ANCA-associated vasculitis is linked to carriage of the Z allele of 1 antitrypsin and its polymers

scientific article published on 05 August 2011

ANCA-associated vasculitis is linked to carriage of the Z allele of 1 antitrypsin and its polymers is …
instance of (P31):
scholarly articleQ13442814

External links are
P356DOI10.1136/ARD.2011.153569
P698PubMed publication ID21821620

P50authorElena MirandaQ37834660
Amy Jayne McKnightQ38322369
Peter MaxwellQ38545687
P2093author name stringJ Williams
D A Lomas
L Guillevin
C D Pusey
A M Wood
H Morris
K Herrmann
C O Savage
J U Holle
S W Smith
J Perez
L Harper
S Wieczorek
M D Morgan
R Stockley
A D Salama
U I Ekeowa
P433issue10
P407language of work or nameEnglishQ1860
P304page(s)1851-1856
P577publication date2011-08-05
P1433published inAnnals of the Rheumatic DiseasesQ4767876
P1476titleANCA-associated vasculitis is linked to carriage of the Z allele of α₁ antitrypsin and its polymers
P478volume70

Reverse relations

cites work (P2860)
Q35124900ATZ11 recognizes not only Z-α1-antitrypsin-polymers and complexed forms of non-Z-α1-antitrypsin but also the von Willebrand factor
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Q42315252Alpha-1 Antitrypsin Deficiency Presenting with MPO-ANCA Associated Vasculitis and Aortic Dissection
Q38114852Alpha-1 antitrypsin deficiency: new developments in augmentation and other therapies
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Q38462072Neutrophil serine proteases exert proteolytic activity on endothelial cells
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Q38604630The Diagnosis and Management of Alpha-1 Antitrypsin Deficiency in the Adult
Q42234561The circulating proteinase inhibitor α-1 antitrypsin regulates neutrophil degranulation and autoimmunity.
Q38092851Twenty years of polymers: a personal perspective on alpha-1 antitrypsin deficiency
Q35233352Why has it been so difficult to prove the efficacy of alpha-1-antitrypsin replacement therapy? Insights from the study of disease pathogenesis
Q64047576[A rare cause of severe panniculitis]

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