Minireview: Clinical severity in sickle cell disease: the challenges of definition and prognostication

scientific article published on 23 March 2016

Minireview: Clinical severity in sickle cell disease: the challenges of definition and prognostication is …
instance of (P31):
review articleQ7318358
scholarly articleQ13442814

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P356DOI10.1177/1535370216640385
P932PMC publication ID4871738
P698PubMed publication ID27013545
P5875ResearchGate publication ID299413817

P50authorCharles T QuinnQ42365105
P2093author name stringCharles T Quinn
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The effect of prolonged administration of hydroxyurea on morbidity and mortality in adult patients with sickle cell syndromes: results of a 17-year, single-center trial (LaSHS).Q43244775
Sickle cell disease as a cause of osteonecrosis of the femoral headQ44105081
The association between tricuspid regurgitation velocity and 5-year survival in a North West London population of patients with sickle cell disease in the United Kingdom.Q44618194
Pulmonary hypertension as a risk factor for death in patients with sickle cell diseaseQ44777573
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G6PD deficiency, absence of alpha-thalassemia, and hemolytic rate at baseline are significant independent risk factors for abnormally high cerebral velocities in patients with sickle cell anemiaQ46388586
The alpha-globin genotype does not influence sickle cell disease severity in a retrospective cross-validation study of the pediatric severity scoreQ46502955
The influence of uridine diphosphate glucuronosyl transferase 1A promoter polymorphisms, beta-globin gene haplotype, co-inherited alpha-thalassemia trait and Hb F on steady-state serum bilirubin levels in sickle cell anemiaQ46590318
Hydroxycarbamide versus chronic transfusion for maintenance of transcranial doppler flow velocities in children with sickle cell anaemia-TCD With Transfusions Changing to Hydroxyurea (TWiTCH): a multicentre, open-label, phase 3, non-inferiority triaQ47100582
UGT1A1 variation and gallstone formation in sickle cell diseaseQ47317656
Prevention of a first stroke by transfusions in children with sickle cell anemia and abnormal results on transcranial Doppler ultrasonographyQ47906551
UDP-glucuronosyltransferase 1 gene promoter polymorphism is associated with increased serum bilirubin levels and cholecystectomy in patients with sickle cell anemiaQ50169464
Influence of bilirubin uridine diphosphate-glucuronosyltransferase 1A promoter polymorphisms on serum bilirubin levels and cholelithiasis in children with sickle cell anemiaQ50179471
G6PD deficiency and absence of α-thalassemia increase the risk for cerebral vasculopathy in children with sickle cell anemiaQ50442869
Influence of the βs haplotype and α-thalassemia on stroke development in a Brazilian population with sickle cell anaemia.Q50479766
Transfusion prevents acute chest syndrome predicted by elevated secretory phospholipase A2.Q50712413
The effect of hydroxcarbamide therapy on survival of children with sickle cell disease.Q51065755
Elevated tricuspid regurgitant velocity as a marker for pulmonary hypertension in children with sickle cell disease: less prevalent and predictive than previously thought?Q53040931
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Mortality in sickle cell disease. Life expectancy and risk factors for early death.Q55065788
Fetal hemoglobin in sickle cell anemia: a glass half full?Q57624642
G6PD deficiency and stroke in the CSSCDQ57624755
Clinical outcomes in children with sickle cell disease living in England: a neonatal cohort in East LondonQ58320124
Effects of thalassemia and microcytosis on the hematologic and vasoocclusive severity of sickle cell anemiaQ71349152
Concurrent sickle-cell anemia and alpha-thalassemia: effect on severity of anemiaQ72655161
Post-natal decline of fetal haemoglobin in homozygous sickle cell disease: relationship to parenteral Hb F levelsQ72678055
Cerebrovascular accidents in sickle cell disease: rates and risk factorsQ73982009
Secretory phospholipase A2 levels in patients with sickle cell disease and acute chest syndromeQ79785208
Clinical differences between children and adults with pulmonary hypertension and sickle cell diseaseQ81397158
Association of UGT1A1 polymorphism with prevalence and age at onset of cholelithiasis in sickle cell anemiaQ81400573
P433issue7
P921main subjectsickle-cell diseaseQ185034
P304page(s)679-688
P577publication date2016-03-23
2016-04-01
P1433published inExperimental Biology and MedicineQ15716535
P1476titleMinireview: Clinical severity in sickle cell disease: the challenges of definition and prognostication
P478volume241

Reverse relations

cites work (P2860)
Q38782100Allogenic bone narrow transplantation in sickle-cell diseases.
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Q50226121Individual variability in response to a single sickling event for normal, sickle cell, and sickle trait erythrocytes
Q97521352Preliminary Data on COVID-19 in Patients with Hemoglobinopathies: A Multicentre ICET-A Study
Q89112351Red Blood Cell Adhesion to Heme-Activated Endothelial Cells Reflects Clinical Phenotype in Sickle Cell Disease
Q42413708Sickle cell disease severity: an introduction
Q36125402Single Nucleotide Polymorphisms at +191 and +292 of Galectin-3 Gene (LGALS3) Related to Lower GAL-3 Serum Levels Are Associated with Frequent Respiratory Tract Infection and Vaso-Occlusive Crisis in Children with Sickle Cell Anemia.