| P2093 | author name string | Scott H Randell | |
| | Alessandra Livraghi | |
| P2860 | cites work | Evidence for periciliary liquid layer depletion, not abnormal ion composition, in the pathogenesis of cystic fibrosis airways disease | Q22008612 |
| | The Ciliopathies: An Emerging Class of Human Genetic Disorders | Q22337032 |
| | Disruption of an inner arm dynein heavy chain gene results in asthenozoospermia and reduced ciliary beat frequency | Q24291253 |
| | Mutations in DNAH5 cause primary ciliary dyskinesia and randomization of left-right asymmetry | Q24292162 |
| | Mislocalization of DNAH5 and DNAH9 in respiratory cells from patients with primary ciliary dyskinesia | Q24297464 |
| | Mutations of DNAI1 in primary ciliary dyskinesia: evidence of founder effect in a common mutation | Q24297678 |
| | Mutations in the DNAH11 (axonemal heavy chain dynein type 11) gene cause one form of situs inversus totalis and most likely primary ciliary dyskinesia | Q24302250 |
| | DNAH5 mutations are a common cause of primary ciliary dyskinesia with outer dynein arm defects | Q24318839 |
| | Effects of reduced mucus oxygen concentration in airway Pseudomonas infections of cystic fibrosis patients | Q24551181 |
| | Antimicrobial polypeptides in host defense of the respiratory tract | Q24551612 |
| | Cloned ferrets produced by somatic cell nuclear transfer | Q24671916 |
| | Assembly and motility of eukaryotic cilia and flagella. Lessons from Chlamydomonas reinhardtii | Q24679249 |
| | Cystic fibrosis | Q28250200 |
| | Increased airway epithelial Na+ absorption produces cystic fibrosis-like lung disease in mice | Q28255797 |
| | Pathophysiology of gene-targeted mouse models for cystic fibrosis | Q28295602 |
| | Mutation of the mouse hepatocyte nuclear factor/forkhead homologue 4 gene results in an absence of cilia and random left-right asymmetry | Q28506579 |
| | Ciliogenesis and left-right axis defects in forkhead factor HFH-4-null mice | Q28511679 |
| | Loss of function of axonemal dynein Mdnah5 causes primary ciliary dyskinesia and hydrocephalus | Q28588205 |
| | The primary cilium as the cell's antenna: signaling at a sensory organelle | Q29615165 |
| | The nature of small-airway obstruction in chronic obstructive pulmonary disease | Q29618682 |
| | Primary ciliary dyskinesia (PCD). | Q33875838 |
| | Pseudomonas aeruginosa pili bind to asialoGM1 which is increased on the surface of cystic fibrosis epithelial cells | Q33905211 |
| | No deleterious mutations in the FOXJ1 (alias HFH-4) gene in patients with primary ciliary dyskinesia (PCD). | Q33923991 |
| | An animal model for cystic fibrosis made by gene targeting | Q33970549 |
| | Role of the cystic fibrosis transmembrane conductance regulator in innate immunity to Pseudomonas aeruginosa infections | Q33988505 |
| | Normal and cystic fibrosis airway surface liquid homeostasis. The effects of phasic shear stress and viral infections | Q34074636 |
| | Nucleotide release provides a mechanism for airway surface liquid homeostasis | Q34145045 |
| | Hydrocephalus, situs inversus, chronic sinusitis, and male infertility in DNA polymerase lambda-deficient mice: possible implication for the pathogenesis of immotile cilia syndrome | Q34277881 |
| | An incredible decade for the primary cilium: a look at a once-forgotten organelle | Q34465976 |
| | A Human Syndrome Caused by Immotile Cilia | Q34509138 |
| | To beat or not to beat: roles of cilia in development and disease | Q34532445 |
| | Mucus clearance as a primary innate defense mechanism for mammalian airways | Q34551378 |
| | Nodal flow and the generation of left-right asymmetry. | Q34652060 |
| | Characteristic multiorgan pathology of cystic fibrosis in a long-living cystic fibrosis transmembrane regulator knockout murine model | Q35097413 |
| | Complement receptor expression on neutrophils at an inflammatory site, the Pseudomonas-infected lung in cystic fibrosis | Q35816211 |
| | Animal models of cystic fibrosis | Q35908456 |
| | Cilia-related diseases | Q35923569 |
| | Cystic fibrosis and airway submucosal glands | Q36109703 |
| | Cilia and disease | Q36139798 |
| | Familial immotile-cilia syndrome in English springer spaniel dogs. | Q36233023 |
| | Regulation of airway surface liquid volume and mucus transport by active ion transport | Q36236753 |
| | Submucosal glands and airway defense | Q36236757 |
| | From mucins to mucus: toward a more coherent understanding of this essential barrier | Q36236761 |
| | Cystic fibrosis since 1938. | Q36242757 |
| | Innate immunity and the lung: defense at the interface between host and environment | Q36266916 |
| | Primary ciliary dyskinesia: clinical presentation, diagnosis and genetics | Q36276303 |
| | Soluble mediators, not cilia, determine airway surface liquid volume in normal and cystic fibrosis superficial airway epithelia | Q36295665 |
| | Innate immunity in the lungs | Q36328672 |
| | Respiratory tract mucin genes and mucin glycoproteins in health and disease | Q36350071 |
| | Airway mucus: From production to secretion. | Q36369409 |
| | Global physiology and pathophysiology of cough: ACCP evidence-based clinical practice guidelines | Q36374694 |
| | Regulation of normal and cystic fibrosis airway surface liquid volume by phasic shear stress | Q36387933 |
| | The physiology of cough | Q36394734 |
| | Effective mucus clearance is essential for respiratory health | Q36417678 |
| | Ciliary function and the role of cilia in clearance | Q36427314 |
| | Novel tools to unravel molecular mechanisms in cilia-related disorders | Q36431322 |
| | Intraflagellar transport and cilium-based signaling | Q36469857 |
| | Innate immune response in CF airway epithelia: hyperinflammatory? | Q36529532 |
| | Lung disease in mice with cystic fibrosis | Q37376391 |
| | Reduced three-dimensional motility in dehydrated airway mucus prevents neutrophil capture and killing bacteria on airway epithelial surfaces | Q40400409 |
| | Anomalies in ion transport in CF mouse tracheal epithelium | Q42496060 |
| | Ultrastructural nasal pathology in children chronically and sequentially exposed to air pollutants | Q42498505 |
| | The CF salt controversy: in vivo observations and therapeutic approaches. | Q43711753 |
| | Respiratory infections with Pseudomonas aeruginosa in children with cystic fibrosis: early detection by serology and assessment of risk factors | Q44019374 |
| | Preservation of Tracheal Mucus by Nonaqueous Fixative | Q44437057 |
| | Loss of binding and entry of liposome-DNA complexes decreases transfection efficiency in differentiated airway epithelial cells | Q45880343 |
| | Cystic fibrosis transmembrane conductance regulator function is suppressed in cigarette smokers. | Q46960635 |
| | Inhibition of chloride secretion in human bronchial epithelial cells by cigarette smoke extract | Q47872407 |
| | Investigation of the possible role of a novel gene, DPCD, in primary ciliary dyskinesia | Q48219291 |
| | Primary ciliary dyskinesia: diagnostic and phenotypic features. | Q51640417 |
| | Further studies on knockout mice lacking a functional dynein heavy chain (MDHC7). 2. A developmental explanation for the asthenozoospermia. | Q52052027 |
| P433 | issue | 1 | |
| P407 | language of work or name | English | Q1860 |
| P921 | main subject | cystic fibrosis | Q178194 |
| P304 | page(s) | 116-129 | |
| P577 | publication date | 2007-01-01 | |
| P1433 | published in | Toxicologic Pathology | Q7830407 |
| P1476 | title | Cystic fibrosis and other respiratory diseases of impaired mucus clearance | |
| P478 | volume | 35 | |