| scholarly article | Q13442814 |
| P2093 | author name string | Keith Blomenkamp | |
| Jeffrey H Teckman | |||
| Jae-Koo An | |||
| Douglas Lindblad | |||
| P2860 | cites work | A novel ER alpha-mannosidase-like protein accelerates ER-associated degradation | Q24522524 |
| Quantitative amplification of genomic DNA from histological tissue sections after staining with nuclear dyes and laser capture microdissection | Q28354335 | ||
| Laser capture microdissection and real-time reverse transcriptase/ polymerase chain reaction of bronchiolar epithelium after bleomycin | Q31014470 | ||
| Dysfunctional variants and the structural biology of the serpins. | Q41684274 | ||
| Fasting in alpha1-antitrypsin deficient liver: constitutive [correction of consultative] activation of autophagy. | Q51540319 | ||
| P433 | issue | 1 | |
| P407 | language of work or name | English | Q1860 |
| P304 | page(s) | 160-167 | |
| P577 | publication date | 2005-01-01 | |
| P1433 | published in | Hepatology | Q15724398 |
| P1476 | title | Quantitative isolation of alphalAT mutant Z protein polymers from human and mouse livers and the effect of heat | |
| P478 | volume | 41 |
| Q91814799 | A Novel Small Molecule Inhibits Intrahepatocellular Accumulation of Z-Variant Alpha 1-Antitrypsin In Vitro and In Vivo |
| Q34123062 | A novel monoclonal antibody to characterize pathogenic polymers in liver disease associated with alpha1-antitrypsin deficiency. |
| Q28550962 | AFM Imaging Reveals Topographic Diversity of Wild Type and Z Variant Polymers of Human α1-Proteinase Inhibitor |
| Q35842192 | Activating transcription factor 6 limits intracellular accumulation of mutant α(1)-antitrypsin Z and mitochondrial damage in hepatoma cells. |
| Q38171382 | Advances in alpha-1-antitrypsin deficiency liver disease |
| Q38234419 | Alpha-1 antitrypsin and liver disease: mechanisms of injury and novel interventions |
| Q36410546 | Alpha-1-antitrypsin deficiency: diagnosis, pathophysiology, and management |
| Q54222676 | Alpha-1-antitrypsin deficiency: from genoma to liver disease. PiZ mouse as model for the development of liver pathology in human. |
| Q40171715 | Alpha-1-antitrypsin mutant Z protein content in individual hepatocytes correlates with cell death in a mouse model. |
| Q38937853 | An ECLIPSE View of Alpha-1 Antitrypsin Deficiency |
| Q37410570 | Antisense oligonucleotide treatment ameliorates alpha-1 antitrypsin-related liver disease in mice. |
| Q37212761 | Autophagic disposal of the aggregation-prone protein that causes liver inflammation and carcinogenesis in alpha-1-antitrypsin deficiency |
| Q52873755 | Autophagy induced by exogenous bile acids is therapeutic in a model of α-1-AT deficiency liver disease. |
| Q51215263 | Bone marrow stem cell therapy partially ameliorates pathological consequences in livers of mice expressing mutant human α1-antitrypsin. |
| Q38165139 | Broad spectrum of hepatocyte inclusions in humans, animals, and experimental models |
| Q41863956 | Characteristics of hepatocellular carcinoma in a murine model of alpha-1-antitrypsin deficiency |
| Q34182669 | Defining the mechanism of polymerization in the serpinopathies |
| Q28547169 | Discovery of an inhibitor of Z-alpha1 antitrypsin polymerization |
| Q41106554 | Gene transfer of master autophagy regulator TFEB results in clearance of toxic protein and correction of hepatic disease in alpha-1-anti-trypsin deficiency |
| Q36758411 | Golgi-situated endoplasmic reticulum α-1, 2-mannosidase contributes to the retrieval of ERAD substrates through a direct interaction with γ-COP. |
| Q37855343 | Hepatic fibrosis and carcinogenesis in α1-antitrypsin deficiency: a prototype for chronic tissue damage in gain-of-function disorders |
| Q34246574 | Hepatic progenitor cell proliferation and liver injury in α-1-antitrypsin deficiency |
| Q40115238 | In vivo post-transcriptional gene silencing of alpha-1 antitrypsin by adeno-associated virus vectors expressing siRNA. |
| Q79152342 | Indomethacin increases liver damage in a murine model of liver injury from alpha-1-antitrypsin deficiency |
| Q48018036 | Knockdown of Z Mutant Alpha-1 Antitrypsin In Vivo Using Modified DNA Antisense Oligonucleotides |
| Q38092867 | Liver disease in alpha-1 antitrypsin deficiency: current understanding and future therapy |
| Q38017699 | Novel treatment strategies for liver disease due to α1-antitrypsin deficiency |
| Q36436568 | Oxidative stress contributes to liver damage in a murine model of alpha-1-antitrypsin deficiency. |
| Q43180243 | Parker B. Francis lectureship. Antitrypsin deficiency, the serpinopathies, and chronic obstructive pulmonary disease |
| Q37149157 | Rapamycin reduces intrahepatic alpha-1-antitrypsin mutant Z protein polymers and liver injury in a mouse model |
| Q48017976 | Semiquantitation of Monomer and Polymer Alpha-1 Antitrypsin by Centrifugal Separation and Assay by Western Blot of Soluble and Insoluble Components |
| Q24645055 | Small molecules block the polymerization of Z alpha1-antitrypsin and increase the clearance of intracellular aggregates |
| Q36378692 | The selective advantage of alpha1-antitrypsin deficiency |
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