von Willebrand disease

scientific article published on 01 February 1987

von Willebrand disease is …
instance of (P31):
review articleQ7318358
scholarly articleQ13442814

External links are
P356DOI10.1016/S0046-8177(87)80332-5
P698PubMed publication ID3100416

P2093author name stringT S Zimmerman
Z M Ruggeri
P2860cites workMolecular cloning of a cDNA encoding human antihaemophilic factorQ28268498
Structure of human factor VIIIQ28630991
Decreased adhesion of giant (Bernard-Soulier) platelets to subendothelium. Further implications on the role of the von Willebrand factor in hemostasisQ33463842
Platelet aggregation induced by 1-desamino-8-D-arginine vasopressin (DDAVP) in Type IIB von Willebrand's diseaseQ33478045
Properties of human asialo-factor VIII. A ristocetin-independent platelet-aggregating agentQ33481601
Pseudo-von Willebrand's disease. An intrinsic platelet defect with aggregation by unmodified human factor VIII/von Willebrand factor and enhanced adsorption of its high-molecular-weight multimersQ33481677
Platelets have more than one binding site for von Willebrand factorQ33821754
A murine monoclonal antibody that completely blocks the binding of fibrinogen to platelets produces a thrombasthenic-like state in normal platelets and binds to glycoproteins IIb and/or IIIaQ33821916
Immunologic differentiation of classic hemophilia (factor 8 deficiency) and von Willebrand's dissase, with observations on combined deficiencies of antihemophilic factor and proaccelerin (factor V) and on an acquired circulating anticoagulant againsQ34055947
Preparation and properties of bovine factor VIII (antihemophilic factor).Q34285283
Studies of the human factor VIII/von Willebrand factor protein. III. Qualitative defects in von Willebrand's diseaseQ34482682
Antihemophilic factor antigen. Localization in endothelial cells by immunofluorescent microscopyQ34512963
Synthesis of Antihemophilic Factor Antigen by Cultured Human Endothelial CellsQ34513117
Asialo von Willebrand factor interactions with platelets. Interdependence of glycoproteins Ib and IIb/IIIa for binding and aggregationQ34521638
Independent modulation of von Willebrand factor and fibrinogen binding to the platelet membrane glycoprotein IIb/IIIa complex as demonstrated by monoclonal antibodyQ34565552
Interaction of von Willebrand factor with human platelets in the plasma milieuQ34602783
Functional domains on von Willebrand factor. Recognition of discrete tryptic fragments by monoclonal antibodies that inhibit interaction of von Willebrand factor with platelets and with collagenQ34613209
Carbohydrate moiety of von Willebrand factor is not necessary for maintaining multimeric structure and ristocetin cofactor activity but protects from proteolytic degradationQ34622020
Interaction of asialo von Willebrand factor with glycoprotein Ib induces fibrinogen binding to the glycoprotein IIb/IIIa complex and mediates platelet aggregationQ34624945
Cultured aortic endothelial cells from pigs with von Willebrand disease: in vitro model for studying the molecular defect(s) of the diseaseQ35054070
Factor VIII recombination after dissociation by CaCl12.Q35110177
Studies on human antihemophilic factor. Evidence for a covalently linked subunit structureQ35199709
Immunologic studies in von Willebrand's disease. Evidence that the antihemophilic factor (AHF) produced after transfusions lacks an antigen associated with normal AHF and the inactive material produced by patients with classic hemophiliaQ35897508
The subunit structure of normal and hemophilic factor VIIIQ35899324
Biosynthesis of von Willebrand protein by human endothelial cells: processing steps and their intracellular localizationQ36212119
Von Willebrand protein binds to extracellular matrices independently of collagenQ36247327
Characterization of the human factor VIII procoagulant protein with a heterologous precipitating antibodyQ36285769
Glanzmann thrombasthenia: deficient binding of von Willebrand factor to thrombin-stimulated plateletsQ36314768
Cloning and characterization of two cDNAs coding for human von Willebrand factor.Q36413864
Molecular cloning of cDNA for human von Willebrand factor: authentication by a new methodQ36487544
Construction of cDNA coding for human von Willebrand factor using antibody probes for colony-screening and mapping of the chromosomal gene.Q36487665
Detection of heterozygotes in both parents of homozygous patients with Von Willebrand's diseaseQ36589298
Thrombin-induced exposure and prostacyclin inhibition of the receptor for factor VIII/von Willebrand factor on human plateletsQ36983829
Aberrant multimeric structure of von Willebrand factor in a new variant of von Willebrand's disease (type IIC)Q36988093
Carbohydrate of the Factor VIII/von Willebrand Factor in von Willebrand's DiseaseQ37017221
Variant von Willebrand's disease: characterization of two subtypes by analysis of multimeric composition of factor VIII/von Willebrand factor in plasma and plateletsQ37023086
Factor VIII/von Willebrand factor protein. Galactose a cryptic determinant of von Willebrand factor activityQ37031115
Disulfide Bonds and the Quaternary Structure of Factor VIII/von Willebrand FactorQ37031904
Immunoradiometric measurement of the factor VIII procoagulant antigenQ37033265
Active release of human platelet factor VIII-related antigen by adenosine diphosphate, collagen, and thrombinQ37034062
Stabilization of factor VIII in plasma by the von Willebrand factor. Studies on posttransfusion and dissociated factor VIII and in patients with von Willebrand's diseaseQ37046074
Synthesis of Factor VIII Antigen by Cultured Guinea Pig MegakaryocytesQ37047673
Factor-VIII-related antigen: multiple molecular forms in human plasmaQ37466525
Interaction of purified type IIB von Willebrand factor with the platelet membrane glycoprotein Ib induces fibrinogen binding to the glycoprotein IIb/IIIa complex and initiates aggregationQ37554183
Biosynthesis of the subunits of factor VIIIR by bovine aortic endothelial cellsQ37610888
Role of carbohydrate in multimeric structure of factor VIII/von Willebrand factor proteinQ37611058
1-Deamino-8-d-arginine vasopressin: a new pharmacological approach to the management of haemophilia and von Willebrands' diseasesQ39433082
Immunoradiometric assay of procoagulant factor-VIII antigen in plasma and serum and its reduction in haemophilia. Preliminary studies on adult and fetal bloodQ39480417
Platelet factor VIII-related antigen: Immunofluorescent localizationQ39530860
The effects of neuraminidase treatment on the biological activities of factor VIIIQ39685981
Von Willebrand's disease: combined qualitative and quantitative abnormalitiesQ40644015
DDAVP: alternative to replacement treatment in mild haemophilia A and von Willebrand-Jürgens syndrome (author's transl)Q40661868
Acquired von Willebrand's disease. Evidence for a quantitative and qualitative factor VIII disorderQ40674913
Acquired von Willebrand's disease, platelet-release defect and angiodysplasiaQ40687284
Radioimmunoassay for coagulant factor VIII-related antigen (VIII:CAg)Q40705110
Two Populations of Factor VIII-Related Antigen in a Family with von Willebrand's DiseaseQ40705767
Human blood platelet adhesion to artery subendothelium is mediated by factor VIII-Von Willebrand factor bound to the subendotheliumQ40713235
The Factor VIII Abnormality in Severe von Willebrand's DiseaseQ40726737
Studies on factor VIII-related protein. II. Estimation of molecular size differences between factor VIII oligomersQ41669423
Subcellular platelet factor VIII antigen and von Willebrand factorQ42940232
Failure of AHF concentrate to control bleeding in von Willebrand's diseaseQ43665677
Diagnosis of von Willebrand's disease. A comparative study of diagnostic tests on nine families with von Willebrand's disease and its differential diagnosis from hemophilia and thrombocytopathyQ43996336
A variant of factor 8 related antigenQ45855059
Factor VIII antigen in the vessel walls in von Willebrand's disease and haemophilia A.Q45855991
Response of factor VIII/von Willebrand factor to DDAVP in healthy subjects and patients with haemophilia A and von Willebrand's diseaseQ45863842
Studies on the relationship between factor VIII related antigen (VIIIRAg) and factor VIII clotting antigen (VIIICAg) by immunoelectrophoresis and autoradiography using 125I anti VIIICAgQ45864085
Acquired von Willebrand Syndrome with Inhibitors Both to Factor VIII Clotting Activity and Ristocetin-Induced Platelet AggregationQ45878307
A Method for Detecting Factor-VIII Clotting Activity Associated with Factor VIII-related Antigen in Agarose GelsQ45878671
Von Willebrand factor: dissociation from antihemophilic factor procoagulant activityQ45890237
Factor VIII of small molecular weight and its aggregationQ47359177
Human von Willebrand factor (vWF): isolation of complementary DNA (cDNA) clones and chromosomal localizationQ48377892
Characterization of the human factor VIII geneQ48385931
Detection of Heterozygotes for Recessive von Willebrand's Disease by the Assay of Antihemophilic-Factor-like AntigenQ54384588
Spectrum of von Willebrand's Disease: a study of 100 cases. Italian Working GroupQ66875981
Urinary excretion of factor VIII after renal transplantationQ66892653
The Chromatographic Separation of Factor VIII on Aminohexyl SepharoseQ66984431
Factor VIII, a series of homologous oligomers and a complex of two proteinsQ67289767
von Willebrand disease type IIC with different abnormalities of von Willebrand factor in the same sibshipQ68792876
Inherited variants of factor-VIII-related protein in von Willebrand's diseaseQ69135742
1-Deamino-8-D-arginine vasopressin and cryoprecipitate in variant von Willebrand diseaseQ69962767
Pool's cryoprecipitate and exhausted plasma in the treatment of von Willebrand's disease and factor-XI deficiencyQ70067523
Structure determination of the major asparagine-linked sugar chain of human factor VIII--von Willebrand factorQ70426198
Von Willebrand factor multimer patterns in von Willebrand's diseaseQ70454272
Congenital bleeding disorders with long bleeding time and normal platelet count. II. Von Willebrand's disease (report of thirty-seven patients)Q71106834
Molecular Forms of Antihaemophilic Globulin in Plasma, Cryoprecipitate and after Thrombin ActivationQ71426909
Heightened interaction between platelets and factor VIII/von Willebrand factor in a new subtype of von Willebrand's diseaseQ71498185
Binding and release of factor VIII/von Willebrand's factor by human endothelial cellsQ71520196
Synthesis and release of factor VIII by cultured human endothelial cellsQ71540905
Studies on the pathophysiology and treatment of von Willebrand's disease. V. Properties of factor VIII after DDAVP infusion in variant von Willebrand's diseaseQ71565187
P433issue2
P304page(s)140-152
P577publication date1987-02-01
P1433published inHuman PathologyQ15756731
P1476titlevon Willebrand disease
P478volume18

Reverse relations

cites work (P2860)
Q35250259Autosomal dominant postaxial polydactyly, nail dystrophy, and dental abnormalities map to chromosome 4p16, in the region containing the Ellis-van Creveld syndrome locus
Q33838757Effect of recombinant factor VIIa on the hemostatic defect in dogs with hemophilia A, hemophilia B, and von Willebrand disease
Q44662705Inheritance and prevalence of von Willebrand's disease severe form in a Brazilian population
Q37576572Laboratory testing for von Willebrand disease: toward a mechanism-based classification
Q33847858Mediation of fibrin-induced release of von Willebrand factor from cultured endothelial cells by the fibrin beta chain
Q34366855Prevention of occlusive coronary artery thrombosis by a murine monoclonal antibody to porcine von Willebrand factor
Q37054000Regulated Secretion in Vascular Endothelium
Q68178306Significance and quantitative analysis of von Willebrand factor in human platelets
Q45873991Two sisters with multiple sclerosis, lamellar ichthyosis, beta thalassaemia minor and a deficiency of factor VIII.
Q53061821Unravelling the mechanism and significance of thrombin binding to platelet glycoprotein Ib
Q67276057von Willebrand disease
Q41043544von Willebrand disease: pathogenesis, classification, and management
Q41157159von Willebrand's disease in the dog and cat.

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