scholarly article | Q13442814 |
P819 | ADS bibcode | 1974PNAS...71.2505W |
P356 | DOI | 10.1073/PNAS.71.6.2505 |
P8608 | Fatcat ID | release_zmug2ymcwbappf7ezgocnsd5va |
P932 | PMC publication ID | 388488 |
P698 | PubMed publication ID | 4152248 |
P5875 | ResearchGate publication ID | 19014014 |
P2093 | author name string | Larsson A | |
Meister A | |||
Sekura R | |||
Wellner VP | |||
P2860 | cites work | Protein measurement with the Folin phenol reagent | Q20900776 |
Enzymatic Conversion of 5-Oxo-L-Proline (L-Pyrrolidone Carboxylate) to L-Glutamate Coupled with Cleavage of Adenosine Triphosphate to Adenosine Diphosphate, a Reaction in the γ-Glutamyl Cycle | Q24616201 | ||
THE OPTICALLY-SPECIFIC ENZYMATIC CYCLIZATION OF D-GLUTAMATE | Q28156017 | ||
The gamma-glutamyl cycle: a possible transport system for amino acids | Q33708826 | ||
On the enzymology of amino acid transport | Q39872601 | ||
Glutathione biosynthesis in human erythrocytes. I. Identification of the enzymes of glutathione synthesis in hemolysates | Q40324482 | ||
Pyroglutamic aciduria. Studies in an infant with chronic metabolic acidosis | Q47867627 | ||
Pyroglutamic aciduria--a new inborn error of metabolism | Q48881161 | ||
Esophageal hiatus hernia and mental retardation: life-threatening postoperative metabolic acidosis and potassium deficiency linked with a new inborn error of nitrogen metabolism | Q52121340 | ||
Partial reactions catalyzed by -glutamylcysteine synthetase and evidence for an activated glutamate intermediate. | Q53938253 | ||
Glutathione Synthetase Deficiency as a Cause of Hereditary Hemolytic Disease | Q54975433 | ||
[Glutathione synthesis during congenital hemolytic anemia with reduced glutathione deficiency. Congenital erythrocytic glutathione-synthetase deficiency?] | Q68375113 | ||
The Metabolism of L-Pyroglutamic Acid in Fibroblasts from a Patient with Pyroglutamic Aciduria: The Demonstration of an L-Pyroglutamate Hydrolase System | Q70403025 | ||
Pyroglutamic aciduria: studies on the enzymic block and on the metabolic origin of pyroglutamic acid | Q70443420 | ||
Tripeptide (Glutathione) Synthetase. Purification, Properties, and Mechanism of Action* | Q72246025 | ||
Disulfide and sulfhydryl compounds in TCA extracts of human blood and plasma | Q72252854 | ||
Congenital nonspherocytic hemolytic anemia, associated with glutathione deficiency of the erythrocytes. Hematologic, biochemical and genetic studies | Q72756091 | ||
Hereditary absence of reduced glutathione in the erythrocytes - a new clinical and biochemical entity? (Preliminary communication) | Q78954575 | ||
P433 | issue | 6 | |
P407 | language of work or name | English | Q1860 |
P921 | main subject | glutathione | Q116907 |
patient | Q181600 | ||
glutathione synthetase deficiency | Q102296856 | ||
P304 | page(s) | 2505-2509 | |
P577 | publication date | 1974-06-01 | |
P1433 | published in | Proceedings of the National Academy of Sciences of the United States of America | Q1146531 |
P1476 | title | Glutathione synthetase deficiency, an inborn error of metabolism involving the gamma-glutamyl cycle in patients with 5-oxoprolinuria (pyroglutamic aciduria). | |
P478 | volume | 71 |
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Q52284591 | Neonatal 5-oxoprolinuria: difficult-to-diagnose? |
Q39307107 | New Aspects of Glutathione Metabolism and Translocation in Mammals |
Q40085021 | On the Cycles of Glutathione Metabolism and Transport |
Q38069523 | On the Function of the γ-Glutamyl Cycle in the Transport of Amino Acids and Peptides |
Q33566233 | On the active site thiol of gamma-glutamylcysteine synthetase: relationships to catalysis, inhibition, and regulation |
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Q39293102 | The Glutathione Status of Cells |
Q34075460 | The Metabolic Formation and Utilization of 5‐Oxo‐ L ‐proline ( L ‐Pyroglutamate, L ‐Pyrrolidone Carboxylate) |
Q58189741 | The cerebral lesions in a patient with generalized glutathione deficiency and pyroglutamic aciduria (5-oxoprolinuria) |
Q24318373 | The identification and structural characterization of C7orf24 as gamma-glutamyl cyclotransferase. An essential enzyme in the gamma-glutamyl cycle |
Q102075434 | The maturity in fetal pigs using a multi-fluid metabolomic approach |
Q54683142 | Thioredoxin and glutathione in cultured fibroblasts from human cases with 5-oxoprolinuria and cystinosis |
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Q39182570 | gamma-Glutamyl transpeptidase. Determination of specificity in the presence of multiple amino acid acceptors |