scholarly article | Q13442814 |
P50 | author | Kristina B. Kruse | Q62635606 |
Ardythe A. McCracken | Q63183185 | ||
P2093 | author name string | J L Brown | |
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Hepatoma secretory proteins migrate from rough endoplasmic reticulum to Golgi at characteristic rates | Q59066067 | ||
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Carbohydrate composition of normal and variant human alpha 1-protease inhibitors | Q66920331 | ||
Secretion of C-reactive protein becomes more efficient during the course of the acute phase response | Q70073719 | ||
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Structural and functional characterization of the abnormal Z alpha 1-antitrypsin isolated from human liver | Q70228345 | ||
Alpha-1-antitrypsin (AAT) and its stimulation in the liver of PiMZ phenotype individuals. A "recruitment-secretory block" ("R-SB") phenomenon | Q70228960 | ||
P433 | issue | 4 | |
P407 | language of work or name | English | Q1860 |
P304 | page(s) | 1406-1414 | |
P577 | publication date | 1989-04-01 | |
P1433 | published in | Molecular and Cellular Biology | Q3319478 |
P1476 | title | Molecular basis for defective secretion of the Z variant of human alpha-1-proteinase inhibitor: secretion of variants having altered potential for salt bridge formation between amino acids 290 and 342. | |
P478 | volume | 9 |
Q44402969 | A class of mutant CHO cells resistant to cholera toxin rapidly degrades the catalytic polypeptide of cholera toxin and exhibits increased endoplasmic reticulum-associated degradation. |
Q35759026 | A lag in intracellular degradation of mutant alpha 1-antitrypsin correlates with the liver disease phenotype in homozygous PiZZ alpha 1-antitrypsin deficiency |
Q36278201 | A study of the effects of altering the sites for N-glycosylation in alpha-1-proteinase inhibitor variants M and S. |
Q27932696 | ADD66, a gene involved in the endoplasmic reticulum-associated degradation of alpha-1-antitrypsin-Z in yeast, facilitates proteasome activity and assembly. |
Q38784755 | Alpha-1-antitrypsin deficiency: accumulation or degradation of mutant variants within the hepatic endoplasmic reticulum |
Q41505232 | Approaches to maximizing stable expression of alpha 1-antitrypsin in transformed CHO cells |
Q41236581 | BiP expression is not increased by the accumulation of PiZ alpha 1-antitrypsin in the endoplasmic reticulum |
Q91386795 | Calcium signalling in mammalian cell lines expressing wild type and mutant human α1-Antitrypsin |
Q41718232 | Comparative properties of human alpha-1-proteinase inhibitor glycosylation variants |
Q41835060 | Conformational instability of the cholera toxin A1 polypeptide |
Q34408182 | Increased PiZ gene frequency for alpha 1 antitrypsin in patients with genetic haemochromatosis |
Q37694671 | Inhibition of cellular protein secretion by poliovirus proteins 2B and 3A |
Q34186098 | Inhibition of endoplasmic reticulum-associated degradation in CHO cells resistant to cholera toxin, Pseudomonas aeruginosa exotoxin A, and ricin |
Q40015288 | Inhibition of endoplasmic reticulum-to-Golgi traffic by poliovirus protein 3A: genetic and ultrastructural analysis |
Q37383352 | Inhibition of intracellular degradation increases secretion of a mutant form of alpha1-antitrypsin associated with profound deficiency |
Q41561414 | Intracellular retention and degradation of human mutant variant of a alpha 1-antitrypsin in stably transfected Chinese hamster ovary cell lines |
Q26851374 | Is there a therapeutic role for selenium in alpha-1 antitrypsin deficiency? |
Q36712966 | Molecular basis of alpha 1-antitrypsin deficiency and emphysema associated with the alpha 1-antitrypsin Mmineral springs allele |
Q28572278 | Negative regulatory activity of a prostaglandin F2 alpha receptor associated protein (FPRP) |
Q49171266 | Protein secretion in plant cells can occur via a default pathway |
Q41509050 | Review: alpha 1-antitrypsin deficiency associated liver disease |
Q24313226 | Role of the lectin VIP36 in post-ER quality control of human alpha1-antitrypsin |
Q44326218 | Secretion of pigment epithelium-derived factor. Mutagenic study |
Q34438486 | Selective protein degradation in the yeast exocytic pathway |
Q34579205 | Synthesis of stress proteins is increased in individuals with homozygous PiZZ alpha 1-antitrypsin deficiency and liver disease |
Q53547782 | Tauroursodeoxycholic acid inhibits apoptosis induced by Z alpha-1 antitrypsin via inhibition of Bad. |
Q41727618 | The effect of amino acid substitutions at position 342 on the secretion of human alpha 1-antitrypsin from Xenopus oocytes |
Q37204565 | The molecular genetics of ?1 antitrypsin deficiency |
Q37623472 | Vesicular transport is not required for the cytoplasmic pool of cholera toxin to interact with the stimulatory alpha subunit of the heterotrimeric g protein. |
Q52226310 | Vitamin E and liver damage in MZ heterozygous infants with alpha 1-antitrypsin deficiency. |
Q42967230 | Yeast mutants deficient in ER-associated degradation of the Z variant of alpha-1-protease inhibitor. |
Q34962759 | Z α-1 antitrypsin deficiency and the endoplasmic reticulum stress response |
Q36816779 | α 1 ‐antitrypsin deficiency and liver disease |