scholarly article | Q13442814 |
P2093 | author name string | Scot C Leary | |
Antoni Barrientos | |||
Aren Boulet | |||
Myriam Bourens | |||
P2860 | cites work | Protein measurement with the Folin phenol reagent | Q20900776 |
SURF1, encoding a factor involved in the biogenesis of cytochrome c oxidase, is mutated in Leigh syndrome | Q22008476 | ||
Fatal infantile cardioencephalomyopathy with COX deficiency and mutations in SCO2, a COX assembly gene | Q22010737 | ||
Cytochrome c oxidase subassemblies in fibroblast cultures from patients carrying mutations in COX10, SCO1, or SURF1 | Q24299371 | ||
Cloning of a human gene involved in cytochrome oxidase assembly by functional complementation of an oxa1- mutation in Saccharomyces cerevisiae | Q24310678 | ||
Mutations of the SCO1 gene in mitochondrial cytochrome c oxidase deficiency with neonatal-onset hepatic failure and encephalopathy. | Q24534480 | ||
Tissue-specific cytochrome c oxidase assembly defects due to mutations in SCO2 and SURF1 | Q24534961 | ||
Targeting DNA double-strand breaks with TAL effector nucleases | Q24605087 | ||
Structure at 2.7 A resolution of the Paracoccus denitrificans two-subunit cytochrome c oxidase complexed with an antibody FV fragment | Q24657440 | ||
Cleavage of Structural Proteins during the Assembly of the Head of Bacteriophage T4 | Q25938983 | ||
The whole structure of the 13-subunit oxidized cytochrome c oxidase at 2.8 A | Q27732721 | ||
Redox-coupled crystal structural changes in bovine heart cytochrome c oxidase | Q27758647 | ||
A mitochondrial protease with two catalytic subunits of nonoverlapping specificities. | Q27930944 | ||
Yeast Oxa1 interacts with mitochondrial ribosomes: the importance of the C-terminal region of Oxa1. | Q27931721 | ||
Identification of Cox20p, a novel protein involved in the maturation and assembly of cytochrome oxidase subunit 2. | Q27932189 | ||
Ribosome binding to the Oxa1 complex facilitates co-translational protein insertion in mitochondria | Q27932930 | ||
Cox18p is required for export of the mitochondrially encoded Saccharomyces cerevisiae Cox2p C-tail and interacts with Pnt1p and Mss2p in the inner membrane. | Q27935218 | ||
Mitochondrial protein synthesis is required for maintenance of intact mitochondrial genomes in Saccharomyces cerevisiae | Q27935904 | ||
Membrane translocation of mitochondrially coded Cox2p: distinct requirements for export of N and C termini and dependence on the conserved protein Oxa1p | Q27935924 | ||
Oxa1p mediates the export of the N- and C-termini of pCoxII from the mitochondrial matrix to the intermembrane space | Q27935994 | ||
Oxa1p, an essential component of the N-tail protein export machinery in mitochondria | Q27939168 | ||
COX16 encodes a novel protein required for the assembly of cytochrome oxidase in Saccharomyces cerevisiae | Q27939371 | ||
Cytochrome c oxidase deficiency | Q28189586 | ||
Human SCO1 and SCO2 have independent, cooperative functions in copper delivery to cytochrome c oxidase | Q28269687 | ||
Assembly of cytochrome-c oxidase in cultured human cells | Q28276105 | ||
The human cytochrome c oxidase assembly factors SCO1 and SCO2 have regulatory roles in the maintenance of cellular copper homeostasis | Q28280598 | ||
A TALE nuclease architecture for efficient genome editing | Q28301656 | ||
Chemiosmotic hypothesis of oxidative phosphorylation | Q28611218 | ||
Formation of the redox cofactor centers during Cox1 maturation in yeast cytochrome oxidase. | Q33627236 | ||
The bicoid stability factor controls polyadenylation and expression of specific mitochondrial mRNAs in Drosophila melanogaster | Q34055376 | ||
Modularly assembled designer TAL effector nucleases for targeted gene knockout and gene replacement in eukaryotes | Q34175308 | ||
Biogenesis and assembly of eukaryotic cytochrome c oxidase catalytic core | Q34220248 | ||
Genetic defects of cytochrome c oxidase assembly. | Q34317653 | ||
Assembly of mitochondrial cytochrome c-oxidase, a complicated and highly regulated cellular process | Q34535761 | ||
Defects in cytochrome oxidase assembly in humans: lessons from yeast | Q34600372 | ||
Human SCO2 is required for the synthesis of CO II and as a thiol-disulphide oxidoreductase for SCO1. | Q34972244 | ||
Multiple roles of the Cox20 chaperone in assembly of Saccharomyces cerevisiae cytochrome c oxidase | Q35748230 | ||
Biogenesis of cytochrome oxidase-sophisticated assembly lines in the mitochondrial inner membrane | Q36132872 | ||
Copper trafficking to the mitochondrion and assembly of copper metalloenzymes | Q36456731 | ||
Modular assembly of yeast cytochrome oxidase | Q36608388 | ||
The endless tale of non-homologous end-joining | Q37048174 | ||
PET genes of Saccharomyces cerevisiae | Q37056313 | ||
Redox and reactive oxygen species regulation of mitochondrial cytochrome C oxidase biogenesis | Q37366433 | ||
Structural features of cytochrome oxidase | Q37904162 | ||
Shy1p is necessary for full expression of mitochondrial COX1 in the yeast model of Leigh's syndrome | Q39646401 | ||
Analysis of aminoacylation of human mitochondrial tRNAs | Q41244333 | ||
Evaluation of the mitochondrial respiratory chain and oxidative phosphorylation system using polarography and spectrophotometric enzyme assays | Q41861486 | ||
Recessive dystonia-ataxia syndrome in a Turkish family caused by a COX20 (FAM36A) mutation | Q44108174 | ||
Mutation in TACO1, encoding a translational activator of COX I, results in cytochrome c oxidase deficiency and late-onset Leigh syndrome. | Q45979469 | ||
A mutation in the FAM36A gene, the human ortholog of COX20, impairs cytochrome c oxidase assembly and is associated with ataxia and muscle hypotonia. | Q47074411 | ||
Characterization of SURF-1 expression and Surf-1p function in normal and disease conditions. | Q50515893 | ||
Oxidative phosphorylation: synthesis of mitochondrially encoded proteins and assembly of individual structural subunits into functional holoenzyme complexes | Q57041666 | ||
Nuclear functions required for cytochrome c oxidase biogenesis in Saccharomyces cerevisiae. Characterization of mutants in 34 complementation groups | Q70146252 | ||
SCO1 and SCO2 act as high copy suppressors of a mitochondrial copper recruitment defect in Saccharomyces cerevisiae | Q71246164 | ||
Biochemical, genetic and immunoblot analyses of 17 patients with an isolated cytochrome c oxidase deficiency | Q73089677 | ||
In vivo labeling and analysis of mitochondrial translation products in budding and in fission yeasts | Q82882608 | ||
P433 | issue | 11 | |
P921 | main subject | mitochondrial cytochrome c oxidase assembly | Q21100869 |
cytochrome c oxidase assembly factor COX20 | Q21109894 | ||
P304 | page(s) | 2901-2913 | |
P577 | publication date | 2014-01-08 | |
P1433 | published in | Human Molecular Genetics | Q2720965 |
P1476 | title | Human COX20 cooperates with SCO1 and SCO2 to mature COX2 and promote the assembly of cytochrome c oxidase | |
P478 | volume | 23 |
Q38721574 | A CMC1-knockout reveals translation-independent control of human mitochondrial complex IV biogenesis. |
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Q56760543 | Assembly of mammalian oxidative phosphorylation complexes I-V and supercomplexes |
Q40814307 | Association between SCO2 mutation and extreme myopia in Japanese patients |
Q47709325 | Building the CuA site of cytochrome c oxidase: a complicated, redox-dependent process driven by a surprisingly large complement of accessory proteins |
Q89729173 | COA6 Facilitates Cytochrome c Oxidase Biogenesis as Thiol-reductase for Copper Metallochaperones in Mitochondria |
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Q24338334 | COA6 is a mitochondrial complex IV assembly factor critical for biogenesis of mtDNA-encoded COX2 |
Q47643939 | COX16 promotes COX2 metallation and assembly during respiratory complex IV biogenesis. |
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Q38559272 | Copper trafficking to the secretory pathway |
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Q38711145 | Human mitochondrial cytochrome c oxidase assembly factor COX18 acts transiently as a membrane insertase within the subunit 2 maturation module |
Q47430825 | In vitro and in vivo studies of the ALS-FTLD protein CHCHD10 reveal novel mitochondrial topology and protein interactions. |
Q47783506 | Mitochondrial cytochrome c oxidase biogenesis: Recent developments. |
Q36551271 | Mitochondrial disease genes COA6, COX6B and SCO2 have overlapping roles in COX2 biogenesis |
Q31136316 | Multiple across-strain and within-strain QTLs suggest highly complex genetic architecture for hypoxia tolerance in channel catfish |
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Q54963717 | Plant Mitochondrial Inner Membrane Protein Insertion. |
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Q47296599 | The mammalian phosphate carrier SLC25A3 is a mitochondrial copper transporter required for cytochrome c oxidase biogenesis. |
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Q41619805 | The ribosome-associated Mba1 escorts Cox2 from insertion machinery to maturing assembly intermediates |
Q33737679 | Tissue- and Condition-Specific Isoforms of Mammalian Cytochrome c Oxidase Subunits: From Function to Human Disease |
Q39024278 | Tissue- and species-specific differences in cytochrome c oxidase assembly induced by SURF1 defects. |
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