| scholarly article | Q13442814 |
| P356 | DOI | 10.1002/JNR.10278 |
| P698 | PubMed publication ID | 12111813 |
| P50 | author | Elizabeth F. Neufeld | Q539886 |
| P2093 | author name string | Yan Cai | |
| Fernando Gómez-Pinilla | |||
| Hong Hua Li | |||
| Hui-Zhi Zhao | |||
| P2860 | cites work | Neuronal defects and delayed wound healing in mice lacking fibroblast growth factor 2 | Q24313613 |
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| Cloning and expression of the gene involved in Sanfilippo B syndrome (mucopolysaccharidosis III B) | Q28609288 | ||
| Running increases cell proliferation and neurogenesis in the adult mouse dentate gyrus | Q29615348 | ||
| Cell surface, heparin-like molecules are required for binding of basic fibroblast growth factor to its high affinity receptor | Q29616189 | ||
| More hippocampal neurons in adult mice living in an enriched environment | Q29617733 | ||
| Knockout of glutamate transporters reveals a major role for astroglial transport in excitotoxicity and clearance of glutamate | Q29620128 | ||
| Regulation of FGF-1 mitogenic activity by heparan sulfate oligosaccharides is dependent on specific structural features: differential requirements for the modulation of FGF-1 and FGF-2. | Q30967062 | ||
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| Proteoglycans as modulators of growth factor activities | Q37656847 | ||
| Interaction of heparan sulfate from mammary cells with acidic fibroblast growth factor (FGF) and basic FGF. Regulation of the activity of basic FGF by high and low affinity binding sites in heparan sulfate | Q38338357 | ||
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| Partial purification and characterization of a heparan sulfate specific endoglucuronidase | Q39798613 | ||
| Reactive astrocytes: cellular and molecular cues to biological function | Q41673434 | ||
| Heparan sulfate potentiates the autocrine action of basic fibroblast growth factor in astrocytes: an in vivo and in vitro study | Q46815443 | ||
| Increased expression of growth-associated protein GAP-43/B-50 following cerebral hemitransection or striatal ischemic injury in the substantia nigra of adult rats | Q48106879 | ||
| In vivo induction of the growth associated protein GAP43/B-50 in rat astrocytes following transient middle cerebral artery occlusion | Q48228285 | ||
| Elevated expression of B-50 (GAP-43)-mRNA in a subpopulation of olfactory bulb mitral cells following axotomy | Q48277523 | ||
| Serial magnetic resonance imaging findings in mucopolysaccharidosis IIIB (Sanfilippo's syndrome B). | Q48770992 | ||
| Brain magnetic resonance imaging in 23 patients with mucopolysaccharidoses and the effect of bone marrow transplantation | Q49292364 | ||
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| Sanfilippo syndrome type C: a clinicopathological autopsy study of a long-term survivor. | Q52201658 | ||
| Developmental Regulation of Neural Response to FGF-1 and FGF-2 by Heparan Sulfate Proteoglycan | Q52225676 | ||
| P433 | issue | 1 | |
| P921 | main subject | astrocyte | Q502961 |
| Sanfilippo syndrome | Q2200359 | ||
| P304 | page(s) | 30-38 | |
| P577 | publication date | 2002-07-01 | |
| P1433 | published in | Journal of Neuroscience Research | Q6295654 |
| P1476 | title | Attenuated plasticity in neurons and astrocytes in the mouse model of Sanfilippo syndrome type B. | |
| P478 | volume | 69 |
| Q36521756 | A GLP-Compliant Toxicology and Biodistribution Study: Systemic Delivery of an rAAV9 Vector for the Treatment of Mucopolysaccharidosis IIIB. |
| Q45881431 | A GLP-compliant toxicology and biodistribution study: systemic delivery of a rAAV9 vector for the treatment of mucopolysaccharidosis IIIB. |
| Q36332885 | A genetic model of substrate reduction therapy for mucopolysaccharidosis |
| Q28534395 | A rapid and sensitive method for measuring N-acetylglucosaminidase activity in cultured cells |
| Q80834423 | Abnormal expression of truncated CRMP-1 protein in the brain cortex of MPSIIIB mice |
| Q45872265 | Abnormal polyamine metabolism is unique to the neuropathic forms of MPS: potential for biomarker development and insight into pathogenesis |
| Q34762478 | Activated microglia in cortex of mouse models of mucopolysaccharidoses I and IIIB |
| Q38300203 | Activation of stress kinases in the brain of mucopolysaccharidosis IIIB mice |
| Q35053456 | Amyloidosis, synucleinopathy, and prion encephalopathy in a neuropathic lysosomal storage disease: the CNS-biomarker potential of peripheral blood |
| Q91140910 | Anatomical changes and pathophysiology of the brain in mucopolysaccharidosis disorders |
| Q61446601 | BMN 250, a fusion of lysosomal alpha-N-acetylglucosaminidase with IGF2, exhibits different patterns of cellular uptake into critical cell types of Sanfilippo syndrome B disease pathogenesis |
| Q33847821 | Blood-brain barrier impairment in an animal model of MPS III B |
| Q51816728 | Canine fucosidosis: a neuroprogressive disorder. |
| Q42059455 | Correction of neurological disease of mucopolysaccharidosis IIIB in adult mice by rAAV9 trans-blood-brain barrier gene delivery |
| Q34077919 | Defects in the medial entorhinal cortex and dentate gyrus in the mouse model of Sanfilippo syndrome type B. |
| Q28512711 | Development of sensory, motor and behavioral deficits in the murine model of Sanfilippo syndrome type B |
| Q34757062 | Differential distribution of heparan sulfate glycoforms and elevated expression of heparan sulfate biosynthetic enzyme genes in the brain of mucopolysaccharidosis IIIB mice |
| Q28472880 | Early neurodegeneration progresses independently of microglial activation by heparan sulfate in the brain of mucopolysaccharidosis IIIB mice |
| Q36322040 | Electrophysiological and Histological Characterization of Rod-Cone Retinal Degeneration and Microglia Activation in a Mouse Model of Mucopolysaccharidosis Type IIIB. |
| Q89161460 | Evaluation of Disease Lesions in the Developing Canine MPS IIIA Brain |
| Q45863181 | Feasibility and Safety of Systemic rAAV9-hNAGLU Delivery for Treating MPS IIIB: Toxicology, Bio-distribution and Immunological Assessments in Primates |
| Q42225564 | Feasibility and safety of systemic rAAV9-hNAGLU delivery for treating mucopolysaccharidosis IIIB: toxicology, biodistribution, and immunological assessments in primates |
| Q42154353 | Functional abnormalities of heparan sulfate in mucopolysaccharidosis-I are associated with defective biologic activity of FGF-2 on human multipotent progenitor cells |
| Q48493230 | GAP43 overexpression and enhanced neurite outgrowth in mucopolysaccharidosis type IIIB cortical neuron cultures. |
| Q45552423 | Improved behavior and neuropathology in the mouse model of Sanfilippo type IIIB disease after adeno-associated virus-mediated gene transfer in the striatum. |
| Q45016195 | Intracerebral injection of sulfamidase delays neuropathology in murine MPS-IIIA. |
| Q48585796 | Intracerebroventricular transplantation of human bone marrow-derived multipotent progenitor cells in an immunodeficient mouse model of mucopolysaccharidosis type I (MPS-I). |
| Q47926676 | Intravenous administration of human umbilical cord blood cells in an animal model of MPS III B. |
| Q82345214 | Investigation of cerebrocortical and cerebellar pathology in canine fucosidosis and comparison to aged brain |
| Q48263257 | Low-dose, continuous enzyme replacement therapy ameliorates brain pathology in the neurodegenerative lysosomal disorder mucopolysaccharidosis type IIIA. |
| Q41838643 | Mannitol-facilitated CNS entry of rAAV2 vector significantly delayed the neurological disease progression in MPS IIIB mice |
| Q89509285 | Molecular Bases of Neurodegeneration and Cognitive Decline, the Major Burden of Sanfilippo Disease |
| Q30495848 | Mucopolysaccharidosis IIIB, a lysosomal storage disease, triggers a pathogenic CNS autoimmune response |
| Q38004963 | Mucopolysaccharidosis type I: current knowledge on its pathophysiological mechanisms |
| Q38988296 | Near-Complete Correction of Profound Metabolomic Impairments Corresponding to Functional Benefit in MPS IIIB Mice after IV rAAV9-hNAGLU Gene Delivery |
| Q37739318 | Pathophysiology of neuropathic lysosomal storage disorders |
| Q89944523 | Proteomic Analysis of Mucopolysaccharidosis IIIB Mouse Brain |
| Q41614431 | Repeated administrations of human umbilical cord blood cells improve disease outcomes in a mouse model of Sanfilippo syndrome type III B. |
| Q51938326 | Retrovirally transduced bone marrow has a therapeutic effect on brain in the mouse model of mucopolysaccharidosis IIIB. |
| Q33439351 | Sanfilippo syndrome type B, a lysosomal storage disease, is also a tauopathy |
| Q37130107 | Sanfilippo syndrome: a mini-review |
| Q38851110 | Serum global metabolomics profiling reveals profound metabolic impairments in patients with MPS IIIA and MPS IIIB. |
| Q93206516 | The role of innate immunity in mucopolysaccharide diseases |
| Q33931583 | Therapeutic efficacy of bone marrow transplant, intracranial AAV-mediated gene therapy, or both in the mouse model of MPS IIIB |
| Q48835669 | Unfolded protein response is not activated in the mucopolysaccharidoses but protein disulfide isomerase 5 is deregulated. |
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