von Willebrand disease

scientific article published on 01 February 1990

von Willebrand disease is …
instance of (P31):
review articleQ7318358
scholarly articleQ13442814

External links are
P356DOI10.1016/S0889-8588(18)30508-2
P698PubMed publication ID2107173

P2093author name stringMiller JL
P2860cites workInducible secretion of large, biologically potent von Willebrand factor multimersQ24296142
Immunolocalization of von Willebrand protein in Weibel-Palade bodies of human endothelial cellsQ24301929
Amino acid sequence of human von Willebrand factorQ28630812
IIB von Willebrand's disease: pathogenetic and therapeutic studiesQ33447346
Investigation of a large kindred with type IIB von Willebrand's disease, dominant inheritance and age-dependent thrombocytopeniaQ33449113
Platelet aggregation induced by 1-desamino-8-D-arginine vasopressin (DDAVP) in Type IIB von Willebrand's diseaseQ33478045
von Willebrand factor binds to platelets and induces aggregation in platelet-type but not type IIB von Willebrand diseaseQ33478102
Properties of human asialo-factor VIII. A ristocetin-independent platelet-aggregating agentQ33481601
Pseudo-von Willebrand's disease. An intrinsic platelet defect with aggregation by unmodified human factor VIII/von Willebrand factor and enhanced adsorption of its high-molecular-weight multimersQ33481677
Unusually large plasma factor VIII:von Willebrand factor multimers in chronic relapsing thrombotic thrombocytopenic purpuraQ33481821
Homozygous and heterozygous deletions of the von Willebrand factor gene in patients and carriers of severe von Willebrand diseaseQ33567446
Platelets have more than one binding site for von Willebrand factorQ33821754
Asialo von Willebrand factor interactions with platelets. Interdependence of glycoproteins Ib and IIb/IIIa for binding and aggregationQ34521638
Subunit composition of plasma von Willebrand factor. Cleavage is present in normal individuals, increased in IIA and IIB von Willebrand disease, but minimal in variants with aberrant structure of individual oligomers (types IIC, IID, and IIE).Q34528381
von Willebrand protein facilitates platelet incorporation in polymerizing fibrinQ34544068
von Willebrand factor interaction with the glycoprotein IIb/IIa complex. Its role in platelet function as demonstrated in patients with congenital afibrinogenemiaQ34574601
Interaction of asialo von Willebrand factor with glycoprotein Ib induces fibrinogen binding to the glycoprotein IIb/IIIa complex and mediates platelet aggregationQ34624945
Acquired von Willebrand's disease: demonstration of a circulating inhibitor to the factor VIII complex in four casesQ70432905
Von Willebrand factor multimer patterns in von Willebrand's diseaseQ70454272
Platelet aggregation induced by DDAVP in platelet-type von Willebrand's diseaseQ71003140
Heightened interaction between platelets and factor VIII/von Willebrand factor in a new subtype of von Willebrand's diseaseQ71498185
Studies on the pathophysiology and treatment of von Willebrand's disease. IV. Mechanism of increased ristocetin-induced platelet aggregation in von Willebrand's diseaseQ71535514
Pathogenesis of antibody-induced acquired von Willebrand SyndromeQ71540345
Factor VIII and human platelet aggregation. III. Further studies on aggregation of humna platelets by neuraminidase-treated human factor VIIIQ95790452
The interaction of bovine factor VIII with human plateletsQ35195700
Genetic linkage of two intragenic restriction fragment length polymorphisms with von Willebrand's disease type IIA. Evidence for a defect in the von Willebrand factor geneQ35811246
Cloning and characterization of two cDNAs coding for human von Willebrand factor.Q36413864
Molecular cloning of cDNA for human von Willebrand factor: authentication by a new methodQ36487544
Construction of cDNA coding for human von Willebrand factor using antibody probes for colony-screening and mapping of the chromosomal gene.Q36487665
Thrombin-induced exposure and prostacyclin inhibition of the receptor for factor VIII/von Willebrand factor on human plateletsQ36983829
Aberrant multimeric structure of von Willebrand factor in a new variant of von Willebrand's disease (type IIC)Q36988093
An explanation for minor multimer species in endothelial cell-synthesized von Willebrand factorQ36994972
Variant von Willebrand's disease: characterization of two subtypes by analysis of multimeric composition of factor VIII/von Willebrand factor in plasma and plateletsQ37023086
Active release of human platelet factor VIII-related antigen by adenosine diphosphate, collagen, and thrombinQ37034062
Stabilization of factor VIII in plasma by the von Willebrand factor. Studies on posttransfusion and dissociated factor VIII and in patients with von Willebrand's diseaseQ37046074
Synthesis of Factor VIII Antigen by Cultured Guinea Pig MegakaryocytesQ37047673
Synthesis of von Willebrand factor by cultured human endothelial cellsQ37444356
Factor-VIII-related antigen: multiple molecular forms in human plasmaQ37466525
In vitro correction of the abnormal multimeric structure of von Willebrand factor in type IIa von Willebrand's diseaseQ37531782
Role of von Willebrand factor in the vessel wallQ39168456
A hemorrhagic syndrome in Waldenström's macroglobulinemia secondary to immunoadsorption of factor VIII. Recovery after splenectomyQ39641337
Nucleotide sequence of pre-pro-von Willebrand factor cDNA.Q40418506
von Willebrand's disease and hemorrhagic telangiectasia: association of two complex disorders of hemostasis resulting in life-threatening hemorrhageQ40642696
Acquired von Willebrand's disease. Evidence for a quantitative and qualitative factor VIII disorderQ40674913
Telangiectasia and von Willebrand's Disease in Two FamiliesQ40694936
Preservation of platelet receptors for platelet aggregating factor/von Willebrand factor by air drying, freezing, or lyophilization: New stable platelet preparations for von Willebrand factor assaysQ40705105
Acquired von Willebrand disease associated with an inhibitor to factor VIII antigen and gastrointestinal telangiectasiaQ40725036
The Factor VIII Abnormality in Severe von Willebrand's DiseaseQ40726737
Gene deletions correlate with the development of alloantibodies in von Willebrand diseaseQ40922128
An immunoradiometric assay for human factor VIII/von Willebrand factor (VIII:vWF) using a monoclonal antibody that defines a functional epitope.Q44363513
Response of factor VIII/von Willebrand factor to DDAVP in healthy subjects and patients with haemophilia A and von Willebrand's diseaseQ45863842
Assay of von Willebrand factor in von Willebrand's disease and hemophilia: use of a macroscopic platelet aggregation testQ45878186
DDAVP in acquired von Willebrand syndrome associated with multiple myelomaQ45886916
Life-threatening reaction to factor VIII concentrate in a patient with severe von Willebrand disease and alloantibodies to von Willebrand factorQ45887412
Multimeric analysis of von Willebrand factor in megakaryocytesQ46859910
Human von Willebrand factor (vWF): isolation of complementary DNA (cDNA) clones and chromosomal localizationQ48377892
Propolypeptide of von Willebrand factor circulates in blood and is identical to von Willebrand antigen IIQ56459904
Adenosine diphosphate induces binding of von Willebrand factor to human plateletsQ59095973
Plasma and platelet von Willebrand factor defects in uremiaQ68100239
Multimeric composition of plasma von Willebrand factor in chronic myelocytic leukaemiaQ68100612
A monoclonal antibody based immunoradiometric assay for von Willebrand factor: survey of a large patient groupQ68817994
Essential thrombocythemia with acquired von Willebrand's diseaseQ68824037
Successful treatment of an acquired von Willebrand factor antibody by extracorporeal immunoadsorptionQ69482394
Hemostatic evaluation in bleeding disorders from native blood. Clinical experience with the hemostatometerQ69488535
Botrocetin- and polybrene-induced platelet aggregation in platelet-type von Willebrand diseaseQ69864886
A comparative study of variables affecting the bleeding time using two disposable devicesQ69935411
von Willebrand diseaseQ70321843
P433issue1
P304page(s)107-128
P577publication date1990-02-01
P1433published inHematology / Oncology Clinics of North AmericaQ15749192
P1476titlevon Willebrand disease
P478volume4

Reverse relations

cites work (P2860)
Q72896911Acquired von Willebrand disease in twins with autoimmune hypothyroidism: response to desmopressin and L-thyroxine therapy
Q37346455Laboratory diagnosis of von Willebrand's disease
Q45099698Management of children with von Willebrand disease undergoing adenotonsillectomy
Q45090528Prevalence of von Willebrand disease in children: a multiethnic study
Q40997967von Willebrand disease in children and adolescents

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