Rumpshaker-like proteolipid protein (PLP) ratio in a mouse model with unperturbed structural and functional integrity of the myelin sheath and axons in the central nervous system

scientific article

Rumpshaker-like proteolipid protein (PLP) ratio in a mouse model with unperturbed structural and functional integrity of the myelin sheath and axons in the central nervous system is …
instance of (P31):
scholarly articleQ13442814

External links are
P356DOI10.1002/GLIA.1071
P698PubMed publication ID11424193

P2093author name stringStoffel W
Büssow H
Spörkel O
Uschkureit T
P2860cites workEvolution of the Myelin Integral Membrane Proteins of the Central Nervous SystemQ21994506
Electrophoretic transfer of proteins from polyacrylamide gels to nitrocellulose sheets: procedure and some applicationsQ24561689
Tight control of gene expression in mammalian cells by tetracycline-responsive promotersQ24564850
Individual exons encode the integral membrane domains of human myelin proteolipid proteinQ24627399
Identification of three forms of human myelin basic protein by cDNA cloningQ24628465
Single-Step Method of RNA Isolation by Acid Guanidinium Thiocyanate–Phenol–Chloroform ExtractionQ25938986
The proteolipid protein gene and myelin disorders in man and animal modelsQ28141963
Transcriptional activation by tetracyclines in mammalian cellsQ28303934
Late-onset neurodegeneration in mice with increased dosage of the proteolipid protein geneQ28509913
Rumpshaker mouse: a new X-linked mutation affecting myelination: evidence for a defect in PLP expressionQ28511941
Quality control of mRNA functionQ34156109
Proteolipid protein (PLP) of CNS myelin: positions of free, disulfide-bonded, and fatty acid thioester-linked cysteine residues and implications for the membrane topology of PLPQ34206903
Formation of germ-line chimaeras from embryo-derived teratocarcinoma cell linesQ34267275
Splice site selection in the proteolipid protein (PLP) gene transcript and primary structure of the DM-20 protein of central nervous system myelinQ34337961
Disruption of the compacted myelin sheath of axons of the central nervous system in proteolipid protein-deficient miceQ35931734
Disrupted proteolipid protein trafficking results in oligodendrocyte apoptosis in an animal model of Pelizaeus-Merzbacher disease.Q36276665
Jimpy mutant mouse: a 74-base deletion in the mRNA for myelin proteolipid protein and evidence for a primary defect in RNA splicingQ36458669
The complete sequence of a full length cDNA for human liver glyceraldehyde-3-phosphate dehydrogenase: evidence for multiple mRNA species.Q36587218
Mammalian nonsense codons can be cis effectors of nuclear mRNA half-life.Q36672156
Structure and molecular arrangement of proteolipid protein of central nervous system myelinQ37562756
Myelin mutants: new models and new observationsQ40926611
A cellular mechanism governing the severity of Pelizaeus-Merzbacher disease.Q41182431
Intracellular transport and sorting of the oligodendrocyte transmembrane proteolipid protein.Q41478764
Myelin glycolipids and their functionsQ41652265
Absence of the major dense line in myelin of the mutant mouse ‘shiverer’Q41702041
Assembly of myelin by association of proteolipid protein with cholesterol- and galactosylceramide-rich membrane domainsQ42259207
Uncoupling of hypomyelination and glial cell death by a mutation in the proteolipid protein geneQ43605216
Death of individual oligodendrocytes in jimpy brain precedes expression of proteolipid proteinQ44063104
Axonal swellings and degeneration in mice lacking the major proteolipid of myelinQ48004959
Developmental expression of major myelin protein genes in the CNS of X-linked hypomyelinating mutant rumpshaker.Q48429843
Rumpshaker: an X-linked mutation causing hypomyelination: developmental differences in myelination and glial cells between the optic nerve and spinal cordQ48589841
Myelination in rat brain: method of myelin isolationQ48629501
Parallel evolution and coexpression of the proteolipid proteins and protein zero in vertebrate myelinQ48988108
Monomethylated cap structures facilitate RNA export from the nucleus.Q50804073
The evolution of lipophilin genes from invertebrates to tetrapods: DM-20 cannot replace proteolipid protein in CNS myelin.Q52168267
A proteolipid protein-specific pre-mRNA (Ppm-1) contains intron 3 and is up-regulated during myelination in the CNS.Q52170605
The "spliceosome": yeast pre-messenger RNA associates with a 40S complex in a splicing-dependent reaction.Q55061116
Paralytic tremor (pt) rabbit: a sex-linked mutation affecting proteolipid protein-gene expressionQ62035802
Stepwise assembly of a pre-mRNA splicing complex requires U-snRNPs and specific intron sequencesQ64380337
Schwann cell myelin ensheathing C.N.S. axons in the nerve fibre layer of the cat retinaQ67329042
Assignment of the gene for myelin proteolipid protein to the X chromosome: implications for X-linked myelin disordersQ69805341
Programmed cell death in the dysmyelinating mutantsQ70785128
Effects of rumpshaker mutation on CNS myelin composition and structureQ70790686
Levels and syntheses of cerebrosides and sulfatides in subcellular fractions of jimpy mutantsQ71012910
Nonsense mutations inhibit RNA splicing in a cell-free system: recognition of mutant codon is independent of protein synthesisQ71046937
Adhesive properties of proteolipid protein are responsible for the compaction of CNS myelin sheathsQ71706053
Manipulation of transgenes by site-specific recombination: use of Cre recombinaseQ72583961
Assembly of CNS myelin in the absence of proteolipid proteinQ73016640
Intracellular distribution of myelin protein gene products is altered in oligodendrocytes of the taiep ratQ73208879
Rumpshaker behaves like juvenile-lethal Plp mutations when combined with shiverer in double mutant miceQ73430708
Proteolipid protein mRNA stability is regulated by axonal contact in the rodent peripheral nervous systemQ73953692
Early onset of axonal degeneration in double (plp-/-mag-/-) and hypomyelinosis in triple (plp-/-mbp-/-mag-/-) mutant miceQ73963893
Myelin proteolipid protein: function in myelin structure is distinct from its role in oligodendrocyte developmentQ77703274
P433issue1
P407language of work or nameEnglishQ1860
P304page(s)63-71
P577publication date2001-07-01
P1433published inGliaQ15716658
P1476titleRumpshaker-like proteolipid protein (PLP) ratio in a mouse model with unperturbed structural and functional integrity of the myelin sheath and axons in the central nervous system
P478volume35

Reverse relations

cites work (P2860)
Q37967602Genetic approaches to study glial cells in the rodent brain.
Q96946557Suppression of proteolipid protein rescues Pelizaeus-Merzbacher disease
Q48765082The VF rat with abnormal myelinogenesis has a mutation in Dopey1.

Search more.