review article | Q7318358 |
scholarly article | Q13442814 |
P356 | DOI | 10.1007/BF00164308 |
P698 | PubMed publication ID | 7934150 |
P2093 | author name string | M R Bye | |
L M Quittell | |||
J M Ewig | |||
P2860 | cites work | Identification of the cystic fibrosis gene: chromosome walking and jumping | Q22299423 |
Identification of the cystic fibrosis gene: cloning and characterization of complementary DNA | Q28119124 | ||
A test for concentration of electrolytes in sweat in cystic fibrosis of the pancreas utilizing pilocarpine by iontophoresis | Q28184639 | ||
Identification of the cystic fibrosis gene: genetic analysis | Q29614402 | ||
Coagulation abnormalities in cystic fibrosis | Q33470013 | ||
Abnormal electrolyte composition of sweat in cystic fibrosis of the pancreas; clinical significance and relationship to the disease. | Q33968708 | ||
Purification and functional reconstitution of the cystic fibrosis transmembrane conductance regulator (CFTR) | Q33970197 | ||
An animal model for cystic fibrosis made by gene targeting | Q33970549 | ||
Aerosol carbenicillin and gentamicin treatment of Pseudomonas aeruginosa infection in patients with cystic fibrosis | Q34054725 | ||
Relative underweight in cystic fibrosis and its prognostic value | Q34055132 | ||
Frequent antibiotic therapy improves survival of cystic fibrosis patients with chronic Pseudomonas aeruginosa infection | Q34056063 | ||
The relation between genotype and phenotype in cystic fibrosis--analysis of the most common mutation (delta F508). | Q34635892 | ||
Effects of an artificial diet on growth of patients with cystic fibrosis | Q34987384 | ||
Variability of airways hyper-reactivity and allergy in cystic fibrosis | Q35115602 | ||
Cystic fibrosis: physical exercise versus chest physiotherapy | Q35116187 | ||
The American Society of Human Genetics statement on cystic fibrosis screening | Q35201309 | ||
Analysis of DNA polymorphism haplotypes linked to the cystic fibrosis locus in North American black and Caucasian families supports the existence of multiple mutations of the cystic fibrosis gene. | Q35247123 | ||
Linkage disequilibrium, cystic fibrosis, and genetic counseling | Q35247199 | ||
A preliminary study of aerosolized recombinant human deoxyribonuclease I in the treatment of cystic fibrosis | Q68062090 | ||
Pharmacokinetics of antimicrobial drugs in cystic fibrosis. Beta-lactam antibiotics | Q68152646 | ||
Person-to-person transmission of Pseudomonas cepacia between patients with cystic fibrosis | Q68160610 | ||
Randomized trial of ceftazidime versus placebo in the management of acute respiratory exacerbations in patients with cystic fibrosis | Q68205329 | ||
Antibiotic treatment. Aerosol therapy | Q68449084 | ||
A pilot study of aerosolized amiloride for the treatment of lung disease in cystic fibrosis | Q68455772 | ||
Effect of Pseudomonas cepacia colonization on survival and pulmonary function of cystic fibrosis patients | Q68709409 | ||
Longitudinal response of pulmonary function to bronchodilators in cystic fibrosis | Q68917024 | ||
Total respiratory system compliance in asymptomatic infants with cystic fibrosis | Q69011260 | ||
What is a "pulmonary exacerbation" in cystic fibrosis? | Q69449682 | ||
Autogenic drainage: a modern approach to physiotherapy in cystic fibrosis | Q69503724 | ||
Pseudomonas cepacia: decrease in colonization in patients with cystic fibrosis | Q69634656 | ||
Relative effects of bronchial drainage and exercise for in-hospital care of patients with cystic fibrosis | Q69658541 | ||
Vitamin D metabolites in adolescents and young adults with cystic fibrosis: effects of sun and season | Q69863974 | ||
Glucose intolerance in cystic fibrosis | Q69881895 | ||
Prenatal diagnosis of cystic fibrosis | Q69906611 | ||
Bronchodilators increase airway instability in cystic fibrosis | Q70102881 | ||
Effect of heart-lung transplantation on airway potential difference in patients with and without cystic fibrosis | Q70146668 | ||
Evaluation of the PEP mask in cystic fibrosis | Q70149023 | ||
A double-blind controlled trial of anti-Pseudomonas chemotherapy of acute respiratory exacerbations in patients with cystic fibrosis | Q70161420 | ||
Chest physiotherapy: a review | Q70246490 | ||
Improved respiratory prognosis in patients with cystic fibrosis with normal fat absorption | Q70375628 | ||
Pneumothorax in cystic fibrosis: management and outcome | Q70375632 | ||
Blood and Liver Concentrations of Vitamins A and E in Children with Cystic Fibrosis of the Pancreas | Q70424782 | ||
Short-term pulmonary effects of total parenteral nutrition in children with cystic fibrosis | Q70476049 | ||
Hemorrhagic Diathesis and Cystic Fibrosis in Infancy | Q70512265 | ||
The changing epidemiology of cystic fibrosis | Q70528025 | ||
125I-Clq-binding and specific antibodies as indicators of pulmonary disease activity in cystic fibrosis | Q70832473 | ||
Bronchial Reactivity in Cystic Fibrosis With Normal Pulmonary Function | Q70930682 | ||
Increased bioelectric potential difference across respiratory epithelia in cystic fibrosis | Q70982010 | ||
Immediate and long-term effects of chest physiotherapy in patients with cystic fibrosis | Q71044361 | ||
Hemoglobin desaturation: its occurrence during sleep in patients with cystic fibrosis | Q71286854 | ||
Cough versus chest physiotherapy. A comparison of the acute effects on pulmonary function in patients with cystic fibrosis | Q71288373 | ||
Improved growth and clinical, nutritional, and respiratory changes in response to nutritional therapy in cystic fibrosis | Q71515779 | ||
Liver function studies and biliary tract investigations in mucoviscidosis. r58 C/*539-44* A/Feigelson J, Pecau Y, Sauvegrain J: Liver function studies and biliary tract investigations in mucoviscidosis | Q71533158 | ||
Mucoid Escherichia coli in cystic fibrosis | Q71548190 | ||
Intussusception in patients with cystic fibrosis | Q71800148 | ||
Energy needs and growth in children with cystic fibrosis | Q71833057 | ||
Flow-volume curves in infants with lung disease | Q71838542 | ||
Insulin receptors in cystic fibrosis: increased receptor number and altered affinity | Q72130919 | ||
Complications of Cystic Fibrosis | Q72417419 | ||
Cystic fibrosis with extensive fat replacement of the liver | Q72875038 | ||
A distinctive type of biliary cirrhosis of the liver associated with cystic fibrosis of the pancreas; recognition through signs of portal hypertension | Q74221452 | ||
THE INTESTINAL LESIONS IN CYSTIC FIBROSIS OF THE PANCREAS | Q76555898 | ||
Therapy and prognosis of fibrocystic disease of the pancreas | Q80317879 | ||
A longitudinal study of bronchodilator responsiveness in cystic fibrosis | Q93566031 | ||
DNA marker haplotype association with pancreatic sufficiency in cystic fibrosis | Q35248559 | ||
Cystic fibrosis: molecular biology and therapeutic implications | Q35319385 | ||
Drug therapy in the 1990s. What can we expect for cystic fibrosis? | Q35323845 | ||
Physical activity and self treatment in cystic fibrosis | Q35602842 | ||
Modulation of airway inflammation in cystic fibrosis. In vivo suppression of interleukin-8 levels on the respiratory epithelial surface by aerosolization of recombinant secretory leukoprotease inhibitor | Q35606533 | ||
Is cough as effective as chest physiotherapy in the removal of excessive tracheobronchial secretions? | Q36474369 | ||
Clinical significance of Staphylococcus aureus in cystic fibrosis | Q37808887 | ||
Pathogenesis of the pseudomonas lung lesion in cystic fibrosis | Q38227182 | ||
Diagnosis of genetic disorders at the DNA level | Q38597743 | ||
Why is the cystic fibrosis gene so frequent? | Q38749495 | ||
Genetic counseling using linked DNA probes: cystic fibrosis as a prototype | Q39542099 | ||
Pharmacokinetics of antimicrobial drugs in cystic fibrosis. Aminoglycoside antibiotics | Q39654167 | ||
Antibacterial therapy in cystic fibrosis. A review of the literature published between 1980 and February 1987. | Q39654171 | ||
Antimicrobial therapy against Staphylococcus aureus, Pseudomonas aeruginosa, and Pseudomonas cepacia | Q39654175 | ||
Pseudomonas cepacia: biology, mechanisms of virulence, epidemiology | Q39732190 | ||
Infection in patients with cystic fibrosis | Q39740286 | ||
Cystic fibrosis and malnutrition | Q39803118 | ||
Nutrition and chronic lung disease | Q39836460 | ||
Pulmonary disease associated with Pseudomonas aeruginosa in cystic fibrosis: current status of the host-bacterium interaction | Q39846012 | ||
Meconium in health and in disease | Q39855990 | ||
Vitamin E and the biological antioxidant theory | Q40012988 | ||
The cardiovascular system in cystic fibrosis. | Q40245542 | ||
Gastrointestinal manifestations of cystic fibrosis: a review | Q40316357 | ||
Liver involvement in cystic fibrosis. A report of 9 cases | Q40343629 | ||
Production of the Pseudomonas aeruginosa neuraminidase is increased under hyperosmolar conditions and is regulated by genes involved in alginate expression | Q40343721 | ||
Clinical management of pulmonary disease in cystic fibrosis | Q40709266 | ||
Antibiotic therapy in cystic fibrosis: evaluation of clinical trials | Q40808575 | ||
Pseudomonas cepacia infection in cystic fibrosis: an emerging problem | Q40829590 | ||
Intravenous linoleic acid supplementation in children with cystic fibrosis | Q41086734 | ||
Comparative trial of manual and mechanical percussion technique with gravity-assisted bronchial drainage in patients with cystic fibrosis | Q41103826 | ||
Gallbladder disease in cystic fibrosis | Q41362386 | ||
In vivo transfer of the human cystic fibrosis transmembrane conductance regulator gene to the airway epithelium | Q41644008 | ||
Defective acidification of intracellular organelles in cystic fibrosis | Q41675496 | ||
Hepatic cirrhosis associated with fibrocystic disease of the pancreas; clinical and pathological reports of five patients | Q41706387 | ||
Diabetic microangiopathy in patients with cystic fibrosis | Q41767672 | ||
Management of esophageal varices in children by injection sclerotherapy | Q42252779 | ||
Outcome after Liver Transplantation for Cystic Fibrosis. | Q42738933 | ||
Effect of chest physiotherapy on the removal of mucus in patients with cystic fibrosis | Q43324799 | ||
The management of portal hypertension in cystic fibrosis | Q43537479 | ||
Early bacteriologic, immunologic, and clinical courses of young infants with cystic fibrosis identified by neonatal screening | Q43602127 | ||
Demonstration That CFTR Is a Chloride Channel by Alteration of Its Anion Selectivity | Q43847410 | ||
Is anti-Pseudomonas therapy warranted in acute respiratory exacerbations in children with cystic fibrosis? | Q44379999 | ||
Pseudomonas cepacia colonization in patients with cystic fibrosis: risk factors and clinical outcome | Q44445035 | ||
Survival and quality of life of cystic fibrosis patients before and after heart-lung transplantation | Q44458955 | ||
Mutation analysis for heterozygote detection and the prenatal diagnosis of cystic fibrosis | Q44646906 | ||
Progression of cystic fibrosis lung disease as a function of serum immunoglobulin G levels: a 5-year longitudinal study | Q44749384 | ||
Orthotopic liver transplantation in patients with cystic fibrosis | Q45177885 | ||
Bronchial hyperreactivity in cystic fibrosis and asthma | Q45851071 | ||
Comparison of oxygen desaturation during sleep and exercise in patients with cystic fibrosis | Q48900021 | ||
Ventilation and oxygenation changes during sleep in cystic fibrosis | Q49103733 | ||
Role of conventional physiotherapy in cystic fibrosis. | Q50563978 | ||
Insulin and glucagon response to arginine infusion in cystic fibrosis | Q51668061 | ||
Cystic fibrosis in the mouse by targeted insertional mutagenesis | Q52477870 | ||
Energy expenditure of patients with cystic fibrosis. | Q52587678 | ||
Efficacy of aerosolized tobramycin in patients with cystic fibrosis. | Q54237890 | ||
Cystic fibrosis and nesidioblastosis. | Q54268879 | ||
Steatorrhea and azotorrhea and their relation to growth and nutrition in adolescents and young adults with cystic fibrosis. | Q54396956 | ||
Opsonophagocytic killing antibody to Pseudomonas aeruginosa mucoid exopolysaccharide in older noncolonized patients with cystic fibrosis. | Q54400222 | ||
Ceftazidime monotherapy vs. combined therapy in Pseudomonas pulmonary infections in cystic fibrosis. | Q54404421 | ||
Bronchial reactivity in cystic fibrosis | Q54587132 | ||
Bronchial Lability in Children Suffering from Some Diseases of the Bronchi | Q54630795 | ||
Cystic fibrosis locus defined by a genetically linked polymorphic DNA marker. | Q55060411 | ||
Cystic fibrosis: the new genetics. | Q55241687 | ||
Evaluation of the forced expiration technique as an adjunct to postural drainage in treatment of cystic fibrosis | Q56689287 | ||
In vivo cell-specific expression of the cystic fibrosis transmembrane conductance regulator | Q59094520 | ||
Symptomatic hepatic disease in cystic fibrosis: incidence, course, and outcome of portal systemic hunting | Q66883217 | ||
Tracheal mucociliary transport in patients with cystic fibrosis and its stimulation by terbutaline | Q66940211 | ||
Pulmonary function tests | Q66947761 | ||
Acute pulmonary exacerbations in cystic fibrosis. A double-blind trial of tobramycin and placebo therapy | Q67252347 | ||
Reduction of sputum Pseudomonas aeruginosa density by antibiotics improves lung function in cystic fibrosis more than do bronchodilators and chest physiotherapy alone | Q67285211 | ||
25-Hydroxycholecalciferol levels in patients with cystic fibrosis | Q67463336 | ||
Prediction of Mortality in Patients with Cystic Fibrosis | Q67469870 | ||
Cystic fibrosis | Q67485363 | ||
Cystic fibrosis: beyond the gene to therapy | Q67532177 | ||
Maximal exercise testing in single and double lung transplant recipients | Q67730745 | ||
Bulging fontanelle as presenting sign in cystic fibrosis. Vitamin A metabolism and effect on cerebrospinal fluid pressure | Q67875153 | ||
Activation by extracellular nucleotides of chloride secretion in the airway epithelia of patients with cystic fibrosis | Q67922336 | ||
Cystic fibrosis gene mutation in two sisters with mild disease and normal sweat electrolyte levels | Q68048707 | ||
Role of mechanical injury on airway surface in the pathogenesis of Pseudomonas aeruginosa | Q68060123 | ||
P433 | issue | 5 | |
P304 | page(s) | 251-270 | |
P577 | publication date | 1994-01-01 | |
P1433 | published in | Lung | Q15765075 |
P1476 | title | Cystic fibrosis | |
P478 | volume | 172 |
Q38059441 | Adaptation of Pseudomonas aeruginosa to the cystic fibrosis airway: an evolutionary perspective |
Q40362563 | Carbon Sources Tune Antibiotic Susceptibility in Pseudomonas aeruginosa via Tricarboxylic Acid Cycle Control |
Q41702023 | Cystic fibrosis. An overview |
Q45088980 | Effects of creatine supplementation in cystic fibrosis: results of a pilot study. |
Q77354919 | Lung transplantation for cystic fibrosis--a single center experience over 8 years |
Q29615286 | Microbial pathogenesis in cystic fibrosis: mucoid Pseudomonas aeruginosa and Burkholderia cepacia |
Q24798231 | Modulation of epithelial sodium channel (ENaC) expression in mouse lung infected with Pseudomonas aeruginosa |
Q77803126 | Rheumatologic manifestations of gastrointestinal diseases |
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