scholarly article | Q13442814 |
P6179 | Dimensions Publication ID | 1013426659 |
P356 | DOI | 10.1038/CDD.2016.127 |
P932 | PMC publication ID | 5299714 |
P698 | PubMed publication ID | 27834955 |
P50 | author | Kanneboyina Nagaraju | Q27662260 |
Jyoti K. Jaiswal | Q50648507 | ||
Marshall W Hogarth | Q51089640 | ||
Adam Horn | Q57881682 | ||
P2093 | author name string | Kristy J Brown | |
Yetrib Hathout | |||
Sree Rayavarapu | |||
Shin'ichi Takeda | |||
Aurelia Defour | |||
Jack H Van der Meulen | |||
Maria C Vila | |||
P2860 | cites work | Rescue of dystrophic skeletal muscle by PGC-1α involves a fast to slow fiber type shift in the mdx mouse | Q27310125 |
Metabolic dysfunction and altered mitochondrial dynamics in the utrophin-dystrophin deficient mouse model of duchenne muscular dystrophy | Q28546070 | ||
Mitofusins Mfn1 and Mfn2 coordinately regulate mitochondrial fusion and are essential for embryonic development | Q28594513 | ||
Use of quantitative membrane proteomics identifies a novel role of mitochondria in healing injured muscles. | Q30524775 | ||
Dysferlin regulates cell membrane repair by facilitating injury-triggered acid sphingomyelinase secretion. | Q30582564 | ||
Alteration in calcium handling at the subcellular level in mdx myotubes. | Q31456406 | ||
Dysferlin and the plasma membrane repair in muscular dystrophy | Q33201061 | ||
Efficacy of MitoTracker Green and CMXrosamine to measure changes in mitochondrial membrane potentials in living cells and tissues | Q33207057 | ||
Chronic administration of membrane sealant prevents severe cardiac injury and ventricular dilatation in dystrophic dogs | Q33755416 | ||
Enhanced Ca²⁺ influx from STIM1-Orai1 induces muscle pathology in mouse models of muscular dystrophy. | Q33784460 | ||
Imaging cell membrane injury and subcellular processes involved in repair | Q33872310 | ||
Membrane sealant Poloxamer P188 protects against isoproterenol induced cardiomyopathy in dystrophin deficient mice | Q33901556 | ||
Preclinical drug trials in the mdx mouse: assessment of reliable and sensitive outcome measures | Q33975979 | ||
Non-invasive optical imaging of muscle pathology in mdx mice using cathepsin caged near-infrared imaging | Q34928429 | ||
VBP15, a novel anti-inflammatory and membrane-stabilizer, improves muscular dystrophy without side effects | Q34981147 | ||
Decreased osmotic stability of dystrophin-less muscle cells from the mdx mouse | Q35009267 | ||
Mechanism of Ca²⁺-triggered ESCRT assembly and regulation of cell membrane repair | Q35099073 | ||
Dystrophin deficiency exacerbates skeletal muscle pathology in dysferlin-null mice | Q35779807 | ||
How much dystrophin is enough: the physiological consequences of different levels of dystrophin in the mdx mouse | Q35821127 | ||
Regulation of cytosolic calcium in skeletal muscle cells of the mdx mouse under conditions of stress | Q35873884 | ||
Dystrophin and dysferlin double mutant mice: a novel model for rhabdomyosarcoma | Q36025454 | ||
A role for the dystrophin-glycoprotein complex as a transmembrane linker between laminin and actin. | Q36232550 | ||
Mechanical function of dystrophin in muscle cells | Q36235185 | ||
Targeted disruption of exon 52 in the mouse dystrophin gene induced muscle degeneration similar to that observed in Duchenne muscular dystrophy. | Q52527217 | ||
Contraction-induced injury to single permeabilized muscle fibers from mdx, transgenic mdx, and control mice. | Q52541082 | ||
High resolution respirometry of permeabilized skeletal muscle fibers in the diagnosis of neuromuscular disorders. | Q53964474 | ||
Dystrophin levels and clinical severity in Becker muscular dystrophy patients. | Q54508616 | ||
Time course of changes in plasma membrane permeability in the dystrophin-deficient mdx mouse | Q58487605 | ||
Dysferlin, annexin A1, and mitsugumin 53 are upregulated in muscular dystrophy and localize to longitudinal tubules of the T-system with stretch. | Q64981707 | ||
Changes in muscle plasma membranes in young mice with X chromosome-linked muscular dystrophy: a freeze-fracture study | Q68049296 | ||
Efficient recovery of dysferlin deficiency by dual adeno-associated vector-mediated gene transfer | Q82892069 | ||
Use of stable isotope labeling by amino acids in cell culture as a spike-in standard in quantitative proteomics | Q83366737 | ||
Peroxisome proliferator-activated receptor γ coactivator1- gene α transfer restores mitochondrial biomass and improves mitochondrial calcium handling in post-necrotic mdx mouse skeletal muscle | Q84829768 | ||
Increased dysferlin expression in Duchenne muscular dystrophy | Q95403251 | ||
Dystrophin protects the sarcolemma from stresses developed during muscle contraction | Q36259954 | ||
Elusive sources of variability of dystrophin rescue by exon skipping | Q36340978 | ||
Metabolic remodeling agents show beneficial effects in the dystrophin-deficient mdx mouse model | Q36351079 | ||
Stem and progenitor cells in skeletal muscle development, maintenance, and therapy | Q36771273 | ||
Poloxamer 188 reduces the contraction-induced force decline in lumbrical muscles from mdx mice | Q36805372 | ||
Identification of disease specific pathways using in vivo SILAC proteomics in dystrophin deficient mdx mouse. | Q36832437 | ||
Mechanisms of muscle degeneration, regeneration, and repair in the muscular dystrophies | Q37276061 | ||
Visualization of ATP levels inside single living cells with fluorescence resonance energy transfer-based genetically encoded indicators | Q37327467 | ||
Calcium influx is sufficient to induce muscular dystrophy through a TRPC-dependent mechanism | Q37419160 | ||
Exogenous cytochrome C restores myocardial cytochrome oxidase activity into the late phase of sepsis | Q37673307 | ||
Muscular dystrophy in dysferlin-deficient mouse models | Q38087717 | ||
Dystrophin abnormalities in Duchenne/Becker muscular dystrophy | Q38768990 | ||
Chronic AMPK activation evokes the slow, oxidative myogenic program and triggers beneficial adaptations in mdx mouse skeletal muscle | Q39527529 | ||
Autophagy regulates satellite cell ability to regenerate normal and dystrophic muscles | Q39571496 | ||
Dominant-negative inhibition of Ca2+ influx via TRPV2 ameliorates muscular dystrophy in animal models | Q39909880 | ||
Increased activity of calcium leak channels caused by proteolysis near sarcolemmal ruptures | Q41752594 | ||
Involvement of TRPC in the abnormal calcium influx observed in dystrophic (mdx) mouse skeletal muscle fibers | Q41882302 | ||
Post-natal induction of PGC-1α protects against severe muscle dystrophy independently of utrophin. | Q41911490 | ||
Reciprocal amplification of ROS and Ca(2+) signals in stressed mdx dystrophic skeletal muscle fibers. | Q42452644 | ||
Increased activity of calcium leak channels in myotubes of Duchenne human and mdx mouse origin | Q44177784 | ||
Effects of stretch-activated channel blockers on [Ca2+]i and muscle damage in the mdx mouse. | Q45140549 | ||
Increased protein degradation results from elevated free calcium levels found in muscle from mdx mice | Q46266620 | ||
Calcium entry through stretch-inactivated ion channels in mdx myotubes | Q46603395 | ||
Dystrophic heart failure blocked by membrane sealant poloxamer | Q46604988 | ||
Impaired mitochondrial oxidative phosphorylation in skeletal muscle of the dystrophin-deficient mdx mouse | Q47878704 | ||
P275 | copyright license | Creative Commons Attribution-NonCommercial-ShareAlike 4.0 International | Q42553662 |
P6216 | copyright status | copyrighted | Q50423863 |
P433 | issue | 2 | |
P921 | main subject | mitochondrion | Q39572 |
P304 | page(s) | 330-342 | |
P577 | publication date | 2016-11-11 | |
P1433 | published in | Cell Death & Differentiation | Q2943974 |
P1476 | title | Mitochondria mediate cell membrane repair and contribute to Duchenne muscular dystrophy | |
P478 | volume | 24 |
Q58606031 | A Screen Using iPSC-Derived Hepatocytes Reveals NAD as a Potential Treatment for mtDNA Depletion Syndrome |
Q90414913 | CRISPR/Cas9-Based Dystrophin Restoration Reveals a Novel Role for Dystrophin in Bioenergetics and Stress Resistance of Muscle Progenitors |
Q92147843 | DSS-induced damage to basement membranes is repaired by matrix replacement and crosslinking |
Q44907195 | Genetic modifiers of muscular dystrophy act on sarcolemmal resealing and recovery from injury |
Q91237933 | Membrane Stabilization by Modified Steroid Offers a Potential Therapy for Muscular Dystrophy Due to Dysferlin Deficit |
Q93385793 | Mitochondria-Targeted Drugs |
Q97420407 | Mitochondrial Dysfunction Is an Early Consequence of Partial or Complete Dystrophin Loss in mdx Mice |
Q96954758 | Mitochondrial Function in Muscle Stem Cell Fates |
Q46311660 | Mitochondrial redox signaling enables repair of injured skeletal muscle cells |
Q90407716 | Modeling disease trajectory in Duchenne muscular dystrophy |
Q96127087 | Motor axonopathies in a mouse model of Duchenne muscular dystrophy |
Q57286631 | Muscle membrane integrity in Duchenne muscular dystrophy: recent advances in copolymer-based muscle membrane stabilizers |
Q60049386 | Myoblasts rely on TAp63 to control basal mitochondria respiration |
Q89767037 | Nutritional intervention with cyanidin hinders the progression of muscular dystrophy |
Q88249085 | Observation of acetyl phosphate formation in mammalian mitochondria using real-time in-organelle NMR metabolomics |
Q64110017 | PGC-1α overexpression partially rescues impaired oxidative and contractile pathophysiology following volumetric muscle loss injury |
Q47151990 | Pharmacological inhibition of REV-ERB stimulates differentiation, inhibits turnover and reduces fibrosis in dystrophic muscle. |
Q61796529 | Reduced mitochondrial respiration and increased calcium deposits in the EDL muscle, but not in soleus, from 12-week-old dystrophic mdx mice |
Q55515149 | Skeletal Muscle Metabolism in Duchenne and Becker Muscular Dystrophy-Implications for Therapies. |
Q60907638 | TAp73 regulates ATP7A: possible implications for ageing-related diseases |
Q90661491 | TGF-β-driven muscle degeneration and failed regeneration underlie disease onset in a DMD mouse model |
Q90750443 | Transcriptome changes during the initiation and progression of Duchenne Muscular Dystrophy in C. elegans |
Q42634544 | Utrophin influences mitochondrial pathology and oxidative stress in dystrophic muscle |