| scholarly article | Q13442814 |
| P6179 | Dimensions Publication ID | 1024977982 |
| P356 | DOI | 10.1023/A:1005303008439 |
| P698 | PubMed publication ID | 9266394 |
| P2093 | author name string | E Agsteribbe | |
| A Ribes | |||
| M A Vilaseca | |||
| A Huckriede | |||
| M Lluch | |||
| P Briones | |||
| A Vernet | |||
| V Cusi | |||
| P2860 | cites work | Protein measurement with the Folin phenol reagent | Q20900776 |
| Mitochondrial heat-shock protein hsp60 is essential for assembly of proteins imported into yeast mitochondria | Q27933539 | ||
| Homologous plant and bacterial proteins chaperone oligomeric protein assembly | Q28283580 | ||
| Pyruvate Carboxylase Deficiency and Lactic Acidosis in a Retarded Child without Leigh's Disease | Q28322389 | ||
| Confocal scanning laser microscopy of mitochondria: a possible tool in the diagnosis of mitochondrial disorders | Q33350458 | ||
| mtDNA depletion with variable tissue expression: a novel genetic abnormality in mitochondrial diseases | Q35196481 | ||
| Defects of mitochondrial DNA | Q35243825 | ||
| Molecular basis of mitochondrial DNA disease | Q40697787 | ||
| Problems with the biochemical diagnosis in mitochondrial (encephalo-)myopathies | Q40881676 | ||
| An electron-transport system associated with the outer membrane of liver mitochondria. A biochemical and morphological study | Q41093578 | ||
| "Cerebral" lactic acidosis: defects in pyruvate metabolism with profound brain damage and minimal systemic acidosis | Q41932603 | ||
| Neuropathology in cerebral lactic acidosis | Q41933108 | ||
| Fatal combined defects in mitochondrial multienzyme complexes in two siblings | Q42452012 | ||
| Variable clinical presentation in patients with defective E1 component of pyruvate dehydrogenase complex | Q42512207 | ||
| The action of digitonin on rat liver mitochondria. The effects on enzyme content | Q42952875 | ||
| A fatal, systemic mitochondrial disease with decreased mitochondrial enzyme activities, abnormal ultrastructure of the mitochondria and deficiency of heat shock protein 60. | Q48282492 | ||
| Pyruvate dehydrogenase deficiency: clinical and biochemical diagnosis | Q48294586 | ||
| Clinical and biochemical findings in a Spanish boy with primary carnitine deficiency | Q60746362 | ||
| Significance of bound glutarate in the diagnosis of glutaric aciduria type I | Q67560162 | ||
| Mitochondrial myopathy of childhood associated with depletion of mitochondrial DNA | Q67739362 | ||
| Combined deficiencies of the pyruvate dehydrogenase complex and enzymes of the respiratory chain in mitochondrial myopathies | Q68147084 | ||
| Mitochondrial myopathies: multiple enzyme defects in the respiratory chain | Q69256496 | ||
| A fourth case of fumarase deficiency | Q69267923 | ||
| Rapid differential diagnosis of carboxylase deficiencies and evaluation for biotin-responsiveness in a single blood sample | Q69938799 | ||
| Benign infantile mitochondrial myopathy due to reversible cytochrome c oxidase deficiency | Q70167731 | ||
| Revised assays for the investigation of congenital lactic acidosis using 14C keto acids, eliminating problems associated with spontaneous decarboxylation | Q70451269 | ||
| The genetic heterogeneity of lactic acidosis: occurrence of recognizable inborn errors of metabolism in pediatric population with lactic acidosis | Q71519179 | ||
| Morphology of the mitochondria in heat shock protein 60 deficient fibroblasts from mitochondrial myopathy patients. Effects of stress conditions | Q71796194 | ||
| Multiple respiratory chain abnormalities associated with hypertrophic cardiomyopathy and 3-methylglutaconic aciduria | Q72097479 | ||
| Decreased synthesis and inefficient mitochondrial import of hsp60 in a patient with a mitochondrial encephalomyopathy | Q72872918 | ||
| P433 | issue | 4 | |
| P304 | page(s) | 569-577 | |
| P577 | publication date | 1997-08-01 | |
| P1433 | published in | Journal of Inherited Metabolic Disease | Q6295359 |
| P1476 | title | A new case of multiple mitochondrial enzyme deficiencies with decreased amount of heat shock protein 60 | |
| P478 | volume | 20 |
| Q52100796 | Chaperonin 60 and mitochondrial disease in Dictyostelium. |
| Q33919004 | Chaperonins in disease: mechanisms, models, and treatments |
| Q27334016 | Cytosolic Hsp60 is involved in the NF-kappaB-dependent survival of cancer cells via IKK regulation |
| Q34623673 | Electron transport chain defects in heart failure |
| Q37170909 | Expression of heat shock protein 60 in the tissues of transported piglets |
| Q49994173 | Folding and assembly defects of pyruvate dehydrogenase deficiency-related variants in the E1α subunit of the pyruvate dehydrogenase complex |
| Q35561244 | Gastrointestinal manifestations of mitochondrial disease |
| Q34911441 | Heat shock proteins modulate keloid formation |
| Q28192185 | Laboratory approach to mitochondrial diseases |
| Q53493404 | Lethal hepatopathy and leukodystrophy caused by a novel mutation in MPV17 gene: description of an alternative MPV17 spliced form. |
| Q44117703 | Mitochondrial Hsp60, resistance to oxidative stress, and the labile iron pool are closely connected in Saccharomyces cerevisiae |
| Q36921749 | Mitochondrial biology and disease in Dictyostelium. |
| Q36735868 | Mitochondrial protein import and human health and disease |
| Q33832717 | Mitochondrial respiratory chain disorders II: neurodegenerative disorders and nuclear gene defects |
| Q81591752 | Molecular genetics of a patient with Mohr-Tranebjaerg Syndrome due to a new mutation in the DDP1 gene |
| Q33637035 | Neonatal presentations of mitochondrial metabolic disorders |
| Q34703664 | On the brotherhood of the mitochondrial chaperones mortalin and heat shock protein 60. |
| Q73179201 | Oxygen consumption measurement in lymphocytes for the diagnosis of pediatric patients with oxidative phosphorylation diseases |
| Q41563175 | Preparation of Rat Gingival Mitochondria with an Improved Isolation Method |
| Q63544601 | Single-nucleotide variations in the genes encoding the mitochondrial Hsp60/Hsp10 chaperone system and their disease-causing potential |
| Q92130320 | Structural basis for active single and double ring complexes in human mitochondrial Hsp60-Hsp10 chaperonin |
| Q30621145 | Temperature tolerance of different larval stages of the spider crab Hyas araneus exposed to elevated seawater PCO2. |
| Q34388771 | The yeast connection to Friedreich ataxia. |
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