| scholarly article | Q13442814 |
| P50 | author | Tammy Kielian | Q60974638 |
| P2093 | author name string | Megan E Bosch | |
| P2860 | cites work | Defective lysosomal arginine transport in juvenile Batten disease | Q24292865 |
| Clarifying lysosomal storage diseases | Q24620532 | ||
| Membrane trafficking and mitochondrial abnormalities precede subunit c deposition in a cerebellar cell model of juvenile neuronal ceroid lipofuscinosis | Q24791822 | ||
| Thrombospondins as key regulators of synaptogenesis in the central nervous system | Q27024828 | ||
| Distinct early molecular responses to mutations causing vLINCL and JNCL presage ATP synthase subunit C accumulation in cerebellar cells | Q27354870 | ||
| Altered Glutamate Reuptake in Relapsing-Remitting and Secondary Progressive Multiple Sclerosis Cortex: Correlation With Microglia Infiltration, Demyelination, and Neuronal and Synaptic Damage | Q61478748 | ||
| Kainate, N-methylaspartate and other excitatory amino acids increase calcium influx into rat brain cortex cells in vitro | Q72554324 | ||
| Cln3(Deltaex7/8) knock-in mice with the common JNCL mutation exhibit progressive neurologic disease that begins before birth | Q78358538 | ||
| Fibrates inhibit the apoptosis of Batten disease lymphoblast cells via autophagy recovery and regulation of mitochondrial membrane potential | Q86893846 | ||
| Astrocyte Ca²⁺ signalling: an unexpected complexity | Q87696402 | ||
| Astrocytes: biology and pathology | Q27490746 | ||
| New tools for investigating astrocyte-to-neuron communication | Q27690725 | ||
| Molecular basis of the neuronal ceroid lipofuscinoses: mutations in CLN1, CLN2, CLN3, and CLN5 | Q28143871 | ||
| Isolation of a novel gene underlying Batten disease, CLN3. The International Batten Disease Consortium | Q28288921 | ||
| Interactions of the proteins of neuronal ceroid lipofuscinosis: clues to function | Q28289653 | ||
| High throughput microplate respiratory measurements using minimal quantities of isolated mitochondria | Q28479257 | ||
| Neuronal vulnerability of CLN3 deletion to calcium-induced cytotoxicity is mediated by calsenilin | Q28504443 | ||
| High resolution 1H NMR-based metabolomics indicates a neurotransmitter cycling deficit in cerebral tissue from a mouse model of Batten disease | Q28505711 | ||
| Motor neuron degeneration of mice is a model of neuronal ceroid lipofuscinosis (Batten's disease) | Q28506323 | ||
| Thrombospondins are astrocyte-secreted proteins that promote CNS synaptogenesis | Q28574686 | ||
| Control of synapse number by glia | Q31832872 | ||
| Alteration of the glutamate and GABA transporters in the hippocampus of the Niemann-Pick disease, type C mouse using proteomic analysis | Q33232283 | ||
| A metabolomic comparison of mouse models of the Neuronal Ceroid Lipofuscinoses | Q34007930 | ||
| Hemichannels in neurodegenerative diseases: is there a link to pathology? | Q34068976 | ||
| Age-dependent therapeutic effect of memantine in a mouse model of juvenile Batten disease | Q34280201 | ||
| Glutamate-mediated astrocyte-neuron signalling | Q34322476 | ||
| Astrocyte calcium signaling: the third wave | Q34510958 | ||
| Juvenile neuronal ceroid-lipofuscinosis (Batten disease): a brief review and update | Q34693507 | ||
| Attenuation of AMPA receptor activity improves motor skills in a mouse model of juvenile Batten disease | Q34707128 | ||
| ATP and glutamate released via astroglial connexin 43 hemichannels mediate neuronal death through activation of pannexin 1 hemichannels | Q35024390 | ||
| The neuronal ceroid-lipofuscinoses | Q35045618 | ||
| Methylglyoxal, the dark side of glycolysis | Q35063131 | ||
| Role of excitatory amino acid transporter-2 (EAAT2) and glutamate in neurodegeneration: opportunities for developing novel therapeutics. | Q35087565 | ||
| Evidence for aberrant astrocyte hemichannel activity in Juvenile Neuronal Ceroid Lipofuscinosis (JNCL). | Q35149204 | ||
| Altered sensitivity of cerebellar granule cells to glutamate receptor overactivation in the Cln3(Δex7/8)-knock-in mouse model of juvenile neuronal ceroid lipofuscinosis | Q35190279 | ||
| The glutamate and neutral amino acid transporter family: physiological and pharmacological implications | Q35581543 | ||
| Current state of clinical and morphological features in human NCL. | Q35681059 | ||
| Molecular mechanisms of glutamate-dependent neurodegeneration in ischemia and traumatic brain injury | Q35723626 | ||
| Unbiased Cell-based Screening in a Neuronal Cell Model of Batten Disease Highlights an Interaction between Ca2+ Homeostasis, Autophagy, and CLN3 Protein Function | Q35860759 | ||
| Astrocytic regulation of glutamate homeostasis in epilepsy | Q36032698 | ||
| Transporters for L-glutamate: an update on their molecular pharmacology and pathological involvement | Q36052481 | ||
| Standardized assessment of seizures in patients with juvenile neuronal ceroid lipofuscinosis | Q36175417 | ||
| Astrocyte-derived thrombospondins mediate the development of hippocampal presynaptic plasticity in vitro | Q36331898 | ||
| Astrocyte dysfunction in neurological disorders: a molecular perspective | Q36404127 | ||
| ??? | Q64787860 | ||
| Astrocytes modulate neural network activity by Ca²+-dependent uptake of extracellular K+. | Q36447585 | ||
| Functional biology of the neuronal ceroid lipofuscinoses (NCL) proteins. | Q36535298 | ||
| Diagnosis of the neuronal ceroid lipofuscinoses: an update | Q36576241 | ||
| Astrocyte calcium waves: what they are and what they do. | Q36606118 | ||
| L-glutamate released from activated microglia downregulates astrocytic L-glutamate transporter expression in neuroinflammation: the 'collusion' hypothesis for increased extracellular L-glutamate concentration in neuroinflammation | Q36618166 | ||
| Calcium and neurodegeneration | Q36747495 | ||
| Glutamate release from astrocytes in physiological conditions and in neurodegenerative disorders characterized by neuroinflammation | Q36902261 | ||
| Extracellular glutamate concentration in hippocampal slice | Q37163189 | ||
| Stress-induced neuroinflammation: mechanisms and new pharmacological targets. | Q37369927 | ||
| Regulation of synaptic connectivity by glia | Q37808619 | ||
| Mitochondrial dynamics in astrocytes. | Q38252272 | ||
| Towards a new understanding of NCL pathogenesis | Q38508905 | ||
| Glutamate excitotoxicity and Ca2+-regulation of respiration: Role of the Ca2+ activated mitochondrial transporters (CaMCs). | Q38802647 | ||
| Batten disease is linked to altered expression of mitochondria-related metabolic molecules. | Q39176588 | ||
| New nomenclature and classification scheme for the neuronal ceroid lipofuscinoses | Q39589019 | ||
| Multifunctional role of astrocytes as gatekeepers of neuronal energy supply | Q39734463 | ||
| Glutamate: A Neurotransmitter in Mammalian Brain | Q40092304 | ||
| Extracellular glutamate: functional compartments operate in different concentration ranges. | Q40255443 | ||
| Astrocytes and glutamate homoeostasis in Alzheimer's disease: a decrease in glutamine synthetase, but not in glutamate transporter-1, in the prefrontal cortex | Q41861166 | ||
| Phenotype of the accessory cell necessary for mitogen-stimulated T and B cell responses in human peripheral blood: delineation by its sensitivity to the lysosomotropic agent, L-leucine methyl ester | Q41920471 | ||
| Glial cells are functionally impaired in juvenile neuronal ceroid lipofuscinosis and detrimental to neurons. | Q42682614 | ||
| Selective Depletion of Microglia from Cerebellar Granule Cell Cultures Using L-leucine Methyl Ester. | Q42731409 | ||
| Inositol 1,4,5-trisphosphate signaling maintains the activity of glutamate uptake in Bergmann glia | Q42854323 | ||
| An autoantibody inhibitory to glutamic acid decarboxylase in the neurodegenerative disorder Batten disease | Q44002736 | ||
| Neuronal activity triggers calcium waves in hippocampal astrocyte networks | Q44496077 | ||
| Loss of glutamine synthetase in the human epileptogenic hippocampus: possible mechanism for raised extracellular glutamate in mesial temporal lobe epilepsy | Q44728453 | ||
| High-resolution magic angle spinning and 1H magnetic resonance spectroscopy reveal significantly altered neuronal metabolite profiles in CLN1 but not in CLN3. | Q45047884 | ||
| Reduced glutamine synthetase in hippocampal areas with neuron loss in temporal lobe epilepsy | Q45236751 | ||
| Thrombospondins 1 and 2 are necessary for synaptic plasticity and functional recovery after stroke | Q46438887 | ||
| Protracted juvenile neuronal ceroid lipofuscinosis--an autopsy report and immunohistochemical analysis | Q46964604 | ||
| Defective synaptic transmission causes disease signs in a mouse model of juvenile neuronal ceroid lipofuscinosis. | Q47140069 | ||
| Progressive Parkinsonism by acute dysfunction of excitatory amino acid transporters in the rat substantia nigra. | Q47804687 | ||
| Microglia in juvenile neuronal ceroid lipofuscinosis are primed toward a pro-inflammatory phenotype | Q47848197 | ||
| The concentration of synaptically released glutamate outside of the climbing fiber-Purkinje cell synaptic cleft | Q48181225 | ||
| Age-dependent alterations in neuronal activity in the hippocampus and visual cortex in a mouse model of Juvenile Neuronal Ceroid Lipofuscinosis (CLN3). | Q48375612 | ||
| Spontaneous intracellular calcium oscillations in cortical astrocytes from a patient with intractable childhood epilepsy (Rasmussen's encephalitis). | Q48574254 | ||
| Elevated basal glutamate and unchanged glutamine and GABA in refractory epilepsy: Microdialysis study of 79 patients at the yale epilepsy surgery program. | Q48785054 | ||
| Thalamocortical neuron loss and localized astrocytosis in the Cln3Deltaex7/8 knock-in mouse model of Batten disease. | Q48818717 | ||
| Localized proton magnetic resonance spectroscopy of cerebral metabolic disturbances in children with neuronal ceroid lipofuscinosis. | Q48895189 | ||
| Late onset neurodegeneration in the Cln3-/- mouse model of juvenile neuronal ceroid lipofuscinosis is preceded by low level glial activation. | Q52087477 | ||
| The profiles of mitochondrial respiration and glycolysis using extracellular flux analysis in porcine enterocyte IPEC-J2. | Q55020544 | ||
| Neuronal ceroid lipofuscinoses | Q56566989 | ||
| P433 | issue | 5 | |
| P921 | main subject | astrocyte | Q502961 |
| juvenile neuronal ceroid lipofuscinosis | Q1753778 | ||
| P304 | page(s) | 612-624 | |
| P577 | publication date | 2018-08-16 | |
| P1433 | published in | Journal of Neurochemistry | Q6295643 |
| P1476 | title | Astrocytes in juvenile neuronal ceroid lipofuscinosis (CLN3) display metabolic and calcium signaling abnormalities | |
| P478 | volume | 148 |
| Q58101765 | Neuronal Ceroid Lipofuscinoses: Connecting Calcium Signalling through Calmodulin |
| Q64244471 | Recent Insights into NCL Protein Function Using the Model Organism |
| Q92332907 | Synapse alterations precede neuronal damage and storage pathology in a human cerebral organoid model of CLN3-juvenile neuronal ceroid lipofuscinosis |
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