scholarly article | Q13442814 |
P50 | author | Barbara K Smith | Q91933148 |
P2093 | author name string | Barry J Byrne | |
A Daniel Martin | |||
Shannon Allen | |||
Samantha Mays | |||
P2860 | cites work | Clinical features and predictors for disease natural progression in adults with Pompe disease: a nationwide prospective observational study | Q21202855 |
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Practical Recommendations for Diagnosis and Management of Respiratory Muscle Weakness in Late-Onset Pompe Disease | Q28067387 | ||
Multi-ethnic reference values for spirometry for the 3-95-yr age range: the global lung function 2012 equations | Q28389258 | ||
Activation of human respiratory muscles during different voluntary manoeuvres | Q28769549 | ||
Reliability of a commercially available threshold loading device in healthy subjects and in patients with chronic obstructive pulmonary disease | Q33775388 | ||
Effect of training on inspiratory load compensation in weaned and unweaned mechanically ventilated ICU patients | Q34150689 | ||
Survival and associated factors in 268 adults with Pompe disease prior to treatment with enzyme replacement therapy | Q35102705 | ||
Lung MRI and impairment of diaphragmatic function in Pompe disease | Q35595602 | ||
Spinal delivery of AAV vector restores enzyme activity and increases ventilation in Pompe mice | Q35665212 | ||
Stimulation of Respiratory Motor Output and Ventilation in a Murine Model of Pompe Disease by Ampakines | Q36049311 | ||
The natural course of non-classic Pompe's disease; a review of 225 published cases | Q36245480 | ||
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Altered activation of the diaphragm in late-onset Pompe disease | Q36908177 | ||
Phase I/II trial of adeno-associated virus-mediated alpha-glucosidase gene therapy to the diaphragm for chronic respiratory failure in Pompe disease: initial safety and ventilatory outcomes | Q36945774 | ||
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Neural deficits contribute to respiratory insufficiency in Pompe disease | Q37224150 | ||
Reduced Phrenic Motoneuron Recruitment during Sustained Inspiratory Threshold Loading Compared to Single-Breath Loading: A Twitch Interpolation Study | Q37405026 | ||
Sleep-Disordered Breathing and Effects of Noninvasive Ventilation in Patients with Late-Onset Pompe Disease | Q37501141 | ||
Clinical and pathophysiological clues of respiratory dysfunction in late-onset Pompe disease: New insights from a comparative study by MRI and respiratory function assessment | Q38959711 | ||
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Late-onset Pompe disease (LOPD): correlations between respiratory muscles CT and MRI features and pulmonary function. | Q53099318 | ||
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Dynamic magnetic resonance imaging in assessing lung volumes, chest wall, and diaphragm motions in adolescent idiopathic scoliosis versus normal controls | Q80200204 | ||
Analysis of diaphragm movement during tidal breathing and during its activation while breath holding using MRI synchronized with spirometry | Q81663082 | ||
Pulmonary complications of neuromuscular disease: a respiratory mechanics perspective | Q82701404 | ||
Supine volume drop and diaphragmatic function in adults with Pompe disease | Q84268678 | ||
Whole-body muscle MRI in 20 patients suffering from late onset Pompe disease: Involvement patterns | Q84625804 | ||
Assessing Inspiratory Muscle Strength for Early Detection of Respiratory Failure in Motor Neuron Disease: Should We Use MIP, SNIP, or Both? | Q90275700 | ||
The nature of respiratory muscle weakness in patients with late-onset Pompe disease | Q92055749 | ||
Imaging respiratory muscle quality and function in Duchenne muscular dystrophy | Q92216289 | ||
Safety and efficacy of short- and long-term inspiratory muscle training in late-onset Pompe disease (LOPD): a pilot study | Q93084951 | ||
P433 | issue | 1 | |
P304 | page(s) | 19006 | |
P577 | publication date | 2019-12-12 | |
P1433 | published in | Scientific Reports | Q2261792 |
P1476 | title | Dynamic respiratory muscle function in late-onset Pompe disease | |
P478 | volume | 9 |
Q90663985 | The Respiratory Phenotype of Pompe Disease Mouse Models | cites work | P2860 |
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