scholarly article | Q13442814 |
P50 | author | Eveline Baumgart-Vogt | Q47158610 |
P2093 | author name string | Barbara Ahlemeyer | |
Magdalena Gottwald | |||
P2860 | cites work | Expression of PEX11beta mediates peroxisome proliferation in the absence of extracellular stimuli | Q22004167 |
Cystic Fibrosis Heterozygote Resistance to Cholera Toxin in the Cystic Fibrosis Mouse Model | Q22299398 | ||
Phenotype-genotype relationships in peroxisome biogenesis disorders of PEX1-defective complementation group 1 are defined by Pex1p-Pex6p interaction | Q24291411 | ||
Fis1, DLP1, and Pex11p coordinately regulate peroxisome morphogenesis | Q24301650 | ||
PEX11alpha is required for peroxisome proliferation in response to 4-phenylbutyrate but is dispensable for peroxisome proliferator-activated receptor alpha-mediated peroxisome proliferation | Q24537850 | ||
A PEX6-defective peroxisomal biogenesis disorder with severe phenotype in an infant, versus mild phenotype resembling Usher syndrome in the affected parents | Q24613849 | ||
Human PEX1 cloned by functional complementation on a CHO cell mutant is responsible for peroxisome-deficient Zellweger syndrome of complementation group I | Q24645143 | ||
Disruption of a PEX1-PEX6 interaction is the most common cause of the neurologic disorders Zellweger syndrome, neonatal adrenoleukodystrophy, and infantile Refsum disease | Q24681184 | ||
A rapid and sensitive method for the quantitation of microgram quantities of protein utilizing the principle of protein-dye binding | Q25938984 | ||
A new mathematical model for relative quantification in real-time RT-PCR | Q27860781 | ||
Pex11p plays a primary role in medium-chain fatty acid oxidation, a process that affects peroxisome number and size in Saccharomyces cerevisiae | Q27934293 | ||
Peroxisome biogenesis disorders | Q28207254 | ||
Adrenoleukodystrophy protein-deficient mice represent abnormality of very long chain fatty acid metabolism | Q28236420 | ||
The PEX Gene Screen: molecular diagnosis of peroxisome biogenesis disorders in the Zellweger syndrome spectrum | Q28293113 | ||
Mitochondrial alterations caused by defective peroxisomal biogenesis in a mouse model for Zellweger syndrome (PEX5 knockout mouse) | Q28360949 | ||
An immunocytochemical analysis of the ontogeny of the microtubule-associated proteins MAP-2 and Tau in the nervous system of the rat. | Q42040001 | ||
Influence of heterozygosity for parkin mutation on onset age in familial Parkinson disease: the GenePD study | Q42688205 | ||
Temperature sensitive acyl-CoA oxidase import in group A peroxisome biogenesis disorders | Q43075476 | ||
Retinoic acid reduces apoptosis and oxidative stress by preservation of SOD protein level | Q43615227 | ||
Optimized protocols for the simultaneous preparation of primary neuronal cultures of the neocortex, hippocampus and cerebellum from individual newborn (P0.5) C57Bl/6J mice | Q46638273 | ||
Adreno-leukodystrophy: oxidative stress of mice and men. | Q46829099 | ||
The sequential appearance of low- and high-molecular-weight forms of MAP2 in the developing cerebellum. | Q47176242 | ||
Axonal loss and neuroinflammation caused by peroxisome-deficient oligodendrocytes | Q48099707 | ||
The neuronal migration defect in mice with Zellweger syndrome (Pex5 knockout) is not caused by the inactivity of peroxisomal beta-oxidation | Q48636627 | ||
Late onset neurological phenotype of the X-ALD gene inactivation in mice: a mouse model for adrenomyeloneuropathy | Q48671536 | ||
Lack of adrenoleukodystrophy protein enhances oligodendrocyte disturbance and microglia activation in mice with combined Abcd1/Mag deficiency | Q50276649 | ||
Developmental regulation of microtubule-associated protein 2 expression in regions of mouse brain. | Q52061599 | ||
Developmental regulation of MAP2 variants during neuronal differentiation in vitro. | Q52204718 | ||
Differential expression of peroxisomal matrix and membrane proteins during postnatal development of mouse brain. | Q53531489 | ||
Clinical Spectrum of Homozygous and Heterozygous PINK1 Mutations in a Large German Family With Parkinson Disease | Q60332322 | ||
Motor system abnormalities in heterozygous relatives of a D90A homozygous CuZn-SOD ALS patient of finnish extraction | Q73128582 | ||
Bile acid treatment alters hepatic disease and bile acid transport in peroxisome-deficient PEX2 Zellweger mice | Q80060299 | ||
Pex11pbeta-mediated growth and division of mammalian peroxisomes follows a maturation pathway | Q84582760 | ||
Absence of peroxisomes in mouse hepatocytes causes mitochondrial and ER abnormalities | Q28508098 | ||
Pex13 inactivation in the mouse disrupts peroxisome biogenesis and leads to a Zellweger syndrome phenotype | Q28511106 | ||
Differential expression of rat brain synaptic proteins in development and aging | Q28572694 | ||
A mouse model for Zellweger syndrome | Q28590797 | ||
Abnormal cerebellar histogenesis in PEX2 Zellweger mice reflects multiple neuronal defects induced by peroxisome deficiency | Q28591457 | ||
Impaired neuronal migration and endochondral ossification in Pex7 knockout mice: a model for rhizomelic chondrodysplasia punctata | Q28591869 | ||
Detection of peroxisomal proteins and their mRNAs in serial sections of fetal and newborn mouse organs | Q28593347 | ||
PEX11β induces peroxisomal gene expression and alters peroxisome number during early Xenopus laevis development | Q31007869 | ||
Oxidative metabolism, apoptosis and perinatal brain injury. | Q31904904 | ||
Targeted inactivation of the X-linked adrenoleukodystrophy gene in mice | Q32159154 | ||
Visualizing the distribution of synapses from individual neurons in the mouse brain | Q33633904 | ||
Heterozygous carriers of a Parkin or PINK1 mutation share a common functional endophenotype | Q33652645 | ||
Human red blood cell polymorphisms and malaria | Q33997329 | ||
PEX11 beta deficiency is lethal and impairs neuronal migration but does not abrogate peroxisome function | Q34280995 | ||
PEX13 deficiency in mouse brain as a model of Zellweger syndrome: abnormal cerebellum formation, reactive gliosis and oxidative stress | Q34458791 | ||
X-linked adrenoleukodystrophy: clinical, biochemical and pathogenetic aspects. | Q34562917 | ||
The evolution of gene duplicates | Q34586458 | ||
Cellular and molecular aspects of Zellweger syndrome and other peroxisome biogenesis disorders | Q34777961 | ||
Role of ALDP (ABCD1) and mitochondria in X-linked adrenoleukodystrophy | Q34811374 | ||
Reactive oxygen species and peroxisomes: struggling for balance | Q34982318 | ||
Mitochondrial mechanisms of cell death and neuroprotection in pediatric ischemic and traumatic brain injury | Q34988707 | ||
A review of morphological techniques for detection of peroxisomal (and mitochondrial) proteins and their corresponding mRNAs during ontogenesis in mice: application to the PEX5-knockout mouse with Zellweger syndrome | Q35125097 | ||
Is there a phenotype/genotype correlation in peroxisome biogenesis disorders (PBDs)? | Q35624394 | ||
Peroxisome biogenesis disorders: the role of peroxisomes and metabolic dysfunction in developing brain | Q36114812 | ||
Targeted deletion of the PEX2 peroxisome assembly gene in mice provides a model for Zellweger syndrome, a human neuronal migration disorder | Q36274978 | ||
A mouse model for X-linked adrenoleukodystrophy | Q36566796 | ||
Survival advantage of the hemochromatosis C282Y mutation | Q37056091 | ||
Gene expression phenotype in heterozygous carriers of ataxia telangiectasia | Q37202992 | ||
Getting a camel through the eye of a needle: the import of folded proteins by peroxisomes | Q37690350 | ||
Peroxisomes as dynamic organelles: peroxisomal matrix protein import | Q37772547 | ||
Superoxide production in rat hippocampal neurons: selective imaging with hydroethidine | Q39428776 | ||
PMP70 knock-down generates oxidative stress and pro-inflammatory cytokine production in C6 glial cells | Q39920011 | ||
Evidence for increased oxidative stress in peroxisomal D-bifunctional protein deficiency | Q40639063 | ||
Peroxisomal disorders: genotype, phenotype, major neuropathologic lesions, and pathogenesis. | Q41698061 | ||
Disorders of peroxisome biogenesis due to mutations in PEX1: phenotypes and PEX1 protein levels | Q42036408 | ||
P433 | issue | 1 | |
P407 | language of work or name | English | Q1860 |
P304 | page(s) | 125-140 | |
P577 | publication date | 2011-10-04 | |
P1433 | published in | Disease Models & Mechanisms | Q1524006 |
P1476 | title | Deletion of a single allele of the Pex11β gene is sufficient to cause oxidative stress, delayed differentiation and neuronal death in mouse brain | |
P478 | volume | 5 |
Q34047964 | A New Immunomodulatory Role for Peroxisomes in Macrophages Activated by the TLR4 Ligand Lipopolysaccharide |
Q35549268 | Compromised peroxisomes in idiopathic pulmonary fibrosis, a vicious cycle inducing a higher fibrotic response via TGF-β signaling. |
Q30840454 | Coupling organelle inheritance with mitosis to balance growth and differentiation |
Q35110393 | Gene expression patterns in the hippocampus during the development and aging of Glud1 (Glutamate Dehydrogenase 1) transgenic and wild type mice |
Q35601225 | Genome-Wide Localization Study of Yeast Pex11 Identifies Peroxisome-Mitochondria Interactions through the ERMES Complex. |
Q64092469 | High-resolution atmospheric-pressure MALDI mass spectrometry imaging workflow for lipidomic analysis of late fetal mouse lungs |
Q90145796 | Impaired Peroxisomal Fitness in Obese Mice, a Vicious Cycle Exacerbating Adipocyte Dysfunction via Oxidative Stress |
Q57071055 | Infection-Induced Peroxisome Biogenesis Is a Metabolic Strategy for Herpesvirus Replication |
Q39062984 | Knockdown of Pex11β reveals its pivotal role in regulating peroxisomal genes, numbers, and ROS levels in Xenopus laevis A6 cells |
Q33778861 | MicroRNAs upregulated during HIV infection target peroxisome biogenesis factors: Implications for virus biology, disease mechanisms and neuropathology |
Q38956337 | Microporation is an efficient method for siRNA-induced knockdown of PEX5 in HepG2 cells: evaluation of the transfection efficiency, the PEX5 mRNA and protein levels and induction of peroxisomal deficiency |
Q51146919 | Peroxisomal membrane channel Pxmp2 in the mammary fat pad is essential for stromal lipid homeostasis and for development of mammary gland epithelium in mice. |
Q92528793 | Peroxisomes in Immune Response and Inflammation |
Q34095390 | Potential targets for protecting against hippocampal cell apoptosis after transient cerebral ischemia-reperfusion injury in aged rats |
Q90008081 | The HIV-1 Accessory Protein Vpu Downregulates Peroxisome Biogenesis |
Q27302267 | The Pex1-G844D mouse: a model for mild human Zellweger spectrum disorder |
Q36632900 | The gene expression profiles of induced pluripotent stem cells from individuals with childhood cerebral adrenoleukodystrophy are consistent with proposed mechanisms of pathogenesis |
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