Uptake and metabolism of radiolabelled GM1-ganglioside in skin fibroblasts from controls and patients with GM1-gangliosidosis

scientific article

Uptake and metabolism of radiolabelled GM1-ganglioside in skin fibroblasts from controls and patients with GM1-gangliosidosis is …
instance of (P31):
scholarly articleQ13442814

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P356DOI10.1007/BF01799941
P698PubMed publication ID1779618

P2093author name stringH Yabuuchi
K Ogura
S Okada
M Midorikawa
S Handa
K Inui
P2860cites workProtein measurement with the Folin phenol reagentQ20900776
Clinical and enzymatic variations in G M1 generalized gangliosidosisQ35569302
G-M1-gangliosidosis. Correlation of clinical and biochemical dataQ36509070
Metabolism of cerebroside sulfate and subcellular distribution of its metabolites in cultured skin fibroblasts from controls, metachromatic leukodystrophy, and globoid cell leukodystrophyQ40510783
Ganglioside GM1 metabolism in living human fibroblasts with beta-galactosidase deficiencyQ41379869
Diagnosis of subtypes of GM1 gangliosidosis in vitro and in vivo--using urinary oligosaccharides as substratesQ41859684
Uptake and metabolism of radioactively labeled sphingomyelin in cultured skin fibroblasts from controls and patients with Niemann-Pick disease and other lysosomal storage diseasesQ42253391
Chronic GM1 gangliosidosis presenting as dystonia: II. Biochemical studiesQ42463513
Characterization of the cellular binding of exogenous gangliosidesQ44032206
Incorporation and degradation of GM1 ganglioside and asialoGM1 ganglioside in cultured fibroblasts from normal individuals and patients with beta-galactosidase deficiency.Q46948755
Generalized gangliosidosis: beta-galactosidase deficiency.Q51185420
Biochemical, immunological, and structural studies on a sphingolipid activator protein (SAP-1).Q52091535
Incorporation and metabolism of ganglioside GM2 in skin fibroblasts from normal and GM2 gangliosidosis subjects.Q54448606
Preparation of GM1 ganglioside molecular species having homogeneous fatty acid and long chain base moietiesQ70091210
A correlation of intracellular cerebroside sulfatase activity in fibroblasts with latency in metachromatic leukodystrophyQ70609536
Specific tritium labeling of gangliosides at the 3-position of sphingosinesQ71045920
P433issue5
P304page(s)721-729
P577publication date1991-01-01
P1433published inJournal of Inherited Metabolic DiseaseQ6295359
P1476titleUptake and metabolism of radiolabelled GM1-ganglioside in skin fibroblasts from controls and patients with GM1-gangliosidosis
P478volume14

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cites work (P2860)
Q48943596Salvage of catabolic products in ganglioside metabolism: a study on rat cerebellar granule cells in culture
Q53395960Uptake and fate of ganglioside GD3 in human intestinal Caco-2 cells.

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