Visualizing the von Willebrand factor/glycoprotein Ib-IX axis with a platelet-type von Willebrand disease mutation

scientific article

Visualizing the von Willebrand factor/glycoprotein Ib-IX axis with a platelet-type von Willebrand disease mutation is …
instance of (P31):
scholarly articleQ13442814

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P356DOI10.1182/BLOOD-2009-03-210823
P932PMC publication ID2798865
P698PubMed publication ID19808696
P5875ResearchGate publication ID26875682

P2093author name stringBrian Storrie
Jerry Ware
Jose A Guerrero
Susan Russell
Junling Liu
T Kent Gartner
Mark Kyei
P2860cites workBiochemistry and genetics of von Willebrand factorQ22003890
Inducible secretion of large, biologically potent von Willebrand factor multimersQ24296142
Glycoproteins V and Ib-IX form a noncovalent complex in the platelet membraneQ24297475
Mutation in the gene encoding the alpha chain of platelet glycoprotein Ib in platelet-type von Willebrand diseaseQ24561673
Purification and preliminary characterization of the glycoprotein Ib complex in the human platelet membraneQ28291722
Generation and rescue of a murine model of platelet dysfunction: the Bernard-Soulier syndromeQ28509360
Shear-induced unfolding triggers adhesion of von Willebrand factor fibersQ30499995
Identification of a novel point mutation in platelet glycoprotein Ibalpha, Gly to Ser at residue 233, in a Japanese family with platelet-type von Willebrand diseaseQ33357025
Megakaryocyte proliferation and ploidy regulated by the cytoplasmic tail of glycoprotein IbalphaQ33361789
Impaired megakaryocytopoiesis in type 2B von Willebrand disease with severe thrombocytopeniaQ33371302
Structural and functional correlation of ADAMTS13.Q33374818
von Willebrand factor binds to platelets and induces aggregation in platelet-type but not type IIB von Willebrand diseaseQ33478102
Expression of the phenotypic abnormality of platelet-type von Willebrand disease in a recombinant glycoprotein Ib alpha fragmentQ33899500
Subunit composition of plasma von Willebrand factor. Cleavage is present in normal individuals, increased in IIA and IIB von Willebrand disease, but minimal in variants with aberrant structure of individual oligomers (types IIC, IID, and IIE).Q34528381
The role of von Willebrand factor in thrombus formationQ34627119
Glycoprotein Ib-IX-V.Q35131686
Platelet glycoprotein Ib alpha supports experimental lung metastasisQ35829198
Platelet dysfunction and a high bone mass phenotype in a murine model of platelet-type von Willebrand diseaseQ36559664
Adhesion mechanisms in platelet functionQ36856340
Identification of a point mutation in type IIB von Willebrand disease illustrating the regulation of von Willebrand factor affinity for the platelet membrane glycoprotein Ib-IX receptorQ37470139
Identification and functional characterization of a novel 27-bp deletion in the macroglycopeptide-coding region of the GPIBA gene resulting in platelet-type von Willebrand diseaseQ45261264
Evidence that differential packaging of the major platelet granule proteins von Willebrand factor and fibrinogen can support their differential release.Q50672582
Dysfunctional platelet membrane receptors: from humans to mice.Q55468635
Platelet-type von Willebrand diseaseQ71570222
Platelet-type von Willebrand's disease: characterization of a new bleeding disorderQ72939306
Expression and functional characterization of an abnormal platelet membrane glycoprotein Ib alpha (Met239 --> Val) reported in patients with platelet-type von Willebrand diseaseQ73516569
Distinct antithrombotic consequences of platelet glycoprotein Ibalpha and VI deficiency in a mouse model of arterial thrombosisQ80233007
P433issue27
P407language of work or nameEnglishQ1860
P921main subjectvisualizationQ451553
P304page(s)5541-5546
P577publication date2009-10-06
P1433published inBloodQ885070
P1476titleVisualizing the von Willebrand factor/glycoprotein Ib-IX axis with a platelet-type von Willebrand disease mutation
P478volume114

Reverse relations

cites work (P2860)
Q38840380Acquired platelet disorders
Q37903933Advances in our understanding of the molecular basis of disorders of platelet function
Q49989075Hereditary thrombocytopenias: a growing list of disorders
Q33432109Inherited thrombocytopenias-recent advances in clinical and molecular aspects
Q38258281Of von Willebrand factor and platelets
Q42931957Reconstitution of the platelet glycoprotein Ib-IX complex in phospholipid bilayer Nanodiscs.
Q33416741Systematic analysis of bleeding phenotype in PT-VWD compared to type 2B VWD using an electronic bleeding questionnaire
Q36274845The ABCC4 membrane transporter modulates platelet aggregation.
Q42134117Thrombocytopathy and type 2B von Willebrand disease
Q33411711von Willebrand factor mutation promotes thrombocytopathy by inhibiting integrin αIIbβ3.

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