Lung transplantation for treatment of infants with surfactant protein B deficiency

scientific article published on 01 February 1997

Lung transplantation for treatment of infants with surfactant protein B deficiency is …
instance of (P31):
scholarly articleQ13442814

External links are
P356DOI10.1016/S0022-3476(97)70348-2
P698PubMed publication ID9042125

P2093author name stringR Nelson
H R Colten
L P Dehner
F S Cole
D E deMello
T L Spray
C B Huddleston
G B Mallory
M Moxley
A Hamvas
L M Nogee
A August
P2860cites workA mutation in the surfactant protein B gene responsible for fatal neonatal respiratory disease in multiple kindredsQ24605337
Tricine-sodium dodecyl sulfate-polyacrylamide gel electrophoresis for the separation of proteins in the range from 1 to 100 kDaQ27861105
Targeted disruption of the surfactant protein B gene disrupts surfactant homeostasis, causing respiratory failure in newborn miceQ34008084
Surfactant chemical composition and biophysical activity in acute respiratory distress syndromeQ34214892
Cystic fibrosis: molecular biology and therapeutic implicationsQ35319385
Pulsating bubble technique for evaluating pulmonary surfactantQ36573848
Bilateral pneumectomy (volume reduction) for chronic obstructive pulmonary diseaseQ39478667
Clinical implications of gene therapy for alpha 1-antitrypsin deficiencyQ40583934
Recent advances in the treatment of cystic fibrosis.Q40758807
A prospective, multicenter, randomized study of high versus low positive end-expiratory pressure during extracorporeal membrane oxygenation.Q41141869
Experimental neonatal respiratory failure induced by a monoclonal antibody to the hydrophobic surfactant-associated protein SP-B.Q41665986
Pulmonary mechanics in normal infants and young children during first 5 years of life.Q54400582
Surface properties in relation to atelectasis and hyaline membrane disease.Q55037269
Radiographically Determined Lung Volumes at Full Inspiration and During Dynamic Forced Expiration in Normal SubjectsQ66913422
Exogenous porcine surfactant (Curosurf) is inactivated by monoclonal antibody to the surfactant-associated hydrophobic protein SP-BQ67572646
Effects of high-frequency and conventional ventilation on the premature lamb lungQ69805621
Brief report: deficiency of pulmonary surfactant protein B in congenital alveolar proteinosisQ70532435
Pulmonary surfactant therapyQ70580675
Molecular and phenotypic variability in the congenital alveolar proteinosis syndrome associated with inherited surfactant protein B deficiencyQ72038236
Surfactant protein B deficiency: antenatal diagnosis and prospective treatment with surfactant replacementQ72153339
Estimation of total lung capacity from chest radiography and chest CT in children: comparison with body plethysmographyQ72324092
Surfactant protein B deficiency: radiographic manifestationsQ72588416
Bilateral pulmonary lobe transplantation: left lower and right middle and lower lobesQ72703421
Experience with pediatric lung transplantationQ72757074
Forced expiratory flows and lung volumes in normal infantsQ72845429
P433issue2
P407language of work or nameEnglishQ1860
P921main subjectlung transplantQ1637912
P304page(s)231-239
P577publication date1997-02-01
P1433published inThe Journal of PediatricsQ7743611
P1476titleLung transplantation for treatment of infants with surfactant protein B deficiency
P478volume130

Reverse relations

cites work (P2860)
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Q37230260Animal-derived surfactants for the treatment and prevention of neonatal respiratory distress syndrome: summary of clinical trials
Q59316801Design of Surfactant Protein B Peptide Mimics Based on the Saposin Fold for Synthetic Lung Surfactants
Q45868535Featured Article: Electroporation-mediated gene delivery of surfactant protein B (SP-B) restores expression and improves survival in mouse model of SP-B deficiency
Q38990551Gene Editing and Genetic Lung Disease. Basic Research Meets Therapeutic Application
Q95823976Gene therapy of beta(c)-deficient pulmonary alveolar proteinosis (beta(c)-PAP): studies in a murine in vivo model
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Q28235256Genetic disorders of surfactant dysfunction
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Q38641141Modified mRNA as a new therapeutic option for pediatric respiratory diseases and hemoglobinopathies
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