| P50 | author | Guilhian Leipnitz | Q73319960 |
| | Moacir Wajner | Q89163680 |
| P2093 | author name string | Angela T S Wyse | |
| | Mateus Grings | |
| P2860 | cites work | Oxidative Stress. | Q51036370 |
| | A selective defect of cytochrome c oxidase is present in brain of Alzheimer disease patients. | Q53341470 |
| | Molybdenum cofactor deficiency: Identification of a patient with homozygote mutation in the MOCS3 gene. | Q53742775 |
| | Species differences in the effects of bezafibrate as a potential treatment of mitochondrial disorders. | Q54544721 |
| | Direct detection of the sulfur trioxide radical anion during the horseradish peroxidase-hydrogen peroxide oxidation of sulfite (aqueous sulfur dioxide) | Q67259975 |
| | Sulfoxide formation from methionine or its sulfide analogs during aerobic oxidation of sulfite | Q71593785 |
| | Oxygen-mediated reaction between 4-thiouracil derivatives and bisulfite. Isolation and characterization of 1-methyluracil 4-thiosulfate as an intermediate in the formation of 1-methyluracil-4-sulfonate | Q71779344 |
| | A method for the complete S sulfonation of cysteine residues in proteins | Q72162431 |
| | Determination of total serum sulfite by HPLC with fluorescence detection | Q72281036 |
| | Oxygen-catalyzed reaction between 4-thiouridine and sodium sulfite | Q72467673 |
| | Dietary therapy in two patients with a mild form of sulphite oxidase deficiency. Evidence for clinical and biological improvement | Q73464412 |
| | Activation of methionine for transmethylation. V. The mechanism of action of the methionine-activating enzyme | Q79027744 |
| | Reactive species and antioxidants. Redox biology is a fundamental theme of aerobic life | Q83947097 |
| | Human sulfide:quinone oxidoreductase catalyzes the first step in hydrogen sulfide metabolism and produces a sulfane sulfur metabolite | Q24294580 |
| | Mutations in the molybdenum cofactor biosynthetic genesMOCS1, MOCS2, andGEPH | Q24302091 |
| | Sulfite oxidizing enzymes | Q24681539 |
| | The rise of mitochondria in medicine | Q26740014 |
| | New insights into PGC-1 coactivators: redefining their role in the regulation of mitochondrial function and beyond | Q26996576 |
| | Targeting Mitochondria and Reactive Oxygen Species-Driven Pathogenesis in Diabetic Nephropathy | Q28083205 |
| | Isolated sulfite oxidase deficiency: a case report with a novel mutation and review of the literature | Q28270461 |
| | Sulfite Oxidase Activity of Cytochrome c: Role of Hydrogen Peroxide | Q28397283 |
| | A mechanism of sulfite neurotoxicity: direct inhibition of glutamate dehydrogenase | Q28565525 |
| | Free-radical chemistry of sulfite | Q28767716 |
| | The importance of dendritic mitochondria in the morphogenesis and plasticity of spines and synapses | Q29615239 |
| | Oxidative risk for atherothrombotic cardiovascular disease | Q33554184 |
| | Mitochondria and neuronal survival | Q33807218 |
| | Neuroprotective strategies for basal ganglia degeneration: Parkinson's and Huntington's diseases | Q33851629 |
| | A compound heterozygote case of isolated sulfite oxidase deficiency | Q33885230 |
| | Neonatal astrocyte damage is sufficient to trigger progressive striatal degeneration in a rat model of glutaric acidemia-I. | Q33941133 |
| | Molybdenum cofactor biosynthesis and deficiency | Q33991147 |
| | Molybdenum cofactors, enzymes and pathways | Q34018919 |
| | Methionine metabolism in mammals | Q34366989 |
| | The pro-oxidant chromium(VI) inhibits mitochondrial complex I, complex II, and aconitase in the bronchial epithelium: EPR markers for Fe–S proteins | Q34423686 |
| | Mitochondrial dysfunction and molecular pathways of disease | Q34604563 |
| | Transcriptional control of mitochondrial biogenesis: the central role of PGC-1alpha. | Q34773068 |
| | Infantile isolated sulphite oxidase deficiency in a Chinese family: a rare neurodegenerative disorder | Q34777031 |
| | Mitochondrial aconitase knockdown attenuates paraquat-induced dopaminergic cell death via decreased cellular metabolism and release of iron and H₂O₂. | Q35240549 |
| | Pharmacologic activation of mitochondrial biogenesis exerts widespread beneficial effects in a transgenic mouse model of Huntington's disease | Q35750228 |
| | The role of oxidative damage in the neuropathology of organic acidurias: insights from animal studies. | Q35859776 |
| | Dysfunctional astrocytes as key players in the pathogenesis of central nervous system disorders. | Q36970752 |
| | Molybdenum cofactor and isolated sulphite oxidase deficiencies: Clinical and molecular spectrum among Egyptian patients | Q37194386 |
| | S100B's double life: intracellular regulator and extracellular signal. | Q37358604 |
| | Mechanism of sulfite cytotoxicity in isolated rat hepatocytes | Q46519632 |
| | Hypoxanthine Intrastriatal Administration Alters Neuroinflammatory Profile and Redox Status in Striatum of Infant and Young Adult Rats. | Q46573970 |
| | 1,25-Dihydroxyvitamin D3 exerts neuroprotective effects in an ex vivo model of mild hyperhomocysteinemia | Q46625114 |
| | Isolated sulfite oxidase deficiency: MR imaging features | Q46702731 |
| | Sulfite increases lipoperoxidation and decreases the activity of catalase in brain of rats | Q46885732 |
| | Effect of sulfite treatment on total antioxidant capacity, total oxidant status, lipid hydroperoxide, and total free sulfydryl groups contents in normal and sulfite oxidase-deficient rat plasma | Q47636492 |
| | Evaluation of mitochondrial bioenergetics, dynamics, endoplasmic reticulum-mitochondria crosstalk, and reactive oxygen species in fibroblasts from patients with complex I deficiency. | Q47653326 |
| | Age-related alterations in antioxidant enzymes, lipid peroxide levels, and somatosensory-evoked potentials: effect of sulfur dioxide | Q48099474 |
| | Effect of ingested sulfite on hippocampus antioxidant enzyme activities in sulfite oxidase competent and deficient rats | Q48114877 |
| | Isolated sulfite oxidase deficiency in the newborn: lactic acidaemia and leukoencephalopathy | Q48118168 |
| | Ions and energy in mammalian brain | Q48133714 |
| | Merit of quinacrine in the decrease of ingested sulfite-induced toxic action in rat brain. | Q48286425 |
| | Autocrine S100B effects on astrocytes are mediated via RAGE. | Q48297630 |
| | The effect of ingested sulfite on visual evoked potentials, lipid peroxidation, and antioxidant status of brain in normal and sulfite oxidase-deficient aged rats | Q48476139 |
| | Regional lipid peroxidation in rat brain in vitro: possible role of endogenous iron | Q48511066 |
| | Higher susceptibility of cerebral cortex and striatum to sulfite neurotoxicity in sulfite oxidase-deficient rats | Q48571386 |
| | Sulfite triggers sustained calcium overload in cultured cortical neurons via a redox-dependent mechanism. | Q48670963 |
| | Prenatal multicystic encephalopathy in isolated sulfite oxidase deficiency with a novel mutaion. | Q48711004 |
| | Effect of physical exercise on changes in activities of creatine kinase, cytochrome c oxidase and ATP levels caused by ovariectomy | Q48785446 |
| | Sulfite disrupts brain mitochondrial energy homeostasis and induces mitochondrial permeability transition pore opening via thiol group modification. | Q48796640 |
| | Bezafibrate prevents mitochondrial dysfunction, antioxidant system disturbance, glial reactivity and neuronal damage induced by sulfite administration in striatum of rats: Implications for a possible therapeutic strategy for sulfite oxidase deficien | Q48799666 |
| | Isolated sulfite oxidase deficiency | Q48835153 |
| | Clinical neuroimaging features and outcome in molybdenum cofactor deficiency | Q48906574 |
| | Severe Hyperhomocysteinemia Decreases Respiratory Enzyme and Na(+)-K(+) ATPase Activities, and Leads to Mitochondrial Alterations in Rat Amygdala | Q49114250 |
| | S100 beta stimulates inducible nitric oxide synthase activity and mRNA levels in rat cortical astrocytes | Q49121692 |
| | Efficacy and safety of cyclic pyranopterin monophosphate substitution in severe molybdenum cofactor deficiency type A: a prospective cohort study. | Q50569035 |
| | Infantile spasms and hyperekplexia associated with isolated sulfite oxidase deficiency. | Q50668615 |
| | Human sulfite oxidase R160Q: identification of the mutation in a sulfite oxidase-deficient patient and expression and characterization of the mutant enzyme. | Q37413075 |
| | Mitochondrial and apoptotic neuronal death signaling pathways in cerebral ischemia. | Q37466054 |
| | Clinical effects of sulphite additives | Q37602203 |
| | Oxidative stress and its role in the pathogenesis of ischaemic stroke | Q37636340 |
| | Turn up the power - pharmacological activation of mitochondrial biogenesis in mouse models. | Q37686240 |
| | Molybdenum cofactor deficiency: Mutations in GPHN, MOCS1, and MOCS2 | Q37804739 |
| | Mitochondrial dysfunction and oxidative stress: a contributing link to acquired epilepsy? | Q37816253 |
| | Regulation of PGC-1α, a nodal regulator of mitochondrial biogenesis | Q37834857 |
| | Behavioral and neurochemical effects of proline | Q37885227 |
| | Molybdenum cofactor deficiency: review of 12 cases (MoCD and review). | Q38057468 |
| | Determination of sulfite with emphasis on biosensing methods: a review | Q38079994 |
| | Sulphite content of Australian pharmaceutical products | Q38139898 |
| | Sulfite-oxidizing enzymes. | Q38254800 |
| | Calcium and mitochondria in the regulation of cell death | Q38496552 |
| | Bioenergetics dysfunction, mitochondrial permeability transition pore opening and lipid peroxidation induced by hydrogen sulfide as relevant pathomechanisms underlying the neurological dysfunction characteristic of ethylmalonic encephalopathy. | Q38721080 |
| | Molybdenum cofactor and human disease. | Q38800902 |
| | Disruption of Energy Transfer and Redox Status by Sulfite in Hippocampus, Striatum, and Cerebellum of Developing Rats. | Q38833299 |
| | Mechanistic basis of hypermethioninemia | Q38910593 |
| | Mitochondrial Ca2+ and regulation of the permeability transition pore | Q38920740 |
| | Bisulfite Modification of Nucleic Acids and their Constituents | Q39078537 |
| | 3-Hydroxy-3-methylglutaric and 3-methylglutaric acids impair redox status and energy production and transfer in rat heart: relevance for the pathophysiology of cardiac dysfunction in 3-hydroxy-3-methylglutaryl-coenzyme A lyase deficiency. | Q39588663 |
| | Sulfites in foods: uses, analytical methods, residues, fate, exposure assessment, metabolism, toxicity, and hypersensitivity. | Q39740229 |
| | In vitro evidence that sulfite impairs glutamatergic neurotransmission and inhibits glutathione metabolism-related enzymes in rat cerebral cortex. | Q41207886 |
| | The isolation of S-sulphoglutathione from the small intestine of the rat | Q42042060 |
| | Sulfite stimulates NADPH oxidase of human neutrophils to produce active oxygen radicals via protein kinase C and Ca2+/calmodulin pathways | Q42288947 |
| | Sulfite-containing pharmaceuticals | Q42365501 |
| | Effect of sulfite on antioxidant enzymes and lipid peroxidation in normal and sulfite oxidase-deficient rat erythrocytes. | Q43008150 |
| | Long-term follow-up of bezafibrate treatment in patients with the myopathic form of carnitine palmitoyltransferase 2 deficiency. | Q43053414 |
| | Successful treatment of molybdenum cofactor deficiency type A with cPMP. | Q43102443 |
| | Functional deficiencies of sulfite oxidase: Differential diagnoses in neonates presenting with intractable seizures and cystic encephalomalacia | Q43269005 |
| | Sulfate anion free radical formation by the peroxidation of (Bi)sulfite and its reaction with hydroxyl radical scavengers | Q43571042 |
| | Destruction of tryptophan during the aerobic oxidation of sulfite ions | Q44112161 |
| | Early features in neuroimaging of two siblings with molybdenum cofactor deficiency | Q44317252 |
| | Sulfite-mediated oxidative stress in kidney cells | Q44724710 |
| | Glycine intracerebroventricular administration disrupts mitochondrial energy homeostasis in cerebral cortex and striatum of young rats. | Q44847548 |
| | Disturbance of brain energy and redox homeostasis provoked by sulfite and thiosulfate: potential pathomechanisms involved in the neuropathology of sulfite oxidase deficiency. | Q45028847 |
| | Effect of sulfite on cognitive function in normal and sulfite oxidase deficient rats | Q45244664 |
| | Sulfite oxidase deficiency--an unusual late and mild presentation | Q45746405 |
| | AMPK Maintains Cellular Metabolic Homeostasis through Regulation of Mitochondrial Reactive Oxygen Species | Q46294749 |
| | Effect of alpha-lipoic acid on visual evoked potentials in rats exposed to sulfite | Q46399589 |
| | The effect of chronic restraint stress and sulfite on visual evoked potentials (VEPs): relation to lipid peroxidation | Q46439936 |
| | Intracerebral Glycine Administration Impairs Energy and Redox Homeostasis and Induces Glial Reactivity in Cerebral Cortex of Newborn Rats | Q46468182 |
| P433 | issue | 2 | |
| P921 | main subject | isolated sulfite oxidase deficiency | Q55782334 |
| P304 | page(s) | 484-494 | |
| P577 | publication date | 2018-12-05 | |
| P1433 | published in | Neurotoxicity Research | Q15764278 |
| P1476 | title | The Role of Oxidative Stress and Bioenergetic Dysfunction in Sulfite Oxidase Deficiency: Insights from Animal Models | |
| P478 | volume | 35 | |