Lost after translation: insights from pulmonary surfactant for understanding the role of alveolar epithelial dysfunction and cellular quality control in fibrotic lung disease

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Lost after translation: insights from pulmonary surfactant for understanding the role of alveolar epithelial dysfunction and cellular quality control in fibrotic lung disease is …
instance of (P31):
review articleQ7318358
scholarly articleQ13442814

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P356DOI10.1152/AJPLUNG.00139.2015
P932PMC publication ID4572416
P698PubMed publication ID26186947

P2093author name stringSurafel Mulugeta
Michael F Beers
Shin-Ichi Nureki
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Post-translational processing of surfactant protein-C proprotein: targeting motifs in the NH(2)-terminal flanking domain are cleaved in late compartmentsQ40821326
Caspase-8 is required for cell death induced by expanded polyglutamine repeats.Q40961806
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Pulmonary surfactant-associated polypeptide C in a mixed organic solvent transforms from a monomeric alpha-helical state into insoluble beta-sheet aggregatesQ42846226
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Secretion of surfactant protein C, an integral membrane protein, requires the N-terminal propeptide.Q50336430
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Trafficking of newly synthesized surfactant protein A in isolated rat alveolar type II cells.Q50755821
Pneumonitis and emphysema in sp-C gene targeted mice.Q51691303
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ABCA3 is critical for lamellar body biogenesis in vivo.Q52579496
Insufficient autophagy in idiopathic pulmonary fibrosis.Q53138134
Carboxyl-terminal fragments of Alzheimer beta-amyloid precursor protein accumulate in restricted and unpredicted intracellular compartments in presenilin 1-deficient cells.Q53237328
Endoplasmic reticulum stress in alveolar epithelial cells is prominent in IPF: association with altered surfactant protein processing and herpesvirus infection.Q53486707
Surfactant protein C mutations are the basis of a significant portion of adult familial pulmonary fibrosis in a dutch cohort.Q54418482
A common mutation in the surfactant protein C gene associated with lung disease.Q54676468
Idiopathic pulmonary fibrosisQ56764887
ABCA3 as a Lipid Transporter in Pulmonary Surfactant BiogenesisQ57591393
XBP-1 deficiency in the nervous system reveals a homeostatic switch to activate autophagyQ60613336
P433issue6
P921main subjectquality controlQ827792
pulmonary surfactantQ28163641
P304page(s)L507-25
P577publication date2015-07-17
P1433published inAmerican Journal of Physiology - Lung Cellular and Molecular PhysiologyQ4352992
P1476titleLost after translation: insights from pulmonary surfactant for understanding the role of alveolar epithelial dysfunction and cellular quality control in fibrotic lung disease
P478volume309

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