Neonatal bone marrow transplantation prevents liver disease in a murine model of erythropoietic protoporphyria

scientific article published on October 23, 2010

Neonatal bone marrow transplantation prevents liver disease in a murine model of erythropoietic protoporphyria is …
instance of (P31):
scholarly articleQ13442814

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P356DOI10.1016/J.JHEP.2010.09.029
P953full work available online athttps://api.elsevier.com/content/article/PII:S0168827810009384?httpAccept=text/plain
https://api.elsevier.com/content/article/PII:S0168827810009384?httpAccept=text/xml
P698PubMed publication ID21145811

P50authorFrançois Moreau-GaudryQ91253887
P2093author name stringNicolas Petit
Hubert de Verneuil
Pierre Dubus
Yann Duchartre
Emmanuel Richard
Magalie Lalanne
Corrine Moya
P2860cites workLiver disease in erythropoietic protoporphyria: insights and implications for managementQ36759851
Gene therapy of a mouse model of protoporphyria with a self-inactivating erythroid-specific lentiviral vector without preselection.Q40775938
Long-term cure of the photosensitivity of murine erythropoietic protoporphyria by preselective gene therapyQ45859178
Low-dose busulphan conditioning and neonatal stem cell transplantation preserves vision and restores hematopoiesis in severe murine osteopetrosisQ45882047
Bone marrow-derived cells promote liver regeneration in mice with erythropoietic protoporphyriaQ50572244
A novel method of myeloablation to enhance engraftment of adult bone marrow cells in newborn miceQ73266655
Biliary fibrosis associated with altered bile composition in a mouse model of erythropoietic protoporphyriaQ78177007
Liver pathology and hepatocarcinogenesis in a long-term mouse model of erythropoietic protoporphyriaQ78813037
Prevention of murine erythropoietic protoporphyria-associated skin photosensitivity and liver disease by dermal and hepatic ferrochelataseQ81283806
A mouse model provides evidence that genetic background modulates anemia and liver injury in erythropoietic protoporphyriaQ81333559
The role for BMT in erythropoietic protoporphyriaQ84068700
C-terminal deletions in the ALAS2 gene lead to gain of function and cause X-linked dominant protoporphyria without anemia or iron overloadQ24642289
Erythropoietic porphyrias: animal models and update in gene-based therapiesQ28282994
Erythropoietic protoporphyria in the house mouse. A recessive inherited ferrochelatase deficiency with anemia, photosensitivity, and liver diseaseQ28586627
Reversion of hepatobiliary alterations By bone marrow transplantation in a murine model of erythropoietic protoporphyriaQ33180600
Liver transplantation for erythropoietic protoporphyria liver disease.Q34562963
Sequential liver and bone marrow transplantation for treatment of erythropoietic protoporphyriaQ34572228
Erythropoiesis and iron metabolism in dominant erythropoietic protoporphyriaQ34680002
Curative bone marrow transplantation in erythropoietic protoporphyria after reversal of severe cholestasis.Q36656649
P433issue1
P407language of work or nameEnglishQ1860
P921main subjecterythropoietic protoporphyriaQ1759600
murine modelQ122890741
P304page(s)162-170
P577publication date2010-10-23
P1433published inJournal of HepatologyQ15724402
P1476titleNeonatal bone marrow transplantation prevents liver disease in a murine model of erythropoietic protoporphyria
P478volume55