| scholarly article | Q13442814 |
| P2093 | author name string | Peter R Durie | |
| M James Phillips | |||
| Cameron A Ackerley | |||
| Geraldine Kent | |||
| P2860 | cites work | Identification of the cystic fibrosis gene: chromosome walking and jumping | Q22299423 |
| An animal model for cystic fibrosis made by gene targeting | Q33970549 | ||
| Enhanced susceptibility to pulmonary infection with Burkholderia cepacia in Cftr(-/-) mice | Q34008714 | ||
| Pathology of cystic fibrosis review of the literature and comparison with 146 autopsied cases | Q34426002 | ||
| A mouse model for the delta F508 allele of cystic fibrosis. | Q35765143 | ||
| Cystic fibrosis mice carrying the missense mutation G551D replicate human genotype-phenotype correlations. | Q35844736 | ||
| Quantitative evaluation of the development of the exocrine pancreas in cystic fibrosis and control infants | Q36092902 | ||
| Lung disease in mice with cystic fibrosis | Q37376391 | ||
| Lavage treatment of distal intestinal obstruction syndrome in children with cystic fibrosis | Q39525226 | ||
| Modulation of disease severity in cystic fibrosis transmembrane conductance regulator deficient mice by a secondary genetic factor | Q41226239 | ||
| Generation of cAMP-Activated Chloride Currents by Expression of CFTR | Q41695755 | ||
| The lung in cystic fibrosis. A quantitative study including prevalence of pathologic findings among different age groups | Q42038566 | ||
| Early alterations in airway mucociliary clearance and inflammation of the lamina propria in CF mice | Q42437504 | ||
| Cystic fibrosis genotypes and views on screening are both heterogeneous and population related | Q43146329 | ||
| Parotid Gland Function in Children with Cystic Fibrosis and Child Control Subjects | Q46768185 | ||
| Generation and characterization of a delta F508 cystic fibrosis mouse model. | Q52207066 | ||
| Cystic fibrosis in the mouse by targeted insertional mutagenesis | Q52477870 | ||
| G551D Cystic Fibrosis Mice Exhibit Abnormal Regulation of Inflammation in Lungs and Macrophages | Q56879965 | ||
| Age-related alterations in immunoreactive pancreatic lipase and cationic trypsinogen in young children with cystic fibrosis | Q61863724 | ||
| The Visibly Fatty Liver | Q67318530 | ||
| Submucosal glands are the predominant site of CFTR expression in the human bronchus | Q67469589 | ||
| Pancreatic function in infants identified as having cystic fibrosis in a neonatal screening program | Q68694684 | ||
| Clinical and genetic comparisons of patients with cystic fibrosis, with or without meconium ileus | Q69601419 | ||
| Early detection of pulmonary function abnormalities in cystic fibrosis | Q70421897 | ||
| Phenotypic abnormalities in long-term surviving cystic fibrosis mice | Q71581605 | ||
| Correction of lethal intestinal defect in a mouse model of cystic fibrosis by human CFTR | Q71661844 | ||
| Lung disease in the cystic fibrosis mouse exposed to bacterial pathogens | Q71698854 | ||
| Studies on parotid saliva in cystic fibrosis | Q72680402 | ||
| The distribution and structure of cells in the tracheal epithelium of the mouse | Q72855518 | ||
| Submucosal gland distribution in the mouse has a genetic determination localized on chromosome 9 | Q73516706 | ||
| A distinctive type of biliary cirrhosis of the liver associated with cystic fibrosis of the pancreas; recognition through signs of portal hypertension | Q74221452 | ||
| The pathological changes in the liver in cystic fibrosis of the pancreas | Q74593967 | ||
| Recommendations for management of liver and biliary tract disease in cystic fibrosis. Cystic Fibrosis Foundation Hepatobiliary Disease Consensus Group | Q77958537 | ||
| P433 | issue | 4 | |
| P407 | language of work or name | English | Q1860 |
| P921 | main subject | cystic fibrosis | Q178194 |
| transmembrane protein | Q424204 | ||
| murine model | Q122890741 | ||
| P304 | page(s) | 1481-1493 | |
| P577 | publication date | 2004-04-01 | |
| P1433 | published in | The American Journal of Pathology | Q4744259 |
| P1476 | title | Characteristic multiorgan pathology of cystic fibrosis in a long-living cystic fibrosis transmembrane regulator knockout murine model | |
| P478 | volume | 164 |
| Q38157708 | A review of animal models of nonneoplastic pancreatic diseases |
| Q34658198 | Absence of diabetes and pancreatic exocrine dysfunction in a transgenic model of carboxyl-ester lipase-MODY (maturity-onset diabetes of the young). |
| Q42813399 | Accumulation of ceramide in the trachea and intestine of cystic fibrosis mice causes inflammation and cell death |
| Q21563467 | Acinar cell apoptosis in Serpini2-deficient mice models pancreatic insufficiency |
| Q40075329 | Acute intratracheal Pseudomonas aeruginosa infection in cystic fibrosis mice is age-independent. |
| Q60920753 | Animal Models in the Pathophysiology of Cystic Fibrosis |
| Q57113804 | Animal models for cystic fibrosis liver disease (CFLD) |
| Q38244716 | Animal models in primary biliary cirrhosis and primary sclerosing cholangitis |
| Q37265316 | Animal models of chronic lung infection with Pseudomonas aeruginosa: useful tools for cystic fibrosis studies |
| Q35178642 | Animal models of gastrointestinal and liver diseases. Animal models of cystic fibrosis: gastrointestinal, pancreatic, and hepatobiliary disease and pathophysiology. |
| Q42198051 | Atrophic-appearing pancreas on magnetic resonance cholangiopancreatography as initial presentation of cystic fibrosis |
| Q35132254 | Azithromycin reduces spontaneous and induced inflammation in DeltaF508 cystic fibrosis mice |
| Q35847294 | Bioelectric properties of chloride channels in human, pig, ferret, and mouse airway epithelia |
| Q34266487 | CFTR-mediated Cl(-) transport in the acinar and duct cells of rabbit lacrimal gland |
| Q33243424 | Caerulein-induced acute pancreatitis in mice that constitutively overexpress Reg/PAP genes |
| Q42005356 | Ceramide in cystic fibrosis: a potential new target for therapeutic intervention |
| Q39884057 | Ceramide mediates lung fibrosis in cystic fibrosis |
| Q35896870 | Characterization of animal models for primary sclerosing cholangitis (PSC). |
| Q36506477 | Cholangiocyte anion exchange and biliary bicarbonate excretion |
| Q57109524 | Cholangiopathies - Towards a molecular understanding |
| Q35561131 | Cholic acid induces a Cftr dependent biliary secretion and liver growth response in mice |
| Q45309271 | Chronic parotitis: not another SPINKosis |
| Q36744020 | Comparative biology of cystic fibrosis animal models |
| Q52586681 | Congenital tracheal malformation in cystic fibrosis transmembrane conductance regulator-deficient mice. |
| Q36746482 | Cystic fibrosis and other respiratory diseases of impaired mucus clearance |
| Q79818622 | Cystic fibrosis mice rehabilitated for studies of airway gland dysfunction |
| Q35568501 | Cystic fibrosis mouse model-dependent intestinal structure and gut microbiome |
| Q36556391 | Cystic fibrosis mouse models |
| Q33913037 | Cystic fibrosis transmembrane conductance regulator dysfunction in VIP knockout mice |
| Q90575044 | Diet-Induced Dysbiosis and Genetic Background Synergize With Cystic Fibrosis Transmembrane Conductance Regulator Deficiency to Promote Cholangiopathy in Mice |
| Q37524945 | Disrupted tight junctions in the small intestine of cystic fibrosis mice |
| Q55399442 | Ductal Mucus Obstruction and Reduced Fluid Secretion Are Early Defects in Chronic Pancreatitis. |
| Q92042117 | Estrogen sulfotransferase in the metabolism of estrogenic drugs and in the pathogenesis of diseases |
| Q34590648 | Expression of S100A8 correlates with inflammatory lung disease in congenic mice deficient of the cystic fibrosis transmembrane conductance regulator |
| Q45140576 | Fat absorption in cystic fibrosis mice is impeded by defective lipolysis and post-lipolytic events |
| Q64376611 | Gene therapy for cystic fibrosis |
| Q36338302 | Growth deficits in cystic fibrosis mice begin in utero prior to IGF-1 reduction |
| Q40177003 | Impact of nutrition on phenotype in CFTR-deficient mice |
| Q39933161 | Increased SULT1E1 activity in HepG2 hepatocytes decreases growth hormone stimulation of STAT5b phosphorylation |
| Q36811246 | Increased susceptibility of Cftr-/- mice to LPS-induced lung remodeling |
| Q34085307 | Inhibition of acinar apoptosis occurs during acute pancreatitis in the human homologue DeltaF508 cystic fibrosis mouse |
| Q34981646 | Intestinal alkaline phosphatase regulates protective surface microclimate pH in rat duodenum |
| Q47280680 | Intestinal phenotype of variable-weight cystic fibrosis knockout mice |
| Q41819454 | Lack of cystic fibrosis transmembrane conductance regulator in CD3+ lymphocytes leads to aberrant cytokine secretion and hyperinflammatory adaptive immune responses |
| Q34657625 | Lessons from the toxic bile concept for the pathogenesis and treatment of cholestatic liver diseases |
| Q37920895 | Lipids in cystic fibrosis |
| Q42199545 | Long-term therapeutic and reporter gene expression in lentiviral vector treated cystic fibrosis mice. |
| Q36770683 | Loss of Cftr function exacerbates the phenotype of Na(+) hyperabsorption in murine airways |
| Q27302962 | Loss of cftr function leads to pancreatic destruction in larval zebrafish. |
| Q44675835 | MicroRNA profiling of cystic fibrosis intestinal disease in mice |
| Q37887172 | Mouse models of cystic fibrosis: phenotypic analysis and research applications |
| Q79493666 | Mucus secretion by single tracheal submucosal glands from normal and cystic fibrosis transmembrane conductance regulator knockout mice |
| Q58586707 | Non-obstructive vas deferens and epididymis loss in cystic fibrosis rats |
| Q37253687 | Overexpression of interleukin-1beta in the murine pancreas results in chronic pancreatitis |
| Q36312709 | Pancreatic and biliary secretion are both altered in cystic fibrosis pigs. |
| Q36424575 | Pancreatic pathophysiology in cystic fibrosis |
| Q45399177 | Partial correction of the CFTR-dependent ABPA mouse model with recombinant adeno-associated virus gene transfer of truncated CFTR gene |
| Q37960966 | Pathogenesis of primary sclerosing cholangitis. |
| Q33703755 | Pathology of gastrointestinal organs in a porcine model of cystic fibrosis |
| Q37269561 | Pathophysiological basis of liver disease in cystic fibrosis employing a DeltaF508 mouse model |
| Q28388425 | Pulmonary fibrosis: pathogenesis, etiology and regulation |
| Q34335468 | Purinergic regulation of duodenal surface pH and ATP concentration: implications for mucosal defence, lipid uptake and cystic fibrosis |
| Q37162444 | Reduced NHE3-mediated Na+ absorption increases survival and decreases the incidence of intestinal obstructions in cystic fibrosis mice |
| Q37373924 | Regulation of hepatic sulfotransferase (SULT) 1E1 expression and effects on estrogenic activity in cystic fibrosis (CF). |
| Q35513939 | Role of IL-1β in experimental cystic fibrosis upon P. aeruginosa infection |
| Q38518598 | Strain-dependent pulmonary gene expression profiles of a cystic fibrosis mouse model |
| Q35891069 | Streptomycin treatment alters the intestinal microbiome, pulmonary T cell profile and airway hyperresponsiveness in a cystic fibrosis mouse model |
| Q35174958 | Swine models of cystic fibrosis reveal male reproductive tract phenotype at birth |
| Q37887177 | The ENaC-overexpressing mouse as a model of cystic fibrosis lung disease |
| Q57126089 | The characterization of the first anti-mouse Muc6 antibody shows an increased expression of the mucin in pancreatic tissue of Cftr-knockout mice |
| Q38103532 | The cystic fibrosis of exocrine pancreas |
| Q26992279 | The genetics of complex cholestatic disorders |
| Q33381294 | The pros and cons of immunomodulatory IL-10 gene therapy with recombinant AAV in a Cftr-/- -dependent allergy mouse model |
| Q89509450 | Tissue Engineering in Liver Regenerative Medicine: Insights into Novel Translational Technologies |
| Q38522938 | Tracking the immunopathological response to Pseudomonas aeruginosa during respiratory infections. |
| Q48190174 | Ursodeoxycholate modulates bile flow and bile salt pool independently from the cystic fibrosis transmembrane regulator (Cftr) in mice |
| Q36750909 | Ventilatory pattern and energy expenditure are altered in cystic fibrosis mice |
| Q36874346 | What have we learned from mouse models for cystic fibrosis? |
| Q45200849 | X-ray microanalysis of airway surface liquid in the mouse. |
Search more.