The redox status of cystinotic fibroblasts

scientific article

The redox status of cystinotic fibroblasts is …
instance of (P31):
scholarly articleQ13442814

External links are
P356DOI10.1016/J.YMGME.2009.12.010
P932PMC publication ID2839033
P698PubMed publication ID20061170
P5875ResearchGate publication ID40898919

P2093author name stringRuma Banerjee
Victor Vitvitsky
Jess Thoene
Marc Witcher
P2860cites workKinetics and inhibition of recombinant human cystathionine gamma-lyase. Toward the rational control of transsulfurationQ22009446
Altered status of glutathione and its metabolites in cystinotic cellsQ24305285
Identification and subcellular localization of a new cystinosin isoformQ24310549
A novel gene encoding an integral membrane protein is mutated in nephropathic cystinosisQ24322985
Cystinosis. Intracellular cystine depletion by aminothiols in vitro and in vivoQ35902688
Potential role of apoptosis in development of the cystinotic phenotypeQ35995221
A review of the role of enhanced apoptosis in the pathophysiology of cystinosisQ36922753
Glutathione precursors replenish decreased glutathione pool in cystinotic cell linesQ40508227
The Fanconi syndrome of cystinosis: insights into the pathophysiologyQ40842323
The quantitatively important relationship between homocysteine metabolism and glutathione synthesis by the transsulfuration pathway and its regulation by redox changesQ40847581
Glutathione depletion and increased apoptosis rate in human cystinotic proximal tubular cellsQ42491489
Sulfasalazine, a potent suppressor of lymphoma growth by inhibition of the x(c)- cystine transporter: a new action for an old drugQ43756729
Lysosomal cystine storage augments apoptosis in cultured human fibroblasts and renal tubular epithelial cellsQ44223955
Elevated oxidized glutathione in cystinotic proximal tubular epithelial cellsQ46734471
Impaired activity of the gamma-glutamyl cycle in nephropathic cystinosis fibroblastsQ46913688
A functional transsulfuration pathway in the brain links to glutathione homeostasis.Q48411596
Increased apoptosis in cystinotic fibroblasts and renal proximal tubule epithelial cells results from cysteinylation of protein kinase Cdelta.Q53587514
Cystine metabolism in human fibroblasts. Comparison of normal, cystinotic, and gamma-glutamylcysteine synethetase-deficient cellsQ67739092
DEFICIENCIES OF -SH-DEPENDENT ENZYMES IN CYSTINOSISQ78448478
P433issue4
P304page(s)384-388
P577publication date2009-12-21
P1433published inMolecular Genetics and MetabolismQ6895949
P1476titleThe redox status of cystinotic fibroblasts
P478volume99

Reverse relations

cites work (P2860)
Q36695581Biosynthesis and Reactivity of Cysteine Persulfides in Signaling
Q92774155Gamma-glutamylcysteine synthetase and tryparedoxin 1 exert high control on the antioxidant system in Trypanosoma cruzi contributing to drug resistance and infectivity
Q46027363N-acetyl-cysteine is associated to renal function improvement in patients with nephropathic cystinosis.
Q60920377The Role of Cystinosin in the Intermediary Thiol Metabolism and Redox Homeostasis in Kidney Proximal Tubular Cells
Q42913520The incidence of atubular glomeruli in nephropathic cystinosis renal biopsies
Q37786450The pathogenesis of cystinosis: mechanisms beyond cystine accumulation

Search more.