The congenital long QT syndrome Type 3: An update.

scientific article

The congenital long QT syndrome Type 3: An update. is …
instance of (P31):
scholarly articleQ13442814

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P356DOI10.1016/J.IPEJ.2017.10.011
P8608Fatcat IDrelease_lsflphoaibcujmlud5qn33gqwq
P932PMC publication ID5840852
P698PubMed publication ID29101013

P50authorIsabel Cristina Esposito SorpresoQ61146592
Andrés R Pérez-RieraQ57551205
P2093author name stringLuiz Carlos de Abreu
Rodrigo Daminello Raimundo
Raimundo Barbosa-Barros
Marianne Penachini da Costa de Rezende Barbosa
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Risk for life-threatening cardiac events in patients with genotype-confirmed long-QT syndrome and normal-range corrected QT intervalsQ35904744
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Importance of Knowing the Genotype and the Specific Mutation When Managing Patients with Long QT SyndromeQ37313296
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Novel long QT syndrome-associated missense mutation, L762F, in CACNA1C-encoded L-type calcium channel imparts a slower inactivation tau and increased sustained and window current.Q38890009
Trafficking defects and gating abnormalities of a novel SCN5A mutation question gene-specific therapy in long QT syndrome type 3.Q39722604
Molecular determinants of local anesthetic action of beta-blocking drugs: Implications for therapeutic management of long QT syndrome variant 3Q39845135
QT Dynamics During Exercise in Asymptomatic Children with Long QT Syndrome Type 3.Q39964440
Contribution of sodium channel mutations to bradycardia and sinus node dysfunction in LQT3 familiesQ40658302
Recognition and significance of pathological T-wave inversions in athletesQ41590669
Y1767C, a novel SCN5A mutation, induces a persistent Na+ current and potentiates ranolazine inhibition of Nav1.5 channelsQ42621770
A novel mechanism for LQT3 with 2:1 block: a pore-lining mutation in Nav1.5 significantly affects voltage-dependence of activationQ42684739
Neonatal long QT syndrome type 3 predicted by positive lidocaine challengeQ43269056
Normalization of ventricular repolarization with flecainide in long QT syndrome patients with SCN5A:DeltaKPQ mutationQ43595378
Discovery of Dihydrobenzoxazepinone (GS-6615) Late Sodium Current Inhibitor (Late INai), a Phase II Agent with Demonstrated Preclinical Anti-Ischemic and Antiarrhythmic PropertiesQ46120532
The long QT syndrome: new diagnostic and therapeutic approach in the era of molecular biology.Q46360306
The SCN5A mutation A1180V is associated with electrocardiographic features of LQT3.Q46367175
Return to play? Athletes with congenital long QT syndromeQ46777813
Common Genotypes of Long QT Syndrome in China and the Role of ECG Prediction.Q50968234
Diurnal pattern of QTc interval: how long is prolonged? Possible relation to circadian triggers of cardiovascular events.Q51049415
A Novel SCN5A Mutation Found in a Familial Case of Long QT Syndrome Complicated by Severe Left Ventricular Dysfunction.Q51239891
Vectorcardiography identifies patients with electrocardiographically concealed long QT syndrome.Q53448030
Electrical alternation of the T-wave: Clinical and experimental evidence of its relationship with the sympathetic nervous system and with the long Q-T syndromeQ58011829
P433issue1
P407language of work or nameEnglishQ1860
P921main subjectlong QT syndromeQ653924
P304page(s)25-35
P577publication date2017-10-31
P1433published inIndian Pacing and Electrophysiology JournalQ15734361
P1476titleThe congenital long QT syndrome Type 3: An update
P478volume18

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cites work (P2860)
Q89893274Spatially Discordant Repolarization Alternans in the Absence of Conduction Velocity Restitution
Q64074155The Brazilian Society of Cardiology and Brazilian Society of Exercise and Sports Medicine Updated Guidelines for Sports and Exercise Cardiology - 2019

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