Extensive phenotyping of individuals at risk for familial interstitial pneumonia reveals clues to the pathogenesis of interstitial lung disease.

scientific article

Extensive phenotyping of individuals at risk for familial interstitial pneumonia reveals clues to the pathogenesis of interstitial lung disease. is …
instance of (P31):
scholarly articleQ13442814

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P356DOI10.1164/RCCM.201406-1162OC
P932PMC publication ID4351594
P698PubMed publication ID25389906
P5875ResearchGate publication ID268524817

P50authorEric S. WhiteQ38324814
Jonathan Andrew KropskiQ89503711
Lorraine B. WareQ91134545
P2093author name stringLisa R Young
Timothy S Blackwell
Joyce E Johnson
Jae Woo Lee
Pierre P Massion
Leena Choi
Jonathan D Kurtis
Steve D Groshong
James E Loyd
Joy D Cogan
Amber L Degryse
Frank B McMahon
Linda A Gleaves
Rinat Zaynagetdinov
Vasiliy V Polosukhin
Mark P Steele
Dong-Sheng Cheng
William E Lawson
Joseph F Solus
John A Worrell
Lisa H Lancaster
Errine T Garnett
Otis B Rickman
Cheryl Markin
Donald F Zoz
Daphne B Mitchell
Brittany R Jones
Melinda E McConaha
Peter F Crossno
Jason M Pritchett
John A Phillips Iii
P2860cites workClinical and pathologic features of familial interstitial pneumoniaQ36234581
Transbronchial biopsy is useful in predicting UIP patternQ36402285
High-resolution CT scan findings in familial interstitial pneumonia do not conform to those of idiopathic interstitial pneumoniaQ36447397
Genetic studies provide clues on the pathogenesis of idiopathic pulmonary fibrosisQ36485998
Short telomeres are a risk factor for idiopathic pulmonary fibrosisQ36861819
Telomere shortening in familial and sporadic pulmonary fibrosisQ36915503
Generalized linear mixed models: a review and some extensionsQ37000464
MUC5B promoter polymorphism and interstitial lung abnormalitiesQ37105760
Maternal infection with Schistosoma japonicum induces a profibrotic response in neonatesQ37548047
Viral infection and aging as cofactors for the development of pulmonary fibrosisQ37815487
Heterozygosity for a surfactant protein C gene mutation associated with usual interstitial pneumonitis and cellular nonspecific interstitial pneumonitis in one kindredQ42675595
Blood biomarkers MMP-7 and SP-A: predictors of outcome in idiopathic pulmonary fibrosis.Q50954787
Endoplasmic reticulum stress in alveolar epithelial cells is prominent in IPF: association with altered surfactant protein processing and herpesvirus infection.Q53486707
Familial idiopathic pulmonary fibrosis. Evidence of lung inflammation in unaffected family membersQ69497791
Serum surfactant proteins A and D as prognostic factors in idiopathic pulmonary fibrosis and their relationship to disease extentQ74316652
Pulmonary fibrosis in familiesQ79076907
Characterization of fibroblast-specific protein 1 in pulmonary fibrosisQ81196614
Histopathologic findings of transbronchial biopsy in usual interstitial pneumoniaQ84343989
VarScan 2: somatic mutation and copy number alteration discovery in cancer by exome sequencingQ24628978
A surfactant protein C precursor protein BRICHOS domain mutation causes endoplasmic reticulum stress, proteasome dysfunction, and caspase 3 activationQ24645087
A mutation in the surfactant protein C gene associated with familial interstitial lung diseaseQ28201394
Familial pulmonary fibrosis is the strongest risk factor for idiopathic pulmonary fibrosisQ28247967
A novel dyskerin (DKC1) mutation is associated with familial interstitial pneumoniaQ28307444
MMP1 and MMP7 as potential peripheral blood biomarkers in idiopathic pulmonary fibrosisQ28472658
Genome-wide association study identifies multiple susceptibility loci for pulmonary fibrosisQ28943334
Epidemiology Standardization Project (American Thoracic Society)Q29614936
Telomerase mutations in families with idiopathic pulmonary fibrosisQ29615671
Genetic defects in surfactant protein A2 are associated with pulmonary fibrosis and lung cancer.Q30374030
Periostin promotes fibrosis and predicts progression in patients with idiopathic pulmonary fibrosisQ30415751
Epithelial endoplasmic reticulum stress and apoptosis in sporadic idiopathic pulmonary fibrosisQ30484036
Epstein-Barr virus replication within pulmonary epithelial cells in cryptogenic fibrosing alveolitis.Q33605234
C-X-C motif chemokine 13 (CXCL13) is a prognostic biomarker of idiopathic pulmonary fibrosisQ33901646
The elevation of serum napsin A in idiopathic pulmonary fibrosis, compared with KL-6, surfactant protein-A and surfactant protein-D.Q34410117
Comparative study of KL-6, surfactant protein-A, surfactant protein-D, and monocyte chemoattractant protein-1 as serum markers for interstitial lung diseases.Q34520692
Schistosoma japonicum soluble egg antigens attenuate invasion in a first trimester human placental trophoblast modelQ34766888
Natural history of pulmonary fibrosis in two subjects with the same telomerase mutationQ34923419
The MUC5B variant is associated with idiopathic pulmonary fibrosis but not with systemic sclerosis interstitial lung disease in the European Caucasian populationQ34935466
Genetics in pulmonary fibrosis--familial cases provide clues to the pathogenesis of idiopathic pulmonary fibrosisQ35010171
Herpesvirus DNA is consistently detected in lungs of patients with idiopathic pulmonary fibrosisQ35027515
A variant in the promoter of MUC5B and idiopathic pulmonary fibrosisQ35083039
Viral infection in acute exacerbation of idiopathic pulmonary fibrosisQ35107245
Peripheral blood proteins predict mortality in idiopathic pulmonary fibrosisQ35683018
Adult-onset pulmonary fibrosis caused by mutations in telomeraseQ35759839
Telomere length assessment in human archival tissues: combined telomere fluorescence in situ hybridization and immunostainingQ35788945
Right place, right time: the evolving role of herpesvirus infection as a "second hit" in idiopathic pulmonary fibrosisQ35850237
Early interstitial lung disease in familial pulmonary fibrosisQ36013730
A common MUC5B promoter polymorphism and pulmonary fibrosis.Q36048530
Transbronchial biopsy in usual interstitial pneumoniaQ36168852
P433issue4
P407language of work or nameEnglishQ1860
P921main subjectpneumoniaQ12192
P304page(s)417-426
P577publication date2015-02-01
P1433published inAmerican Journal of Respiratory and Critical Care MedicineQ4744267
P1476titleExtensive phenotyping of individuals at risk for familial interstitial pneumonia reveals clues to the pathogenesis of interstitial lung disease
P478volume191

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