Dynamic respiratory muscle function in late-onset Pompe disease

scientific article published on 12 December 2019

Dynamic respiratory muscle function in late-onset Pompe disease is …
instance of (P31):
scholarly articleQ13442814

External links are
P356DOI10.1038/S41598-019-54314-8
P932PMC publication ID6908708
P698PubMed publication ID31831753

P50authorBarbara K SmithQ91933148
P2093author name stringBarry J Byrne
A Daniel Martin
Shannon Allen
Samantha Mays
P2860cites workClinical features and predictors for disease natural progression in adults with Pompe disease: a nationwide prospective observational studyQ21202855
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Lung MRI and impairment of diaphragmatic function in Pompe diseaseQ35595602
Spinal delivery of AAV vector restores enzyme activity and increases ventilation in Pompe miceQ35665212
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MRI of the lung (2/3). Why … when … how?Q36347046
Altered activation of the diaphragm in late-onset Pompe diseaseQ36908177
Phase I/II trial of adeno-associated virus-mediated alpha-glucosidase gene therapy to the diaphragm for chronic respiratory failure in Pompe disease: initial safety and ventilatory outcomesQ36945774
Proton magnetic resonance imaging for assessment of lung function and respiratory dynamicsQ36949165
Neural deficits contribute to respiratory insufficiency in Pompe diseaseQ37224150
Reduced Phrenic Motoneuron Recruitment during Sustained Inspiratory Threshold Loading Compared to Single-Breath Loading: A Twitch Interpolation StudyQ37405026
Sleep-Disordered Breathing and Effects of Noninvasive Ventilation in Patients with Late-Onset Pompe DiseaseQ37501141
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Neuropathology in respiratory-related motoneurons in young Pompe (Gaa(-/-)) miceQ39963807
Functional Measurement of Respiratory Muscle Motor Behaviors Using Transdiaphragmatic Pressure.Q41455898
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Semi-Automated Analysis of Diaphragmatic Motion with Dynamic Magnetic Resonance Imaging in Healthy Controls and Non-Ambulant Subjects with Duchenne Muscular Dystrophy.Q49521240
Muscle impairment in neuromuscular disease using an expiratory/inspiratory pressure ratio.Q51666996
Specificity and reversibility of inspiratory muscle training.Q51687817
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A standardized method for the evaluation of respiratory muscle endurance in patients with Duchenne muscular dystrophy.Q52138107
The effects of learning on the ventilatory responses to inspiratory threshold loading.Q52183402
Late-onset Pompe disease (LOPD): correlations between respiratory muscles CT and MRI features and pulmonary function.Q53099318
Evaluation of the THRESHOLD trainer for inspiratory muscle endurance training: comparison with the weighted plunger method.Q53978883
Ventilatory responses to inspiratory threshold loading and role of muscle fatigue in task failure.Q54218505
Postural effects on lung and chest wall volumes in late onset type II glycogenosis patientsQ61943836
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MR analysis of lung volume and thoracic dimensions in patients with emphysema before and after lung volume reduction surgeryQ74272116
Dynamic magnetic resonance imaging in assessing lung volumes, chest wall, and diaphragm motions in adolescent idiopathic scoliosis versus normal controlsQ80200204
Analysis of diaphragm movement during tidal breathing and during its activation while breath holding using MRI synchronized with spirometryQ81663082
Pulmonary complications of neuromuscular disease: a respiratory mechanics perspectiveQ82701404
Supine volume drop and diaphragmatic function in adults with Pompe diseaseQ84268678
Whole-body muscle MRI in 20 patients suffering from late onset Pompe disease: Involvement patternsQ84625804
Assessing Inspiratory Muscle Strength for Early Detection of Respiratory Failure in Motor Neuron Disease: Should We Use MIP, SNIP, or Both?Q90275700
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Imaging respiratory muscle quality and function in Duchenne muscular dystrophyQ92216289
Safety and efficacy of short- and long-term inspiratory muscle training in late-onset Pompe disease (LOPD): a pilot studyQ93084951
P433issue1
P304page(s)19006
P577publication date2019-12-12
P1433published inScientific ReportsQ2261792
P1476titleDynamic respiratory muscle function in late-onset Pompe disease
P478volume9

Reverse relations

Q90663985The Respiratory Phenotype of Pompe Disease Mouse Modelscites workP2860

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