |
| P932 | PMC publication ID | 4019519 |
| P698 | PubMed publication ID | 24823368 |
| P5875 | ResearchGate publication ID | 262303440 |
| P50 | author | Guy Lenaers | Q56488643 |
| Cécile Delettre | Q85171096 | ||
| P2093 | author name string | Christian Hamel | |
| Yukio Tanizawa | |||
| Nesrine Benkafadar | |||
| Jolanta Jagodzinska | |||
| Delphine Bonnet Wersinger | |||
| P2860 | cites work | Wolfram syndrome and WFS1 gene | Q37782389 |
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| WFS1-deficiency increases endoplasmic reticulum stress, impairs cell cycle progression and triggers the apoptotic pathway specifically in pancreatic beta-cells | Q28508342 | ||
| Dynamic interaction of BiP and ER stress transducers in the unfolded-protein response | Q29547299 | ||
| Autophagy is activated for cell survival after endoplasmic reticulum stress | Q29614485 | ||
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| Autocrine tumor necrosis factor alpha links endoplasmic reticulum stress to the membrane death receptor pathway through IRE1alpha-mediated NF-kappaB activation and down-regulation of TRAF2 expression | Q34563098 | ||
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| Mouse phenome research: implications of genetic background | Q36425309 | ||
| Sep15, a thioredoxin-like selenoprotein, is involved in the unfolded protein response and differentially regulated by adaptive and acute ER stresses | Q37424231 | ||
| Expression of the diabetes risk gene wolframin (WFS1) in the human retina | Q37458535 | ||
| Four cases of Wolfram syndrome: ophthalmologic findings and complications | Q72640961 | ||
| MRI of Wolfram syndrome (DIDMOAD) | Q73157683 | ||
| Optic atrophy in Wolfram (DIDMOAD) syndrome | Q74427625 | ||
| Simple and efficient: validation of a cotton wick electrode for animal electroretinography | Q82317378 | ||
| Wolfram syndrome 1 gene (WFS1) product localizes to secretory granules and determines granule acidification in pancreatic beta-cells | Q83103488 | ||
| Neurologic features and genotype-phenotype correlation in Wolfram syndrome | Q83739551 | ||
| P275 | copyright license | Creative Commons Attribution 4.0 International | Q20007257 |
| P6216 | copyright status | copyrighted | Q50423863 |
| P433 | issue | 5 | |
| P407 | language of work or name | English | Q1860 |
| P304 | page(s) | e97222 | |
| P577 | publication date | 2014-05-13 | |
| P1433 | published in | PLOS One | Q564954 |
| P1476 | title | Impairment of visual function and retinal ER stress activation in Wfs1-deficient mice | |
| P478 | volume | 9 |
| Q26765956 | Adaptive preconditioning in neurological diseases – therapeutic insights from proteostatic perturbations |
| Q91651809 | Developmental hypomyelination in Wolfram syndrome: new insights from neuroimaging and gene expression analyses |
| Q47847250 | Knockdown of wfs1, a fly homolog of Wolfram syndrome 1, in the nervous system increases susceptibility to age- and stress-induced neuronal dysfunction and degeneration in Drosophila. |
| Q36049592 | Layer 2/3 pyramidal cells in the medial prefrontal cortex moderate stress induced depressive behaviors |
| Q30382075 | Loss of function of Ywhah in mice induces deafness and cochlear outer hair cells' degeneration. |
| Q47713821 | Mutations in DNM1L, as in OPA1, result indominant optic atrophy despite opposite effectson mitochondrial fusion and fission |
| Q37008516 | Prolactin protects retinal pigment epithelium by inhibiting sirtuin 2-dependent cell death |
| Q38635262 | Retinal thickness as a marker of disease progression in longitudinal observation of patients with Wolfram syndrome |
| Q27342152 | Role of Mitochondrial Dynamics in Neuronal Development: Mechanism for Wolfram Syndrome |
| Q41581688 | Wfs1- deficient rats develop primary symptoms of Wolfram syndrome: insulin-dependent diabetes, optic nerve atrophy and medullary degeneration |
| Q52671146 | Wolfram syndrome: MAMs' connection? |
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