| scholarly article | Q13442814 |
| P356 | DOI | 10.1093/HMG/DDR145 |
| P953 | full work available online at | http://hmg.oxfordjournals.org/content/20/12/2379.full.pdf+html |
| https://academic.oup.com/hmg/article/20/12/2379/2527088/Mimicking-a-SURF1-allele-reveals-uncoupling-of | ||
| P698 | PubMed publication ID | 21470975 |
| P5875 | ResearchGate publication ID | 51030295 |
| P50 | author | David U Mick | Q63170099 |
| Peter Rehling | Q28355437 | ||
| P2093 | author name string | Martina Balleininger | |
| Bettina Bareth | |||
| Mirjam Wissel | |||
| Robert Reinhold | |||
| P2860 | cites work | SURF1, encoding a factor involved in the biogenesis of cytochrome c oxidase, is mutated in Leigh syndrome | Q22008476 |
| Fatal infantile cardioencephalomyopathy with COX deficiency and mutations in SCO2, a COX assembly gene | Q22010737 | ||
| A mutation in the human heme A:farnesyltransferase gene (COX10 ) causes cytochrome c oxidase deficiency | Q22253915 | ||
| Energy transduction: proton transfer through the respiratory complexes | Q22255654 | ||
| Cytochrome c oxidase subassemblies in fibroblast cultures from patients carrying mutations in COX10, SCO1, or SURF1 | Q24299371 | ||
| Mutations in COX15 produce a defect in the mitochondrial heme biosynthetic pathway, causing early-onset fatal hypertrophic cardiomyopathy | Q24328756 | ||
| The Tim core complex defines the number of mitochondrial translocation contact sites and can hold arrested preproteins in the absence of matrix Hsp70-Tim44. | Q24532734 | ||
| Tissue-specific cytochrome c oxidase assembly defects due to mutations in SCO2 and SURF1 | Q24534961 | ||
| The formation of respiratory chain complexes in mitochondria is under the proteolytic control of the m-AAA protease | Q42652189 | ||
| The ClpB homolog Hsp78 is required for the efficient degradation of proteins in the mitochondrial matrix | Q44141110 | ||
| Mutation in TACO1, encoding a translational activator of COX I, results in cytochrome c oxidase deficiency and late-onset Leigh syndrome. | Q45979469 | ||
| Sequence conservation from human to prokaryotes of Surf1, a protein involved in cytochrome c oxidase assembly, deficient in Leigh syndrome | Q47072011 | ||
| Import of precursor proteins into isolated yeast mitochondria | Q47740744 | ||
| Analysis of mitochondrial subunit assembly into respiratory chain complexes using Blue Native polyacrylamide gel electrophoresis | Q50470433 | ||
| SURFEIT-1 gene analysis and two-dimensional blue native gel electrophoresis in cytochrome c oxidase deficiency | Q50515850 | ||
| Maternal Segmental Disomy in Leigh Syndrome with Cytochrome c Oxidase Deficiency Caused by Homozygous SURF1 Mutation | Q56866591 | ||
| A Role for Tim21 in Membrane-Potential-Dependent Preprotein Sorting in Mitochondria | Q57808256 | ||
| Isolation of Yeast Mitochondria | Q63211589 | ||
| Assembly of nuclear DNA-encoded subunits into mitochondrial complex IV, and their preferential integration into supercomplex forms in patient mitochondria | Q63359727 | ||
| Afg3p, a mitochondrial ATP-dependent metalloprotease, is involved in degradation of mitochondrially-encoded Cox1, Cox3, Cob, Su6, Su8 and Su9 subunits of the inner membrane complexes III, IV and V | Q71103986 | ||
| Subacute necrotizing encephalomyelopathy in an infant | Q24564004 | ||
| Supercomplexes in the respiratory chains of yeast and mammalian mitochondria | Q24599994 | ||
| The whole structure of the 13-subunit oxidized cytochrome c oxidase at 2.8 A | Q27732721 | ||
| Mrpl36 is important for generation of assembly competent proteins during mitochondrial translation | Q27930043 | ||
| Mitochondrial mislocalization and altered assembly of a cluster of Barth syndrome mutant tafazzins | Q27930348 | ||
| Evidence for a pro-oxidant intermediate in the assembly of cytochrome oxidase | Q27930529 | ||
| Prohibitins interact genetically with Atp23, a novel processing peptidase and chaperone for the F1Fo-ATP synthase. | Q27930949 | ||
| Oma1, a novel membrane-bound metallopeptidase in mitochondria with activities overlapping with the m-AAA protease | Q27931615 | ||
| Analysis of Leigh syndrome mutations in the yeast SURF1 homolog reveals a new member of the cytochrome oxidase assembly factor family | Q27933372 | ||
| The membrane-bound GTPase Guf1 promotes mitochondrial protein synthesis under suboptimal conditions | Q27933617 | ||
| Shy1 couples Cox1 translational regulation to cytochrome c oxidase assembly | Q27933832 | ||
| Coa1 links the Mss51 post-translational function to Cox1 cofactor insertion in cytochrome c oxidase assembly. | Q27934347 | ||
| Cox25 Teams Up with Mss51, Ssc1, and Cox14 to Regulate Mitochondrial Cytochrome c Oxidase Subunit 1 Expression and Assembly in Saccharomyces cerevisiae | Q27934526 | ||
| Characterization of COX17, a yeast gene involved in copper metabolism and assembly of cytochrome oxidase | Q27934782 | ||
| Mss51p and Cox14p jointly regulate mitochondrial Cox1p expression in Saccharomyces cerevisiae | Q27935299 | ||
| Coa3 and Cox14 are essential for negative feedback regulation of COX1 translation in mitochondria | Q27936564 | ||
| Coa2 is an assembly factor for yeast cytochrome c oxidase biogenesis that facilitates the maturation of Cox1. | Q27937418 | ||
| Dual functions of Mss51 couple synthesis of Cox1 to assembly of cytochrome c oxidase in Saccharomyces cerevisiae mitochondria | Q27938879 | ||
| SHY1, the yeast homolog of the mammalian SURF-1 gene, encodes a mitochondrial protein required for respiration | Q27939004 | ||
| High efficiency transformation of intact yeast cells using single stranded nucleic acids as a carrier | Q28131646 | ||
| Expression and functional analysis of SURF1 in Leigh syndrome patients with cytochrome c oxidase deficiency | Q28137735 | ||
| Missense mutations in SURF1 associated with deficient cytochrome c oxidase assembly in Leigh syndrome patients | Q28140418 | ||
| Two novel mutations of SURF1 in Leigh syndrome with cytochrome c oxidase deficiency | Q28143304 | ||
| Cytochrome c oxidase deficiency | Q28189586 | ||
| Role of the deafness dystonia peptide 1 (DDP1) in import of human Tim23 into the inner membrane of mitochondria | Q28211318 | ||
| Mutations in the SURF1 gene associated with Leigh syndrome and cytochrome C oxidase deficiency | Q28214123 | ||
| Assembly of cytochrome-c oxidase in the absence of assembly protein Surf1p leads to loss of the active site heme | Q28239483 | ||
| X-linked cardioskeletal myopathy and neutropenia (Barth syndrome): an update | Q28257595 | ||
| Assembly of cytochrome-c oxidase in cultured human cells | Q28276105 | ||
| The human cytochrome c oxidase assembly factors SCO1 and SCO2 have regulatory roles in the maintenance of cellular copper homeostasis | Q28280598 | ||
| Psb27, a cyanobacterial lipoprotein, is involved in the repair cycle of photosystem II | Q28485572 | ||
| Mice lacking COX10 in skeletal muscle recapitulate the phenotype of progressive mitochondrial myopathies associated with cytochrome c oxidase deficiency | Q28512560 | ||
| Biogenesis of eukaryotic cytochrome c oxidase | Q28646289 | ||
| Mitochondrial respiratory-chain diseases | Q29614474 | ||
| Importing mitochondrial proteins: machineries and mechanisms | Q29616477 | ||
| Translocation of proteins into mitochondria | Q29616478 | ||
| Two nuclear mutations that block mitochondrial protein import in yeast | Q29618080 | ||
| Transport of proteins across or into the mitochondrial outer membrane | Q30157039 | ||
| Oxidative phosphorylation at the fin de siècle | Q33538525 | ||
| The role of Coa2 in hemylation of yeast Cox1 revealed by its genetic interaction with Cox10 | Q33558128 | ||
| Formation of the redox cofactor centers during Cox1 maturation in yeast cytochrome oxidase. | Q33627236 | ||
| LRPPRC and SLIRP interact in a ribonucleoprotein complex that regulates posttranscriptional gene expression in mitochondria. | Q33787234 | ||
| Gluing the respiratory chain together. Cardiolipin is required for supercomplex formation in the inner mitochondrial membrane | Q33961781 | ||
| The carboxyl-terminal end of Cox1 is required for feedback assembly regulation of Cox1 synthesis in Saccharomyces cerevisiae mitochondria. | Q34251080 | ||
| Mutations of SURF-1 in Leigh disease associated with cytochrome c oxidase deficiency | Q34388122 | ||
| Disorders of mitochondrial protein synthesis | Q35203201 | ||
| Initiation and elongation factors in mammalian mitochondrial protein biosynthesis | Q35805073 | ||
| Quality control of mitochondria: protection against neurodegeneration and ageing | Q36446844 | ||
| Evolution of the molecular machines for protein import into mitochondria | Q36542525 | ||
| Human mitochondrial complex I assembly: a dynamic and versatile process | Q36940191 | ||
| Cytochrome c oxidase biogenesis: new levels of regulation | Q37071707 | ||
| Roles of Oxa1-related inner-membrane translocases in assembly of respiratory chain complexes | Q37135208 | ||
| Disorders of mitochondrial function | Q37214470 | ||
| Mss51p promotes mitochondrial Cox1p synthesis and interacts with newly synthesized Cox1p. | Q37368127 | ||
| Surf1, associated with Leigh syndrome in humans, is a heme-binding protein in bacterial oxidase biogenesis | Q37377668 | ||
| The role of cytochrome c oxidase deficiency in ROS and amyloid plaque formation | Q37606352 | ||
| Co-translational membrane insertion of mitochondrially encoded proteins | Q37644798 | ||
| On the mechanism of preprotein import by the mitochondrial presequence translocase | Q37681128 | ||
| Assembly factors and ATP-dependent proteases in cytochrome c oxidase biogenesis | Q37732540 | ||
| Inventory control: cytochrome c oxidase assembly regulates mitochondrial translation | Q37823208 | ||
| Shy1p is necessary for full expression of mitochondrial COX1 in the yeast model of Leigh's syndrome | Q39646401 | ||
| Transcriptional activators HAP/NF-Y rescue a cytochrome c oxidase defect in yeast and human cells | Q40043360 | ||
| The yeast Aac2 protein exists in physical association with the cytochrome bc1-COX supercomplex and the TIM23 machinery | Q42421276 | ||
| P433 | issue | 12 | |
| P407 | language of work or name | English | Q1860 |
| P304 | page(s) | 2379-2393 | |
| P577 | publication date | 2011-04-05 | |
| P1433 | published in | Human Molecular Genetics | Q2720965 |
| P1476 | title | Mimicking a SURF1 allele reveals uncoupling of cytochrome c oxidase assembly from translational regulation in yeast | |
| P478 | volume | 20 |
| Q46104406 | Disulfide bond formation: sulfhydryl oxidase ALR controls mitochondrial biogenesis of human MIA40. |
| Q38962266 | Leigh syndrome in Drosophila melanogaster: morphological and biochemical characterization of Surf1 post-transcriptional silencing |
| Q24609442 | MINOS1 is a conserved component of mitofilin complexes and required for mitochondrial function and cristae organization |
| Q24306654 | MITRAC links mitochondrial protein translocation to respiratory-chain assembly and translational regulation |
| Q39357005 | Overlapping Role of Respiratory Supercomplex Factor Rcf2 and Its N-terminal Homolog Rcf3 in Saccharomyces cerevisiae |
| Q27938469 | The channel-forming Sym1 protein is transported by the TIM23 complex in a presequence-independent manner |
| Q34366873 | The heme a synthase Cox15 associates with cytochrome c oxidase assembly intermediates during Cox1 maturation |
| Q37418894 | The power of yeast to model diseases of the powerhouse of the cell. |
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