| scholarly article | Q13442814 |
| P50 | author | Shinichi Takahashi | Q47160161 |
| P2093 | author name string | Daisuke Ito | |
| Norihiro Suzuki | |||
| Kyoko Mashima | |||
| Kana Mitsuhashi | |||
| Munenori Oyama | |||
| P2860 | cites work | Stress granules as crucibles of ALS pathogenesis. | Q36804082 |
| Toxic gain of function from mutant FUS protein is crucial to trigger cell autonomous motor neuron loss | Q36906420 | ||
| TDP-43 proteinopathy in frontotemporal lobar degeneration and amyotrophic lateral sclerosis: protein misfolding diseases without amyloidosis | Q36965517 | ||
| Stages of pTDP-43 pathology in amyotrophic lateral sclerosis | Q37202139 | ||
| ALS-linked mutations enlarge TDP-43-enriched neuronal RNA granules in the dendritic arbor | Q37650180 | ||
| DDA3 stabilizes microtubules and suppresses neurite formation | Q39370802 | ||
| RNA targets of wild-type and mutant FET family proteins | Q39603230 | ||
| Intracellular localization and splicing regulation of FUS/TLS are variably affected by amyotrophic lateral sclerosis-linked mutations | Q39627330 | ||
| FUS/TLS deficiency causes behavioral and pathological abnormalities distinct from amyotrophic lateral sclerosis | Q39927199 | ||
| Structure and Mechanism of Dimer-Monomer Transition of a Plant Poly(A)-Binding Protein upon RNA Interaction: Insights into Its Poly(A) Tail Assembly. | Q40900130 | ||
| Accelerated Differentiation in Response to Retinoic Acid After Retrovirally Mediated Gene Transfer of GAP-43 into Mouse Neuroblastoma Cells | Q41644293 | ||
| Requirements for stress granule recruitment of fused in sarcoma (FUS) and TAR DNA-binding protein of 43 kDa (TDP-43) | Q42110964 | ||
| Characterization of alternative isoforms and inclusion body of the TAR DNA-binding protein-43. | Q42940304 | ||
| A critical role for amino-terminal glutamine/asparagine repeats in the formation and propagation of a yeast prion | Q46347783 | ||
| Identification of amino-terminally cleaved tau fragments that distinguish progressive supranuclear palsy from corticobasal degeneration | Q48101684 | ||
| Mislocated FUS is sufficient for gain-of-toxic-function amyotrophic lateral sclerosis phenotypes in mice | Q48645659 | ||
| Decreased number of Gemini of coiled bodies and U12 snRNA level in amyotrophic lateral sclerosis. | Q50932808 | ||
| Nuclear transport impairment of amyotrophic lateral sclerosis-linked mutations in FUS/TLS. | Q52607544 | ||
| Novel missense and truncating mutations in FUS/TLS in familial ALS | Q84595745 | ||
| Mutations in prion-like domains in hnRNPA2B1 and hnRNPA1 cause multisystem proteinopathy and ALS | Q24629495 | ||
| ALS-associated fused in sarcoma (FUS) mutations disrupt Transportin-mediated nuclear import | Q24630100 | ||
| Conjoint pathologic cascades mediated by ALS/FTLD-U linked RNA-binding proteins TDP-43 and FUS | Q24634807 | ||
| RNA granules | Q24683783 | ||
| Converging mechanisms in ALS and FTD: disrupted RNA and protein homeostasis | Q26863439 | ||
| Ubiquitinated TDP-43 in frontotemporal lobar degeneration and amyotrophic lateral sclerosis | Q28131672 | ||
| TDP-43 and FUS in amyotrophic lateral sclerosis and frontotemporal dementia | Q28294001 | ||
| Tar DNA Binding Protein-43 (TDP-43) Associates with Stress Granules: Analysis of Cultured Cells and Pathological Brain Tissue | Q28475724 | ||
| Type VI adenylyl cyclase regulates neurite extension by binding to Snapin and Snap25 | Q28511414 | ||
| Cell-free formation of RNA granules: low complexity sequence domains form dynamic fibers within hydrogels | Q29614781 | ||
| Stress granules: the Tao of RNA triage | Q29615263 | ||
| TDP-43 is a component of ubiquitin-positive tau-negative inclusions in frontotemporal lobar degeneration and amyotrophic lateral sclerosis | Q29615597 | ||
| Dynamic shuttling of TIA-1 accompanies the recruitment of mRNA to mammalian stress granules | Q30014821 | ||
| TDP-43 transgenic mice develop spastic paralysis and neuronal inclusions characteristic of ALS and frontotemporal lobar degeneration | Q30493749 | ||
| Overexpression of human wild-type FUS causes progressive motor neuron degeneration in an age- and dose-dependent fashion | Q30532680 | ||
| Prion-like transmission of protein aggregates in neurodegenerative diseases | Q33544162 | ||
| Elevated expression of TDP-43 in the forebrain of mice is sufficient to cause neurological and pathological phenotypes mimicking FTLD-U. | Q34044401 | ||
| Altered distributions of Gemini of coiled bodies and mitochondria in motor neurons of TDP-43 transgenic mice. | Q34136342 | ||
| The tip of the iceberg: RNA-binding proteins with prion-like domains in neurodegenerative disease. | Q34263380 | ||
| Roles of ataxin-2 in pathological cascades mediated by TAR DNA-binding protein 43 (TDP-43) and Fused in Sarcoma (FUS) | Q34304833 | ||
| Mutant FUS proteins that cause amyotrophic lateral sclerosis incorporate into stress granules | Q34308339 | ||
| Wild-type human TDP-43 expression causes TDP-43 phosphorylation, mitochondrial aggregation, motor deficits, and early mortality in transgenic mice | Q34664325 | ||
| Long pre-mRNA depletion and RNA missplicing contribute to neuronal vulnerability from loss of TDP-43. | Q34982074 | ||
| ALS-causative mutations in FUS/TLS confer gain and loss of function by altered association with SMN and U1-snRNP. | Q35114564 | ||
| TDP-43 pathology and neuronal loss in amyotrophic lateral sclerosis spinal cord | Q35260685 | ||
| De novo design of synthetic prion domains | Q35921831 | ||
| Neuronal sensitivity to TDP-43 overexpression is dependent on timing of induction | Q35985332 | ||
| Exome sequencing identifies FUS mutations as a cause of essential tremor | Q36152927 | ||
| Targeted depletion of TDP-43 expression in the spinal cord motor neurons leads to the development of amyotrophic lateral sclerosis-like phenotypes in mice | Q36201764 | ||
| TDP-43 is intercellularly transmitted across axon terminals | Q36310560 | ||
| FUS-SMN protein interactions link the motor neuron diseases ALS and SMA | Q36354418 | ||
| ALS-associated mutant FUS induces selective motor neuron degeneration through toxic gain of function | Q36548825 | ||
| Spliceosome integrity is defective in the motor neuron diseases ALS and SMA. | Q36602121 | ||
| TDP-43 repression of nonconserved cryptic exons is compromised in ALS-FTD. | Q36781316 | ||
| P4510 | describes a project that uses | ImageJ | Q1659584 |
| P433 | issue | 1 | |
| P407 | language of work or name | English | Q1860 |
| P921 | main subject | amyotrophic lateral sclerosis | Q206901 |
| protein design | Q410814 | ||
| RNA design | Q55213896 | ||
| prion protein family | Q24724413 | ||
| P304 | page(s) | 16871 | |
| P577 | publication date | 2017-12-04 | |
| P1433 | published in | Scientific Reports | Q2261792 |
| P1476 | title | De novo design of RNA-binding proteins with a prion-like domain related to ALS/FTD proteinopathies | |
| P478 | volume | 7 |
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