Cystic fibrosis

scientific article published on 01 January 1994

Cystic fibrosis is …
instance of (P31):
review articleQ7318358
scholarly articleQ13442814

External links are
P356DOI10.1007/BF00164308
P698PubMed publication ID7934150

P2093author name stringM R Bye
L M Quittell
J M Ewig
P2860cites workIdentification of the cystic fibrosis gene: chromosome walking and jumpingQ22299423
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Frequent antibiotic therapy improves survival of cystic fibrosis patients with chronic Pseudomonas aeruginosa infectionQ34056063
The relation between genotype and phenotype in cystic fibrosis--analysis of the most common mutation (delta F508).Q34635892
Effects of an artificial diet on growth of patients with cystic fibrosisQ34987384
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Cystic fibrosis: physical exercise versus chest physiotherapyQ35116187
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Linkage disequilibrium, cystic fibrosis, and genetic counselingQ35247199
A preliminary study of aerosolized recombinant human deoxyribonuclease I in the treatment of cystic fibrosisQ68062090
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Person-to-person transmission of Pseudomonas cepacia between patients with cystic fibrosisQ68160610
Randomized trial of ceftazidime versus placebo in the management of acute respiratory exacerbations in patients with cystic fibrosisQ68205329
Antibiotic treatment. Aerosol therapyQ68449084
A pilot study of aerosolized amiloride for the treatment of lung disease in cystic fibrosisQ68455772
Effect of Pseudomonas cepacia colonization on survival and pulmonary function of cystic fibrosis patientsQ68709409
Longitudinal response of pulmonary function to bronchodilators in cystic fibrosisQ68917024
Total respiratory system compliance in asymptomatic infants with cystic fibrosisQ69011260
What is a "pulmonary exacerbation" in cystic fibrosis?Q69449682
Autogenic drainage: a modern approach to physiotherapy in cystic fibrosisQ69503724
Pseudomonas cepacia: decrease in colonization in patients with cystic fibrosisQ69634656
Relative effects of bronchial drainage and exercise for in-hospital care of patients with cystic fibrosisQ69658541
Vitamin D metabolites in adolescents and young adults with cystic fibrosis: effects of sun and seasonQ69863974
Glucose intolerance in cystic fibrosisQ69881895
Prenatal diagnosis of cystic fibrosisQ69906611
Bronchodilators increase airway instability in cystic fibrosisQ70102881
Effect of heart-lung transplantation on airway potential difference in patients with and without cystic fibrosisQ70146668
Evaluation of the PEP mask in cystic fibrosisQ70149023
A double-blind controlled trial of anti-Pseudomonas chemotherapy of acute respiratory exacerbations in patients with cystic fibrosisQ70161420
Chest physiotherapy: a reviewQ70246490
Improved respiratory prognosis in patients with cystic fibrosis with normal fat absorptionQ70375628
Pneumothorax in cystic fibrosis: management and outcomeQ70375632
Blood and Liver Concentrations of Vitamins A and E in Children with Cystic Fibrosis of the PancreasQ70424782
Short-term pulmonary effects of total parenteral nutrition in children with cystic fibrosisQ70476049
Hemorrhagic Diathesis and Cystic Fibrosis in InfancyQ70512265
The changing epidemiology of cystic fibrosisQ70528025
125I-Clq-binding and specific antibodies as indicators of pulmonary disease activity in cystic fibrosisQ70832473
Bronchial Reactivity in Cystic Fibrosis With Normal Pulmonary FunctionQ70930682
Increased bioelectric potential difference across respiratory epithelia in cystic fibrosisQ70982010
Immediate and long-term effects of chest physiotherapy in patients with cystic fibrosisQ71044361
Hemoglobin desaturation: its occurrence during sleep in patients with cystic fibrosisQ71286854
Cough versus chest physiotherapy. A comparison of the acute effects on pulmonary function in patients with cystic fibrosisQ71288373
Improved growth and clinical, nutritional, and respiratory changes in response to nutritional therapy in cystic fibrosisQ71515779
Liver function studies and biliary tract investigations in mucoviscidosis. r58 C/*539-44* A/Feigelson J, Pecau Y, Sauvegrain J: Liver function studies and biliary tract investigations in mucoviscidosisQ71533158
Mucoid Escherichia coli in cystic fibrosisQ71548190
Intussusception in patients with cystic fibrosisQ71800148
Energy needs and growth in children with cystic fibrosisQ71833057
Flow-volume curves in infants with lung diseaseQ71838542
Insulin receptors in cystic fibrosis: increased receptor number and altered affinityQ72130919
Complications of Cystic FibrosisQ72417419
Cystic fibrosis with extensive fat replacement of the liverQ72875038
A distinctive type of biliary cirrhosis of the liver associated with cystic fibrosis of the pancreas; recognition through signs of portal hypertensionQ74221452
THE INTESTINAL LESIONS IN CYSTIC FIBROSIS OF THE PANCREASQ76555898
Therapy and prognosis of fibrocystic disease of the pancreasQ80317879
A longitudinal study of bronchodilator responsiveness in cystic fibrosisQ93566031
DNA marker haplotype association with pancreatic sufficiency in cystic fibrosisQ35248559
Cystic fibrosis: molecular biology and therapeutic implicationsQ35319385
Drug therapy in the 1990s. What can we expect for cystic fibrosis?Q35323845
Physical activity and self treatment in cystic fibrosisQ35602842
Modulation of airway inflammation in cystic fibrosis. In vivo suppression of interleukin-8 levels on the respiratory epithelial surface by aerosolization of recombinant secretory leukoprotease inhibitorQ35606533
Is cough as effective as chest physiotherapy in the removal of excessive tracheobronchial secretions?Q36474369
Clinical significance of Staphylococcus aureus in cystic fibrosisQ37808887
Pathogenesis of the pseudomonas lung lesion in cystic fibrosisQ38227182
Diagnosis of genetic disorders at the DNA levelQ38597743
Why is the cystic fibrosis gene so frequent?Q38749495
Genetic counseling using linked DNA probes: cystic fibrosis as a prototypeQ39542099
Pharmacokinetics of antimicrobial drugs in cystic fibrosis. Aminoglycoside antibioticsQ39654167
Antibacterial therapy in cystic fibrosis. A review of the literature published between 1980 and February 1987.Q39654171
Antimicrobial therapy against Staphylococcus aureus, Pseudomonas aeruginosa, and Pseudomonas cepaciaQ39654175
Pseudomonas cepacia: biology, mechanisms of virulence, epidemiologyQ39732190
Infection in patients with cystic fibrosisQ39740286
Cystic fibrosis and malnutritionQ39803118
Nutrition and chronic lung diseaseQ39836460
Pulmonary disease associated with Pseudomonas aeruginosa in cystic fibrosis: current status of the host-bacterium interactionQ39846012
Meconium in health and in diseaseQ39855990
Vitamin E and the biological antioxidant theoryQ40012988
The cardiovascular system in cystic fibrosis.Q40245542
Gastrointestinal manifestations of cystic fibrosis: a reviewQ40316357
Liver involvement in cystic fibrosis. A report of 9 casesQ40343629
Production of the Pseudomonas aeruginosa neuraminidase is increased under hyperosmolar conditions and is regulated by genes involved in alginate expressionQ40343721
Clinical management of pulmonary disease in cystic fibrosisQ40709266
Antibiotic therapy in cystic fibrosis: evaluation of clinical trialsQ40808575
Pseudomonas cepacia infection in cystic fibrosis: an emerging problemQ40829590
Intravenous linoleic acid supplementation in children with cystic fibrosisQ41086734
Comparative trial of manual and mechanical percussion technique with gravity-assisted bronchial drainage in patients with cystic fibrosisQ41103826
Gallbladder disease in cystic fibrosisQ41362386
In vivo transfer of the human cystic fibrosis transmembrane conductance regulator gene to the airway epitheliumQ41644008
Defective acidification of intracellular organelles in cystic fibrosisQ41675496
Hepatic cirrhosis associated with fibrocystic disease of the pancreas; clinical and pathological reports of five patientsQ41706387
Diabetic microangiopathy in patients with cystic fibrosisQ41767672
Management of esophageal varices in children by injection sclerotherapyQ42252779
Outcome after Liver Transplantation for Cystic Fibrosis.Q42738933
Effect of chest physiotherapy on the removal of mucus in patients with cystic fibrosisQ43324799
The management of portal hypertension in cystic fibrosisQ43537479
Early bacteriologic, immunologic, and clinical courses of young infants with cystic fibrosis identified by neonatal screeningQ43602127
Demonstration That CFTR Is a Chloride Channel by Alteration of Its Anion SelectivityQ43847410
Is anti-Pseudomonas therapy warranted in acute respiratory exacerbations in children with cystic fibrosis?Q44379999
Pseudomonas cepacia colonization in patients with cystic fibrosis: risk factors and clinical outcomeQ44445035
Survival and quality of life of cystic fibrosis patients before and after heart-lung transplantationQ44458955
Mutation analysis for heterozygote detection and the prenatal diagnosis of cystic fibrosisQ44646906
Progression of cystic fibrosis lung disease as a function of serum immunoglobulin G levels: a 5-year longitudinal studyQ44749384
Orthotopic liver transplantation in patients with cystic fibrosisQ45177885
Bronchial hyperreactivity in cystic fibrosis and asthmaQ45851071
Comparison of oxygen desaturation during sleep and exercise in patients with cystic fibrosisQ48900021
Ventilation and oxygenation changes during sleep in cystic fibrosisQ49103733
Role of conventional physiotherapy in cystic fibrosis.Q50563978
Insulin and glucagon response to arginine infusion in cystic fibrosisQ51668061
Cystic fibrosis in the mouse by targeted insertional mutagenesisQ52477870
Energy expenditure of patients with cystic fibrosis.Q52587678
Efficacy of aerosolized tobramycin in patients with cystic fibrosis.Q54237890
Cystic fibrosis and nesidioblastosis.Q54268879
Steatorrhea and azotorrhea and their relation to growth and nutrition in adolescents and young adults with cystic fibrosis.Q54396956
Opsonophagocytic killing antibody to Pseudomonas aeruginosa mucoid exopolysaccharide in older noncolonized patients with cystic fibrosis.Q54400222
Ceftazidime monotherapy vs. combined therapy in Pseudomonas pulmonary infections in cystic fibrosis.Q54404421
Bronchial reactivity in cystic fibrosisQ54587132
Bronchial Lability in Children Suffering from Some Diseases of the BronchiQ54630795
Cystic fibrosis locus defined by a genetically linked polymorphic DNA marker.Q55060411
Cystic fibrosis: the new genetics.Q55241687
Evaluation of the forced expiration technique as an adjunct to postural drainage in treatment of cystic fibrosisQ56689287
In vivo cell-specific expression of the cystic fibrosis transmembrane conductance regulatorQ59094520
Symptomatic hepatic disease in cystic fibrosis: incidence, course, and outcome of portal systemic huntingQ66883217
Tracheal mucociliary transport in patients with cystic fibrosis and its stimulation by terbutalineQ66940211
Pulmonary function testsQ66947761
Acute pulmonary exacerbations in cystic fibrosis. A double-blind trial of tobramycin and placebo therapyQ67252347
Reduction of sputum Pseudomonas aeruginosa density by antibiotics improves lung function in cystic fibrosis more than do bronchodilators and chest physiotherapy aloneQ67285211
25-Hydroxycholecalciferol levels in patients with cystic fibrosisQ67463336
Prediction of Mortality in Patients with Cystic FibrosisQ67469870
Cystic fibrosisQ67485363
Cystic fibrosis: beyond the gene to therapyQ67532177
Maximal exercise testing in single and double lung transplant recipientsQ67730745
Bulging fontanelle as presenting sign in cystic fibrosis. Vitamin A metabolism and effect on cerebrospinal fluid pressureQ67875153
Activation by extracellular nucleotides of chloride secretion in the airway epithelia of patients with cystic fibrosisQ67922336
Cystic fibrosis gene mutation in two sisters with mild disease and normal sweat electrolyte levelsQ68048707
Role of mechanical injury on airway surface in the pathogenesis of Pseudomonas aeruginosaQ68060123
P433issue5
P304page(s)251-270
P577publication date1994-01-01
P1433published inLungQ15765075
P1476titleCystic fibrosis
P478volume172

Reverse relations

cites work (P2860)
Q38059441Adaptation of Pseudomonas aeruginosa to the cystic fibrosis airway: an evolutionary perspective
Q40362563Carbon Sources Tune Antibiotic Susceptibility in Pseudomonas aeruginosa via Tricarboxylic Acid Cycle Control
Q41702023Cystic fibrosis. An overview
Q45088980Effects of creatine supplementation in cystic fibrosis: results of a pilot study.
Q77354919Lung transplantation for cystic fibrosis--a single center experience over 8 years
Q29615286Microbial pathogenesis in cystic fibrosis: mucoid Pseudomonas aeruginosa and Burkholderia cepacia
Q24798231Modulation of epithelial sodium channel (ENaC) expression in mouse lung infected with Pseudomonas aeruginosa
Q77803126Rheumatologic manifestations of gastrointestinal diseases

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