scholarly article | Q13442814 |
P2093 | author name string | Ruma Banerjee | |
Victor Vitvitsky | |||
Jess Thoene | |||
Marc Witcher | |||
P2860 | cites work | Kinetics and inhibition of recombinant human cystathionine gamma-lyase. Toward the rational control of transsulfuration | Q22009446 |
Altered status of glutathione and its metabolites in cystinotic cells | Q24305285 | ||
Identification and subcellular localization of a new cystinosin isoform | Q24310549 | ||
A novel gene encoding an integral membrane protein is mutated in nephropathic cystinosis | Q24322985 | ||
Cystinosis. Intracellular cystine depletion by aminothiols in vitro and in vivo | Q35902688 | ||
Potential role of apoptosis in development of the cystinotic phenotype | Q35995221 | ||
A review of the role of enhanced apoptosis in the pathophysiology of cystinosis | Q36922753 | ||
Glutathione precursors replenish decreased glutathione pool in cystinotic cell lines | Q40508227 | ||
The Fanconi syndrome of cystinosis: insights into the pathophysiology | Q40842323 | ||
The quantitatively important relationship between homocysteine metabolism and glutathione synthesis by the transsulfuration pathway and its regulation by redox changes | Q40847581 | ||
Glutathione depletion and increased apoptosis rate in human cystinotic proximal tubular cells | Q42491489 | ||
Sulfasalazine, a potent suppressor of lymphoma growth by inhibition of the x(c)- cystine transporter: a new action for an old drug | Q43756729 | ||
Lysosomal cystine storage augments apoptosis in cultured human fibroblasts and renal tubular epithelial cells | Q44223955 | ||
Elevated oxidized glutathione in cystinotic proximal tubular epithelial cells | Q46734471 | ||
Impaired activity of the gamma-glutamyl cycle in nephropathic cystinosis fibroblasts | Q46913688 | ||
A functional transsulfuration pathway in the brain links to glutathione homeostasis. | Q48411596 | ||
Increased apoptosis in cystinotic fibroblasts and renal proximal tubule epithelial cells results from cysteinylation of protein kinase Cdelta. | Q53587514 | ||
Cystine metabolism in human fibroblasts. Comparison of normal, cystinotic, and gamma-glutamylcysteine synethetase-deficient cells | Q67739092 | ||
DEFICIENCIES OF -SH-DEPENDENT ENZYMES IN CYSTINOSIS | Q78448478 | ||
P433 | issue | 4 | |
P304 | page(s) | 384-388 | |
P577 | publication date | 2009-12-21 | |
P1433 | published in | Molecular Genetics and Metabolism | Q6895949 |
P1476 | title | The redox status of cystinotic fibroblasts | |
P478 | volume | 99 |
Q36695581 | Biosynthesis and Reactivity of Cysteine Persulfides in Signaling |
Q92774155 | Gamma-glutamylcysteine synthetase and tryparedoxin 1 exert high control on the antioxidant system in Trypanosoma cruzi contributing to drug resistance and infectivity |
Q46027363 | N-acetyl-cysteine is associated to renal function improvement in patients with nephropathic cystinosis. |
Q60920377 | The Role of Cystinosin in the Intermediary Thiol Metabolism and Redox Homeostasis in Kidney Proximal Tubular Cells |
Q42913520 | The incidence of atubular glomeruli in nephropathic cystinosis renal biopsies |
Q37786450 | The pathogenesis of cystinosis: mechanisms beyond cystine accumulation |
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