Myofiber integrity depends on desmin network targeting to Z-disks and costameres via distinct plectin isoforms.

scientific article published on May 2008

Myofiber integrity depends on desmin network targeting to Z-disks and costameres via distinct plectin isoforms. is …
instance of (P31):
scholarly articleQ13442814

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P356DOI10.1083/JCB.200711058
P932PMC publication ID2386106
P698PubMed publication ID18490514
P5875ResearchGate publication ID5358951

P50authorPeter FuchsQ59683312
Patryk KoniecznyQ63443233
Siegfried ReipertQ40741582
Wolfram S. KunzQ42436495
P2093author name stringGerhard Wiche
Irmgard Fischer
Denise Paulin
Anikó Zeöld
Rolf Schröder
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Human synemin gene generates splice variants encoding two distinct intermediate filament proteinsQ24291974
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Plectin 5'-transcript diversity: short alternative sequences determine stability of gene products, initiation of translation and subcellular localization of isoformsQ44618199
Impaired mitochondrial oxidative phosphorylation in skeletal muscle of the dystrophin-deficient mdx mouseQ47878704
Unusual 5' transcript complexity of plectin isoforms: novel tissue-specific exons modulate actin binding activityQ47912980
Disorganization of the desmin cytoskeleton and mitochondrial dysfunction in plectin-related epidermolysis bullosa simplex with muscular dystrophyQ48575004
Cardiovascular lesions and skeletal myopathy in mice lacking desmin.Q51114742
Null mutation in the desmin gene gives rise to a cardiomyopathy.Q52526996
Plectin defects in epidermolysis bullosa simplex with muscular dystrophy.Q52573505
Conditional targeting of plectin in prenatal and adult mouse stratified epithelia causes keratinocyte fragility and lesional epidermal barrier defectsQ58321837
Biochemical and immunocytochemical analysis of the intermediate filament cytoskeleton in human hepatocellular carcinomas and in hepatic neoplastic nodules of miceQ58439440
Quantitative analysis of relative protein contents by Western blotting: comparison of three members of the dystrophin-glycoprotein complex in slow and fast rat skeletal muscleQ73569553
Synemin may function to directly link muscle cell intermediate filaments to both myofibrillar Z-lines and costameresQ74064872
A muscle-specific insulin receptor knockout exhibits features of the metabolic syndrome of NIDDM without altering glucose toleranceQ77652485
A dysfunctional desmin mutation in a patient with severe generalized myopathyQ24313070
Missense mutations in desmin associated with familial cardiac and skeletal myopathyQ24322607
Defective expression of plectin/HD1 in epidermolysis bullosa simplex with muscular dystrophyQ24562137
A compound heterozygous one amino-acid insertion/nonsense mutation in the plectin gene causes epidermolysis bullosa simplex with plectin deficiencyQ24685930
Plectin is a linker of intermediate filaments to Z-discs in skeletal muscle fibersQ28137741
Adhesion-dependent tyrosine phosphorylation of (beta)-dystroglycan regulates its interaction with utrophinQ28142159
Association of mitochondria with plectin and desmin intermediate filaments in striated muscleQ28145982
Costameres: the Achilles' heel of Herculean muscleQ28205938
Progress in epidermolysis bullosa: the phenotypic spectrum of plectin mutationsQ28243587
Targeted inactivation of plectin reveals essential function in maintaining the integrity of skin, muscle, and heart cytoarchitectureQ28255914
The roles of intracellular protein-degradation pathways in neurodegenerationQ28269322
Role of plectin in cytoskeleton organization and dynamicsQ28279366
Cloning and characterization of cytokeratins 8 and 19 in adult rat striated muscle. Interaction with the dystrophin glycoprotein complexQ28507349
Syncoilin, a novel member of the intermediate filament superfamily that interacts with alpha-dystrobrevin in skeletal muscleQ28511511
Targeted ablation of plectin isoform 1 uncovers role of cytolinker proteins in leukocyte recruitmentQ30476548
Plectin-controlled keratin cytoarchitecture affects MAP kinases involved in cellular stress response and migrationQ30480460
Creatine kinase transcript accumulation: effect of nerve during muscle developmentQ30741467
Sarcolemmal organization in skeletal muscle lacking desmin: evidence for cytokeratins associated with the membrane skeleton at costameresQ33893625
Remodeling muscles with calcineurinQ33936668
Desmin myopathyQ34289931
Disruption of muscle architecture and myocardial degeneration in mice lacking desminQ34395897
The cytoskeleton in neurodegenerative diseasesQ34446779
Costameres: repeating structures at the sarcolemma of skeletal muscle.Q34977825
Animal models for muscular dystrophy show different patterns of sarcolemmal disruption.Q36273863
Desmin cytoskeleton linked to muscle mitochondrial distribution and respiratory function.Q36293799
Muscle intermediate filaments and their links to membranes and membranous organellesQ36825339
Plectin transcript diversity: identification and tissue distribution of variants with distinct first coding exons and rodless isoformsQ38345907
Plectin 1f scaffolding at the sarcolemma of dystrophic (mdx) muscle fibers through multiple interactions with beta-dystroglycan.Q39734956
Plectin-isoform-specific rescue of hemidesmosomal defects in plectin (-/-) keratinocytesQ40609141
Dystrophin-associated proteins are greatly reduced in skeletal muscle from mdx miceQ42052137
P4510describes a project that usesImageJQ1659584
P433issue4
P407language of work or nameEnglishQ1860
P304page(s)667-681
P577publication date2008-05-01
P1433published inJournal of Cell BiologyQ1524550
P1476titleMyofiber integrity depends on desmin network targeting to Z-disks and costameres via distinct plectin isoforms
P478volume181

Reverse relations

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