Impairment of skeletal muscle adenosine triphosphate-sensitive K+ channels in patients with hypokalemic periodic paralysis

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Impairment of skeletal muscle adenosine triphosphate-sensitive K+ channels in patients with hypokalemic periodic paralysis is …
instance of (P31):
scholarly articleQ13442814

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P356DOI10.1172/JCI4552
P932PMC publication ID408119
P698PubMed publication ID10074484
P5875ResearchGate publication ID13215385

P2093author name stringK Jurkat-Rott
S Servidei
D C Camerino
D Tricarico
P Tonali
P2860cites workA calcium channel mutation causing hypokalemic periodic paralysisQ28242375
Dihydropyridine receptor mutations cause hypokalemic periodic paralysisQ28243593
ATP-regulated K+ channels in cardiac muscleQ28265565
Cloning of the beta cell high-affinity sulfonylurea receptor: a regulator of insulin secretionQ34308492
Cloning and functional expression of the cDNA encoding a novel ATP-sensitive potassium channel subunit expressed in pancreatic beta-cells, brain, heart and skeletal muscleQ36789864
Calcium currents and transients of native and heterologously expressed mutant skeletal muscle DHP receptor alpha1 subunits (R528H)Q41057145
Ion-channel defects and aberrant excitability in myotonia and periodic paralysisQ41095963
Molecular pathophysiology of voltage-gated ion channelsQ41100795
Electrophysiological properties of the hypokalaemic periodic paralysis mutation (R528H) of the skeletal muscle alpha 1s subunit as expressed in mouse L cells.Q41215041
Hypokalemic periodic paralysis: an autosomal dominant muscle disorder caused by mutations in a voltage-gated calcium channel.Q41510537
Modification by protons of frog skeletal muscle KATP channels: effects on ion conduction and nucleotide inhibitionQ42671954
Pharmacological characterization of the sulphonylurea receptor in rat isolated aortaQ42674444
The biophysical and pharmacological characteristics of skeletal muscle ATP-sensitive K+ channels are modified in K+-depleted rat, an animal model of hypokalemic periodic paralysisQ42680605
Effects of potassium depletion and insulin on resting and stimulated skeletal rat muscleQ42723278
Nucleotide diphosphates activate the ATP-sensitive potassium channel in mouse skeletal muscleQ44606161
Different sulfonylurea and ATP sensitivity characterizes the juvenile and the adult form of KATP channel complex of rat skeletal muscle.Q52195735
Low-conductance states of K+ channels in adult mouse skeletal muscle.Q53767397
Changes of the biophysical properties of calcium-activated potassium channels of rat skeletal muscle fibres during aging.Q53963663
Modulation of ATP-sensitive K+ channel by insulin in rat skeletal muscle fibers.Q53971983
ATP-sensitive K+ channels of skeletal muscle fibers from young adult and aged rats: possible involvement of thiol-dependent redox mechanisms in the age-related modifications of their biophysical and pharmacological properties.Q54022623
Insulin modulation of ATP-sensitive K+ channel of rat skeletal muscle is impaired in the hypokalaemic state.Q54106462
Enhancement of K+ conductance improves in vitro the contraction force of skeletal muscle in hypokalemic periodic paralysisQ68798219
Insulin-induced hyperpolarization in mammalian skeletal muscleQ69486736
Cromakalim (BRL 34915) restores in vitro the membrane potential of depolarized human skeletal muscle fibresQ69617777
Potassium channels in hypokalaemic periodic paralysis: a key to the pathogenesis?Q70490489
Normal insulin release during sustained hyperglycaemia in hypokalaemic periodic paralysis: role of the potassium channel opener pinacidil in impaired muscle strengthQ71832047
Mapping of the hypokalaemic periodic paralysis (HypoPP) locus to chromosome 1q31-32 in three European familiesQ72017458
Cytoplasmic acidosis induces multiple conductance states in ATP-sensitive potassium channels of cardiac myocytesQ72239336
Genotype-phenotype correlations of DHP receptor alpha 1-subunit gene mutations causing hypokalemic periodic paralysisQ73299439
P433issue5
P407language of work or nameEnglishQ1860
P921main subjectadenosine triphosphateQ80863
hypokalemic periodic paralysisQ622828
P304page(s)675-682
P577publication date1999-03-01
P1433published inJournal of Clinical InvestigationQ3186904
P1476titleImpairment of skeletal muscle adenosine triphosphate-sensitive K+ channels in patients with hypokalemic periodic paralysis
P478volume103

Reverse relations

cites work (P2860)
Q36498120A calcium channel mutant mouse model of hypokalemic periodic paralysis
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Q26744723ATP Sensitive Potassium Channels in the Skeletal Muscle Function: Involvement of the KCNJ11(Kir6.2) Gene in the Determination of Mechanical Warner Bratzer Shear Force
Q34589475Acetazolamide prevents vacuolar myopathy in skeletal muscle of K(+) -depleted rats.
Q35171519Advances in cardiac ATP-sensitive K+ channelopathies from molecules to populations
Q34738564An expanding view for the molecular basis of familial periodic paralysis
Q60708365Calcium Channelopathies
Q28082428Channelopathies of skeletal muscle excitability
Q33944905Disruption of Sur2-containing K(ATP) channels enhances insulin-stimulated glucose uptake in skeletal muscle
Q35045276Dualistic actions of cromakalim and new potent 2H-1,4-benzoxazine derivatives on the native skeletal muscle K ATP channel
Q48907500Effects of mutations causing hypokalaemic periodic paralysis on the skeletal muscle L-type Ca2+ channel expressed in Xenopus laevis oocytes
Q79448284Gene analysis of the calcium channel 1 subunit and clinical studies for two patients with hypokalemic periodic paralysis
Q34811193Genetic disorders of neuromuscular ion channels
Q33906965Human K(ATP) channelopathies: diseases of metabolic homeostasis
Q34304691Hybrid assemblies of ATP-sensitive K+ channels determine their muscle-type-dependent biophysical and pharmacological properties
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Q35208537Voltage-sensor sodium channel mutations cause hypokalemic periodic paralysis type 2 by enhanced inactivation and reduced current

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