scholarly article | Q13442814 |
P6179 | Dimensions Publication ID | 1028284737 |
P356 | DOI | 10.1038/335735A0 |
P698 | PubMed publication ID | 3173492 |
P2093 | author name string | Turner PR | |
Steinhardt RA | |||
Regen CM | |||
Westwood T | |||
P2860 | cites work | The Duchenne muscular dystrophy gene product is localized in sarcolemma of human skeletal muscle | Q24297845 |
Dystrophin: the protein product of the Duchenne muscular dystrophy locus | Q29618077 | ||
Regulation of cortical vesicle exocytosis in sea urchin eggs by inositol 1,4,5-trisphosphate and GTP-binding protein | Q36214084 | ||
Measurement of cytosolic free Ca2+ in individual small cells using fluorescence microscopy with dual excitation wavelengths | Q36487628 | ||
Calcium gradients in single smooth muscle cells revealed by the digital imaging microscope using Fura-2. | Q36491669 | ||
Cellular and subcellular heterogeneity of [Ca2+]i in single heart cells revealed by fura-2. | Q39310325 | ||
Role of intracellular calcium in promoting muscle damage: A strategy for controlling the dystrophic condition | Q39782584 | ||
The activation of protein degradation in muscle by Ca2+ or muscle injury does not involve a lysosomal mechanism | Q42165303 | ||
Calcium rises abruptly and briefly throughout the cell at the onset of anaphase | Q42525633 | ||
Properties of isolated adult rat muscle fibres maintained in tissue culture | Q45744986 | ||
Subcellular fractionation of dystrophin to the triads of skeletal muscle | Q46932900 | ||
Changes of free calcium levels with stages of the cell division cycle | Q56864056 | ||
Measurements of calcium and other elements in muscle biopsy samples from patients with Duchenne Muscular Dystrophy | Q58487664 | ||
Calcium transients in mammalian muscles | Q59066141 | ||
Immunoelectron microscopic localization of dystrophin in myofibres | Q59096146 | ||
Ca2+ capacity and uptake rate in skinned fibers of myodystrophic muscle | Q67275037 | ||
Free cytoplasmic Ca++ at rest and after cholinergic stimulus is increased in cultured muscle cells from Duchenne muscular dystrophy patients | Q68278618 | ||
Calcium and magnesium content in fetuses at risk and prenecrotic Duchenne muscular dystrophy | Q70655724 | ||
Muscle calcium and magnesium content in Duchenne muscular dystrophy | Q71840156 | ||
P433 | issue | 6192 | |
P407 | language of work or name | English | Q1860 |
P304 | page(s) | 735-738 | |
P577 | publication date | 1988-10-01 | |
P1433 | published in | Nature | Q180445 |
P1476 | title | Increased protein degradation results from elevated free calcium levels found in muscle from mdx mice | |
P478 | volume | 335 |
Q34175938 | A Human-Specific Deletion in Mouse Cmah Increases Disease Severity in the mdx Model of Duchenne Muscular Dystrophy |
Q46064246 | A critical evaluation of resting intracellular free calcium regulation in dystrophic mdx muscle |
Q36323554 | A novel mechanism of myocyte degeneration involving the Ca2+-permeable growth factor-regulated channel |
Q36422465 | Absence of Dystrophin Disrupts Skeletal Muscle Signaling: Roles of Ca2+, Reactive Oxygen Species, and Nitric Oxide in the Development of Muscular Dystrophy. |
Q54066068 | Acetylcholine activates two types of ion channels in sarcolemma from adult muscular dystrophic (mdx) mice |
Q71535892 | Acetylcholine receptor and calcium leakage activity in nondystrophic and dystrophic myotubes (MDX) |
Q44627078 | Acetylcholine receptor distribution and synapse elimination at the developing neuromuscular junction of mdx mice |
Q28591318 | Acetylcholine receptors in innervated muscles of dystrophic mdx mice degrade as after denervation |
Q41961997 | Acute effects of phorbol esters on the protein-synthetic rate and carbohydrate metabolism of normal and mdx mouse muscles |
Q44985983 | Acute failure of action potential conduction in mdx muscle reveals new mechanism of contraction-induced force loss. |
Q33726108 | Alteration of sarcoplasmic reticulum ca release in skeletal muscle from calpain 3-deficient mice. |
Q36915922 | Animal models of muscular dystrophy |
Q36856649 | Animal models of muscular dystrophy – what can they teach us? |
Q39424672 | Are Antioxidants a Potential Therapy for FSHD? A Review of the Literature |
Q91627122 | Blockade of IGF2R improves muscle regeneration and ameliorates Duchenne muscular dystrophy |
Q52227796 | Ca2+ levels in myotubes grown from the skeletal muscle of dystrophic (mdx) and normal mice. |
Q46603395 | Calcium entry through stretch-inactivated ion channels in mdx myotubes |
Q73070067 | Calcium homeostasis in dystrophic muscle |
Q34283184 | Calcium indicators and calcium signalling in skeletal muscle fibres during excitation-contraction coupling |
Q35027943 | Calcium influx inhibition by steroids and analogs in C2C12 skeletal muscle cells |
Q37419160 | Calcium influx is sufficient to induce muscular dystrophy through a TRPC-dependent mechanism |
Q68164364 | Calmodulin specifically binds three proteins of the dystrophin-glycoprotein complex |
Q46489174 | Calpain II expression is increased by changes in mechanical loading of muscle in vivo |
Q38103213 | Cardiac and respiratory dysfunction in Duchenne muscular dystrophy and the role of second messengers. |
Q42641718 | Cationic channels in normal and dystrophic human myotubes |
Q36953163 | Cell-lineage regulated myogenesis for dystrophin replacement: a novel therapeutic approach for treatment of muscular dystrophy |
Q67908907 | Changes in tetanic and resting [Ca2+]i during fatigue and recovery of single muscle fibres from Xenopus laevis |
Q72684984 | Changes of tension and [Ca2+]i during beta-adrenoceptor activation of single, intact fibres from mouse skeletal muscle |
Q38217473 | Chaperoning heat shock proteins: proteomic analysis and relevance for normal and dystrophin-deficient muscle. |
Q33644573 | Characteristics of skeletal muscle in mdx mutant mice |
Q37148808 | Comparative Genomics of X-linked Muscular Dystrophies: The Golden Retriever Model |
Q46388856 | Comparison of the myoplasmic calcium transient elicited by an action potential in intact fibres of mdx and normal mice |
Q42627877 | Components of energy expenditure in the mdx mouse model of Duchenne muscular dystrophy |
Q44473148 | Consequence of parvalbumin deficiency in the mdx mouse: histological, biochemical and mechanical phenotype of a new double mutant. |
Q90176142 | Contribution of TRPC Channels to Intracellular Ca2 + Dyshomeostasis in Smooth Muscle From mdx Mice |
Q58829497 | Creatine supplementation improves intracellular Ca2+ handling and survival in mdx skeletal muscle cells |
Q61448535 | DP71 and SERCA2 alteration in human neurons of a Duchenne muscular dystrophy patient |
Q35151702 | Dantrolene ameliorates the metabolic hallmarks of sepsis in rats and improves survival in a mouse model of endotoxemia |
Q34307101 | Debio-025 is more effective than prednisone in reducing muscular pathology in mdx mice |
Q44777446 | Decreased expression of ryanodine receptors alters calcium-induced calcium release mechanism in mdx duodenal myocytes |
Q35009267 | Decreased osmotic stability of dystrophin-less muscle cells from the mdx mouse |
Q43798227 | Defective mitochondrial oxidative phosphorylation in myopathies with tubular aggregates originating from sarcoplasmic reticulum |
Q42494294 | Defective regulation of energy metabolism in mdx-mouse skeletal muscles |
Q59089242 | Deficiency of a glycoprotein component of the dystrophin complex in dystrophic muscle |
Q28365018 | Depletion of Ca2+ in the sarcoplasmic reticulum stimulates Ca2+ entry into mouse skeletal muscle fibres |
Q41188037 | Development and therapeutic potential of calpain inhibitors |
Q68922217 | Digestion of proteins associated with the Z-disc by calpain |
Q74439882 | Dihydropyridine receptor gene expression in skeletal muscle from mdx and control mice |
Q70915847 | Dihydropyridine receptors in transverse tubules from normal and dystrophic chicken skeletal muscle |
Q43876648 | Distinctive patterns of basic fibroblast growth factor (bFGF) distribution in degenerating and regenerating areas of dystrophic (mdx) striated muscles |
Q90211836 | Dynamics of Dystrophin's Actin-Binding Domain |
Q44147291 | Dysregulation of Intracellular Ca2+ in Dystrophic Cortical and Hippocampal Neurons |
Q38257886 | Dysregulation of calcium homeostasis in muscular dystrophies. |
Q38198560 | Dystrophin and the integrity of the sarcolemma in Duchenne muscular dystrophy |
Q42755001 | Dystrophin deficiency is associated with myotendinous junction defects in prenecrotic and fully regenerated skeletal muscle. |
Q60533862 | Dystrophin is not essential for the integrity of the cytoskeleton |
Q36259954 | Dystrophin protects the sarcolemma from stresses developed during muscle contraction |
Q40373239 | Dystrophin, its gene, and the dystrophinopathies |
Q40666237 | Dystrophin-dependent efficiency of metabolic pathways in mouse skeletal muscles |
Q43107646 | Dystrophin-glycoprotein complex is highly enriched in isolated skeletal muscle sarcolemma |
Q38365284 | Dystrophin-related muscular dystrophies |
Q46311565 | Dystrophin-related protein in the platelet membrane skeleton. Integrin-induced change in detergent-insolubility and cleavage by calpain in aggregating platelets |
Q34147741 | Effect of calcium on the oxidative phosphorylation cascade in skeletal muscle mitochondria |
Q35051963 | Effects of Dantrolene Therapy on Disease Phenotype in Dystrophin Deficient mdx Mice. |
Q45140549 | Effects of stretch-activated channel blockers on [Ca2+]i and muscle damage in the mdx mouse. |
Q35700706 | Elevated subsarcolemmal Ca2+ in mdx mouse skeletal muscle fibers detected with Ca2+-activated K+ channels. |
Q36960845 | Emerging strategies for cell and gene therapy of the muscular dystrophies |
Q36381102 | Enhanced expression of the alpha 7 beta 1 integrin reduces muscular dystrophy and restores viability in dystrophic mice |
Q36903526 | Enhanced sensitivity of hippocampal pyramidal neurons from mdx mice to hypoxia-induced loss of synaptic transmission |
Q52723891 | Enhancing Endogenous Nitric Oxide by Whole Body Periodic Acceleration Elicits Neuroprotective Effects in Dystrophic Neurons. |
Q47232628 | Evolution of proteolytic indicators during storage of broiler wooden breast meat |
Q38111711 | Exercise and muscular dystrophy: implications and analysis of effects on musculoskeletal and cardiovascular systems |
Q24310529 | Expression of recombinant dystrophin and its localization to the cell membrane |
Q59489917 | Extrajunctional resting Ca2+ influx is not increased in a severely dystrophic expiratory muscle (triangularis sterni) of the mdx mouse |
Q40474236 | Extraocular muscles: Basic and clinical aspects of structure and function |
Q42473766 | Facilitated NMDA receptor-mediated synaptic plasticity in the hippocampal CA1 area of dystrophin-deficient mice |
Q79171939 | Gadolinium reduces short-term stretch-induced muscle damage in isolated mdx mouse muscle fibres |
Q37127322 | Genetic and pharmacologic inhibition of mitochondrial-dependent necrosis attenuates muscular dystrophy |
Q28085320 | Genetic evidence in the mouse solidifies the calcium hypothesis of myofiber death in muscular dystrophy |
Q40639635 | Global/temporal gene expression in diaphragm and hindlimb muscles of dystrophin-deficient (mdx) mice |
Q37253876 | Hereditary human myopathies in muscle culture |
Q36757538 | Heterokaryon myotubes with normal mouse and Duchenne nuclei exhibit sarcolemmal dystrophin staining and efficient intracellular free calcium control. |
Q34204770 | How calcium influx through calcium leak channels is responsible for the elevated levels of calcium-dependent proteolysis in dystrophic myotubes |
Q28591442 | Hsp72 preserves muscle function and slows progression of severe muscular dystrophy |
Q24308714 | Hypernitrosylated ryanodine receptor calcium release channels are leaky in dystrophic muscle |
Q77959497 | Hypotonic medium increases calcium permeant channels activity in human normal and dystrophic myotubes |
Q33950422 | Identification of a neuronal nitric oxide synthase in isolated cardiac mitochondria using electrochemical detection |
Q44864203 | Immunohistochemical detection of neural cell adhesion molecule and laminin in X-linked dystrophic dogs and mdx mice |
Q47878704 | Impaired mitochondrial oxidative phosphorylation in skeletal muscle of the dystrophin-deficient mdx mouse |
Q40542404 | Improvement of calcium handling and changes in calcium-release properties after mini- or full-length dystrophin forced expression in cultured skeletal myotubes |
Q42512800 | In situ measurements of calpain activity in isolated muscle fibres from normal and dystrophin-lacking mdx mice |
Q36530501 | Increased calcium influx in dystrophic muscle |
Q36033118 | Increased resting intracellular calcium modulates NF-κB-dependent inducible nitric-oxide synthase gene expression in dystrophic mdx skeletal myotubes |
Q44826878 | Increased sarcolipin expression and decreased sarco(endo)plasmic reticulum Ca2+ uptake in skeletal muscles of mouse models of Duchenne muscular dystrophy |
Q33907241 | Indo-1 fluorescence signals elicited by membrane depolarization in enzymatically isolated mouse skeletal muscle fibers |
Q72111438 | Intracellular Ca2+ concentrations are not elevated in resting cultured muscle from Duchenne (DMD) patients and in MDX mouse muscle fibres |
Q73087615 | Intracellular calcium signals measured with indo-1 in isolated skeletal muscle fibres from control and mdx mice |
Q37929155 | Intracellular calcium, cell injury and relationships to free radicals and fatty acid metabolism |
Q46881117 | Intramembrane charge movement and sarcoplasmic calcium release in enzymatically isolated mammalian skeletal muscle fibres. |
Q41882302 | Involvement of TRPC in the abnormal calcium influx observed in dystrophic (mdx) mouse skeletal muscle fibers |
Q36416103 | Ion-dependent inactivation of barium current through L-type calcium channels. |
Q42497208 | Isolation of Mouse Periocular Tissue for Histological and Immunostaining Analyses of the Extraocular Muscles and Their Satellite Cells |
Q70671305 | Lack of dystrophin but normal calcium homeostasis in smooth muscle from dystrophic mdx mice |
Q30665842 | Lack of dystrophin is associated with altered integration of the mitochondria and ATPases in slow-twitch muscle cells of MDX mice |
Q45072511 | Laminin-alpha1 globular domains 3 and 4 induce heterotrimeric G protein binding to alpha-syntrophin's PDZ domain and alter intracellular Ca2+ in muscle |
Q30813768 | Large-scale analysis of differential gene expression in the hindlimb muscles and diaphragm of mdx mouse |
Q36202652 | Lipogenesis mitigates dysregulated sarcoplasmic reticulum calcium uptake in muscular dystrophy |
Q74558580 | Long-term study of Ca(2+) homeostasis and of survival in collagenase-isolated muscle fibres from normal and mdx mice |
Q33649312 | Long-term treatment with naproxcinod significantly improves skeletal and cardiac disease phenotype in the mdx mouse model of dystrophy |
Q36580725 | Loss of cIAP1 attenuates soleus muscle pathology and improves diaphragm function in mdx mice |
Q74529467 | Mdx myotubes have normal excitability but show reduced contraction-relaxation dynamics |
Q43005358 | Measurements of [Ca2+]i with the diffusible Fura-2 AM: can some potential pitfalls be evaluated? |
Q36235185 | Mechanical function of dystrophin in muscle cells |
Q36937768 | Mechanisms of Exercise-Induced Muscle Fibre Injury |
Q33950716 | Mechanisms of muscle weakness in muscular dystrophy |
Q33680413 | Mechanisms of resistance to pathogenesis in muscular dystrophies |
Q36185924 | Mechanisms of stretch-induced muscle damage in normal and dystrophic muscle: role of ionic changes. |
Q72681998 | Membrane potential, resting calcium and calcium transients in isolated muscle fibres from normal and dystrophic mice |
Q36295718 | Mini-dystrophin expression down-regulates IP3-mediated calcium release events in resting dystrophin-deficient muscle cells |
Q34627089 | Mitigation of muscular dystrophy in mice by SERCA overexpression in skeletal muscle |
Q37633713 | Mitochondria mediate cell membrane repair and contribute to Duchenne muscular dystrophy |
Q35873186 | Modulation by prednisolone of calcium handling in skeletal muscle cells. |
Q28506016 | Modulation of Myoblast Fusion by Caveolin-3 in Dystrophic Skeletal Muscle Cells: Implications for Duchenne Muscular Dystrophy and Limb-Girdle Muscular Dystrophy-1C |
Q74702690 | Multivariate evaluation of the functional recovery obtained by the overexpression of utrophin in skeletal muscles of the mdx mouse |
Q50525829 | Muscle fibers of mdx mice are more vulnerable to exercise than those of normal mice. |
Q38329774 | Muscle weakness in myotonic dystrophy associated with misregulated splicing and altered gating of Ca(V)1.1 calcium channel |
Q38363484 | Myofibrillar misalignment correlated to triad disappearance of mdx mouse gastrocnemius muscle probed by SHG microscopy |
Q34627033 | Myogenic Akt signaling attenuates muscular degeneration, promotes myofiber regeneration and improves muscle function in dystrophin-deficient mdx mice |
Q34445717 | Myotubes from transgenic mdx mice expressing full-length dystrophin show normal calcium regulation |
Q72798826 | N-terminal domain of dystrophin |
Q41228417 | N-terminal α Dystroglycan (αDG-N): A Potential Serum Biomarker for Duchenne Muscular Dystrophy |
Q44122960 | Na(+)/Ca(2+) exchange in human myotubes: intracellular calcium rises in response to external sodium depletion are enhanced in DMD. |
Q47812772 | Neurological and Motor Disorders: TRPC in the Skeletal Muscle |
Q35006083 | New aspects of calcium signaling in skeletal muscle cells: implications in Duchenne muscular dystrophy |
Q36560597 | New insights in the regulation of calcium transfers by muscle dystrophin-based cytoskeleton: implications in DMD. |
Q35069506 | Nifedipine treatment reduces resting calcium concentration, oxidative and apoptotic gene expression, and improves muscle function in dystrophic mdx mice |
Q35027817 | Nitrosative stress elicited by nNOSµ delocalization inhibits muscle force in dystrophin-null mice |
Q34880821 | Orthograde dihydropyridine receptor signal regulates ryanodine receptor passive leak |
Q33649295 | Partial restoration of cardiac function with ΔPDZ nNOS in aged mdx model of Duchenne cardiomyopathy |
Q34271469 | Plasma Membrane Disruption: Repair, Prevention, Adaptation |
Q82037630 | Posttetanic potentiation in mdx muscle |
Q71347918 | Prednisone can protect against exercise-induced muscle damage |
Q46669833 | Propagation in the transverse tubular system and voltage dependence of calcium release in normal and mdx mouse muscle fibres |
Q38264369 | Prospect for pharmacological therapies to treat skeletal muscle dysfunction |
Q42217671 | Protein turnover is elevated in muscle of mdx mice in vivo |
Q45982332 | Proteolysis results in altered leak channel kinetics and elevated free calcium in mdx muscle. |
Q33398588 | Proteomic profiling of antisense-induced exon skipping reveals reversal of pathobiochemical abnormalities in dystrophic mdx diaphragm. |
Q74425819 | Rapid recovery following contraction-induced injury to in situ skeletal muscles in mdx mice |
Q35534859 | Recent advances in understanding muscular dystrophy |
Q54326493 | Recovery of fatigued Xenopus muscle fibres is markedly affected by the extracellular tonicity. |
Q61796529 | Reduced mitochondrial respiration and increased calcium deposits in the EDL muscle, but not in soleus, from 12-week-old dystrophic mdx mice |
Q37701305 | Regulation by scaffolding proteins of canonical transient receptor potential channels in striated muscle |
Q35873884 | Regulation of cytosolic calcium in skeletal muscle cells of the mdx mouse under conditions of stress |
Q68589242 | Resting calcium concentrations in isolated skeletal muscle fibres of dystrophic mice |
Q33589307 | Role of TRPC1 channel in skeletal muscle function |
Q34465820 | Role of nitric oxide in the pathogenesis of muscular dystrophies: a "two hit" hypothesis of the cause of muscle necrosis |
Q47665947 | Ryanodine channel complex stabilizer compound S48168/ARM210 as a disease modifier in dystrophin-deficient mdx mice: proof-of-concept study and independent validation of efficacy |
Q36549694 | Sarcolemmal ion channels in dystrophin-deficient skeletal muscle fibres |
Q35789210 | Sarcoplasmic reticulum Ca2+ permeation explored from the lumen side in mdx muscle fibers under voltage control |
Q51928332 | Stra13 regulates oxidative stress mediated skeletal muscle degeneration. |
Q42506955 | Stretch-activated cation channels in skeletal muscle myotubes from sarcoglycan-deficient hamsters |
Q44788698 | The action potential-evoked sarcoplasmic reticulum calcium release is impaired in mdx mouse muscle fibres |
Q35893242 | The decrease of expression of ryanodine receptor sub-type 2 is reversed by gentamycin sulphate in vascular myocytes from mdx mice |
Q72124815 | The distribution of intracellular calcium concentration in isolated single fibres of mouse skeletal muscle during fatiguing stimulation |
Q37946876 | The dystrophin-glycoprotein complex in the prevention of muscle damage |
Q41947600 | The effect of glutamine on protein turnover in chick skeletal muscle in vitro |
Q70507058 | The influence of intracellular pH on contraction, relaxation and [Ca2+]i in intact single fibres from mouse muscle |
Q64090347 | The intracellular Ca2+ concentration is elevated in cardiomyocytes differentiated from hiPSCs derived from a Duchenne muscular dystrophy patient |
Q35848770 | The membrane hypothesis of Duchenne muscular dystrophy: quest for functional evidence |
Q41738877 | The molecular basis of activity-induced muscle injury in Duchenne muscular dystrophy |
Q38654037 | The role of mechanobiology in progression of rotator cuff muscle atrophy and degeneration |
Q34800803 | The role of proteases in excitation-contraction coupling failure in muscular dystrophy |
Q40644356 | The structural and functional diversity of dystrophin |
Q34714876 | Theoretical and experimental SHG angular intensity patterns from healthy and proteolysed muscles |
Q72572686 | Time course study of the isometric contractile properties of mdx mouse striated muscles |
Q37479349 | Transient receptor potential canonical type 1 (TRPC1) operates as a sarcoplasmic reticulum calcium leak channel in skeletal muscle |
Q52663455 | Ultra-structural time-course study in the C. elegans model for Duchenne muscular dystrophy highlights a crucial role for sarcomere-anchoring structures and sarcolemma integrity in the earliest steps of the muscle degeneration process. |
Q33836366 | Understanding dystrophinopathies: an inventory of the structural and functional consequences of the absence of dystrophin in muscles of the mdx mouse |
Q57907120 | Velocity of Actomyosin Slidingin VitroIs Reduced in Dystrophic Mouse Diaphragm |
Q35847178 | Viral-mediated gene therapy for the muscular dystrophies: successes, limitations and recent advances |
Q37138490 | Wasting mechanisms in muscular dystrophy. |
Q45963266 | What does dystrophin do in normal muscle? |
Q35140775 | When calcium goes wrong: genetic alterations of a ubiquitous signaling route |
Q35236912 | Whole body periodic acceleration is an effective therapy to ameliorate muscular dystrophy in mdx mice |
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