| P2093 | author name string | Bo Wang | |
| | Li Zeng | |
| | Henry L Paulson | |
| | Roger L Albin | |
| | Sara J Tallaksen-Greene | |
| | Maria do Carmo Costa | |
| | Biswarathan Ramani | |
| | Eiko N Minakawa | |
| | Sean A Merillat | |
| | Matthew D Perkins | |
| P2860 | cites work | The de-ubiquitinating enzyme ataxin-3 does not modulate disease progression in a knock-in mouse model of Huntington disease | Q37663855 |
| | Removing protein aggregates: the role of proteolysis in neurodegeneration | Q37875163 |
| | Ubiquilins in the crosstalk among proteolytic pathways | Q38013079 |
| | Ubiquilin 2: a component of the ubiquitin-proteasome system with an emerging role in neurodegeneration | Q38192847 |
| | Ubiquilin interacts and enhances the degradation of expanded-polyglutamine proteins | Q39695136 |
| | Suppression of polyglutamine-induced toxicity in cell and animal models of Huntington's disease by ubiquilin | Q40320091 |
| | Identification of ubiquitin-interacting proteins in purified polyglutamine aggregates | Q40530955 |
| | Evidence of a link between ubiquilin 2 and optineurin in amyotrophic lateral sclerosis | Q45232740 |
| | Ubiquilin-1 immunoreactivity is concentrated on Hirano bodies and dystrophic neurites in Alzheimer's disease brains. | Q48040772 |
| | Ubiquilin immunoreactivity in cytoplasmic and nuclear inclusions in synucleinopathies, polyglutamine diseases and intranuclear inclusion body disease | Q48484899 |
| | YAC transgenic mice carrying pathological alleles of the MJD1 locus exhibit a mild and slowly progressive cerebellar deficit | Q48620970 |
| | Intranuclear inclusions of expanded polyglutamine protein in spinocerebellar ataxia type 3. | Q48644018 |
| | Identification of ubiquilin, a novel presenilin interactor that increases presenilin protein accumulation | Q24290515 |
| | Ubiquilin interacts with ubiquitylated proteins and proteasome through its ubiquitin-associated and ubiquitin-like domains | Q24293422 |
| | The UBL domain of PLIC-1 regulates aggresome formation | Q24311874 |
| | Alzheimer's disease-associated ubiquilin-1 regulates presenilin-1 accumulation and aggresome formation | Q24314297 |
| | Ubiquilin functions in autophagy and is degraded by chaperone-mediated autophagy | Q24317381 |
| | Laforin is required for the functional activation of malin in endoplasmic reticulum stress resistance in neuronal cells | Q24320315 |
| | Ubiquilin and p97/VCP bind erasin, forming a complex involved in ERAD | Q24324707 |
| | Live-cell imaging reveals divergent intracellular dynamics of polyglutamine disease proteins and supports a sequestration model of pathogenesis. | Q24534867 |
| | Mutations in UBQLN2 cause dominant X-linked juvenile and adult-onset ALS and ALS/dementia | Q24600027 |
| | Ubiquilin-1 is a molecular chaperone for the amyloid precursor protein | Q24634983 |
| | Structural studies of the interaction between ubiquitin family proteins and proteasome subunit S5a | Q27637621 |
| | ALS-linked mutations in ubiquilin-2 or hnRNPA1 reduce interaction between ubiquilin-2 and hnRNPA1 | Q28115018 |
| | The hPLIC proteins may provide a link between the ubiquitination machinery and the proteasome | Q28138493 |
| | Ubiquitin-related proteins regulate interaction of vimentin intermediate filaments with the plasma membrane | Q28146189 |
| | The roles of intracellular protein-degradation pathways in neurodegeneration | Q28269322 |
| | Ubiquitin ligase Hrd1 enhances the degradation and suppresses the toxicity of polyglutamine-expanded huntingtin | Q28276832 |
| | Neurological abnormalities in a knock-in mouse model of Huntington's disease | Q28508179 |
| | Reversing neurodegeneration: a promise unfolds | Q33897927 |
| | Early autophagic response in a novel knock-in model of Huntington disease | Q34112214 |
| | Ubiquilin 2 is not associated with tau pathology | Q35006416 |
| | A knockin mouse model of spinocerebellar ataxia type 3 exhibits prominent aggregate pathology and aberrant splicing of the disease gene transcript. | Q35063135 |
| | Signature changes in ubiquilin expression in the R6/2 mouse model of Huntington's disease | Q35122320 |
| | Pattern of ubiquilin pathology in ALS and FTLD indicates presence of C9ORF72 hexanucleotide expansion | Q36464731 |
| | Toward RNAi therapy for the polyglutamine disease Machado-Joseph disease | Q37254846 |
| | Ubiquilin-1 overexpression increases the lifespan and delays accumulation of Huntingtin aggregates in the R6/2 mouse model of Huntington's disease | Q37521285 |
| | Unbiased screen reveals ubiquilin-1 and -2 highly associated with huntingtin inclusions | Q37555526 |
| | An emerging role for Ubiquilin 1 in regulating protein quality control system and in disease pathogenesis | Q37601590 |
| P304 | page(s) | 281-288 | |
| P577 | publication date | 2015-06-30 | |
| P1433 | published in | Neurobiology of Disease | Q15716606 |
| P1476 | title | Differential recruitment of UBQLN2 to nuclear inclusions in the polyglutamine diseases HD and SCA3. | |
| P478 | volume | 82 | |