scholarly article | Q13442814 |
P2093 | author name string | Stuart A Sievers | |
Magdalena I Ivanova | |||
Michael R Sawaya | |||
P John Hart | |||
David S Eisenberg | |||
Duane D Winkler | |||
Lisa M Johnson | |||
Ahmad Galaleldeen | |||
Elizabeth L Guenther | |||
P2860 | cites work | Superoxide dismutase 1 and tgSOD1 mouse spinal cord seed fibrils, suggesting a propagative cell death mechanism in amyotrophic lateral sclerosis | Q21136374 |
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Motor neurons in Cu/Zn superoxide dismutase-deficient mice develop normally but exhibit enhanced cell death after axonal injury | Q28511628 | ||
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Structural similarity of wild-type and ALS-mutant superoxide dismutase-1 fibrils using limited proteolysis and atomic force microscopy | Q36991027 | ||
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Extracellular aggregated Cu/Zn superoxide dismutase activates microglia to give a cytotoxic phenotype. | Q39217852 | ||
Fibrillar inclusions and motor neuron degeneration in transgenic mice expressing superoxide dismutase 1 with a disrupted copper-binding site | Q44070818 | ||
Copper-binding-site-null SOD1 causes ALS in transgenic mice: aggregates of non-native SOD1 delineate a common feature | Q44579313 | ||
Familial amyotrophic lateral sclerosis with His46Arg mutation in Cu/Zn superoxide dismutase presenting characteristic clinical features and Lewy body-like hyaline inclusions | Q45090366 | ||
Dissociation of human copper-zinc superoxide dismutase dimers using chaotrope and reductant. Insights into the molecular basis for dimer stability | Q45107835 | ||
Expression of wild-type human superoxide dismutase-1 in mice causes amyotrophic lateral sclerosis | Q48355423 | ||
Clinical and functional investigation of 10 missense mutations and a novel frameshift insertion mutation of the gene for copper-zinc superoxide dismutase in UK families with amyotrophic lateral sclerosis | Q73144671 | ||
P433 | issue | 1 | |
P407 | language of work or name | English | Q1860 |
P921 | main subject | amyotrophic lateral sclerosis | Q206901 |
P304 | page(s) | 197-201 | |
P577 | publication date | 2014-01-07 | |
P1433 | published in | Proceedings of the National Academy of Sciences of the United States of America | Q1146531 |
P1476 | title | Aggregation-triggering segments of SOD1 fibril formation support a common pathway for familial and sporadic ALS | |
P478 | volume | 111 |
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