Management of hyperbilirubinemia and prevention of kernicterus in 20 patients with Crigler-Najjar disease

scientific article published on 25 January 2006

Management of hyperbilirubinemia and prevention of kernicterus in 20 patients with Crigler-Najjar disease is …
instance of (P31):
scholarly articleQ13442814

External links are
P356DOI10.1007/S00431-005-0055-2
P698PubMed publication ID16435131
P5875ResearchGate publication ID7338712

P2093author name stringDonna L Robinson
Hendrik J Vreman
Erik G Puffenberger
D Holmes Morton
Kevin A Strauss
Graham Hart
P2860cites workEffect of penicillins on bilirubin-albumin bindingQ68489796
Increase of plasma nonesterified fatty acid concentration and decrease of albumin binding affinity after intravenous injection of glycocholate-lecithin mixed micellesQ68867673
Displacement of bilirubin from adult and newborn serum albumin by a drug and fatty acidQ69369972
Ceftriaxone effect on bilirubin-albumin bindingQ69454887
Comparison between two preparations of human serum albumin in treatment of neonatal hyperbilirubinaemiaQ70500477
Toxic effects in the Gunn rat of combined treatment with bilirubin and orotic acidQ70500587
Bilirubin-displacing effect of furosemide and sulfisoxazole. An in vitro and in vivo study in neonatal serumQ71035200
Influence of free fatty acids and glucose infusion on serum bilirubin and bilirubin binding to albumin: clinical implicationsQ71669047
Mapping of the consequences of bilirubin exposure in the immature rat: local cerebral metabolic rates for glucose during moderate and severe hyperbilirubinemiaQ71749485
Albumin Reserve for Binding of Bilirubin in Maternal and Cord Serum under Treatment with SulphasalazineQ72522627
Ceftriaxone--bilirubin-albumin interactions in the neonate: an in vivo studyQ72840540
Does ibuprofen affect bilirubin-albumin binding in newborn infant serum?Q72988824
Congenital familial nonhemolytic jaundice with kernicterusQ73968795
Practice patterns in neonatal hyperbilirubinemiaQ73996356
A difference in mortality rate and incidence of kernicterus among premature infants allotted to two prophylactic antibacterial regimensQ74267298
Influence of light on the hyperbilirubinaemia of infantsQ77225231
Crigler-Najjar syndrome in Saudi ArabiaQ77304074
Predictive ability of a predischarge hour-specific serum bilirubin for subsequent significant hyperbilirubinemia in healthy term and near-term newbornsQ77901611
Lessons from the pastQ81377528
Mapping of sudden infant death with dysgenesis of the testes syndrome (SIDDT) by a SNP genome scan and identification of TSPYL loss of functionQ24564082
Determination of the Vacant Amount of High-Affinity Bilirubin Binding Site on Serum AlbuminQ28330549
The blood-brain barrier and bilirubin encephalopathyQ33847807
Management of hyperbilirubinemia in the newborn infant 35 or more weeks of gestationQ34330809
Overview of pediatric liver transplantationQ35561269
In vitro displacement of bilirubin by antibiotics and 2-hydroxybenzoylglycine in newbornsQ35564504
Phototherapy: current methods and future directionsQ36027222
Bilirubin-albumin binding and neonatal jaundiceQ36027228
Risk management of severe neonatal hyperbilirubinemia to prevent kernicterusQ36074961
Bilirubin Displacing Effect of Drugs Used in NeonatologyQ36939656
Home phototherapy: use and attitudes among community pediatriciansQ38566203
Neonatal bilirubin toxicity. A review of kernicterus and the implications of drug-induced bilirubin displacementQ39665704
Drug-Induced Displacement of Bilirubin from Albumin in the NewbornQ40157856
Neurologic perspectives of Crigler-Najjar syndrome type I.Q40851763
Bilirubin. Solubility and interaction with albumin and phospholipidQ41498582
The future demise of exchange transfusions for neonatal hyperbilirubinemiaQ41554589
Albumin binding of anti-inflammatory drugs. Utility of a site-oriented versus a stoichiometric analysis.Q42255744
Effect of lactate, pyruvate, acetone, acetoacetate, and beta-hydroxybutyrate on albumin binding of bilirubinQ42258807
Bilirubin-displacing effect of ampicillin, indomethacin, chlorpromazine, gentamicin, and parabens in vitro and in newborn infantsQ42259360
Unbound Bilirubin in a Term Newborn With KernicterusQ43567144
Binding of bilirubin and long-chain fatty acids to human serum albumin with general remarks on displacement of firmly bound ligandsQ43691924
Effect of hypothermia on bilirubin-induced alterations in brain cell membrane function and energy metabolism in newborn pigletsQ43823155
System-based approach to management of neonatal jaundice and prevention of kernicterusQ43990415
Decreased mortality from technical failure improves results in pediatric liver transplantationQ46269536
Treatment of Crigler-Najjar type 1 disease: relevance of early liver transplantationQ48238424
Pediatricians' awareness of and attitudes about four clinical practice guidelinesQ48630517
Current therapy for Crigler-Najjar syndrome type 1: report of a world registryQ48959643
Kernicterus in an adult who is heterozygous for Crigler-Najjar syndrome and homozygous for Gilbert-type genetic defectQ50156621
Lack of deafness in Crigler-Najjar syndrome type 1: a patient survey.Q50506252
Binding effect of albumin on uptake of bilirubin by brain.Q52599062
Displacement of bilirubin from albumin by indomethacinQ67404791
The effect of paraben preservatives on albumin binding of bilirubinQ67791494
Effect of Drug Combinations on Bilirubin-Albumin BindingQ67885461
Effect of cephalosporins on bilirubin-albumin bindingQ68259522
P433issue5
P921main subjectbilirubin metabolic disorderQ390475
P304page(s)306-319
P577publication date2006-01-25
P1433published inEuropean Journal of PediatricsQ15755736
P1476titleManagement of hyperbilirubinemia and prevention of kernicterus in 20 patients with Crigler-Najjar disease
P478volume165

Reverse relations

cites work (P2860)
Q97423864A Quantitative In Vitro Potency Assay for Adeno-Associated Virus Vectors Encoding for the UGT1A1 Transgene
Q37313599A translationally optimized AAV-UGT1A1 vector drives safe and long-lasting correction of Crigler-Najjar syndrome
Q35954282Acute cholangitis in an old patient with Crigler-Najjar syndrome type II - a case report
Q27028088Amish revisited: next-generation sequencing studies of psychiatric disorders among the Plain people
Q37066120Application of whole-organ tissue engineering in hepatology
Q45728938Bilirubin accumulation and Cyp mRNA expression in selected brain regions of jaundiced Gunn rat pups
Q42266741Biliverdin Reductase inhibitors did not improve severe unconjugated hyperbilirubinemia in vivo
Q90280901Crigler-Najjar Syndrome Type 1: Pathophysiology, Natural History, and Therapeutic Frontier
Q37333994De Novo Donor-Specific HLA Antibody Formation in Two Patients With Crigler-Najjar Syndrome Type I Following Human Hepatocyte Transplantation With Partial Hepatectomy Preconditioning
Q44966651Disruption of the ugt1 locus in mice resembles human Crigler-Najjar type I disease
Q50528431Erythrocyte pyruvate kinase deficiency in an old-order Amish cohort: longitudinal risk and disease management.
Q36052685Evaluating the beneficial and detrimental effects of bile pigments in early and later life
Q39012956Evaluation of region selective bilirubin-induced brain damage as a basis for a pharmacological treatment
Q95353303Evaluation of the pediatric patient for liver transplantation: 2014 practice guideline by the American Association for the Study of Liver Diseases, American Society of Transplantation and the North American Society for Pediatric Gastroenterology, He
Q38260248Gene replacement therapy for genetic hepatocellular jaundice
Q37015311Gene therapy for inborn errors of liver metabolism: progress towards clinical applications
Q37945218Gene therapy with helper-dependent adenoviral vectors: current advances and future perspectives
Q48100807Germline genetic variants with implications for disease risk and therapeutic outcomes
Q37582126Helper-Dependent Adenoviral Vectors.
Q38025743Hepatocyte transplantation for inherited metabolic diseases of the liver.
Q48499059Hepatocyte transplantation: Consider infusion before incision
Q36346898Impairment of enzymatic antioxidant defenses is associated with bilirubin-induced neuronal cell death in the cerebellum of Ugt1 KO mice
Q42252510In the rat liver, Adenoviral gene transfer efficiency is comparable to AAV.
Q38872573Liver transplantation for pediatric inherited metabolic disorders: Considerations for indications, complications, and perioperative management
Q41927913Liver transplantation for treatment of severe S-adenosylhomocysteine hydrolase deficiency
Q43902131Living related liver transplantation in Crigler-Najjar syndrome type 1.
Q26826934New pathophysiological concepts underlying pathogenesis of pigment gallstones
Q46934869Orlistat treatment of unconjugated hyperbilirubinemia in Crigler-Najjar disease: a randomized controlled trial
Q34344245Phototherapy device effectiveness in Nigeria: irradiance assessment and potential for improvement
Q90012812Prevalence and Relevance of Pre-Existing Anti-Adeno-Associated Virus Immunity in the Context of Gene Therapy for Crigler-Najjar Syndrome
Q38601073Progress toward improved therapies for inborn errors of metabolism
Q52594620Quantitative Systems Pharmacology Model of hUGT1A1-modRNA Encoding for the UGT1A1 Enzyme to Treat Crigler-Najjar Syndrome Type 1.
Q36617362Recommendations for pregnancies in patients with crigler-najjar syndrome
Q30515514Rescue of bilirubin-induced neonatal lethality in a mouse model of Crigler-Najjar syndrome type I by AAV9-mediated gene transfer
Q48033678Sister Jean Ward, phototherapy, and jaundice: a unique human and photochemical interaction
Q36744280Stem cell therapy for inherited metabolic disorders of the liver
Q41967780Successful plasmapheresis for acute and severe unconjugated hyperbilirubinemia in a child with crigler najjar type I syndrome.
Q99708873The Role of Bilirubin and the Other "Yellow Players" in Neurodegenerative Diseases
Q37684677Therapeutic hepatocyte transplant for inherited metabolic disorders: functional considerations, recent outcomes and future prospects
Q85364981Tin-mesoporphyrin in the treatment of refractory hyperbilirubinemia due to Rh incompatibility
Q33586303Vector and helper genome rearrangements occur during production of helper-dependent adenoviral vectors

Search more.