Leukocyte Adhesion Deficiency Type II is a generalized defect of de novo GDP-fucose biosynthesis. Endothelial cell fucosylation is not required for neutrophil rolling on human nonlymphoid endothelium

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Leukocyte Adhesion Deficiency Type II is a generalized defect of de novo GDP-fucose biosynthesis. Endothelial cell fucosylation is not required for neutrophil rolling on human nonlymphoid endothelium is …
instance of (P31):
scholarly articleQ13442814

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P356DOI10.1172/JCI905
P932PMC publication ID508833
P698PubMed publication ID9616215

P2093author name stringH D Ochs
J M Harlan
R K Winn
A Karsan
R Gershoni-Baruch
A Etzioni
B R Schwartz
C J Cornejo
N Lannir
W Way
P2860cites workMolecular cloning of a cDNA encoding a novel human leukocyte alpha-1,3-fucosyltransferase capable of synthesizing the sialyl Lewis x determinantQ24316888
Synthesis of GDP-L-fucose by the human FX proteinQ24319017
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Brief report: recurrent severe infections caused by a novel leukocyte adhesion deficiencyQ29028780
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E-selectin supports neutrophil rolling in vitro under conditions of flowQ33909692
An epimerase-reductase in L-fucose synthesis.Q34174934
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Adhesion through L-selectin requires a threshold hydrodynamic shearQ34369202
Neutrophils use both shared and distinct mechanisms to adhere to selectins under static and flow conditionsQ35764552
Neutrophil adhesion in leukocyte adhesion deficiency syndrome type 2Q35768903
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Monocyte adhesion to activated aortic endothelium: role of L-selectin and heparan sulfate proteoglycansQ36254610
Neutrophil-neutrophil interactions under hydrodynamic shear stress involve L-selectin and PSGL-1. A mechanism that amplifies initial leukocyte accumulation of P-selectin in vitroQ37359036
Selectin ligands: will the real ones please stand up?Q37362400
High affinity binding of the leucocyte adhesion molecule L-selectin to 3'-sulphated-Le(a) and -Le(x) oligosaccharides and the predominance of sulphate in this interaction demonstrated by binding studies with a series of lipid-linked oligosaccharidesQ38325258
The neutrophil selectin LECAM-1 presents carbohydrate ligands to the vascular selectins ELAM-1 and GMP-140.Q38333447
Glycoproteins: what are the sugar chains for?Q38344212
Isolation and properties of porcine thyroid fucokinaseQ39280065
The role of N-glycans in the secretory pathway.Q40517153
The major glycosylation pathways of mammalian membranes. A summaryQ40735014
In vivo behavior of neutrophils from two patients with distinct inherited leukocyte adhesion deficiency syndromesQ41021858
Selectins and their ligands: current concepts and controversies.Q41192497
L-selectin can mediate leukocyte rolling in untreated mesenteric venules in vivo independent of E- or P-selectinQ41532547
Calcium-Dependent Heparin-Like Ligands For L-Selectin in Nonlymphoid Endothelial CellsQ41541458
L-selectin mediates neutrophil rolling in inflamed venules through sialyl LewisX-dependent and -independent recognition pathways.Q41546428
Differentiation-dependent expression of sialyl stage-specific embryonic antigen-1 and I-antigens on human lymphoid cells and its implications for carbohydrate-mediated adhesion to vascular endotheliumQ41586430
Rambam-Hasharon syndrome of psychomotor retardation, short stature, defective neutrophil motility, and Bombay phenotypeQ41930148
Human myeloid alpha 3-fucosyltransferase is involved in the expression of the sialyl-Lewis(x) determinant, a ligand for E- and P-selectinQ42804797
Two Chinese hamster ovary glycosylation mutants affected in the conversion of GDP-mannose to GDP-fucoseQ42812768
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Sulphation requirement for GlyCAM-1, an endothelial ligand for L-selectinQ44187789
In vivo neutrophil and lymphocyte function studies in a patient with leukocyte adhesion deficiency type II.Q44869616
The effect of pristane on ascites tumor formation and monoclonal antibody productionQ45162690
Ulex europaeus I lectin as a marker for vascular endothelium in human tissues.Q55062376
Pathway of the Synthesis of Fucose from Glucose in Klebsiella aerogenesQ58941107
The α(1,3)Fucosyltransferase Fuc-TVII Controls Leukocyte Trafficking through an Essential Role in L-, E-, and P-selectin Ligand BiosynthesisQ60719538
A Comparison of the Binding Specificities of Lectins from Ulex Europaeus and Lotus TetragonolobusQ67063807
Function and evolutionary conservation of distinct epitopes on the leukocyte adhesion molecule-1 (TQ-1, Leu-8) that regulate leukocyte migrationQ67695886
Investigation of the metabolism of L-fucose in aortic tissue and cultured arterial wall cellsQ68078010
Effect of flow on polymorphonuclear leukocyte/endothelial cell adhesionQ69418028
A routine method for the establishment of permanent growing lymphoblastoid cell linesQ70146139
Definition of a common leukocyte cell-surface antigen (Lp95-150) associated with diverse cell-mediated immune functionsQ71105741
Recognition of consensus CHO structure in ligands for selectins by novel antibody against sialyl Lewis XQ71553226
An important role for the alpha 1,3 fucosyltransferase, FucT-VII, in leukocyte adhesion to E-selectinQ71571070
Inhibition of leukocyte L-selectin function with a monoclonal antibody attenuates reperfusion injury to the rabbit earQ71648297
Neutrophil tethering to and rolling on E-selectin are separable by requirement for L-selectinQ71680566
A Bombay individual lacking H and Le antigens but expressing normal levels of alpha-2- and alpha-4-fucosyltransferasesQ71770261
Fucose expression in skeletal muscle: a lectin histochemical studyQ72102435
Characterization of the immunophenotype and functional properties of fibroblast-like synoviocytes in comparison to skin fibroblasts and umbilical vein endothelial cellsQ72180817
Mouse lymphoma cell lines resistant to pea lectin are defective in fucose metabolismQ72620641
On the biosynthesis of L-fucose by Aerobacter aerogenesQ74637508
The conversion of D-glucose to L-fucose by Aerobacter cloacaeQ74785460
Studies on the biosynthesis of guanosine diphosphate L-fucoseQ78849321
On the biosynthesis of L-fucose and L-fucose metabolism in manQ79027180
Biosynthesis of L-fucose by mammalian tissueQ79389186
Purification and characterization of GDP-D-mannose 4,6-dehydratase from porcine thyroidQ93659261
P433issue11
P407language of work or nameEnglishQ1860
P921main subjectendotheliumQ111140
P304page(s)2438-2445
P577publication date1998-06-01
P1433published inJournal of Clinical InvestigationQ3186904
P1476titleLeukocyte Adhesion Deficiency Type II is a generalized defect of de novo GDP-fucose biosynthesis. Endothelial cell fucosylation is not required for neutrophil rolling on human nonlymphoid endothelium
P478volume101

Reverse relations

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