N-terminal α Dystroglycan (αDG-N): A Potential Serum Biomarker for Duchenne Muscular Dystrophy

scientific article published on May 2016

N-terminal α Dystroglycan (αDG-N): A Potential Serum Biomarker for Duchenne Muscular Dystrophy is …
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scholarly articleQ13442814

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P356DOI10.3233/JND-150127
P932PMC publication ID5541672
P698PubMed publication ID27854211

P2093author name stringKevin M Flanigan
Paul T Martin
Guohong Shao
Kelly E Crowe
P2860cites workProcessing and secretion of the N-terminal domain of alpha-dystroglycan in cell culture mediaQ24306720
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Plectin 1f scaffolding at the sarcolemma of dystrophic (mdx) muscle fibers through multiple interactions with beta-dystroglycan.Q39734956
Embryonic overexpression of Galgt2 inhibits skeletal muscle growth via activation of myostatin signalingQ39904673
Proteolytic enzymes and altered glycosylation modulate dystroglycan function in carcinoma cells.Q40519860
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Fibronectin is a serum biomarker for Duchenne muscular dystrophyQ57389875
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The mdx mouse diaphragm reproduces the degenerative changes of Duchenne muscular dystrophyQ59051261
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The molecular basis of muscular dystrophy in the mdx mouse: a point mutationQ69514522
Use of serum creatine kinase, pyruvate kinase, and genetic linkage for carrier detection in Duchenne and Becker dystrophyQ69892059
Skeletal and cardiac myopathies in mice lacking utrophin and dystrophin: a model for Duchenne muscular dystrophyQ73677664
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Evidence-based path to newborn screening for Duchenne muscular dystrophyQ83749785
Secretion of N-terminal domain of α-dystroglycan in cerebrospinal fluidQ84528305
The N-terminal domain of α-dystroglycan, released as a 38 kDa protein, is increased in cerebrospinal fluid in patients with Lyme neuroborreliosisQ84769257
P433issue2
P921main subjectbiomarkerQ864574
P304page(s)247-260
P577publication date2016-05-01
P1433published inJournal of neuromuscular diseasesQ27726242
P1476titleN-terminal α Dystroglycan (αDG-N): A Potential Serum Biomarker for Duchenne Muscular Dystrophy
P478volume3