| scholarly article | Q13442814 |
| P6179 | Dimensions Publication ID | 1003664613 |
| P356 | DOI | 10.1038/15513 |
| P3181 | OpenCitations bibliographic resource ID | 1474515 |
| P698 | PubMed publication ID | 10545952 |
| P5875 | ResearchGate publication ID | 12754771 |
| P50 | author | Ichizo Nishino | Q37828689 |
| Michio Hirano | Q89906306 | ||
| P2093 | author name string | S Krishna | |
| D M Glerum | |||
| D C De Vivo | |||
| C M Sue | |||
| S DiMauro | |||
| S Shanske | |||
| E A Schon | |||
| W Walker | |||
| E Bonilla | |||
| P Kaplan | |||
| M M Davidson | |||
| K Tanji | |||
| R Lebel | |||
| G Lyon | |||
| J Selby | |||
| E Scalais | |||
| J E Sadlock | |||
| L C Papadopoulou | |||
| R V Coster | |||
| P2860 | cites work | SURF1, encoding a factor involved in the biogenesis of cytochrome c oxidase, is mutated in Leigh syndrome | Q22008476 |
| Identification and characterization of human cDNAs specific to BCS1, PET112, SCO1, COX15, and COX11, five genes involved in the formation and function of the mitochondrial respiratory chain | Q22008622 | ||
| Cloning of a human gene involved in cytochrome oxidase assembly by functional complementation of an oxa1- mutation in Saccharomyces cerevisiae | Q24310678 | ||
| Isolation of a human cDNA for heme A:farnesyltransferase by functional complementation of a yeast cox10 mutant | Q24319047 | ||
| Isolation of a cDNA encoding the human homolog of COX17, a yeast gene essential for mitochondrial copper recruitment | Q24323240 | ||
| SCO1, a yeast nuclear gene essential for accumulation of mitochondrial cytochrome c oxidase subunit II. | Q27932499 | ||
| Characterization of COX17, a yeast gene involved in copper metabolism and assembly of cytochrome oxidase | Q27934782 | ||
| Immunological identification of yeast SCO1 protein as a component of the inner mitochondrial membrane | Q27939251 | ||
| Human members of the SCO1 gene family: complementation analysis in yeast and intracellular localization | Q28142444 | ||
| A systematic mutation screen of 10 nuclear and 25 mitochondrial candidate genes in 21 patients with cytochrome c oxidase (COX) deficiency shows tRNA(Ser)(UCN) mutations in a subgroup with syndromal encephalopathy | Q33681493 | ||
| Mutations of SURF-1 in Leigh disease associated with cytochrome c oxidase deficiency | Q34388122 | ||
| Accumulation of the cytochrome c oxidase subunits I and II in yeast requires a mitochondrial membrane-associated protein, encoded by the nuclear SCO1 gene | Q34450341 | ||
| Mitochondrial DNA mutations and pathogenesis | Q41547371 | ||
| Biochemical and molecular analysis of cytochrome c oxidase deficiency in Leigh's syndrome | Q44595873 | ||
| Steady-state transcript levels of cytochrome c oxidase genes during human myogenesis indicate subunit switching of subunit VIa and co-expression of subunit VIIa isoforms | Q44771353 | ||
| Cytochrome c oxidase: structure and spectroscopy | Q47910949 | ||
| Molecular analysis of cytochrome c oxidase deficiency in Leigh's syndrome | Q48054632 | ||
| Cytochrome c oxidase deficiency in Leigh syndrome | Q48203324 | ||
| The identification of 18 nuclear genes required for the expression of the yeast mitochondrial gene encoding cytochrome c oxidase subunit 1 | Q67487792 | ||
| Yeast SCO1 protein is required for a post-translational step in the accumulation of mitochondrial cytochrome c oxidase subunits I and II | Q68486954 | ||
| Benign infantile mitochondrial myopathy due to reversible cytochrome c oxidase deficiency | Q70167731 | ||
| SCO1 and SCO2 act as high copy suppressors of a mitochondrial copper recruitment defect in Saccharomyces cerevisiae | Q71246164 | ||
| Cytochemistry and immunocytochemistry of mitochondria in tissue sections | Q71890063 | ||
| Fatal infhntile mitochondrial myopathy and renal dysfunction due to cytochrome-c-oxidase deficiency | Q72863474 | ||
| Mitochondrial copper metabolism in yeast: mutational analysis of Sco1p involved in the biogenesis of cytochrome c oxidase | Q74609082 | ||
| P433 | issue | 3 | |
| P407 | language of work or name | English | Q1860 |
| P304 | page(s) | 333-7 | |
| P577 | publication date | 1999-11-01 | |
| P1433 | published in | Nature Genetics | Q976454 |
| P1476 | title | Fatal infantile cardioencephalomyopathy with COX deficiency and mutations in SCO2, a COX assembly gene | |
| P478 | volume | 23 |
| Q92543630 | A Novel Pathogenic Variant in MT-CO2 Causes an Isolated Mitochondrial Complex IV Deficiency and Late-Onset Cerebellar Ataxia |
| Q101477998 | A Novel Variant in COX16 Causes Cytochrome c Oxidase Deficiency, Severe Fatal Neonatal Lactic Acidosis, Encephalopathy, Cardiomyopathy and Liver Dysfunction |
| Q35123687 | A Sco protein among the hypothetical proteins of Bacillus lehensis G1: Its 3D macromolecular structure and association with Cytochrome C Oxidase |
| Q44911329 | A case of sporadic infantile histiocytoid cardiomyopathy caused by the A8344G (MERRF) mitochondrial DNA mutation. |
| Q28199158 | A deletion in the human QP-C gene causes a complex III deficiency resulting in hypoglycaemia and lactic acidosis |
| Q33622307 | A functional screen for copper homeostasis genes identifies a pharmacologically tractable cellular system. |
| Q24535681 | A genomewide linkage-disequilibrium scan localizes the Saguenay-Lac-Saint-Jean cytochrome oxidase deficiency to 2p16 |
| Q53075411 | A history of mitochondrial diseases. |
| Q34088669 | A mutant mitochondrial respiratory chain assembly protein causes complex III deficiency in patients with tubulopathy, encephalopathy and liver failure. |
| Q34768367 | A mutation in C2orf64 causes impaired cytochrome c oxidase assembly and mitochondrial cardiomyopathy |
| Q47074411 | A mutation in the FAM36A gene, the human ortholog of COX20, impairs cytochrome c oxidase assembly and is associated with ataxia and muscle hypotonia. |
| Q37774749 | A neurological perspective on mitochondrial disease. |
| Q28213285 | A role for mitochondrial enzymes in inherited neoplasia and beyond |
| Q28509157 | A stabilizing factor for mitochondrial respiratory supercomplex assembly regulates energy metabolism in muscle |
| Q35019411 | A targetable fluorescent sensor reveals that copper-deficient SCO1 and SCO2 patient cells prioritize mitochondrial copper homeostasis. |
| Q37018318 | Abundance and Significance of Iron, Zinc, Copper, and Calcium in the Hearts of Patients With Friedreich Ataxia |
| Q73943201 | Activities of mitochondrial oxidative phosphorylation enzymes in cultured amniocytes |
| Q28589741 | Analysis of mouse models of cytochrome c oxidase deficiency owing to mutations in Sco2 |
| Q41859118 | Analysis of reported SCO2 gene mutations affecting cytochrome c oxidase activity in various diseases |
| Q36239807 | Antibody-based approaches to diagnosis and characterization of oxidative phosphorylation diseases |
| Q37220086 | Approaches to finding the molecular basis of mitochondrial oxidative phosphorylation disorders |
| Q34535761 | Assembly of mitochondrial cytochrome c-oxidase, a complicated and highly regulated cellular process |
| Q40814307 | Association between SCO2 mutation and extreme myopia in Japanese patients |
| Q36796192 | Biochemical assays of respiratory chain complex activity |
| Q92455084 | Biochemistry of Copper Site Assembly in Heme-Copper Oxidases: A Theme with Variations |
| Q34220248 | Biogenesis and assembly of eukaryotic cytochrome c oxidase catalytic core |
| Q47709325 | Building the CuA site of cytochrome c oxidase: a complicated, redox-dependent process driven by a surprisingly large complement of accessory proteins |
| Q24655437 | CABC1 gene mutations cause ubiquinone deficiency with cerebellar ataxia and seizures |
| Q92087519 | COA6 Is Structurally Tuned to Function as a Thiol-Disulfide Oxidoreductase in Copper Delivery to Mitochondrial Cytochrome c Oxidase |
| Q24338334 | COA6 is a mitochondrial complex IV assembly factor critical for biogenesis of mtDNA-encoded COX2 |
| Q27939371 | COX16 encodes a novel protein required for the assembly of cytochrome oxidase in Saccharomyces cerevisiae |
| Q36680529 | COX19 mediates the transduction of a mitochondrial redox signal from SCO1 that regulates ATP7A-mediated cellular copper efflux |
| Q36906195 | Cancer metabolism, stemness and tumor recurrence: MCT1 and MCT4 are functional biomarkers of metabolic symbiosis in head and neck cancer |
| Q35693895 | Cardiac deficiency of single cytochrome oxidase assembly factor scox induces p53-dependent apoptosis in a Drosophila cardiomyopathy model |
| Q39413241 | Cellular copper homeostasis: current concepts on its interplay with glutathione homeostasis and its implication in physiology and human diseases |
| Q40733578 | Characterization and identification of promoter elements in the mouse COX17 gene |
| Q34280992 | Clinical and molecular studies of mitochondrial disease |
| Q73912619 | Clinical differences in patients with mitochondriocytopathies due to nuclear versus mitochondrial DNA mutations |
| Q34386724 | Clinical spectrum and diagnosis of mitochondrial disorders |
| Q36097913 | Coiled coil domain-containing protein 56 (CCDC56) is a novel mitochondrial protein essential for cytochrome c oxidase function |
| Q39517896 | Comparative DNA methylation and gene expression analysis identifies novel genes for structural congenital heart diseases. |
| Q45124854 | Congenital cardiomyopathy and pulmonary hypertension: another fatal variant of cytochrome-c oxidase deficiency. |
| Q24337420 | Cooperation between COA6 and SCO2 in COX2 maturation during cytochrome c oxidase assembly links two mitochondrial cardiomyopathies |
| Q36243954 | Copper and bezafibrate cooperate to rescue cytochrome c oxidase deficiency in cells of patients with SCO2 mutations |
| Q35050254 | Copper chaperones for cytochrome c oxidase and human disease |
| Q37808945 | Copper handling machinery of the brain |
| Q34209733 | Copper modulates the degradation of copper chaperone for Cu,Zn superoxide dismutase by the 26 S proteosome. |
| Q24534079 | Copper supplementation restores cytochrome c oxidase activity in cultured cells from patients with SCO2 mutations |
| Q24337613 | Copper supplementation restores cytochrome c oxidase assembly defect in a mitochondrial disease model of COA6 deficiency |
| Q38942904 | Copper transporters and chaperones: Their function on angiogenesis and cellular signalling |
| Q27936222 | Crystal structure of human SCO1: implications for redox signaling by a mitochondrial cytochrome c oxidase "assembly" protein |
| Q28189586 | Cytochrome c oxidase deficiency |
| Q35038648 | Cytochrome c oxidase deficiency |
| Q92028567 | Cytochrome c oxidase deficiency caused by biallelic SCO2 mutations in two sibs with cerebellar ataxia and progressive peripheral axonal neuropathy |
| Q24299371 | Cytochrome c oxidase subassemblies in fibroblast cultures from patients carrying mutations in COX10, SCO1, or SURF1 |
| Q40816638 | Cytochrome c oxidase-deficient patients have distinct subunit assembly profiles |
| Q34594190 | Cytochrome oxidase in health and disease. |
| Q34064462 | Defective complex I assembly due to C20orf7 mutations as a new cause of Leigh syndrome |
| Q34600372 | Defects in cytochrome oxidase assembly in humans: lessons from yeast |
| Q30331712 | Defects in mitochondrial respiratory complexes III and IV, and human pathologies. |
| Q33922286 | Defects in multiple complexes of the respiratory chain are present in ageing human colonic crypts |
| Q36267201 | Dietary copper supplementation reverses hypertrophic cardiomyopathy induced by chronic pressure overload in mice |
| Q51682565 | Disease-related mutations in cytochrome c oxidase studied in yeast and bacterial models. |
| Q37279228 | Doxorubicin inactivates myocardial cytochrome c oxidase in rats: cardioprotection by Mito-Q |
| Q47074213 | Early developmental pathology due to cytochrome c oxidase deficiency is revealed by a new zebrafish model |
| Q74518028 | Early-onset multisystem mitochondrial disorder caused by a nonsense mutation in the mitochondrial DNA cytochrome C oxidase II gene |
| Q42556101 | Effect of p53 on mitochondrial morphology, import, and assembly in skeletal muscle. |
| Q90426371 | Elesclomol restores mitochondrial function in genetic models of copper deficiency |
| Q36238864 | Essential role for mammalian copper transporter Ctr1 in copper homeostasis and embryonic development |
| Q47721349 | Evaluation of SCO1 deletion on Saccharomyces cerevisiae metabolism through a proteomic approach. |
| Q42316612 | Exogenous addition of histidine reduces copper availability in the yeast Saccharomyces cerevisiae |
| Q34203277 | Exome sequencing identifies MRPL3 mutation in mitochondrial cardiomyopathy |
| Q24301657 | Exome sequencing identifies mitochondrial alanyl-tRNA synthetase mutations in infantile mitochondrial cardiomyopathy |
| Q40259007 | Exome sequencing reveals SCO2 mutations in a family presented with fatal infantile hyperthermia |
| Q37649092 | Expression of alternative oxidase in Drosophila ameliorates diverse phenotypes due to cytochrome oxidase deficiency |
| Q57245327 | Fatal neonatal mitochondrial cytopathy with disseminated fatty nodules in the liver |
| Q35436157 | Frequency of mitochondrial transfer RNA mutations and deletions in 225 patients presenting with respiratory chain deficiencies |
| Q24617140 | GRACILE syndrome, a lethal metabolic disorder with iron overload, is caused by a point mutation in BCS1L |
| Q38042727 | Genetic axonal neuropathies and neuronopathies of pre-natal and infantile onset |
| Q35879073 | Genetics of inherited cardiomyopathies |
| Q36024352 | Genome-wide patterns of copy number variation in the Chinese yak genome |
| Q48312308 | Genomic structure of mouse copper chaperone, COX17. |
| Q35932266 | HIF1α induced switch from bivalent to exclusively glycolytic metabolism during ESC-to-EpiSC/hESC transition |
| Q35819361 | Heart mitochondria signaling pathways: appraisal of an emerging field |
| Q36812709 | Heavy metal ions in normal physiology, toxic stress, and cytoprotection. |
| Q34631359 | Hepatic transport systems |
| Q28661465 | Historical perspective on mitochondrial medicine |
| Q46238305 | Hodgkin lymphoma: A complex metabolic ecosystem with glycolytic reprogramming of the tumor microenvironment. |
| Q33582770 | Human COX20 cooperates with SCO1 and SCO2 to mature COX2 and promote the assembly of cytochrome c oxidase |
| Q34972244 | Human SCO2 is required for the synthesis of CO II and as a thiol-disulphide oxidoreductase for SCO1. |
| Q28266498 | Human Sco1 and Sco2 function as copper-binding proteins |
| Q24290607 | Human complex I defects can be resolved by monoclonal antibody analysis into distinct subunit assembly patterns |
| Q34067750 | Human cytochrome oxidase deficiency |
| Q57175222 | Human diseases associated with defects in assembly of OXPHOS complexes |
| Q38711145 | Human mitochondrial cytochrome c oxidase assembly factor COX18 acts transiently as a membrane insertase within the subunit 2 maturation module |
| Q47198282 | Human recombinant mutated forms of the mitochondrial COX assembly Sco2 protein differ from wild-type in physical state and copper binding capacity |
| Q47719245 | Impaired p53/CEP-1 is associated with lifespan extension through an age-related imbalance in the energy metabolism of C. elegans. |
| Q104472489 | In vivo biodistribution study of TAT-L-Sco2 fusion protein, developed as protein therapeutic for mitochondrial disorders attributed to SCO2 mutations |
| Q35089820 | In vivo correction of COX deficiency by activation of the AMPK/PGC-1α axis |
| Q40775533 | In vivo regulation of oxidative phosphorylation in cells harboring a stop-codon mutation in mitochondrial DNA-encoded cytochrome c oxidase subunit I. |
| Q27935659 | Inaccurately assembled cytochrome c oxidase can lead to oxidative stress-induced growth arrest. |
| Q34009643 | Inborn errors of metabolism around time of birth |
| Q44099489 | Infantile leukoencephalopathy owing to mitochondrial enzyme dysfunction |
| Q40132047 | Influence of common and rare genetic variation on warfarin dose among African-Americans and European-Americans using the exome array |
| Q40394628 | Inheritance of mitochondrial disorders |
| Q33786829 | Inherited Paediatric Motor Neuron Disorders: Beyond Spinal Muscular Atrophy |
| Q37735366 | Inhibiting Cytochrome C Oxidase Leads to Alleviated Ischemia Reperfusion Injury |
| Q39361708 | Insights into the mechanisms of copper dyshomeostasis in amyotrophic lateral sclerosis |
| Q44532294 | Insulin-like growth factor-1 prevents loss of electrochemical gradient in cardiac muscle mitochondria via activation of PI 3 kinase/Akt pathway. |
| Q60205139 | Introducing a novel human mtDNA mutation into the Paracoccus denitrificans COX I gene explains functional deficits in a patient |
| Q48199735 | Investigating the cardiac pathology of SCO2-mediated hypertrophic cardiomyopathy using patients induced pluripotent stem cell-derived cardiomyocytes |
| Q41260893 | Iron and copper in mitochondrial diseases |
| Q36727229 | Isolated cytochrome c oxidase deficiency in G93A SOD1 mice overexpressing CCS protein |
| Q35183941 | Krüppel-like factor 6 regulates mitochondrial function in the kidney |
| Q28192185 | Laboratory approach to mitochondrial diseases |
| Q24533500 | Large-scale deletion and point mutations of the nuclear NDUFV1 and NDUFS1 genes in mitochondrial complex I deficiency |
| Q48308173 | Leigh disease due to SCO2 mutations revealed at extended autopsy. |
| Q37302025 | Light microscopic methods to visualize mitochondria on tissue sections |
| Q38806341 | Loss of LRPPRC causes ATP synthase deficiency |
| Q34964534 | Loss of function of Sco1 and its interaction with cytochrome c oxidase |
| Q28587981 | Mammalian copper chaperone Cox17p has an essential role in activation of cytochrome C oxidase and embryonic development |
| Q83120532 | Measurement of ATP production in mitochondrial disorders |
| Q36225141 | Mining copper transport genes |
| Q36524727 | Mitochondrial DNA mutations in human colonic crypt stem cells |
| Q35190973 | Mitochondrial Diseases Part I: mouse models of OXPHOS deficiencies caused by defects in respiratory complex subunits or assembly factors |
| Q36517059 | Mitochondrial Dysfunction may explain symptom variation in Phelan-McDermid Syndrome |
| Q60303203 | Mitochondrial Sco proteins are involved in oxidative stress defense |
| Q30588636 | Mitochondrial cardioencephalomyopathy due to a novel SCO2 mutation in a Brazilian patient: case report and literature review |
| Q33827986 | Mitochondrial copper metabolism and delivery to cytochrome c oxidase |
| Q73209476 | Mitochondrial copper metabolism in yeast: interaction between Sco1p and Cox2p |
| Q47783506 | Mitochondrial cytochrome c oxidase biogenesis: Recent developments. |
| Q26769015 | Mitochondrial cytochrome c oxidase deficiency |
| Q34543745 | Mitochondrial disease |
| Q36551271 | Mitochondrial disease genes COA6, COX6B and SCO2 have overlapping roles in COX2 biogenesis |
| Q41934213 | Mitochondrial disease in 22q13 duplication syndrome |
| Q36707793 | Mitochondrial disease--its impact, etiology, and pathology. |
| Q78517318 | Mitochondrial diseases |
| Q37970121 | Mitochondrial diseases and the heart: an overview of molecular basis, diagnosis, treatment and clinical course |
| Q36765849 | Mitochondrial diseases: a nosological update. |
| Q37890682 | Mitochondrial disorders caused by mutations in respiratory chain assembly factors |
| Q35038630 | Mitochondrial disorders of the nervous system: clinical, biochemical, and molecular genetic features |
| Q33810406 | Mitochondrial disorders of the nuclear genome |
| Q27000484 | Mitochondrial disorders: challenges in diagnosis & treatment |
| Q24337810 | Mitochondrial disulfide relay mediates translocation of p53 and partitions its subcellular activity |
| Q92932334 | Mitochondrial dysfunction and its role in tissue-specific cellular stress |
| Q24630557 | Mitochondrial dysfunction in autism spectrum disorders: a systematic review and meta-analysis |
| Q82029875 | Mitochondrial encephalomyopathies |
| Q35085834 | Mitochondrial encephalomyopathies |
| Q36085696 | Mitochondrial respiration protects against oxygen-associated DNA damage |
| Q35685889 | Mitochondriopathies |
| Q35038672 | Models of mitochondrial disease |
| Q33623775 | Modulation of mitochondrial protein phosphorylation by soluble adenylyl cyclase ameliorates cytochrome oxidase defects |
| Q44069100 | Molecular characterization of Saccharomyces cerevisiae Sco2p reveals a high degree of redundancy with Sco1p |
| Q37206274 | Molecular diagnostics and mitochondrial dysfunction: a future perspective. |
| Q34662075 | Molecular mechanisms of copper uptake and distribution |
| Q37120797 | Mouse models of oxidative phosphorylation defects: powerful tools to study the pathobiology of mitochondrial diseases |
| Q37404541 | Multisystem manifestations of mitochondrial disorders |
| Q44289091 | Mutation analysis of copper transporter genes in patients with ethylmalonic encephalopathy, mitochondriopathies and copper deficiency phenotypes |
| Q47962448 | Mutation in mitochondrial complex IV subunit COX5A causes pulmonary arterial hypertension, lactic acidemia, and failure to thrive |
| Q28204376 | Mutation screening in patients with isolated cytochrome c oxidase deficiency |
| Q24301791 | Mutations in C12orf62, a factor that couples COX I synthesis with cytochrome c oxidase assembly, cause fatal neonatal lactic acidosis |
| Q50218362 | Mutations in COA3 cause isolated complex IV deficiency associated with neuropathy, exercise intolerance, obesity, and short stature |
| Q24328756 | Mutations in COX15 produce a defect in the mitochondrial heme biosynthetic pathway, causing early-onset fatal hypertrophic cardiomyopathy |
| Q24339538 | Mutations in SCO2 are associated with autosomal-dominant high-grade myopia |
| Q42863252 | Mutations in cytochrome assembly and periplasmic redox pathways in Bordetella pertussis |
| Q28646237 | Mutations in the complex I NDUFS2 gene of patients with cardiomyopathy and encephalomyopathy |
| Q24534480 | Mutations of the SCO1 gene in mitochondrial cytochrome c oxidase deficiency with neonatal-onset hepatic failure and encephalopathy. |
| Q38818384 | Myoglobin and the regulation of mitochondrial respiratory chain complex IV. |
| Q39414816 | Myopathology of Adult and Paediatric Mitochondrial Diseases |
| Q33735567 | NAD(+)-dependent activation of Sirt1 corrects the phenotype in a mouse model of mitochondrial disease |
| Q37724335 | Neonatal neuroimaging findings in inborn errors of metabolism |
| Q35647359 | New approaches to the treatment of mitochondrial disorders |
| Q43497460 | New perspectives on the assembly process of mitochondrial respiratory chain complex cytochrome c oxidase. |
| Q36894743 | No Evidence for Association of SCO2 Heterozygosity with High-Grade Myopia or Other Diseases with Possible Mitochondrial Dysfunction |
| Q43920593 | Novel mutations in SCO1 as a cause of fatal infantile encephalopathy and lactic acidosis. |
| Q34147373 | Novel transporter required for biogenesis of cbb3-type cytochrome c oxidase in Rhodobacter capsulatus |
| Q38963725 | Nutritional interventions in primary mitochondrial disorders: Developing an evidence base. |
| Q48864554 | Optical imaging techniques (histochemical, immunohistochemical, and in situ hybridization staining methods) to visualize mitochondria |
| Q36796199 | Optical imaging techniques (histochemical, immunohistochemical, and in situ hybridization staining methods) to visualize mitochondria |
| Q39420445 | Orchestration of dynamic copper navigation - new and missing pieces |
| Q37412986 | Pathogenic mutations of nuclear genes associated with mitochondrial disorders |
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| Q37321107 | Polo-like kinases mediate cell survival in mitochondrial dysfunction |
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| Q53640842 | [Pediatric cardiology in the genomic era]. |
| Q53662201 | [The mitochondrial organelle and the heart]. |
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