| scholarly article | Q13442814 |
| P356 | DOI | 10.1007/S10858-011-9491-7 |
| P2888 | exact match | https://scigraph.springernature.com/pub.10.1007/s10858-011-9491-7 |
| P932 | PMC publication ID | 4123122 |
| P698 | PubMed publication ID | 21461951 |
| P50 | author | Reza M. Salek | Q29406339 |
| Jonathan D. Cooper | Q37835226 | ||
| Julian L Griffin | Q84304363 | ||
| Russell J Mortishire-Smith | Q117256970 | ||
| P2093 | author name string | Hannah M Mitchison | |
| David A Pearce | |||
| Michael R Pears | |||
| P2860 | cites work | The neuronal ceroid lipofuscinoses in human EPMR and mnd mutant mice are associated with mutations in CLN8 | Q22010604 |
| CLN3 protein is targeted to neuronal synapses but excluded from synaptic vesicles: new clues to Batten disease | Q24291761 | ||
| The gene mutated in variant late-infantile neuronal ceroid lipofuscinosis (CLN6) and in nclf mutant mice encodes a novel predicted transmembrane protein | Q24291949 | ||
| Defective lysosomal arginine transport in juvenile Batten disease | Q24292865 | ||
| Interconnections of CLN3, Hook1 and Rab proteins link Batten disease to defects in the endocytic pathway | Q24306585 | ||
| Biosynthesis and intracellular targeting of the CLN3 protein defective in Batten disease | Q24310339 | ||
| Accumulation of the adenosine triphosphate synthase subunit C in the mnd mutant mouse. A model for neuronal ceroid lipofuscinosis | Q24676562 | ||
| A role in vacuolar arginine transport for yeast Btn1p and for human CLN3, the protein defective in Batten disease | Q27935391 | ||
| Action of BTN1, the yeast orthologue of the gene mutated in Batten disease | Q27940056 | ||
| Intraneuronal N-acetylaspartate supplies acetyl groups for myelin lipid synthesis: evidence for myelin-associated aspartoacylase | Q28214332 | ||
| A mouse gene knockout model for juvenile ceroid-lipofuscinosis (Batten disease) | Q28504695 | ||
| High resolution 1H NMR-based metabolomics indicates a neurotransmitter cycling deficit in cerebral tissue from a mouse model of Batten disease | Q28505711 | ||
| Apparent loss and hypertrophy of interneurons in a mouse model of neuronal ceroid lipofuscinosis: evidence for partial response to insulin-like growth factor-1 treatment | Q28512342 | ||
| Retinal degeneration in motor neuron degeneration: a mouse model of ceroid lipofuscinosis | Q28585329 | ||
| Neuronal ceroid lipofuscinosis (nclf), a new disorder of the mouse linked to chromosome 9 | Q28591663 | ||
| Targeted disruption of the Cln3 gene provides a mouse model for Batten disease. The Batten Mouse Model Consortium [corrected] | Q28593659 | ||
| A comparison of cell and tissue extraction techniques using high-resolution 1H-NMR spectroscopy | Q30673134 | ||
| A metabolomic study of the CRND8 transgenic mouse model of Alzheimer's disease | Q33558010 | ||
| Progress towards understanding the neurobiology of Batten disease or neuronal ceroid lipofuscinosis | Q35088229 | ||
| Selectivity and types of cell death in the neuronal ceroid lipofuscinoses | Q35681068 | ||
| Two motifs target Batten disease protein CLN3 to lysosomes in transfected nonneuronal and neuronal cells | Q40648630 | ||
| The neuronal ceroid-lipofuscinoses. Recent advances. | Q40870662 | ||
| Proton NMR chemical shifts and coupling constants for brain metabolites | Q41742652 | ||
| Changes in GABAergic neuron distribution in situ and in neuron cultures in ovine (OCL6) Batten disease | Q42510998 | ||
| Isolation and chromosomal mapping of a mouse homolog of the Batten disease gene CLN3. | Q42638704 | ||
| An autoantibody inhibitory to glutamic acid decarboxylase in the neurodegenerative disorder Batten disease | Q44002736 | ||
| Glutamate-glutamine cycling in the epileptic human hippocampus | Q44053296 | ||
| Impaired glutamate transport and glutamate-glutamine cycling: downstream effects of the Huntington mutation | Q44075664 | ||
| Vitamin E deficiency and metabolic deficits in neuronal ceroid lipofuscinosis described by bioinformatics. | Q44186141 | ||
| Analysis of phospholipid molecular species in brains from patients with infantile and juvenile neuronal-ceroid lipofuscinosis using liquid chromatography-electrospray ionization mass spectrometry | Q44326511 | ||
| Glutamine synthetase and glutamate dehydrogenase in the prefrontal cortex of patients with schizophrenia | Q44466187 | ||
| Regional and cellular neuropathology in the palmitoyl protein thioesterase-1 null mutant mouse model of infantile neuronal ceroid lipofuscinosis | Q44933210 | ||
| Altered arginine metabolism in the central nervous system (CNS) of the Cln3-/- mouse model of juvenile Batten disease | Q46089492 | ||
| A metabolomic study of brain tissues from aged mice with low expression of the vesicular monoamine transporter 2 (VMAT2) gene | Q46880259 | ||
| The relationship between lipofuscin pigment and ageing in the human nervous system | Q48184293 | ||
| Late onset neurodegeneration in the Cln3-/- mouse model of juvenile neuronal ceroid lipofuscinosis is preceded by low level glial activation. | Q52087477 | ||
| btn1, the Schizosaccharomyces pombe homologue of the human Batten disease gene CLN3, regulates vacuole homeostasis. | Q53648890 | ||
| Orthogonal projections to latent structures (O-PLS) | Q56435041 | ||
| Ultrastructural changes in neurons of the spinal anterior horn of ageing mice with particular reference to the accumulation of lipofuscin pigment | Q69757110 | ||
| P433 | issue | 3-4 | |
| P407 | language of work or name | English | Q1860 |
| P304 | page(s) | 175-184 | |
| P577 | publication date | 2011-04-03 | |
| P1433 | published in | Journal of Biomolecular NMR | Q3186900 |
| P1476 | title | A metabolomic comparison of mouse models of the Neuronal Ceroid Lipofuscinoses | |
| P478 | volume | 49 |
| Q83459950 | Application of NMR spectroscopy in metabolomics |
| Q89380382 | Astrocytes in juvenile neuronal ceroid lipofuscinosis (CLN3) display metabolic and calcium signaling abnormalities |
| Q47140069 | Defective synaptic transmission causes disease signs in a mouse model of juvenile neuronal ceroid lipofuscinosis. |
| Q37561375 | Efficacy of phosphodiesterase-4 inhibitors in juvenile Batten disease (CLN3). |
| Q35149204 | Evidence for aberrant astrocyte hemichannel activity in Juvenile Neuronal Ceroid Lipofuscinosis (JNCL). |
| Q35262533 | Intracellular redox state revealed by in vivo (31) P MRS measurement of NAD(+) and NADH contents in brains |
| Q47848197 | Microglia in juvenile neuronal ceroid lipofuscinosis are primed toward a pro-inflammatory phenotype |
| Q38119451 | NMR-based metabolomics coupled with pattern recognition methods in biomarker discovery and disease diagnosis |
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