scholarly article | Q13442814 |
P356 | DOI | 10.1007/BF01799941 |
P698 | PubMed publication ID | 1779618 |
P2093 | author name string | H Yabuuchi | |
K Ogura | |||
S Okada | |||
M Midorikawa | |||
S Handa | |||
K Inui | |||
P2860 | cites work | Protein measurement with the Folin phenol reagent | Q20900776 |
Clinical and enzymatic variations in G M1 generalized gangliosidosis | Q35569302 | ||
G-M1-gangliosidosis. Correlation of clinical and biochemical data | Q36509070 | ||
Metabolism of cerebroside sulfate and subcellular distribution of its metabolites in cultured skin fibroblasts from controls, metachromatic leukodystrophy, and globoid cell leukodystrophy | Q40510783 | ||
Ganglioside GM1 metabolism in living human fibroblasts with beta-galactosidase deficiency | Q41379869 | ||
Diagnosis of subtypes of GM1 gangliosidosis in vitro and in vivo--using urinary oligosaccharides as substrates | Q41859684 | ||
Uptake and metabolism of radioactively labeled sphingomyelin in cultured skin fibroblasts from controls and patients with Niemann-Pick disease and other lysosomal storage diseases | Q42253391 | ||
Chronic GM1 gangliosidosis presenting as dystonia: II. Biochemical studies | Q42463513 | ||
Characterization of the cellular binding of exogenous gangliosides | Q44032206 | ||
Incorporation and degradation of GM1 ganglioside and asialoGM1 ganglioside in cultured fibroblasts from normal individuals and patients with beta-galactosidase deficiency. | Q46948755 | ||
Generalized gangliosidosis: beta-galactosidase deficiency. | Q51185420 | ||
Biochemical, immunological, and structural studies on a sphingolipid activator protein (SAP-1). | Q52091535 | ||
Incorporation and metabolism of ganglioside GM2 in skin fibroblasts from normal and GM2 gangliosidosis subjects. | Q54448606 | ||
Preparation of GM1 ganglioside molecular species having homogeneous fatty acid and long chain base moieties | Q70091210 | ||
A correlation of intracellular cerebroside sulfatase activity in fibroblasts with latency in metachromatic leukodystrophy | Q70609536 | ||
Specific tritium labeling of gangliosides at the 3-position of sphingosines | Q71045920 | ||
P433 | issue | 5 | |
P304 | page(s) | 721-729 | |
P577 | publication date | 1991-01-01 | |
P1433 | published in | Journal of Inherited Metabolic Disease | Q6295359 |
P1476 | title | Uptake and metabolism of radiolabelled GM1-ganglioside in skin fibroblasts from controls and patients with GM1-gangliosidosis | |
P478 | volume | 14 |
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