Defining peripheral nervous system dysfunction in the SOD-1G93A transgenic rat model of amyotrophic lateral sclerosis

scientific article published on July 2014

Defining peripheral nervous system dysfunction in the SOD-1G93A transgenic rat model of amyotrophic lateral sclerosis is …
instance of (P31):
scholarly articleQ13442814

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P356DOI10.1097/NEN.0000000000000081
P698PubMed publication ID24918640

P50authorLinda ChaabaneQ39188638
Caterina BendottiQ39188656
Nilo RivaQ39188671
Angelo QuattriniQ56451650
Teuta DomiQ57005746
Giancarlo ComiQ66759549
P2093author name stringFrancesca Bianchi
Paola Podini
Ubaldo Del Carro
Federica Cerri
Massimo Corbo
Giorgia Dina
Daniela Ungaro
Marco Peviani
Giorgia Spano
P2860cites workProgressive changes in microglia and macrophages in spinal cord and peripheral nerve in the transgenic rat model of amyotrophic lateral sclerosisQ21245232
Role of axonal transport in neurodegenerative diseasesQ28284096
Deficits in axonal transport precede ALS symptoms in vivoQ30497554
Inflammation in ALS and SMA: sorting out the good from the evilQ33664711
Axonal mitochondrial clusters containing mutant SOD1 in transgenic models of ALS.Q33742751
ALS-causing SOD1 mutants generate vascular changes prior to motor neuron degenerationQ33954016
The epidemiology of motor neuron diseases: a review of recent studiesQ34417934
The brachial plexus branches to the pectoral muscles in adult rats: morphological aspects and morphometric normative dataQ34453882
Efficacy of minocycline in patients with amyotrophic lateral sclerosis: a phase III randomised trial.Q34584573
Axon pathology in neurological disease: a neglected therapeutic targetQ34831556
Early changes of neuromuscular transmission in the SOD1(G93A) mice model of ALS start long before motor symptoms onsetQ34989403
Endogenous regulatory T lymphocytes ameliorate amyotrophic lateral sclerosis in mice and correlate with disease progression in patients with amyotrophic lateral sclerosisQ34992177
The Role of immune and inflammatory mechanisms in ALS.Q35238394
Detection of preclinical motor neurone loss in SOD1 mutation carriers using motor unit number estimationQ35468233
Disruption of Mtmr2 produces CMT4B1-like neuropathy with myelin outfolding and impaired spermatogenesisQ36322774
Axonal degeneration in motor neuron diseaseQ36970066
Efficacy of thalidomide for the treatment of amyotrophic lateral sclerosis: a phase II open label clinical trialQ37288200
Neuromuscular junction destruction during amyotrophic lateral sclerosis: insights from transgenic modelsQ37455509
Activation of innate and humoral immunity in the peripheral nervous system of ALS transgenic miceQ37469800
Chapter 6: Methods and protocols in peripheral nerve regeneration experimental research: part III-electrophysiological evaluationQ37580159
Microglia in ALS: the good, the bad, and the restingQ37592030
Review: neuromuscular synaptic vulnerability in motor neurone disease: amyotrophic lateral sclerosis and spinal muscular atrophyQ37702459
The "dying-back" phenomenon of motor neurons in ALS.Q37807909
Evidence-based drug treatment in amyotrophic lateral sclerosis and upcoming clinical trialsQ37823334
Amyotrophic lateral sclerosis: a neurovascular disease.Q37883632
Inflammation and neurovascular changes in amyotrophic lateral sclerosis.Q38056551
Concepts for regulation of axon integrity by enwrapping gliaQ38175969
The onset of amyotrophic lateral sclerosisQ40089644
Sodium valproate exerts neuroprotective effects in vivo through CREB-binding protein-dependent mechanisms but does not improve survival in an amyotrophic lateral sclerosis mouse modelQ40128564
Disease progression of human SOD1 (G93A) transgenic ALS model ratsQ40366167
Familial amyotrophic lateral sclerosis with a mutation in exon 4 of the Cu/Zn superoxide dismutase gene: pathological and immunocytochemical changesQ41187994
Impaired blood-brain and blood-spinal cord barriers in mutant SOD1-linked ALS rat.Q42459722
Additive neuroprotective effects of creatine and cyclooxygenase 2 inhibitors in a transgenic mouse model of amyotrophic lateral sclerosisQ44726519
Vasculitis-like neuropathy in amyotrophic lateral sclerosis unresponsive to treatmentQ44757477
Implications of ALS focality: rostral-caudal distribution of lower motor neuron loss postmortemQ44929159
Thalidomide and lenalidomide extend survival in a transgenic mouse model of amyotrophic lateral sclerosis.Q46970968
Degeneration of respiratory motor neurons in the SOD1 G93A transgenic rat model of ALS.Q47751488
Relationship of microglial and astrocytic activation to disease onset and progression in a transgenic model of familial ALS.Q47951637
Electrophysiological analysis of a murine model of motoneuron disease.Q50544366
In vivo assessment of peripheral nerve regeneration by diffusion tensor imaging.Q53270755
A central role for the ERK-signaling pathway in controlling Schwann cell plasticity and peripheral nerve regeneration in vivo.Q54527244
Amyotrophic lateral sclerosisQ55877676
Inhibition of p38 mitogen activated protein kinase activation and mutant SOD1G93A-induced motor neuron deathQ57244949
Mutant superoxide dismutase disrupts cytoplasmic dynein in motor neuronsQ57450096
Analysis of neuromuscular junctions and effects of anabolic steroid administration in the SOD1G93A mouse model of ALSQ58852435
Chronic motor axonal neuropathyQ58880724
Motor nerve biopsy: Clinical usefulness and histopathological criteriaQ58880727
P433issue7
P407language of work or nameEnglishQ1860
P921main subjectamyotrophic lateral sclerosisQ206901
P304page(s)658-670
P577publication date2014-07-01
P1433published inJournal of Neuropathology & Experimental NeurologyQ15716771
P1476titleDefining peripheral nervous system dysfunction in the SOD-1G93A transgenic rat model of amyotrophic lateral sclerosis
P478volume73

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cites work (P2860)
Q41380885Neurodevelopmental Malformations of the Cerebellar Vermis in Genetically Engineered Rats
Q48278519Peripheral nerve diffusion tensor imaging as a measure of disease progression in ALS.
Q53185951Quantifying disease progression in amyotrophic lateral sclerosis using peripheral nerve sonography.
Q98184087Retromer stabilization results in neuroprotection in a model of Amyotrophic Lateral Sclerosis
Q91781195The Peripheral Nervous System in Amyotrophic Lateral Sclerosis: Opportunities for Translational Research

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