scholarly article | Q13442814 |
P2093 | author name string | Tina Wenz | |
Carlos T Moraes | |||
Francisca Diaz | |||
Susana Peralta | |||
Alessandra Torraco | |||
Sofia Garcia | |||
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2-Deoxy-D-glucose treatment induces ketogenesis, sustains mitochondrial function, and reduces pathology in female mouse model of Alzheimer's disease | Q28478912 | ||
Tissue-specific splicing of an Ndufs6 gene-trap insertion generates a mitochondrial complex I deficiency-specific cardiomyopathy | Q28505379 | ||
mTERF2 regulates oxidative phosphorylation by modulating mtDNA transcription | Q28512464 | ||
Proteomic and metabolomic analyses of mitochondrial complex I-deficient mouse model generated by spontaneous B2 short interspersed nuclear element (SINE) insertion into NADH dehydrogenase (ubiquinone) Fe-S protein 4 (Ndufs4) gene | Q28579972 | ||
Cytochrome c oxidase is required for the assembly/stability of respiratory complex I in mouse fibroblasts | Q28585444 | ||
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Chronic systemic pesticide exposure reproduces features of Parkinson's disease | Q29614763 | ||
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A defect in the mitochondrial complex III, but not complex IV, triggers early ROS-dependent damage in defined brain regions. | Q30416049 | ||
High frequency of mitochondrial complex I mutations in Parkinson's disease and aging | Q30434711 | ||
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Cytochrome c oxidase deficiency in neurons decreases both oxidative stress and amyloid formation in a mouse model of Alzheimer's disease | Q30443526 | ||
Ketogenic diet slows down mitochondrial myopathy progression in mice | Q43157369 | ||
Analysis of the subunit composition of complex I from bovine heart mitochondria | Q44367201 | ||
Evidence for a defect in NADH: ubiquinone oxidoreductase (complex I) in Huntington's disease | Q45294442 | ||
Functional modules and structural basis of conformational coupling in mitochondrial complex I. | Q45730820 | ||
Capacity for substrate utilization in oxidative metabolism by neurons, astrocytes, and oligodendrocytes from developing brain in primary culture | Q48237711 | ||
Role of carnitine palmitoyltransferase I in the control of ketogenesis in primary cultures of rat astrocytes | Q48388052 | ||
Superoxide production is inversely related to complex I activity in inherited complex I deficiency. | Q50471908 | ||
Human mitochondrial complex I assembles through the combination of evolutionary conserved modules: a framework to interpret complex I deficiencies. | Q50488580 | ||
Formation of 8-hydroxyguanine residues in DNA by X-irradiation | Q70754172 | ||
The Charge Heterogeneity of the Mitochondrial Acetyl-CoA Acetyltransferase from Rat Liver | Q72521322 | ||
CaMKIIalpha-Cre transgene expression and recombination patterns in the mouse brain | Q73473631 | ||
Mice with mitochondrial complex I deficiency develop a fatal encephalomyopathy | Q30484862 | ||
Gene-trap mutagenesis: past, present and beyond | Q30728811 | ||
Mitochondrial DNA damage in a mouse model of Alzheimer's disease decreases amyloid beta plaque formation | Q33608218 | ||
Neurotoxic in vivo models of Parkinson's disease recent advances. | Q33708283 | ||
Complex I deficiency due to loss of Ndufs4 in the brain results in progressive encephalopathy resembling Leigh syndrome | Q33934412 | ||
Bovine complex I is a complex of 45 different subunits. | Q33999203 | ||
The harlequin mouse mutation downregulates apoptosis-inducing factor | Q34152182 | ||
Definition of the nuclear encoded protein composition of bovine heart mitochondrial complex I. Identification of two new subunits. | Q34154561 | ||
Somatic mtDNA mutations cause aging phenotypes without affecting reactive oxygen species production | Q34212784 | ||
Mitochondria and degenerative disorders | Q34386737 | ||
Mitochondrial dysfunction during hypoxia/reoxygenation and its correction by anaerobic metabolism of citric acid cycle intermediates | Q35082127 | ||
Ketone body synthesis in the brain: possible neuroprotective effects | Q35652465 | ||
Novel role for mitochondria: protein kinase Ctheta-dependent oxidative signaling organelles in activation-induced T-cell death | Q35856966 | ||
D-beta-hydroxybutyrate rescues mitochondrial respiration and mitigates features of Parkinson disease | Q35919815 | ||
The epidemiology of mitochondrial disorders--past, present and future | Q35970168 | ||
Fatal breathing dysfunction in a mouse model of Leigh syndrome | Q36070987 | ||
Cerebral ketone body metabolism | Q36118288 | ||
Mouse mtDNA mutant model of Leber hereditary optic neuropathy. | Q36471358 | ||
The mitochondrial impairment, oxidative stress and neurodegeneration connection: reality or just an attractive hypothesis? | Q37134820 | ||
Electrophoresis techniques to investigate defects in oxidative phosphorylation | Q37307214 | ||
Mitochondrial complex I deficiency: from organelle dysfunction to clinical disease. | Q37428322 | ||
NDUFS4: creation of a mouse model mimicking a Complex I disorder | Q37440629 | ||
Mammalian mitochondrial complex I: biogenesis, regulation, and reactive oxygen species generation. | Q37608294 | ||
AIF deficiency compromises oxidative phosphorylation | Q37671807 | ||
Mouse models for nuclear DNA-encoded mitochondrial complex I deficiency. | Q37682674 | ||
Mitochondrial disorders caused by mutations in respiratory chain assembly factors | Q37890682 | ||
Understanding mitochondrial complex I assembly in health and disease | Q37933572 | ||
Assembly factors as a new class of disease genes for mitochondrial complex I deficiency: cause, pathology and treatment options | Q37950745 | ||
Mitochondrial complex I deficiency of nuclear origin II. Non-structural genes | Q37958285 | ||
Mitochondrial complex I deficiency of nuclear origin I. Structural genes | Q37964862 | ||
Which way does the citric acid cycle turn during hypoxia? The critical role of α-ketoglutarate dehydrogenase complex. | Q38078892 | ||
Acetyl-CoA acetyltransferase from bovine liver mitochondria Molecular properties of multiple forms | Q39225716 | ||
Mechanism of action of a wound-induced ω-hydroxyfatty acid:NADP oxidoreductase isolated from potato tubers (Solanum tuberosum L) | Q39236604 | ||
Inhibition of complex I of the electron transport chain causes O2-. -mediated mitochondrial outgrowth. | Q39704890 | ||
Respiratory active mitochondrial supercomplexes. | Q39913363 | ||
Evaluation of the mitochondrial respiratory chain and oxidative phosphorylation system using polarography and spectrophotometric enzyme assays | Q41861486 | ||
Evaluation of the mitochondrial respiratory chain and oxidative phosphorylation system using blue native gel electrophoresis | Q42606879 | ||
P433 | issue | 6 | |
P921 | main subject | Succinate dehydrogenase complex, subunit B, iron sulfur (Ip) | Q14916128 |
Cytochrome c oxidase subunit I | Q21984161 | ||
Ubiquinol cytochrome c reductase core protein 2 | Q21987463 | ||
NADH:ubiquinone oxidoreductase subunit A5 | Q21988742 | ||
NADH:ubiquinone oxidoreductase core subunit S4 | Q21988755 | ||
NADH:ubiquinone oxidoreductase subunit B8 | Q21988757 | ||
NADH:ubiquinone oxidoreductase subunit A9 | Q21988760 | ||
NADH:ubiquinone oxidoreductase core subunit S3 | Q21988764 | ||
P304 | page(s) | 1399-1412 | |
P577 | publication date | 2013-10-23 | |
P1433 | published in | Human Molecular Genetics | Q2720965 |
P1476 | title | Partial complex I deficiency due to the CNS conditional ablation of Ndufa5 results in a mild chronic encephalopathy but no increase in oxidative damage | |
P478 | volume | 23 |
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Q37722131 | Systematic analysis of microarray datasets to identify Parkinson's disease‑associated pathways and genes |
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